Bundu risinganzwisisike pamuviri wako here? Ringave Hamartoma! Ngatitaurei nezvazvo - Nirogi Lanka

Bundu risinganzwisisike pamuviri wako here? Ringave Hamartoma! Ngatitaurei nezvazvo - Nirogi Lanka

Physician Reviewed — Not Medical Advice

Wakambonzwa bundu diki kana kuti dumbu pamuviri wako here ukanzwa uchinetseka, uchifunga kuti, "Chii ichi?" Kana kuti pamwe chiremba akataura izwi rekuti "Hamartoma," ukasara uchinzwa kuvhiringidzika? Chii chaizvo chinonzi hamartoma? Ngationgororei nemashoko ari nyore kunzwisisa pano paNirogi Lanka.

Chii chinonzi Hamartoma? Ngatirambei tiri nyore!

Saka, chii chaizvo chinonzi hamartoma? Kuti zvive nyore, kukura kusiri kwekenza (kusingakuvadzi). Kunoumbwa nemasero akafanana anowanzo kuwanikwa muchikamu ichocho chemuviri wako. Zvisinei, pane musiyano mudiki: masero aya akarongwa nenzira isina kurongeka kana kuti isina kurongeka. Zvakafanana nekutora murwi wematoyi akafanana woakanda mumurwi pane kuaronga zvakanaka.

Izwi rekuti "hamartoma" rinobva pamashoko maviri echiGiriki: "hamartia," zvinoreva "chikanganiso" kana "chikanganiso," uye "oma," zvinoreva "bundu." Chaizvoizvo, zvinoreva kukura kunoumbwa nekuda kwekusarongeka kwemaumbirwo.

Chinhu chakakosha kurangarira ndechekuti hamartomas HAISI kenza . Kusiyana nemasero ekenza , haapararire mumuviri wako wese. Saka, hapana chikonzero chekuvhunduka. Zvisinei, zvichienderana nekuti ari kupi, dzimwe nguva anogona kukonzera matambudziko madiki.

Hamartoma inogona kuumbwa kupi mumuviri?

Hamartomas inogona kuonekwa chero kupi zvako mumuviri, asi kune nzvimbo shoma dzakajairika:

  • Mapapu : Hamartomas anowanzo kuwanikwa mumapapu. Kutaura zvazviri, ndiwo anokonzera angangoita 10% yemabundu ese asina njodzi emapapu. Kazhinji, anowanikwa netsaona panguva yeX-ray yenguva dzose yechipfuva nekuda kwechimwe chikonzero.
  • Ganda: Maronda eganda anowanzoonekwa pamusoro, pamutsipa, uye kunyanya kumeso, miromo, kana nzeve. Dzimwe nguva, anogona kutaridzika sechiratidzo chekuzvarwa.
  • Mwoyo : Izvi zvinogonawo kuumbwa mumoyo. "Cardiac rhabdomyoma" rudzi rusingawanzoonekwi rwehamartoma yemoyo. Izvi zvinowanzoonekwa mwana achiri mudumbu ( panguva yekuzvitakura ) kana nguva pfupi mushure mekuzvarwa. Kunyange zvazvo zvisingawanzoitiki, zviri pakati pemabundu emwoyo anowanzoonekwa muvacheche.
  • Uropi: Rudzi rwakasiyana rwunozivikanwa se "hypothalamic hamartomas" runowanikwa mu hypothalamus, nzvimbo ine basa rekugadzirisa mashandiro emuviri. Kunyange zvazvo izvi zvingangove zviripo kubva pakuzvarwa, zvinowanzo ratidza zviratidzo panguva yehudiki kana kuyaruka, zvakaita sepfari , matambudziko ekuona , kana kuyaruka kwevana vasati vasvika panguva yekuzvitakura .
  • Zamu: Zvikamu zvishanu kubva muzana zvemapundu asina njodzi mumadzimai zvinogona kunge zviri zvema hamartomas. Anonyanya kuonekwa mumadzimai anopfuura makore makumi matatu nemashanu.

