Tsinga huru yemwoyo yemwana wenyu yakamanikana here? Ngatidzidzei nezvekusanganiswa kweAorta neNirogi Lanka!

Tsinga huru yemwoyo yemwana wenyu yakamanikana here? Ngatidzidzei nezvekusanganiswa kweAorta neNirogi Lanka!

Physician Reviewed — Not Medical Advice

Wakambozvibvunza here kuti moyo midiki yevana vedu inoshanda zvinoshamisa sei? Dzimwe nguva, zvisinei, nekuda kwemamwe mamiriro ekuzvarwa nawo, mashandiro emwoyo anogona kusangana nezvipingamupinyi zvidiki. Chimwe chezvirwere zvemoyo zvakadaro chinogona kuitika mune vamwe vacheche chinonzi "Coarctation of the Aorta." Kunyange zvazvo zita racho ringanzwika serakaoma, ndapota musavhunduka. Ngatitaurei nezvazvo nemashoko akareruka.

Chii chinonzi Coarctation yeAorta? Muchidimbu...

Muchidimbu, kupatsanurwa kweAorta zvinoreva kuti chikamu cheaorta yemwana wako—tsinga huru inotakura ropa rine oxygen kubva pamoyo ichienda kumuviri wese—inotsvedzwa kana kudzvanywa. Uku ndiko kusakwana kwemoyo, zvichireva kuti kunowanikwa kubva pakuzvarwa.

Funga nezvazvo semugwagwa mukuru. Kana motokari dzichifamba nekumhanya kukuru, asi chikamu chemugwagwa chikamanikana kusvika pakuvakirwa mugwagwa mumwe chete, chii chinoitika? Motokari dzinowanda, uye mota dzinomanikidzwa kudzikira, handiti? Izvi zvinoitikawo mumamiriro ezvinhu aya. Zvinova zvakaoma kuti ropa riyerere zvakanaka kupfuura nzvimbo yakamanikana yeaorta.

Kazhinji, kutetepa uku (coarctation) kunoitika nguva pfupi aorta isati yatanga kupa ropa kumuviri wepazasi, senge makumbo. Nekuda kweizvi, BP yemwana wako inowedzera mumuviri wepamusoro (semaoko) asi inodonha mumuviri wepazasi (makumbo). Musiyano uyu mukuru weBP pakati pemuviri wepamusoro newepazasi chiratidzo chechirwere ichi. Kunyangwe pasina zvimwe zviratidzo zviri pachena, musiyano uyu weBP unowanzo zivisa vanachiremba nezvedambudziko rinogona kuitika.

Zvichienderana nenhamba dzemuUS, mwana mumwe chete pavana 1,700 vanoberekwa pagore anogona kunge aine Aortic Coarctation. Vamwe vacheche vanogona kunge vaine zvimwe zvirwere zvemwoyo zvekuzvarwa nazvo pamwe chete nechirwere ichi.

Ndezvipi zviratidzo zvingaratidzwa nevana vadiki?

Zviratidzo zvinoenderana nekuti aorta yakatetepa zvakadii. Kazhinji, kana kutetepa kwacho kwakanyanya, zviratidzo zvinoonekwa mukati mevhiki yekutanga kana maviri ehupenyu. Zvisinei, kana kutetepa kwacho kuri kudiki, kunogona kusaonekwa kusvika mwana akura, kana kuti vangasamboratidza zviratidzo zvachose.

Zviratidzo muVacheche

Kana mwana achangoberekwa aine chirwere ichi (CoA), unogona kuona zvinotevera:

  • Kurara nguva dzose uye kusadya zvakanaka
  • Kurova kwemoyo nekukurumidza (kurova kwemoyo nekukurumidza)
  • Kudikitira zvakanyanya
  • Kugumbuka nekuchema nguva nenguva
  • Ganda rakachenuruka kana kuti grey
  • Kutadza kufema kana kufema nekukurumidza/kwakaoma
  • Kuomerwa nekuyamwisa kana kuyamwisa mubhodhoro

Kana mwana achangoberekwa akachekwa zvakanyanya mutsinga yeropa (aorta ) uye ikasaonekwa uye ikasarapwa nekukasika, mwana anogona kupinda mumamiriro ekuvhunduka , izvo zvinogona kuisa upenyu panjodzi. Kusiyana neizvi, vamwe vacheche vane kuchekwa kudiki vangasaratidza zviratidzo zvachose.

