Kutheni kukho ukwehla ngequbuliso komthamo wegazi? Masithethe nge-Aplastic Crisis

Ngaba wakha wayibona okanye weva ngemeko apho abanye abantu, ingakumbi abantwana abancinci, ngequbuliso belahlekelwa ligazi kakhulu, bazive bediniwe kakhulu, kwaye ngamanye amaxesha banokubeka ubomi esichengeni? Le yenye yeemeko ezinzima esiza kuthetha ngazo namhlanje, ebizwa ngokuba yi -aplastic crisis . Nangona eli gama lisenokuvakala lisoyikisa kancinci, ukuba siyazi, singamelana nale meko kakuhle.

Yintoni kanye kanye le ngxaki yokungakhululeki kweplastiki?

Ngamafutshane, ingxaki ye-aplastic iyenzeka xa umongo wethambo emzimbeni wethu uyeka ukuvelisa iiseli ezibomvu zegazi ezintsha ngequbuliso. Ngoku usenokuba ucinga, "Kuza kwenzeka ntoni ke ukuba ukuveliswa kweeseli ezibomvu zegazi kuyeka?" Ezi seli zibomvu zegazi zezona zithwala ioksijini emizimbeni yethu yonke. Ngoko ke xa ziyeka ukuvelisa, inani leeseli ezibomvu zegazi emzimbeni liyehla kakhulu, nto leyo ebangela i-anemia enzima . Le yimeko enokuba yingozi ebomini.

Ingxaki ye-Aplastic idla ngokuchaphazela abantu abaneengxaki zegazi ezifana ne-sickle cell anemia . Eyona nto ibangela oku kusulelo oluqhelekileyo lwentsholongwane olubizwa ngokuba yiParvovirus B19 . Musa ukumangaliswa, nangona le ntsholongwane ichaphazela abantu abaninzi, ingxaki ye-aplastic yenzeka kuphela xa abantu abaneengxaki zegazi besosulelwa yile ntsholongwane. Le meko ixhaphake kakhulu kubantwana abancinci, ingakumbi iintsana. Kodwa kukho iindaba ezimnandi, kukho unyango lwale nto olufana notofelo-gazi kunye ne -intravenous immunoglobulin (IVIG) .

Ingaba esi sisifo esichaphazela wonke umntu?

Hayi, akunjalo konke konke. Njengoko benditshilo ngaphambili, iParvovirus B19 yintsholongwane eqhelekileyo kakhulu. Nangona kunjalo, ayinguye wonke umntu osuleleke yile ntsholongwane ofumana ingxaki ye-aplastic. Oku kwenzeka kuphela xa umntu onesifo esithile segazi esulelwe yiParvovirus B19.

Iintsana ezisandul’ ukuzalwa, iintsana, kunye nabantwana abane- sickle cell anemia basengozini enkulu. Abantu abanezinye izifo ezibangela ukutshatyalaliswa kweeseli ezibomvu zegazi kunye ne-hemolytic anemia nabo basengozini enkulu yokuba nengxaki ye-aplastic ukuba bosulelwa yi-parvovirus B19. Ezinye zezi meko ziquka:

• I-Spherocytosis yelifa
• Isifo seHemoglobin C
• I-Thalassemia
• Isifo sokungabikho kwe-G6PD
• Ukunqongophala kwe-Pyruvate Kinase
• I-Autoimmune Hemolytic Anemia
• I-Paroxysmal Nocturnal Hemoglobinuria
• I-Elliptocytosis yelifa

Ukuba wena okanye umntwana wakho ninesifo segazi esinjalo, kubaluleke kakhulu ukuba nisinyamekele ngakumbi.

Zithini iimpawu zengxaki ye-aplastic?

Abantu abadala, kunye nabantwana neentsana, abanengxaki yokungapheleli kakuhle emzimbeni, badla ngokuba neempawu ezinxulumene ne-anemia enzima. Iintsana nabantwana abancinci banokuba neengxolo okanye bacaphuke kakhulu kunesiqhelo. Umzekelo, ukuba umntwana wakho ukhala kakhulu, akathandi nto, okanye ubonakala enomsindo ngalo lonke ixesha, oku kungaba luphawu lwento efana nale.

Nazi ezinye zeempawu eziphambili:

• Ukudinwa: Ukuziva udiniwe kakhulu, ungakwazi ukwenza nantoni na.
• Umkhuhlane: Ubushushu bomzimba bunokufikelela kuma-38 degrees Celsius (101 degrees Fahrenheit) okanye ngaphezulu.
• Ukudinwa: Kuvakala ngathi intloko yakho iyajikeleza, kwaye amehlo akho anokuba luhlaza okwesibhakabhaka.
• Ukuphefumla kancinci/ukuphelelwa ngamandla: Ukuphefumla kancinci nokuba uhamba kancinci, uzive udiniwe kakhulu xa unyuka izinyuko.
• Ukubetha kwentliziyo okungaqhelekanga okanye okukhawulezayo: Ukubetha kwentliziyo kusenokuba ngokukhawuleza kunesiqhelo, okanye kusenokuba ngokungangqalanga kwaye kungabetheki kwicala elinye.
• Umbala ongwevu: Ulusu, imilebe, iintsini, okanye iinzipho ziyajika zibe mhlophe kunesiqhelo. Lo ngumbala obonakala xa igazi lingekho.