Pamusoro pezvo, zvichibatanidzwa nemamwe mamiriro ezvinhu emumajini akadai sePTEN hamartoma tumor syndrome (PHTS), kukura uku kunogonawo kuonekwa muitsvo, spleen, thyroid gland, uye mapfupa.

Ko Hamartomas inopararira mumuviri wese here?

Izvi zvinowanzoitika. Kwete, hamartomas haina kufanana nekenza; haapararire. Anogara panzvimbo chaiyo yaakaumba. Zvisinei, kana bundu rikakura zvakakwana, rinogona kudzvanya nhengo kana nhengo dzine hutano dziri pedyo, zvichikonzera kusagadzikana. Zvisinei, izvi hazviwanzoitiki.

Pane zvimwe zvirwere zvine chekuita neHamartomas here?

Ehe, hamartomas inogona kusanganiswa nemamwe marudzi ezvirwere zvemajini asingawanzoitiki, uko kushanduka kwemajini kunotungamira pakuumbwa kwawo.

  • Pallister-Hall syndrome (PHS): Yakabatana nekuchinja kwemajini eGLI3. Vanhu vanosvika 5% vane hypothalamic hamartomas vanogona kunge vaine chirwere ichi.
  • Tuberous sclerosis: Chirwere ichi chinogona kukonzera hamartomas kukura muuropi, mwoyo, itsvo, ganda, nemaziso.
  • Neurofibromatosis Type 1 (NF1) : Chirwere chemajini chisingawanzoitiki apo hamartomas inogona kuumbwa patsinga dzemuviri wese.
  • PTEN hamartoma tumor syndrome (PHTS): Boka rezvirwere zvinosanganisira Cowden syndrome neBannayan-Riley-Ruvalcaba syndrome (BRRS), uko hamartomas inogona kuumbwa mumazamu, chibereko, thyroid, GI tract, uye ganda.
  • Peutz-Jeghers syndrome (PJS): Yakabatana ne STK11/LKB1 gene mutation, vanhu vane PJS vane njodzi yakakura yekubatwa ne hamartomas mumapapu, mudumbu, dundira, muura hudiki, muura hwemudumbu, uye mudumbu.

Kana uine chirwere chakadaro chemajini, chiremba wako anogona kukurudzira kuongororwa kwemajini kana kupiwa mazano.

Ndezvipi zviratidzo zveHamartoma?

Kazhinji, hamartoma haina zviratidzo , zvichireva kuti unogona kuva nayo usingambonzwa kusagadzikana. Kana zviratidzo zvikaitika, kazhinji zvinokonzerwa nekuti kukura kwacho kwakura zvakakwana kuti udzvanye nyama dziri pedyo. Zviratidzo zvinoenderana chete nenzvimbo ye hamartoma.

Semuenzaniso, hamartoma yemapapu inogona kukonzera kukosora kunogara kwenguva refu kana kufema kushoma kana ikakura. Hamartoma yeuropi inogona kukonzera pfari kana matambudziko ekuona.

Chii chinokonzera Hamartoma?

Masayendisiti haazive nguva dzose chikonzero chaicho che hamartoma yega yega. Zvisinei, sezvataurwa, kazhinji zvine chekuita nemamiriro ezvinhu emajini, ayo anogona kugara nhaka kubva kuvabereki nekuda kwekuchinja kwemajini.

Hamartoma inogona kukonzera matambudziko here?

Mazhinji ema hamartoma haana njodzi. Zvisinei, kana akakura zvakakwana kuti avhiringidze mashandiro enhengo inokosha, matambudziko anogona kumuka. Semuenzaniso, rhabdomyoma yemwoyo inogona kukanganisa mashandiro emoyo, zvichikonzera kutadza kwemoyo. Saizvozvowo, hamartoma ye hypothalamic inogona kukanganisa kuenzana kwemahormone kana mashandiro epfungwa. Ndapota iva nechokwadi chekuti chiremba wako anogona kutarisa kukura uku kana kukubvisa kana zvichidikanwa.

