Chirwere ichi chinonzi 'Atypical Genitalia' chakajairika zvakadii?
Ichi chirwere chisingawanzoitiki . Zvichienderana nehuwandu, mwana mumwe chete pavana vacheche 1,000 kusvika 4,500 ndiye anobatwa nechirwere ichi. Saka, kunyange zvazvo chisingawanzoitiki, zvakakosha kuziva nezvazvo.Nhengo dzemwana dzinokura sei?
Kuti unzwisise izvi, unofanira kuziva zvishoma nezvekukura kwenhengo dzepabonde dzemwana mudumbu. Fungidzira, iyi inzira yakaoma uye inoshamisa. Izvi zvinoitika mumatanho matatu makuru: 1. Kuziva zvepabonde zvemajini: Chinhu chekutanga chinoitika ndechekuti bonde remajini remwana rinoonekwa. Izvi zvinoitika kana mbeu inobva kuna baba yakabatana nezai kubva kuna amai. Amai vanogara vachigamuchira X chromosome. Baba vanogona kugamuchira X kana Y chromosome. Saka, kana X kubva kuna amai ne X kubva kuna baba zvikabatana (XX), musikana anozvarwa. Kana X kubva kuna amai ne Y kubva kuna baba zvikabatana (XY), mukomana anozvarwa. 2. Kuumbwa kwegonad: Tevere, gonad dzemwana dzinokura zvichienderana nebonde iri remajini. Mumwana wechikadzi, maovari anokura, uye mumwana wechirume, matestes anokura. 3. Kukura kwenhengo dzemukati nedzekunze: Chekupedzisira, mahormone anogadzirwa negonad idzi ndiwo anokonzera kukura kwenhengo dzemukati dzemwana nedzekunze dzenhengo dzemuviri. Saka, kana paine shanduko mune chero chikamu cheizvi, ipapo chirwere chinonzi Dissociative Developmental Disorder (DSD), kana kuti 'Atypical Genitalia', chinogona kuitika. Kazhinji, izvi zvinokonzerwa nematambudziko emahormone. Mahormone aya anogona kupfuudzwa kuburikidza nemajini kubva kuvabereki, kana kuti anogona kuitika pasina chikonzero chakajeka.Ndezvipi zvinokonzera 'Atypical Genitalia'?
Kazhinji, chikonzero chikuru cheizvi imhaka yekusashanda zvakanaka kwemahormone mumuviri wemwana panguva yekuzvitakura.Mahormone aya anodzora kukura kwenhengo dzepabonde dzemwana. Saka, kana paine kusawirirana mumahormone aya, zvinokanganisa kukura kwenhengo dzepabonde dzemwana. Zvikonzero izvi zvinogona kusiyana zvichienderana nemachromosomes epabonde emwana.46 XX DSD (DSD ine patani yechromosome yevakadzi)
Mumamiriro ezvinhu aya, majini emwana ndeechikadzi (XX). Izvi zvinoreva kuti mwana ane mazai uye chibereko mukati. Zvisinei, nhengo dzekunze dzemwana dzinogona kutaridzika sedzechirume, dzine nhengo yemurume nemachende. Izvi zvinoitika kana nhengo dzekunze dzemwana dzikasangana nemazinga akawedzera emahormone echirume (androgens) panguva yekukura kwenhengo dzekunze dzemwana. Chikonzero chikuru cheizvi chirwere chinonzi 'Congenital Adrenal Hyperplasia' (CAH). Apa ndipo apo adrenal glands yemwana inoburitsa mahormone echirume akawandisa .46 XY DSD (DSD ine patani yechromosome yemurume)
Muchiitiko ichi, majini emwana ndeemurume (XY). Izvi zvinoreva kuti mwana anofanira kunge aine machende (machende) mukati. Zvisinei, nhengo dzekunze dzemuviri hadziratidzi hunhu hwemurume zvakajeka, uye dzinogona kutofanana nehunhu hwemukadzi. Pane zvikonzero zvikuru zveizvi:- Machende emwana haasi kukura zvakanaka.
- Machende haakwanise kugadzira testosterone yakakwana yehormone yechirume.
- Kunyangwe testosterone ichigadzirwa, muviri wemwana haugone kuishandisa nemazvo.
Matambudziko ekusiyana kweGonadal
Chinoitika muchiitiko ichi ndechekuti magonadhi emwana haakure zvizere kuita matestes kana maovari.- Kusashanda zvakanaka kweGonadal: Muizvi, gonads (matestes kana maovari ) hadzina kukura zvakakwana.
- Kusashanda zvakanaka kweGonadal: Muizvi, kunyange zvazvo mamwe matishu emudumbu akaumbwa mugonad yemwana, matishu iwayo haashande zvakanaka.
- Kusashanda zvakanaka kweGonadal: Muizvi, magonadhi ese ari maviri anobuda nguva isati yakwana, zvichireva kuti haakure kuita machende kana maovari.
