Kei te pāngia koe e te ngoikore me te mamae nui i tō kaki, i ō pakihiwi, i ō ringaringa rānei i ētahi wā? Kāore rānei koe e mōhio ki ētahi wāhanga o tō tinana? Mena he nui atu i te kotahi o ēnei tohu, tera pea nā tētahi mate onge e kiia nei ko te syringomyelia, ā, ka kōrerohia e tātou. Kaua e manukanuka, ehara tēnei i te mea e pā ana ki te tini o te tangata. Engari he mea nui kia māmā noa iho tēnei mai i te tīmatanga.
He aha rawa tēnei syringomyelia?
He whakarāpopototanga noa iho, koinei te ingoa i hoatu ki te hanganga o tētahi pēke kī tonu i te wai, i roto rānei i tō tātou taurakira. Ka karangatia tēnei pēke kī tonu i te wai e ngā tākuta he 'syrinx'. Koia te take e karangatia ai tēnei mate e ētahi tāngata ko Hydromyelia, Syringohydromyelia.
I te nuinga o te wā, kāore pea koe e kite. Engari i ētahi wā, ki te tipu haere tēnei whē i roto i te wā, ka tīmata pea te pēhi me te kino i ngā io ngawari o tō tuaiwi. Mēnā koinā, me rongoā.
Ko tēnei mate te mea tino noa i waenga i ngā pakeke i waenga i te 20 me te 40 tau te pakeke. He nui ake hoki te kitea i roto i ngā tāne i ngā wāhine.
He aha pea ngā tohu?
Ko ngā tohu o tēnei ka whakawhirinaki ki te wāhi kei reira te cyst i roto i te tuaiwi me tōna rahi. I roto i te wā, i te tipu haere o te cyst, ka taea e ia te kino i ngā io o te tuaiwi. Koinā te wā ka tīmata ai ngā raruraru.
He maha ngā wā ka puta pōturi ngā tohu, mō ngā tau maha. Heoi, i ētahi wā ka puta ohorere ngā tohu i muri i tētahi aituā, pērā i te hinganga.
Kei te ripanga i raro nei ētahi o ngā tohu matua ka kitea.
| Kāwai tohu | Ngā mea hei tiro |
|---|---|
| Te mamae me te kare ā-roto | Mamae, ngoikore, wera, kare rānei e werohia ana te kaki, ngā pakihiwi, ngā ringaringa me ngā ringaringa. Ngaro te rongo i te wera/mātao, pērā i te wai wera, te huka rānei, i roto i ngā ringaringa, ngā maihao, me te uma o runga. |
| ngoikore o te uaua | Te ngoikore o ngā uaua (ina koa i ngā ringaringa me ngā pakihiwi), te uaua ki te hikoi nā te pakari o ngā uaua, me te ngaronga o ngā urupare ā-tinana. |
| Ngā huringa tinana | Te piko o te tuaiwi, he āhuatanga e kīia nei e tātou he scoliosis . Ngā huringa, ngā uauatanga rānei ki te whakahaere i te wharepaku, i te mimi rānei. |
| Ētahi atu āhuatanga | Te ānini o te upoko, te werawera nui, ngā huringa rerekē o te toto toto, ngā raruraru moepuku, me ngā nekehanga kore taunga. |
I ētahi wā, ki te pakaru te io o te mata me ngā kanohi i tēnei whēwhē, ka puta he āhuatanga e kiia nei ko te mate Horner . I tēnei wā, ka kitea pea ētahi āhuatanga pēnei i te piko o te kamo i te taha o te mata e pāngia ana, he iti te karu, me te heke o te werawera i taua taha.
He aha i puta ai tēnei mea?
Whakaarohia kei te karapotia tō tātou roro me tō tātou taurakira e tētahi wai motuhake e kiia nei ko te wai cerebrospinal. Ina rere noa tēnei wai, kāore he raruraru. Engari ki te āraia te ara o tēnei wai mō tētahi take, ka taea e taua wai te kohikohi i roto i te taurakira ka hanga i te whēwhē i kōrerotia e tātou. E rua ngā momo take matua mō tēnei.
Ngā Take Whakatupu
Koinei te tino take. Ina whānau mai ētahi pēpi, ka panaia pea te wāhanga o raro o tō rātou roro (cerebellum) ki raro ki te tuaiwi. Ka kiia tēnei e ngā tākuta he mate Chiari I. Ka aukatihia te rere o te wai, ā, ka puta he pūwero. Heoi, ehara i te mea ka pāngia te katoa e tēnei mate Chiari I e te syringomyelia . Ko te tikanga ka puta ngā tohu i waenga i te 25 me te 40 tau te pakeke.