Hamartomas inoonekwa sei?

Nekuti ma hamartoma mazhinji haana zviratidzo, anowanzoonekwa netsaona panguva yekuongororwa kunoitwa nechinangwa chimwe. Dzimwe nguva kusiyanisa hamartoma negomarara kunogona kuoma, zvichienderana nenzvimbo yaro. Chiremba wako achaita ongororo yemuviri uye kuongorora nhoroondo yako yezvekurapa. Kazhinji, mifananidzo yekuongorora kana bvunzo dzinodiwa kuti zvionekwe kuti kukura kwacho i hamartoma zvechokwadi. Kana uine dambudziko, ndapota tsvaga rubatsiro rwechiremba nekukasika kana kubata emergency services kana ukaona zviratidzo zvakakomba.

Ndezvipi zviedzo zvekuongorora zvinoshandiswa?

  • X-ray: Inoshandisa mwaranzi shoma kugadzira mifananidzo yemapfupa ako nenyama dzakapfava. Manyoka emapapu dzimwe nguva anoonekwa se "popcorn" paX-ray, izvo zvinobatsira vanachiremba kusiyanisa kubva kumabundu ane kenza.
  • Ultrasound: Inoshandisa mafungu eruzha kugadzira mifananidzo yenyama dzakapfava dziri mumuviri wako.
  • CT scan (computed tomography): Inoshandisa maX-ray akawanda kuti ipe mifananidzo yemukati menyama yako yakapfava nemapfupa. CT scan inoshanda zvikuru pakuona mapapu ane hamartoma.
  • MRI (Magnetic resonance imaging): Inoshandisa magineti akasimba nemasaisai eredhiyo kuti ibudise mifananidzo yakadzama uye yakajeka yenyama dzakapfava dzemuviri wako.
  • Mammogram: Inoshandisa mwaranzi shoma kuongorora nyama dzezamu. Mazamu akawanda emhasuru dzezamu anowanikwa netsaona panguva yekuongororwa kenza kwemammogram.
  • Kuongororwa kwemuviri:Chiremba anobvisa chidimbu chidiki chekukura kwemasero ochitumira kurabhoritari. Nyanzvi yezvirwere inozoongorora masero aya pasi pemaikorosikopu. Iyi biopsy ndiyo nzira chaiyo yekuona kana kukura kwacho kuine masero asina njodzi akadai sehamartoma kana kuti ane kenza. Iyi ndiyo nzira yakanakisisa yekuongorora chirwere.

Matambudziko eHamartomas anorapwa sei?

Chirongwa chekurapa kwako chinoenderana nenzvimbo ye hamartoma uye kana iri kukonzera zviratidzo.

  • Kana isina zviratidzo: Kana kukura kwacho kusiri kukonzera matambudziko kana zviratidzo, chiremba wako anogona kusarudza kungokutarisa. Izvi zvinosanganisira kuongorora nguva nenguva kuti aone kana paine shanduko muhukuru kana chitarisiko.
  • Kana uine zviratidzo kana kuti uchifunga kuti une gomarara: Muzviitiko izvi, kubviswa kwechirwere chegomarara ndicho chinonyanya kukosha.

Ndezvipi kuvhiyiwa kwakananga kunoshandiswa kubvisa hamartomas?

Maitiro acho anosiyana zvichienderana nenzvimbo ye hamartoma.

Kune hamartoma yemapapu:

  • Kubviswa kwechidimbu: Chikamu chidiki chemapapu chine bundu chinobviswa, pamwe chete nechikamu chenyama ine hutano.
  • Kubviswa kweLobectomy: Lob rese remapapu rinobviswa kana hamartoma iri ipapo. Tine ma lob matatu mumapapu ekurudyi uye maviri kuruboshwe.
  • Kubviswa kwemapapu: Kubviswa kwemapapu ese. Izvi hazviwanzodiwa kune hamartoma.