DSD yeOvotesticular (DSD yezai-yemazamu)
Ichi chirwere chisingawanzoitiki. Panyaya iyi, magonadhi emwana anogona kunge aine matinji emudumbu pamwe nematinji emudumbu. Kana kuti, panogona kunge paine ovary kune rumwe rutivi uye testicle kune rumwe.Ko 'Atypical Genitalia' inotaridzika sei kunze?
Kuonekwa kwechirwere ichi kunosiyana zvichienderana nema chromosomes akakanganiswa uye mamiriro emahormone. Nhengo dzepabonde dzisina kujairika mumwana ane majini echikadzi (XX chromosomes) dzinogona kuva nezviratidzo zvinotevera:- Clitoris inokura uye inoita kunge mboro diki.
- Muburi weurethra uri pasi pemaburi emukadzi kana mukati memukadzi kwete panzvimbo yawo yakajairika.
- Mazamu akabatana, achitaridzika semaburi emudumbu.
- Panogona kunge paine bundu renyama pakati pemazamu, rinogona kunge rakaita sehomwe ine machende.
- Nhengo yemurume haisipo zvachose kana kuti diki kwazvo, ichitaridzika senhengo yemurume yakakura (micropenis).
- Muburi weurethra uri pasi penhengo yemurume kana pakati pemaburi panzvimbo pekumusoro (chirwere ichi chinonziwo 'Hypospadias').
- Chipfuko chedumbu chakatetepa, chakakamurwa nepakati, uye chakaita semazamu emukadzi.
- Machende abva mudumbu uye haasisiri mudumbu ( machende asina kukwira ).
Ndezvipi zvimwe zviratidzo zve'Atypical Genitalia'?
Chitarisiko chenhengo dzekunze dzemuviri ndicho chinhu chikuru chinoratidza izvi. Pamusoro pezvo, unogona kuona zvinhu zvakaita se:- Kusawirirana kwemahormone .
- Kana ari musikana, kuenda kumwedzi kunogona kutanga nekukurumidza, kunonoka, kana kusatomboitika zvachose.
- Hypospadias inguva apo buri remuuro risiri pamucheto wenhengo yemurume.
Vanachiremba vanoongorora sei chirwere ichi?
Vanachiremba vanowanzoona chirwere ichi mwana achangoberekwa . Kana, panguva yekuongororwa kwemwana kwekutanga zvakanaka. Kana zvisina kujeka kuti mwana wacho mukomana here kana musikana, chiremba wemwana acharaira kuti aongorore zvimwe zvirwere.Chii chaunotarisira panguva yekuongororwa kwemwana wako nachiremba?
Chiremba achatanga nekukubvunza nezvenhoroondo yezveutano hwemhuri yako. Zvadaro, achanyatsoongorora nhengo dzekunze dzemwana. Miedzo inotevera inogona kuitwa kuti pave nechirwere chakarurama:- Kuongororwa kweropa: Kuongorora huwandu hwemahormone nechromosomes emwana.
- Kuongororwa kwemifananidzo: Izvi zvinogona kutarisa nhengo dzemukati dzemwana, dzakadai se ultrasound, X-ray, kana MRI (Magnetic Resonance Imaging).
- Biopsy kana Laparoscopy: Kutora chidimbu chidiki chenyama kubva mugonadhi yemwana kuti chiongororwe.
'Atypical Genitalia' inorapwa sei?
Usati watanga kurapwa, danho rekutanga nderekutsvaga chikonzero chaicho chechirwere ichi. Zvadaro, zvichibva pamhedzisiro yekuongororwa kwemahormone nedzimwe bvunzo, timu yezvekurapa ichasarudza hurongwa hwekurapa uye basa rakakodzera rebonde remwana. Sezvo iyi iri nyaya yakaoma uye inonetsa, timu yemapoka akasiyana-siyana ichavepo kuti ikubatsire. Zvakakosha kuwana vanhu vane ruzivo mune izvi zvirwere. Ndivo vanogona kukupa mazano akanakisa. Chikwata ichi chinogona kusanganisira nyanzvi dzakadai se:- Chiremba wevana vacheche
- Nyanzvi yezvemajini
- Chiremba weEndocrinologist
- Chiremba
- Chiremba wezvedundira
- Nyanzvi yezvepfungwa
- Chikonzero chemamiriro emwana.
- Kuonekwa kwenhengo dzesikarudzi dzemwana.
- Zvido zvemhuri yako uye zvitendero zvetsika.
- Kurapa Kutsiva Mahormone (HRT): Kana paine kusawirirana kwemahormone, chirwere ichi chinogona kudzorwa nekurapwa kwemahormone chete.
