Ka ngenge ngāwari ō uaua? Me kōrero tātou mō te Myasthenia Gravis!

Kei te ahua ngoikore tō kauae, ā, he uaua ki te ngaungau kai i a koe e kai ana? Engari i muri i tētahi wā, ka memeha haere te mamae, ā, ka taea e koe te kai anō i te āhua noa? Mena kua pā tēnei ki a koe, he mea nui tēnei kaupapa e kōrerohia ana e tātou i tēnei rā ki a koe. He mate tēnei e kiia nei ko te Myasthenia Gravis .

He aha te Myasthenia Gravis?

Ki te kī māmā noa, he mate mau tonu te myasthenia gravis e ngenge ai, e ngoikore ai hoki ngā uaua o te tinana. Ko te āhuatanga tino motuhake o tēnei ko te ngoikore o ngā uaua ina whakamahia, kātahi ka kaha anō i muri i te okiokinga. He rite ki te pākahiko e mate ana ina mahi koe, engari ka whakakī anō ina waiho ki tahaki mō tētahi wā.

Ka pā pea tēnei āhuatanga ki ngā rōpū uaua rerekē o te tinana. Mēnā ka pā mai, ka kiia ko te 'generalized myasthenia gravis'. Ka uaua pea tēnei ki te ngaungau kai, ki te horomi, ki te menemene, ki te hiki i ngā pakihiwi, ki te hapai i te ringa, ki te pupuri pūmau i tētahi mea, ki te tū ake, me te piki arawhata.

Ahakoa ka pāngia te tangata e tēnei mate, he mea tino noa i roto i ngā wāhine i waenga i te 20 me te 40 tau te pakeke, me ngā tāne i waenga i te 50 me te 70 tau te pakeke. Mēnā ka whānau he tamaiti i te whaea e pāngia ana e tēnei mate, ka taea e ētahi o ngā pūmua (paturopi) i roto i te toto o te whaea te tuku ki te tamaiti, ka ngoikore ai ngā uaua mō te wā poto. Engari kāore he mea hei manukanuka, nā te mea ka whakakorea e te tinana o te tamaiti ēnei matū i roto i ētahi wiki, ā, ka hoki anō ngā uaua o te tamaiti ki te āhua noa.

He aha ngā tohu noa o tēnei mate?

Mō te tini o te tangata, ka tīmata te mate i ngā kanohi. Nō reira, ko ngā tohu tuatahi pea ko te kamo e piko ana, te tirohanga pōuri, te tirohanga takirua rānei. I roto i te tau kotahi, e rua rānei, ka horapa pea tēnei ngoikore ki ētahi atu uaua o te tinana.

Me whakamārama ake anō ēnei tohu i te ripanga i raro nei.

He aha tēnei e tupu nei? He aha te take?

Hei mārama ki tēnei, me mōhio tātou ki te mahi a ō tātou io me ngā uaua. Whakaarohia, ina hiahia koe ki te hapai i tō ringa, ka puta mai he karere mai i tō roro mā roto i ngā io. Ka tae atu tēnei karere ki te uaua i te hononga iti i waenganui i ngā pito io me te uaua. Ko te matū karere e kawe ana i tēnei karere ko te acetylcholine . Ina herea tēnei matū, te acetylcholine, ki ngā kaiwhakawhiwhi i roto i te uaua, ka whakawhāiti te uaua, arā, ka mahi.

Ko te Myasthenia gravis he mate pūnaha ārai mate.Arā, ka hē te pūnaha ārai mate e tiaki ana i tō tātou tinana, ka whakaeke i ngā wāhanga hauora o tō tātou ake tinana. Ko te mea ka tupu i roto i tēnei mate, ko ngā paturopi i hangaia e te pūnaha ārai mate ka aukati, ka whakangaro rānei i ngā kaiwhakawhiwhi acetylcholine i kōrerotia e au i mua ake nei. Kātahi ka kore te karere e puta mai ana i ngā io e tae tika ki ngā uaua. Koia te take ka ngoikore ai ngā uaua.

Me pēhea te tautuhi a te tākuta i tēnei mate?

Mena kei a koe ēnei tohu, me toro atu koe ki tētahi tākuta i te tuatahi. Ka tirotirohia koe e ia mō tō pūnaha io. Kātahi ka tūtohu pea rātou i ētahi whakamātautau hei tātaritanga i te mate.