Ngā Take i Whiwhihia
I ētahi wā ka puta anō tēnei āhuatanga i te kino o te tuaiwi, arā, he mea ka puta i muri i te whānautanga.
- Te whara o te taurakira
- Ngā mate urutā pērā i te meningitis
- Puku tuaiwi
- Te pupuhi o ngā kiriuhi e hipoki ana i te tuaiwi
- HereaTe āhua o te taurakira (e totoro rawa ana te pito o raro o te taurakira).
He tino onge, ka puta mai me te kore he take mārama. Ka kiia e ngā tākuta he idiopathic syringomyelia .
Me pēhea rawa te kitea o tēnei?
Ko te huarahi pai rawa atu, me te huarahi tino tika hoki ki te tautuhi i tēnei mate ko te whai i tētahi matawai MRI (Magnetic Resonance Imaging) . Ka matawaihia tō roro me tō tuaiwi katoa. Ka taea e tēnei te whakaatu mārama mēnā kei reira te pukupuku, tōna rahi, me te take o taua mate (hei tauira, he mate Chiari).
I ētahi wā, ka kitea noatia tēnei āhuatanga i te wā o te MRI mō tētahi atu take. I ētahi wā, ka tūtohu pea tō tākuta i tētahi matawai CT (Computed Tomography) .
Me pēhea te rongoā?
Ko te maimoatanga ka whiwhi koe ka whakawhirinaki ki te āhua o ngā tohu me te kaha o aua tohu. Kāore e rite te maimoatanga mō te katoa.
Mena kāore he tohu, he iti noa rānei: mātakitaki
Mena kāore he tohu, he iti noa iho rānei ō tohu, kāore pea koe e hiahia ki tētahi maimoatanga nui. Engari ka tirotirohia pea koe e tō tākuta i ia wā . Ka mahia e rātou he matawai MRI i ia wā hei tirotiro i ngā tohu hou, hei tirotiro rānei mēnā kei te nui haere te pukupuku. Ka tohutohu anō hoki rātou kia karohia ngā mahi uaua, pērā i te hiki i ngā mea taumaha. Ka tohua pea e rātou he rongoā mamae, ā, ka tukuna koe ki te whakaora tinana.
Mena he kino ngā tohu: Pokanga
Mena he nui rawa ō tohumate ka whakararuraru i tō oranga o ia rā, me mahi pokanga pea koe. Ko te whāinga matua o te pokanga he whakahoki mai i te rere o te wai kua aukatia.
Ko te momo pokanga ka mahia e koe ka whakawhirinaki ki te take o tō mate. Hei tauira, mēnā ko te Chiari I malformation te take, ka whakahaerehia pea e tō tākuta he tikanga e kiia nei ko te posterior fossa decompression . Ko te tikanga o tēnei ko te tango i tētahi wahi iti o te wheua mai i te tuara o te angaanga me te tihi o te tuaiwi kia nui ake ai te wāhi mō te roro me ngā io. Mā tēnei ka whakaiti i te pēhanga, ā, ka taea te rere noa o te wai.
He mea tino nui kia kōrerohia e koe ngā mōrearea me ngā painga o te pokanga me tō tākuta i mua i te whakatau.
He aha te mea ka tupu i muri i te maimoatanga?
He mea pai kia mōhio koe ki tēnei. I ētahi wā, ahakoa i muri i te pokanga, kāore te raruraru e tino ea. Ka taea e te wai te kohi anō. Waihoki, ko te kino ki ngā io ka pumau tonu i ētahi wā.
Nō reira, ahakoa i muri i te pokanga,He mea nui kia mau tonu te whakapā atu ki tō tākuta. Me whai koe i ngā matawai MRI auau hei tirotiro mēnā kua hoki mai anō te pukupuku. He mate tēnei e hiahia ana kia roa te wā e rongoatia ai. Nō reira, he mea tino nui kia whai i ngā tohutohu a tō tākuta.
Karere Tangohia ki te Kāinga
- He mate onge te syringomyelia e puta ai he whēwhē kī tonu i te wai i roto i te taurakira.
- Ko te mamae o te kaki, o ngā ringa, te ngoikore, me te ngaronga o te rongo i te wera/mātao pea ngā tohu matua.
- Ko te tino take o tēnei ko te aukati i te rere o te wai i roto i te roro me te taurakira. Ko te hapa whānau tino noa ko te mate Chiari I.
- He mea nui te matawai MRI hei tautuhi i te mate.
- Ko ngā kōwhiringa maimoatanga ko te tirotiro mēnā kāore he tohu, me te pokanga mēnā he kino rawa ngā tohu. Kōrero ki tō tākuta mō ngā tohu katoa kei a koe.











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