Zviratidzo muVana neVadiki Vakuru

Muvana vakuru nevechidiki vane Aortic Coarctation, unogona kuona:

  • Musoro unowanzo rwadza
  • Kukwira kweropa
  • Kubuda ropa mumhino kakawanda
  • Kurwadziwa kwegumbo panguva yekurovedza muviri, kumhanya, kana kuita basa remuviri

Vamwe vana havana zviratidzo zvinoonekwa. Kazhinji, chirwere ichi chinotanga kuonekwa panguva yekuongororwa kweropa nguva dzose kana paine chirwere cheBP chakakwira .

Kana zviratidzo zvikaonekwa pamunhu mukuru, zvinowanzoratidza kudzikira kwetsinga yeropa (aortic recoarctation) mushure mekurapwa kare. Kashoma kuti (CoA) isaonekwe kusvika yakura.

Sei izvi zvichiitika? Ndezvipi zvinokonzera?

Kunyange hazvo chikonzero chaicho che (CoA) chisati chajeka, nyanzvi dzinotenda kuti pane chikamu chemajini . Izvi zvinoreva kuti shanduko dzemajini dzinoitika mwana ari mudumbu dzinogona kukonzera kuti aorta isaumbwe nemazvo.

Dzimwe nguva kusiyana kwemajini uku kunogona kugarwa nhaka. Tsvagiridzo inoratidza kuti kana wakambova ne (CoA), mukana wekuti mwana wako ave ne (CoA) kana chimwe chirema chemwoyo wakakwira kupfuura kune munhu asina chirwere ichi.

Uyezve, mamwe majini anowedzera njodzi. Semuenzaniso, vacheche vanozvarwa neTurner syndrome vane mukana wekuva neAortic Coarctation kwete chete asiwo nezvimwe zvirema zvekuzvarwa nazvo, zvakaita sebicuspid aortic valve.

Zvikonzero zveKuzviparadzanisa (CoA)

Kana pasina zvimwe zvirwere zvemwoyo ("isolated CoA"), chinhu chikuru ndechekuvharika kwetsinga diki inonzi ductus arteriosus panguva yekukura kwemwana ari mudumbu. Ductus arteriosus itsinga diki inobatanidza fetal aorta netsinga yemapapu. Sezvo mapapu emwana asingashande ari mudumbu, tsinga iyi inokosha pakuparadzira ropa rine oxygen.

Kana mwana angoberekwa uye atanga kufema, ductus arteriosus haichadiwi uye inowanzovhara yega mukati memazuva mashoma. Zvisinei, painovhara, mamwe matishu anobva mutsinga iyi anogona kubatana netsinga yeaortic. Kana izvi zvikaitika, ductus arteriosus inogona kudhonza aorta painovhara, zvichiita kuti itetepe (coarctation).

Ndezvipi zvinetso zvinogona kuitika kubva muchirwere ichi?

Kana kuvharika kweAorta kukasarapwa kwenguva yakareba, matambudziko anotevera anogona kuitika:

  • Kurwara neBP kwenguva refu mumuviri wese.
  • Kukora kwetsandanyama yemwoyo (hypertrophy ye ventricular yekuruboshwe).
  • Kuungana kweplaque mutsinga dzemwoyo nguva isati yakwana (chirwere chetsinga dzemoyo).
  • Kuumbwa kwe aneurysm (kubhururuka) kana kutsemuka (kubvaruka) mu aorta.
  • Kuumbwa kweaneurysm yeuropi.
  • Kutadza kushanda kwemoyo nekuda kwekutadza kupomba ropa zvinobudirira.

