Dzimwe nguva unonzwa kuneta zvisina kujairika pasina chikonzero here? Majoini ako, kunyanya mabvi ako nezvigunwe, zvinorwadza here, uye ganda rako rinoita serakachenuruka kana kuti rakaita sebhuronzi? Tinowanzo ramba zvinhu izvi se "sezvatinokura." Asi izvi zvinogona kuva zviratidzo zvechirwere umo huwandu hwesimbi mumuviri wedu hunowedzera zvine njodzi. Chirwere ichi chinonzi Hemochromatosis mune zvokurapa. Izvi ndizvo zvatiri kutaura nezvazvo nhasi.
Zvichitaurwa zviri nyore, chii chinonzi Hemochromatosis?
Hemochromatosis chirwere apo muviri wako unounganidza iron yakawandisa . Vamwe vanhu vanoidaidzawo kuti " kuwedzerwa iron ."
Kazhinji, miviri yedu inongotora huwandu hwesimbi hwatinoda kubva muchikafu chatinodya. Zvisinei, kune vanhu vane hemochromatosis, muviri unotora simbi yakawanda kupfuura yaunoda. Dambudziko nderekuti hapana nzira yekubvisa iyi simbi yakawandisa mumuviri.
Saka muviri unochengetera kupi iyi iron yakawandisa? Inochengetwa mumajoini ako, pamwe chete nenhengo dzinokosha dzakadai sechiropa chako , moyo , ganda, pituitary gland, uye pancreas . Nekufamba kwenguva, iyi iron yakaungana inotanga kukuvadza nhengo idzodzo. Kana ikasarapwa, nhengo idzi dzinogona kutomira kushanda.
Kune mhando mbiri huru dzechirwere ichi.
Mamiriro ezvinhu aya anogona kukamurwa kuita mhando mbiri.
1. Primary Hemochromatosis: Iyi ndiyo mhando inonyanya kuwanikwa. Inogarwa nhaka. Zvichitaurwa zviri nyore, kuti uwane chirwere ichi, unofanira kugara nhaka jini rakakanganisika kubva kuna amai vako nababa vako. Kana ukagara nhaka kubva kumubereki mumwe chete, hauzove nechirwere ichi, asi unogona kunge uri mutakuri wejini racho.
2. Secondary Hemochromatosis: Izvi zvinoitika nekuda kwezvimwe zvikonzero. Semuenzaniso, chirwere ichi chinogona kuitika kune munhu anoda kuwedzerwa ropa nguva nenguva nekuda kwechirwere chakadai seanemia yakanyanya.
Chii chinokonzera mamiriro ezvinhu aya?
Ngationei kuti ndezvipi zvikonzero zveizvi.
Zvikonzero zvenhaka (Primary Hemochromatosis)
Miviri yedu ine jini rinonzi `HFE`. Izvi ndizvo zvinodzora huwandu hwesimbi yatinotora kubva muchikafu chatinodya. Kuchinja-chinja kuviri mujini iri re`HFE`, iro rinonzi `C282Y` ne`H63D`, ndiko kunokonzera vazhinji vevarwere vane hemochromatosis inogarwa nhaka.
Pamusoro pezvo, kuchinja kwemajini mamwe, akadai se'HJV' ne'HAMP', kunogonawo kukonzera chirwere ichi kuvanhu vashoma (vanenge 10%-15%). Vanhu vanobatwa nemajini aya vanowanzova nezviratidzo vachiri vadiki.
Zvinokonzerwa nezvimwe zvirwere (Secondary Hemochromatosis)
Rudzi urwu runowanzo kukonzerwa nekuwedzerwa ropa nguva nenguva nekuda kwezvirwere zvakaita sekushaya ropa kwakanyanya (senge sickle cell anemia) kana kutadza kushanda zvakanaka kwemubofu. Masero matsvuku eropa anopiwa kana wapa ropa ane iron yakawanda. Sezvo muviri usina nzira yekubvisa iron iyi, anotanga kuungana.