• Whakamātautau toto: Ka mahia tēnei whakamātautau hei tirotiro mēnā kei roto i tō toto ngā paturopi motuhake e whakaeke ana i ngā kaiwhakawhiwhi acetylcholine i kōrerotia e au.
• Whakamātautau hukapapa: Ki te piko tō kamo, ka whakatakotoria he hukapapa ki runga mō te rua meneti pea. Ka mahia tēnei hei tirotiro mēnā ka whakaitihia e te makariri te ngoikore o te uaua mō te wā poto.
• Ngā whakamātautau whakaohooho io auau: Ka whakatakotoria ngā hikohiko ki te kiri, ā, ka tukuna ngā tohu hiko iti hei ine i te tere me te whai huatanga o ngā karere mai i ngā io ki ngā uaua.
• Whakamātautau EMG (Electromyography muka-kotahi): Ka whakauruhia he hiko tino angiangi, he rite ki te ngira, mā roto i te kiri ki roto i te uaua, ā, ka aroturukitia te mahi hiko i waenga i te roro me te uaua.
• Ngā matawai whakaahua: Tērā pea ka tonoa koe kia whai matawai CT , MRI rānei hei tirotiro mō te pukupuku thymus (thymoma).
• Ngā whakamātautau mahi a ngā pukahukahu: Ka mahia ēnei whakamātautau hei rapu mēnā kua pāngia te mahi a ngā pukahukahu e te mate.

Ngā maimoatanga me ngā mea ka taea e koe te mahi i te kāinga

Ko te maimoatanga mō tēnei mate ka whakawhirinaki ki tō tau, te kaha o ō tohu, me te tere o te horapa o te mate.

Ngā rongoā

Ka tūtohu pea tō tākuta i ngā rongoā pēnei i:

• Ngā aukati cholinesterase: Ka whakapai ake ēnei rongoā i te whakawhitiwhiti kōrero i waenga i ngā io me ngā uaua, ka āwhina i te whakapakari i ngā uaua.
• Corticosteroids: Ka whakahaere ēnei i te mahi a te pūnaha ārai mate, ā, ka whakaiti i te hanga o ngā paturopi kino.
• Ngā rongoā ārai mate: Ka hoatu hoki ēnei rongoā hei whakaiti i te urupare a te pūnaha ārai mate.

Ngā Whakaora Motuhake

Mēnā ka kino haere ngā tohu, i mua rānei i te pokanga, ka tūtohu pea tō tākuta i te rongoā ā-uaua (IV).

• Plasmapheresis: Ko te tikanga o tēnei ko te tuku i ō toto mā roto i tētahi mīhini hei tātari i ngā paturopi kino. Ahakoa he tere ngā hua, he poto noa te wā e mau ana.
• Immunoglobulin ā-uaua (IVIg): Ko tēnei maimoatanga he werohanga i ngā paturopi hauora ki roto i tō toto. Ka huri ēnei i te mahi a tō pūnaha ārai mate, ā, ka whakahaere hoki i ō tohumate.

Pokanga - Thymectomy

Mena he pukupuku kei roto i te repe thymus te take o te mate, ka tangohia katoatia te repe mā te pokanga. Ahakoa kāore he pukupuku, ka pai ake ngā tohu o ētahi tūroro ina tangohia te repe thymus.

Ngā huringa āhua noho

Haunga te rongoā, mā te hanga i ngā huringa iti ki tō momo noho ka āwhina anō hoki ki te whakahaere i ngā tohumate.

• Penapenahia te pūngao i te wā e kai ana: Ki te uaua ki te ngaungau kai, kai i te wā e nui ana te pūngao. Engari i te kai i ngā kai nui, kai i ētahi kai iti i te roanga o te rā. Kōwhiria ngā kai mātotoru.
• Whakamahia ngā taputapu haumaru: Tāutahia ngā pae hopu tata ki te wharepaku me te moenga, me ētahi atu. Tangohia ngā whāriki me ētahi atu taonga mai i te papa hei whakaiti i te tūponotanga o te paheke me te hinga.
• Rapua he āwhina mai i ngā mīhini: Penapenahia tō pūngao mā te whakamahi i ngā taputapu hiko (paraihe niho hiko, whakapuare kēne) hei utu mō ngā mahi ā-ringa.
• Whakamahia he taupoki kanohi: Ka āwhina tēnei i te tirohanga rua. Ina mātaki pouaka whakaata, ina pānui pukapuka rānei, katia tetahi kanohi, ā, whakamahia ngā kanohi e rua kia rerekē te āhua.
• Whakamaherehia tō rā: Whakamahia tō kaha me te whakaaro nui. Kimihia te wā o te rā e tino hihiko ana koe, ā, mahia ngā mahi o te whare me ngā mahi o waho.