Cherechedza: Kana muchifunga kuti pane zviratidzo zvekukurumidzira, ndapota taurai nevashandi vekukurumidzira (911) nekukasika kana kuti endererai kudhipatimendi rekukurumidzira riri pedyo.

Dambudziko iri, rinonzi Coarctation of the Aorta (CoA), rinova nengozi zvikuru kana rikaramba risina kuongororwa uye risingarapwe. Saka, zvakakosha kuti uzvizive nekukurumidza sezvinobvira—zvikuru panguva yehucheche—kuti uve nechokwadi chekuti mwana wako anowana rubatsiro rwechiremba runodiwa uye nguva dzose anotariswa.

Vanachiremba vanoongorora sei izvi? (Kuongororwa)

Kazhinji, vanachiremba vemwoyo vevana ndivo nyanzvi dzinoona Coarctation yeAorta muvacheche kana vana vadiki. Kukurumidza kuongororwa kwechirwere kunoenderana nekuoma kwezviratidzo.

Vacheche vane zviratidzo zvakakomba vanowanzoonekwa mukati memazuva ekuzvarwa. Zvisinei, avo vane zviratidzo zvishoma kana kuti vasina zviratidzo zvinooneka vanogona kusaonekwa kusvika pava padiki apo BP inokwira. Kuonekwa kwechirwere ichi muvanhu vakuru hakuwanzoonekwa.

Muzviitiko zvakawanda, CoA inoonekwa panguva yekuongororwa kwemuviri nguva dzose kana chiremba akaona zviratidzo zvidiki , zvakaita se:

  • Kukwira kweropa mumaoko/pamuviri wepamusoro zvichienzaniswa nekuderera kweropa zvakanyanya mumakumbo/muviri wepazasi.
  • Musiyano unooneka pakati pesimba rekurova kwemoyo pakati pemutsipa nepahudyu.
  • Kugunun'una kwemwoyo kwakaonekwa chiremba paanoteerera chipfuva chemwana wako achishandisa stethoscope.

Vamwe vacheche vanoonekwa kunyange zviratidzo zvisati zvaonekwa kuburikidza nekuyedzwa kwepulse oximetry, iyo inoongorora huwandu hweokisijeni muropa. Kana huwandu hweokisijeni hwakaderera, zvinogona kuratidza chirwere chemwoyo chakakomba chekuzvarwa nacho, zvichiita kuti kuongororwa kwakawedzerwa kuNirogi Lanka kana kune imwe nzvimbo yechipatara yakasarudzika.

Kuti vasimbise kuongororwa kweCoA, vanachiremba vanowanzo shandisa echocardiogram (ultrasound yemoyo). Vanogonawo kuraira CT scan kana MRI kuti vawane ruzivo rwakadzama rwe aorta yemwana wenyu.

Pane zvimwe zvirwere zvemwoyo zvine chekuita neCoarctation yeAorta here?

Ehe, vana vane CoA vanogona kunge vaine zvimwe zvirwere zvemwoyo. Semuenzaniso, 45% kusvika 75% yevanhu vane CoA vanewo bicuspid aortic valve , uko vharuvhu inodzora kuyerera kweropa kubva pamwoyo kuenda kuaorta ine maflaps maviri panzvimbo pematatu akajairwa.

Mamwe mamiriro ezvinhu anogona kuitika pamwe chete neCoA anosanganisira:

  • Zvirwere zvemwoyo zvakaita seatrial septal defect kana ventricular septal defect (maburi mumoyo).
  • Patent ductus arteriosus (tsinga yeropa inofanira kunge yakavharwa mushure mekusununguka inoramba yakavhurika).
  • Aortic arch hypoplasia kana hypoplastic left heart syndrome (uko zvikamu zvemoyo kana aorta zvisina kukura zvakanaka).
  • Kuoma kwetsinga yemoyo (aortic kana mitral valve stenosis)

Vanachiremba vedu vemwoyo vachaongorora mamiriro emwoyo wemwana wenyu kuti vagadzire hurongwa hwekurapa hwakagadzirirwa iye. Kurapa zvikanganiso zvakawanda zvemwoyo kunoda nzira yakaoma kupfuura kurapa CoA yakazvimiririra.