- Kuvhiyiwa kwekugadzirisa: Dzimwe nguva, timu yezvekurapa inogona kukurukura newe uye kukupa zano rekuvhiyiwa mwana wako achiri mudiki. Zvisinei, kune maonero akasiyana nezve kuvhiyiwa uku kwekugadzirisa kwe 'Atypical Genitalia'. Dzimwe nguva, semuenzaniso, kana mwana asina mukana wekuti weti ipinde, kuvhiyiwa kunodiwa pakurapa. Zvisinei, kana kuvhiyiwa kwacho kuri kwekuvandudza chitarisiko, vamwe vabereki vanosarudza kumirira kusvika mwana akura uye vanogona kuita sarudzo nezvemuviri wavo. Ichi chisarudzo chakakosha uye chakafungwa zvakanaka.
Yeukai: Sarudzo iyi yekuvhiyiwa inogona kukanganisa zvikuru hupenyu hwemwana wenyu mune ramangwana, saka zvakanaka kutaura nemupi wezano ane ruzivo munyaya iyi.
Kana mwana wangu aine 'Atypical Genitalia', chii chandinofanira kutarisira?
Dambudziko rekuti 'Atypical Genitalia' rine mhedzisiro yakakura pamwana kwete panyama chete, asiwo pamagariro evanhu nepfungwa.Zvinogona kukonzerwa nerudzi rwenhengo dzesikarudzi, izvo zvinogona kukanganisa maonero emwana nezvaari. Sarudzo yekuvhiyiwa inogona kukanganisa hupenyu hwemwana. Ndosaka zvichikosha kutsvaga mazano enyanzvi nezveizvi. Kunyangwe kuongororwa kwe'Atypical Genitalia' kuchigona kunetsa zvikuru, timu yako yezvekurapa ichakubatsira kusarudza nzira yakanakisisa yekurapa.Ndirini pandinofanira kutsvaga rubatsiro rwechiremba nezvedambudziko remwana wangu re'Atypical Genitalia'?
Chiremba anowanzo ongorora chirwere ichi pakuzvarwa kana panguva yekuongororwa kwekutanga kwemwana. Chiremba anozokurukura newe nezvechirwere ichi uye nzira dzekurapa nadzo.Mibvunzo ipi yandinofanira kubvunza chiremba wemwana wangu?
Panguva yakaita seiyi, ungave nemibvunzo yakawanda mupfungwa dzako. Mibvunzo iyi inogona kukubatsira:- Mwana wangu anoda kurapwa nekukasika here, kana kuti tinogona kumirira kwenguva yakati rebei tozoita sarudzo gare gare?
- Ndivanaani vanachipangamazano vanofanira kushanyirwa nemwana wangu?
- Tinofanira kuona mupi wezano wezvemajini here?
- Remangwana remwana wangu richave rakaita sei?
- Kune mapoka ekutsigira vanhu nemhuri dzine 'Atypical Genitalia' here?
Mwana wangu achakwanisa here kuva nevana mune ramangwana?
Kubereka kwemwana mune ramangwana uye kushanda kwepabonde zvinoenderana nechikonzero chechirwere ichi, Atypical Genitalia. Dzimwe ongororo dzakawana kuti:- Vasikana vane Congenital Adrenal Hyperplasia (CAH) vanogona kubata pamuviri mushure mekurapwa nemahormone.
- Vakomana vane kanenge kamwe chete kechirume kanoshanda zvakanaka vanogona kubereka vana.
- Vanhu vane Ovotesticular DSD vane ovary inoshanda zvakanaka vanogona kukwanisa kuva nevana.
- Kunyangwe paine kusagadzikana kwemachende, avo vane chibereko chakakura zvakanaka vanogona kukwanisa kuchengetedza mwana akaisirwa muchibereko.
Pakupedzisira, zvekurangarira (Mharidzo Yekuenda Kumba)
Tinonzwisisa kuti kuziva kuti mwana wako achangoberekwa ane 'Atypical Genitalia' kunogona kuva chiitiko chinoshungurudza zvikuru, chinoshungurudza uye chinovhiringidza iwe nemhuri yako. Muchafanira kukurukura nyaya dzakawanda dzezvekurapa, dzetsika uye dzepfungwa nemhuri yako nechikwata chevanachiremba.Asi ndapota yeukai, hamusi mega murwendo urwu. Chikwata chenyu chezvekurapa chichakupai ruzivo, rutsigiro, uye mazano aunoda. Nerubatsiro rwavo, munogona kuita sarudzo dzakanakisisa nezvebonde remwana wenyu uye kurapwa kwake, kupa mwana wenyu hupenyu hwakanakisisa, uye kuwana mhedzisiro yakanakisisa. Musarasikirwa neushingi. Neruzivo rwakakodzera nerutsigiro, muchawana simba rekutarisana nedambudziko iri.
'Zvirwere zvenhengo dzesikarudzi zvisingawanzoitiki, Zvirwere zvenhengo dzesikarudzi zvisina kujeka, DSD, Zvirwere zvenhengo dzesikarudzi, Mahormone, Machromosome, Hutano hweVana, Matambudziko eGenetic, Congenital Adrenal Hyperplasia, Kukura kweBonde











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