Uyewo, kukuvara kwechiropa, semuenzaniso, nekuda kwechirwere chechiropa chine mafuta ( cirrhosis ) kana hepatitis B kana C isingaperi, zvinogona kukonzera kuti iron iungane mumuviri.
Ndiani ari panjodzi huru yekubatwa nechirwere ichi?
Kunyange zvazvo munhu wese achigona kuwana hemochromatosis, vamwe vanhu vari panjodzi huru.
Chinhu chinonyanya kukosha ndechekuti, kunyangwe uine zvinhu izvi zvine njodzi kana kuti kwete, kana uine zviratidzo, unofanira kuona chiremba.
| Chinhu chine njodzi | Tsananguro |
|---|---|
| Kuva nemajini maviri eHFE asina kunaka | Kana wakagara nhaka jini rakakanganisika kubva kuna amai vako nababa vako. |
| Nhoroondo yemhuri | Kana mumwe wevabereki vako kana vanin'ina vako vane chirwere ichi. |
| Kuva murume | Varume vane mukana wekuwana chirwere ichi kanenge kashanu kupfuura vakadzi. |
| Vakadzi vakamboenda kumwedzi | Kana kuenda kumwedzi kukamisa muviri kubvisa iron, njodzi yekuunganidzwa kwesimbi inowedzera. Njodzi iyi inoshandawo kuvakadzi vakabviswa chibereko. |
Unewo zviratidzo izvi here?
Vanhu vanosvika hafu yevanhu vane hemochromatosis havaratidzi zviratidzo. Varume vanowanzova nezviratidzo vari pakati pemakore makumi matatu nemakumi mashanu, nepo vakadzi vachiwanzova nezviratidzo mushure memakore makumi mashanu kana mushure mekuguma kuenda kumwedzi.
| Zviratidzo zvakajairika | |
|---|---|
| Kurwadziwa kwemajoini (kunyanya mumajoini nemabvi) | Kuneta uye kuneta kakawanda |
| Kuderedza uremu pasina chikonzero | Ruvara rweganda rwunoshanduka kuita bhuronzi kana kuti grey |
| Kurwadziwa kwedumbu | Kuderera kwechido chepabonde |
| Kurasikirwa nebvudzi mumuviri | Ndangariro isina kujeka, kuoma kuisa pfungwa pachinhu chimwe chete |
| Matambudziko anogona kuitika kana chirwere chikawedzera | |
| Matambudziko echiropa (semuenzaniso, cirrhosis) | Chirwere cheshuga |
| Kusarongeka kwekurova kwemoyo (Arrhythmia) | Kusashanda zvakanaka kwenhengo dzemurume muvanhurume |
Zvakakosha: Dambudziko iri rinogona kutowedzera kuipa kana ukatora mapiritsi evhitamini C kana kudya zvekudya zvakawanda zvine vhitamini C, sezvo vhitamini C inowedzera kupinza kwesimbi kubva muchikafu.
Unoona sei izvi, Chiremba?
Nekuti zviratidzo izvi zvinogona kuonekwa mune zvimwe zvirwere, dzimwe nguva zvinogona kuoma kuona. Chiremba wako achakubvunza nezvenhoroondo yezveutano hwemhuri yako uye achakuongororwawo mumuviri.
Uye zvakare, bvunzo idzi dzinogona kuitwa:
- Kuongororwa kweropa: Kuongororwa kukuru kunoitwa pano.
- Kuzara kwesimbi muropa: Izvi zvinoyera kuti iron yakawanda sei inosungwa neprotein (transferrin) inotakura iron muropa.
- Serum Ferritin: Izvi zvinoyera huwandu hwepuroteni (ferritin) inochengeta iron muropa.
Kana bvunzo idzi dzichiratidza kuti simbi yako yakawanda, chiremba wako anogonawo kuita bvunzo yemajini kuti aone kana uine jini rinokonzera hemochromatosis.
