Ese wigeze ubona ikintu kimeze nk'umutuku ku mubiri w'umwana wawe cyangwa uwawe? Wenda wakoze ku kintu gito ukoresheje urutoki rwawe, maze gihita gihinduka umutuku, gitangira kubyimba, maze hagaragara agahu gato hejuru. Niba iki kibazo ukizi, ni ngombwa cyane kumenya indwara tuvuga uyu munsi.
Mu magambo make, Urticaria Pigmentosa ni iki?
Urticaria Pigmentosa ni ubwoko bw'uduheri tuba ku ruhu. Ikunze kugaragara cyane ku bana bato n'abakuze. Mu by'ukuri ni ubwoko bw'indwara yitwa 'mastocytosis'.
Noneho ushobora kuba wibaza icyo `mastocytosis` ari cyo. Biroroshye cyane. ``mast cells`` ni ubwoko bwihariye bw'uturemangingo mu budahangarwa bw'umubiri wacu. Bameze nk'abarinzi b'umubiri. Iyo ku mpamvu runaka utu turemangingo tw'umuhondo twikusanyirije mu gace kamwe k'uruhu, tuyita Urticaria Pigmentosa. Ariko, utu turemangingo tw'umuhondo dushobora kwikusanyiriza mu ruhu gusa, ndetse rimwe na rimwe no mu zindi ngingo nk'amagufwa n'amara. Hanyuma bigahinduka indwara yitwa ``systemic mastocytosis``. Ariko ntugahangayike, akenshi, Urticaria Pigmentosa mu bana igarukira ku ruhu gusa.
Muri iyi ndwara, iyo hagaragaye ikizinga cy'umukara ku ruhu, kiba umutuku, kikabyimba, kikarya, kikazamuka nk'aho cyagonzwe n'imodoka. Mu buvuzi, iki kimenyetso cyitwa "ikimenyetso cya Darier."
Kuki ikintu nk'iki kibaho?
Impamvu nyamukuru ibitera ni "uturemangingo twa mast" twavuze mbere. Utu turemangingo ni ubwoko bw'uturemangingo tw'amaraso twera tukorerwa mu igufwa ryacu. Utu turemangingo tuboneka hirya no hino mu mibiri yacu, cyane cyane aho duhura n'isi yo hanze, nko mu ruhu, mu bihaha no mu mara. Iyo ikintu kimeze nk'umugera winjiye mu mubiri, utwo turemangingo twa mast dusohora imiti yitwa "histamine" kugira ngo ifashe mu kurinda umubiri.
Urticaria Pigmentosa iterwa n'impinduka mu ngirabuzimafatizo ituma utwo turemangingo twiyongera cyane mu ruhu. Iyi mpinduka mu ngirabuzimafatizo ikunze kubaho umwana akiri mu nda. Ariko, si ikintu ababyeyi bakura ku bana . Impamvu nyayo y'iyi mpinduka ntiramenyekana.
Iyo abantu bakuru barwaye iyi ndwara, ishobora kuba ikomeye cyane. Yitwa 'indolent systemic mastocytosis'. Muri iki gihe, uturemangingo twa mast twikusanyiriza ahantu nk'umusokoro w'amagufwa hamwe n'uruhu. Ni gake cyane, iyi ndwara ishobora kuvamo kanseri yitwa 'mast cell leukemia'. Ariko nanone, ibi ni ibintu bidasanzwe . 99% bya Urticaria Pigmentosa igaragara ku bana ntabwo iba ikomeye cyane.
Ni ibihe bimenyetso by'iyi ndwara?
Ikimenyetso nyamukuru kandi kigaragara cyane ni `ikimenyetso cya Darier' twavuze. Ni ukuvuga ko amabara y'umukara ahinduka umutuku kandi agashya iyo asutswe. Byongeye kandi, hari abantu bashobora no kugira ibimenyetso bikurikira.
| Ibimenyetso | Ibisobanuro byoroshye |
|---|---|
| Umutima utera cyane | Igipimo cy'umutima kiriyongera nk'aho wumva ufite ubwoba. |
| Impiswi (kubabara mu gifu) | Bishobora guterwa no gukora k'uturemangingo tw'igifu mu buryo bw'igogora. |
| Gusukura amazi | Guturika mu maso no hejuru y'umubiri bitunguranye. |
| Guhumeka bigoranye (Guhumeka nabi) | Ijwi rya 'foromaje-foromaje' iyo umuntu ahumeka, nk'iry'abarwayi ba asima. |
| Kuzinduka | Gutakaza ubwenge bitewe no kugabanuka gutunguranye k'umuvuduko w'amaraso. |
| Umutwe | Umutwe. |
Abarenga 75% by'abarwayi ba Urticaria Pigmentosa ni abana bari munsi y'imyaka 10. Mu bana benshi, iyi ndwara igarukira ku ruhu gusa kandi igenda irushaho kuba myiza uko imyaka igenda ikura.
Ni gute umuganga asuzuma ibi?
Kenshi na kenshi, muganga wawe ashobora gusuzuma iyi ndwara byoroshye arebye uduce turi ku ruhu rwawe akagenzura ikimenyetso cya Darier. Nta bindi bipimo bikenewe.