Ndezvipi zvingasarudzwa pakurapa?

Kurapwa kunoenderana nezera remwana wako, kuoma kwekudzikira kwetsinga yeropa, uye kuvapo kwezvimwe zvirwere zvemwoyo. Kune vacheche nevana vadiki, kuvhiyiwa ndiko kunonyanya kushanda.Muvana vakura, kana kuti apo kutetepa kwacho kusina kunyanya kuoma, nzira yekurapa inonzi cardiac catheterization inogona kunge yakakodzera. Izvi zvinoshandiswawo pakutetepa (recoarctation) kana kuvanhu vakuru.

Kuvhiya

Nzira huru dzekuvhiya dzekugadzirisa CoA dzinosanganisira:

  • Kuvhiyiwa kwekubvisa tsinga nekubvisa tsinga kubva pamucheto kusvika pamucheto: Chiremba anobvisa chikamu chakamanikana obva asona magumo etsinga yeropa ane hutano pamwe chete.
  • Kubviswa kwemasero nekubvisa tsinga dzeropa dzakareba: Kana tsinga dzeropa dzakatetepawo, chiremba anobvisa tsinga dzakatetepa obatanidza tsinga dzinodzika netsinga refu dzeropa. Iyi ndiyo nzira inofarirwa kana paine tsinga dzeropa dzakachinjika.

Vana vacheche vane zviratidzo zvakakomba vanogona kugadziriswa vasati vavhiyiwa nemishonga, yakadai seProstaglandin (PGE-1) kuchengetedza ductus arteriosus yakavhurika, kana mimwe mishonga inotsigira kushanda kwemoyo.

Kuisa katheta mumoyo

Kana mwana wako aine chirwere chekuchembera zvishoma kana kuti akambotangazve chirwere chacho, zvinotevera zvinogona kukurudzirwa:

  • Kuvhiyiwa kwebharumu: Bharumu diki rinofuridzirwa mukati meaorta kuti nzvimbo yakamanikana ikure.
  • Kuvhiyiwa kwebharumu nekuisa stent: Chubhu diki, inowedzerwa (stent) inoiswa kuti chikamu chakamanikana cheaorta chirambe chakavhurika.

Unofanira kutsvaga rubatsiro rwekukurumidzira rini? (Kutevera & Kukurumidzira)

Chikwata chevanachiremba chemwana wenyu chichakupai purogiramu chaiyo yekusangana nemwana wenyu. Muhupenyu hwemwana wenyu, vachada kuongororwa nguva dzose vachitungamirirwa nachiremba wezvirwere zvemwoyo. Nyanzvi iyi inotarisira zvinotevera:

  • Kugara uchitarisa BP yemwana wako.
  • Kuongororwa kwemifananidzo nguva nenguva kuti vaone mashandiro emwoyo uye kuona kana paine zviratidzo zvematambudziko.
  • Mazano ekusarudza zvekudya zvine hutano pamoyo uye kurovedza muviri kwakakodzera.
  • Kunyora mishonga uye kugadzirisa mwero wemishonga sezvinodiwa.

Munhu ane chirwere ichi anotarisirwa kurarama hupenyu hwakaita sei?

Nekuda kwenzira dzemazuva ano dzekuongorora chirwere uye kurapa kwepamusoro, vanhu vane Coarctation of the Aorta (CoA) vanogona kurarama hupenyu hwakazara, hune zvibereko kusvika vava nemakore ekuma60 zvichikwira. Kare, makore ekurarama aive akaderera zvakanyanya, saka iyi ikufambira mberi kwekurapa kunokurudzira zvikuru.