- Kuongororwa kwechiropa: Chiremba anotora kanyama kadiki kechiropa okaongorora nemaikorosikopu kuti aone kana paine kukuvara kwechiropa.
- MRI scan: Izvi zvinogona kutora mifananidzo yakajeka yenhengo dzako uye kuona kana dzine simbi.
Ndezvipi zviri kurapwa?
Kana uine chirwere chePrimary Hemochromatosis, kurapwa kwacho kuri nyore kwazvo. Kunosanganisira kubvisa ropa mumuviri wako nenguva yakatarwa. Izvi zvinonzi Phlebotomy.
Kuvhiyiwa kwePhlebotomy
Izvi zvakafanana nekupa ropa. Chiremba kana mukoti akadzidziswa anoisa tsono mutsinga iri muruoko rwako oburitsa ropa mubhegi reropa.
- Kurapwa kwekutanga: Pakutanga, uchafanirwa kuenda kuchipatara kamwe chete kana kaviri pasvondo kunotorwa ropa kusvika huwandu hwesimbi mumuviri wako hwadzokera pahwakajairika. Izvi zvinogona kutora mwedzi yakati wandei kana gore.
- Kurapa Kwekuchengetedza: Kana huwandu hwesimbi hwadzokera pahwakajairika, kuwanda kwekuisirwa ropa kunodzikira, kazhinji kusvika kaviri kusvika kana kana pagore.
Kurapa nemishonga (Chelation Therapy)
Kana uine chirwere che secondary hemochromatosis, kana kuti kana tsinga dzako dzisina kusimba zvakakwana zvekusvika pakukweva ropa, chiremba wako anogona kukupa mushonga unonzi `Chelation Therapy.` Muizvi, unopiwa mushonga unobatsira muviri wako kubvisa iron yakawandisa kuburikidza neweti yako netsvina.
Dambudziko iri rinogona kugadziriswa kumba here?
Munhu ari kurapwa ne phlebotomy kazhinji haafanire kuchinja zvakanyanya kudya kwake, sezvo kurapwa kwacho kuchidzora huwandu hwesimbi mumuviri wake. Zvisinei, unogona kuita zvinotevera kuderedza njodzi yekusangana nematambudziko:
- Dzivisa doro zvachose. Doro rinokuvadza chiropa, zvichiita kuti chive nengozi zvikuru nechirwere ichi.
- Dzivisa kudya hove mbishi kana hove dzemugungwa. Mabhakitiriya ari mune izvi anogona kukonzera hutachiona hwakakomba kuvanhu vane simbi yakawanda.
- Dzivisa kutora mishonga yekuwedzera vhitamini C. Zvisinei, hapana dambudziko pakudya michero nemiriwo ine vhitamini C.
- Dzivisa kutora mapiritsi esimbi kana mavhitamini akawanda ane iron.
- Dzivisa zviyo zvekudya zvemangwanani zvine iron.
Mharidzo Yekuenda Nayo Kumba
- Hemochromatosis chirwere chinokonzerwa nesimbi yakawandisa mumuviri. Kana ikasarapwa, inogona kukuvadza nhengo dzakadai sechiropa nemoyo.
- Usaregeredza zviratidzo zvakaita sekuneta nguva nenguva, kurwadziwa kwemajoini, uye kutsvuka kweganda. Taura nachiremba wako.
- Izvi zvinowanzo konzerwa nenhaka, asi zvinogonawo kukonzerwa nedzimwe zvirwere.
- Kurapa kukuru kubvisa ropa nguva dzose (phlebotomy), inova nzira yekurapa inoshanda zvikuru uye yakachengeteka.
- Pamwe chete nekurapwa, chirwere ichi chinogona kugadziriswa zvakanaka kuburikidza nekuchinja mararamiro, sekurega kunwa doro.











💬 Comments (0)
Hapana zvakataurwa parizvino. Isa mhinduro yako pano kekutanga.
Wedzera zvaunofunga