Ariko, niba hari gushidikanya niba iyi ndwara idashingiye ku ruhu gusa ahubwo ko yanagize ingaruka ku bindi bice by'umubiri, muganga ashobora kukugira inama yo gupima ibi bikurikira.
- Isuzuma ry'amaraso (`Umubare w'amaraso`): Menya ubwoko butandukanye n'ingano y'uturemangingo mu maraso.
- Ikizamini cya serum tryptase: Gisuzuma niba hari enzyme mu maraso irekurwa n'uturemangingo twa mast.
- Gupima ubucucike bw'amagufwa: Reba uburyo amagufwa yawe akomeye.
- Ikizamini cy'umusemburo w'amagufwa: Kigenzura niba umusemburo w'amagufwa urimo gukora uturemangingo tuzima.
Uburyo bwo kuvura n'uburyo bwo kugenzura indwara
Inkuru nziza ni uko ku bana benshi, Urticaria Pigmentosa izakira ubwayo uko bagenda bakura . Nta buryo bwihariye bwo kuvura kugira ngo hatabaho uduce dushya. Uduce dusanzweho dushobora gufata imyaka myinshi kugira ngo dushire.
Mu gihe iyo ndwara igarukira ku ruhu gusa, nta buvuzi bukomeye busanzwe bukenewe. Muganga wawe ashobora kukugira inama zikurikira kugira ngo umenye ibimenyetso byawe:
- Imiti igabanya ububabare ikoreshwa mu kunywa: Igabanya ububabare no kubyimba.
- Amavuta yo kwisiga ya Corticosteroid: Siga ahantu hashyushye.
- Cromolyn sodium: Umuti utangwa mu kuvura ibimenyetso nko kuruka no gucibwamo.
- EpiPen: Igikoresho gihabwa abantu bafite ubwivumbure bukomeye cyane (reaction anaphylactic) kugira ngo bakikoreshe mu gihe cy’impanuka. Si buri wese ugikeneye.
Ibintu byo kwirinda by'umwihariko
Ikintu cy'ingenzi muri iyi ndwara ni ukwirinda ibintu bitera ibimenyetso byongera, ni ukuvuga ibintu bituma ibyo bisebe bishya bigahinduka umutuku.
| Imiti yo kwirinda | Ibindi bintu byo kwirinda |
|---|---|
| Asipirine | Gukora imyitozo ngororamubiri (cyane cyane isaba imbaraga nyinshi) |
| Inzoga | Gusiga uruhu cyane ukoresheje ibitambaro |
| Imiti igabanya ububabare nka morphine na codeine (`Opiates`) | Kwiyuhagira mu mazi ashyushye |
| Thiamine (Vitamine B1) | Ibinyobwa bishyushye |
| Quinine (`Quine` - umuti wa malariya) | Kwibasirwa n'izuba rikabije |
| Dextromethorphan (umuti w'inkorora) | Guhura n'ubukonje bukabije |
| Imiti imwe n'imwe igabanya ububabare n'irangi rya X-ray | Ibiryo bishyushye kandi biryoshye |
Icy'ingenzi: Niba wowe cyangwa umwana wawe mukeneye gufata imiti y'indi ndwara, menya neza ko mwabimenyesheje muganga wanyu ibijyanye na Urticaria Pigmentosa.
Ese ibibazo bishobora kubaho?
Ni gake cyane, iyi ndwara ishobora kugera kuri `systemic mastocytosis`. Abantu nk'abo baba bafite ibyago byinshi byo kugira allergie ikomeye yitwa `anaphylactic shock`, ishobora gushyira ubuzima mu kaga. Niba ugize ibimenyetso nko kugorwa no guhumeka no guta ubwenge , ugomba guhita ugana ishami ryihutiye gutabara (ETU) ku bitaro .
Izindi ngorane ziterwa na mastocytosis y’umubiri zirimo:
- Osteoporose: Kugabanuka kw'amagufwa.
- Cytopenia: Kugabanuka k'umusaruro w'uturemangingo tw'amaraso mu mubiri.
- Ibibazo by'umwijima.
- Kanseri (idasanzwe cyane).
Ibi kandi ni ingorane zidakunze kugaragara. Ni gake cyane ku bana barwaye Urticaria Pigmentosa.
Ubutumwa bwo kujyana mu rugo
- Urticaria Pigmentosa ni indwara y'uruhu yibasira cyane cyane abana. Ntabwo yandura cyangwa ngo ihere ku babyeyi.
- Ikimenyetso nyamukuru ni uko iyo ibara ry'umukara rigabanutse, rihinduka umutuku, rikabyimba, kandi rigashya (`ikimenyetso cya Darier`).
- Ntugatinye bitari ngombwa, kuko iyi ndwara izagenda irushaho kuba nziza ku bana benshi uko bagenda bakura.
- Uburyo bwiza bwo kubyifatamo ni ukwirinda ibiryo, imiti, n'ibikorwa byongera ibimenyetso.
- Niba wowe cyangwa umwana wawe mufite kimwe muri ibi bimenyetso, menya neza ko mwagiye kwa muganga kugira ngo agufashe gusuzuma neza kandi aguhe inama zikenewe.
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