Kana mwana wako akaonekwa aine chirwere cheCoarctation of the Aorta, zvinonzwisisika kuti sei izvi zvakaitika. Kazhinji hatigoni kuziva chikonzero chaicho chezvirwere zvemwoyo zvatakazvarwa nazvo. Zvisinei, tinoziva kuti kuongororwa nekukurumidza uye kupindira panguva yakakodzera kunogona kuderedza zvakanyanya kukanganisa hupenyu hwemwana wako kwenguva refu.

Chikwata chenyu chekurapa kuNirogi Lanka chiripo kuti chikutsigirei nhanho imwe neimwe yerwendo rwenyu. Vakagadzirira kupindura mibvunzo yenyu uye kukubatsirai kunzwisisa zvinorehwa nechirwere ichi kumwana wenyu. Kubatana nevamwe vabereki vane vana vari kurarama nezvirwere zvemwoyo zvakafanana kunogonawo kukupai simba repfungwa.

Zvinhu Zvikuru Zvaunofanira Kuziva

Tinovimba kuti manzwisisa zvakajeka nezve Coarctation yeAorta. Heano zvinhu zvakakosha zvekurangarira:

  • Idambudziko remwoyo rinoberekwa naro —kutetepa kweaorta, tsinga huru inotakura ropa kubva pamwoyo kuenda kumuviri wose.
  • Zviratidzo zvinogona kuonekwa muhucheche kana kuti zvichazobuda gare gare. Kana ukaona kuneta kwakanyanya, kufema zvakaoma, kana kusadya zvakanaka mumwana wako, tsvaga rubatsiro rwekukurumidzira nekukasika.
  • Kuongororwa kwechirwere nekukasika uye kupindira kunopa mwana wako mukana wakanakisisa wekurarama hupenyu hwakanaka uye hwakanaka.
  • Dambudziko iri rinogona kurapwa zvinobudirira kuburikidza nekuvhiyiwa nedzimwe nzira dzemazuva ano dzekurapa.
  • Kutarisirwa nachiremba kwehupenyu hwese kwakakosha, kunyangwe mushure mekurapwa kwakabudirira.

Ndapota musazvidya mwoyo; mushonga wemazuva ano wafambira mberi zvikuru. Chikwata chedu chezvekurapa chine hunyanzvi chiripo kuti chipe mwana wenyu rubatsiro rwepamusoro-soro. Matanho akakosha kugara muchiziva zviri kuitika, kunyatsotarisa hutano hwemwana wenyu, uye kutevedzera zano rachiremba wenyu.

👩🏽‍⚕️ Mibvunzo Inowanzo bvunzwa (Mibvunzo Inowanzo bvunzwa)

💬 Chii chinonzi Coarctation yeAorta?

Uku ndiko kurwara kwemoyo kwakaberekwa nako kubva pakuzvarwa. Kunoitika kana chikamu cheaorta (tsinga huru yemuviri inotakura ropa rine oxygen kubva pamoyo) chakatetepa zvisingawanzoitiki, zvichitadzisa kufamba kweropa kwakajairika.

💬 Chii chinonyanya kukonzera chirwere ichi mumuviri?

Nekuti kuyerera kweropa kunomanikidzwa panzvimbo yakamanikana, muviri wepamusoro unowanzo sangana neBP yakakwira, nepo muviri wepasi uchiwana ropa rakaderera. Izvi zvinogona dzimwe nguva kukonzera ganda rebhuruu kana kusawirirana kukuru kweBP pakati pemakumbo nemakumbo.

💬 Chirwere ichi chinorapwa sei?

Kurapa kunowanzoda kuvhiyiwa kugadzirisa tsinga yakamanikana, kana dzimwe nguva nzira inozivikanwa se balloon angioplasty yekuwedzera nzvimbo yakamanikana.


Mashoko Akakosha: Kubatana kweAorta, Chirwere cheMwoyo, Vana, Zvirwere zveMwoyo zveVakaberekwa, Kutetepa kweAortic, Hutano hweVana, Kumanikidzwa kweRopa