Zvehuropi (Hypothalamic hamartomas):

  • Kuvhiyiwa kwekuvhiyiwa: Chiremba wepfungwa anovhiya kubvisa bundu racho nekuvhiya.
  • Kubvisa: Kupisa kwakanyanya kana kuti simba re laser rinoshandiswa kuparadza tishu.
  • GammaKnife® radiosurgery: Haisi nzira yekuvhiya yechinyakare, nzira iyi inoshandisa mwaranzi chaiyo, ine simba guru kuparadza kukura kwacho nenzira chaiyo sekubvisa kwakaitwa pakuvhiya.

Chii chinoitika kana ndikava ne hamartoma?

Mazhinji ema hamartoma haasi matambudziko akakomba, saka ndapota musazvidya mwoyo zvisina kufanira. Kana hamartoma iri kukanganisa nhengo yemuviri kana kuti ine njodzi yematambudziko mune ramangwana, kuvhiyiwa kunogona kugadzirisa dambudziko racho zvinobudirira.

Dzimwe nguva, kubvisa kunogona kuoma. Semuenzaniso, kana hypothalamic hamartoma iri pedyo ne optic nerve, kuvhiyiwa kune njodzi yekukuvadza tsinga.

Saka, zvakakosha kuti mutaurirane pachena nachiremba wenyu nezve kana hamartoma yenyu ichida kubviswa uye kuti njodzi dzinogona kuitika kana matambudziko anokonzerwa nekuvhiyiwa uku anogona kunge ari api.

Ko hamartoma inogona kushanduka kuita kenza here?

Izvi zvinowanzoitika. Mikana yekuti hamartoma ive negomarara yakaderera zvikuru; chiitiko chisingawanzoitiki.

Zvisinei, yeuka kuti mamwe mamiriro ezvinhu emumajini ane chekuita nehamartomas (akadai seCowden syndrome, rudzi rwePHTS) anogona kuwedzera njodzi yekenza. Muzviitiko izvi, chirwere chemajini chiripo, kwete hamartoma pachayo, ndicho chinowedzera njodzi. Kana uine chirwere chemajini chakadaro, kuongororwa kenza nguva dzose kwakakosha.

Mibvunzo ipi yandinofanira kubvunza chiremba wangu?

Kana wangoonekwa uine hamartoma, ungave nemibvunzo yakati wandei. Sununguka kubvunza chiremba wako zvinotevera:

  • Chii chakakonzera kuti hamartoma iyi ibude?
  • Zvinodiwa here kubvisa?
  • Ndezvipi zviratidzo zvandinofanira kutarisa kuti ndizive kana zvichidikanwa kurapwa?
  • Hamartoma iyi ingave chiratidzo chechirwere chakakomba here?
  • Kupihwa mazano kana kuongororwa kwemajini kwaizobatsira ini kana mhuri yangu here?

Mharidzo Yekupedzisira Yekuenda Kumba

Ndinovimba ruzivo urwu rwakupa kunzwisisa kwakajeka nezve hamartomas. Chinonyanya kukosha, yeuka kuti hamartomas haisi njodzi. Haasi kenza uye haapararire mumuviri wese.

Kazhinji, hapana mushonga unodiwa. Zvisinei, kana ukaona zviratidzo kana kana chiremba wako aine zvinokunetsa, kuvhiyiwa inzira inoshanda yekugadzirisa dambudziko racho.

Kana ukaudzwa kuti une hamartoma, usanyanya kutya. Taura nachiremba wako zvakakwana kuti usarudze matanho akakodzera kwauri. Kuchengetedza hutano hwako ndicho chinhu chakakosha chaunogona kuita kuNirogi Lanka.