Ukuba ubona enye okanye ngaphezulu kwezi mpawu, ingakumbi ukuba wena okanye umntwana wakho unesifo segazi, kubaluleke kakhulu ukufuna ingcebiso kagqirha ngokukhawuleza .

Kutheni le nto kukho le ngxaki yokungakhululeki kweplastiki? Yintoni unobangela?

Igama elithi "aplastic" lithetha ukuba into ethile emzimbeni wakho iyekile ukusebenza. Yiloo nto eyenzekayo kule ngxaki ye-aplastic. Umongo wakho wethambo awunakuvelisa iiseli ezibomvu zegazi eziphilileyo. Isizathu saloo nto yiParvovirus B19 endiyikhankanyileyo ngaphambili. Le ntsholongwane ijolise ngqo kwiiseli ezibomvu zegazi ezingakavuthwa. Iyazilimaza.

Imizimba yethu ifumana izinto ezifana neeseli ezibomvu zegazi, ezinye iiseli ezimhlophe zegazi, kunye neplasma evela kumongo wethambo. Ngoko ke xa ukuveliswa okuqhubekayo kweeseli ezibomvu zegazi kuyeka, uba ne -anemia enzima . Khawuthelekelele, oku kwenzekayo xa umzi-mveliso wegazi wemizimba yethu uyeka ukusebenza ngequbuliso.

Ziziphi iingxaki ezinokubakho ngenxa yale meko?

Ingxaki ye-Aplastic ingakhokelela kwiingxaki ezahlukeneyo, ingakumbi kubantu abane -sickle cell anemia . Ezi nazo zinzima kakhulu.

• Ingxaki ende yeVaso-occlusive (VOC):I-VOC yintlungu ebuhlungu ngequbuliso eyenzeka kubantu abane-sickle cell anemia. Le ntlungu inokuhlala ixesha elide ngenxa yengxaki ye-aplastic.
• I-Myocarditis: Oku kukudumba kwemisipha yentliziyo, okufana nokudumba.
• Ukususwa kwe-splenetic: Iiseli ezibomvu zegazi ezingaqhelekanga zibanjwa kwi-spleen, nto leyo ebangela ukuba i-spleen ikhule.
• I-Glomerulonephritis: Esi sisifo sezintso, ukuba asinyangwa kakuhle, sinokukhokelela ekungasebenzini kwezintso.

Kungoko ke sithi kubaluleke kakhulu ukuba uqaphele le meko.

Oogqirha bayibona njani le nto?

Xa wena okanye umntwana wakho ebonakalisa ezi mpawu, xa ubona ugqirha, uza kuqala akubuze ngeempawu zakho. Emva koko uza kwenza uvavanyo lomzimba. Ukongeza, kunokwenziwa iimvavanyo ezininzi ukuqinisekisa imeko:

• Ubalo lweGazi olupheleleyo (CBC): Oku kujonga inani leeseli ezibomvu zegazi, iiseli ezimhlophe zegazi, kunye neeplatelets emzimbeni. Kwingxaki ye-aplastic, inani leeseli ezibomvu zegazi liphantsi kakhulu.
• Inani lee-reticulocyte: Ii-reticulocytes ziiseli ezibomvu zegazi ezingavuthwanga. Olu vavanyo lulinganisa inani leeseli ezibomvu zegazi ezintsha eziveliswa yi-bone marrow. Kwi-aplastic crisis, eli nani liphantsi kakhulu.
• Uvavanyo lweParvovirus B19: Olu vavanyo lwenzelwe ukuqinisekisa ukuba ukhe wosulelwa yile ntsholongwane.

Emva kwezi mvavanyo, ugqirha unokuqinisekisa ukuba le yingxaki yokungaqini kakuhle okanye yinto eyahlukileyo.

Zithini iindlela zonyango zoku?

Unyango oluphambili lwengxaki ye-aplastic kukufakelwa igazi . Oku kuthetha ukunika igazi elivela ngaphandle. Oku kunokubuyisela ngokukhawuleza inani eliphantsi leeseli ezibomvu zegazi emzimbeni. Ukongeza, unyango olubizwa ngokuba yi -Intravenous Immunoglobulin (IVIG) luyanikwa. Olu nyango lunikezelwa emzimbeni ngemithambo yegazi (IV).

Uninzi lwezigulana luyaphola kwiintsuku ezili-10 ukuya kwezili-14 emva kokuqala unyango. Enye into entle kukuba xa umntu esulelekile yi-parvovirus B19, ulwa nentsholongwane ubomi bakhe bonke. Oku kuthetha ukuba umngcipheko wokuba nesifo se-aplastic esibangelwa yintsholongwane uyancipha kakhulu.

Ngaba ikho indlela yokuthintela ingxaki ye-aplastic?

Kunzima ukutsho. Kuba, ingxaki ye-aplastic yenzeka xa umntu onesifo segazi esosulelwa yi- parvovirus B19 . I-Parvovirus B19 yintsholongwane exhaphakileyo, kwaye akukho gonyo lokuyilwa okwangoku.

Kodwa, kuwe nakumntwana wakhoUkuba unesifo segazi esifana ne-sickle cell anemia, kubalulekile ukubuza ugqirha wakho ukuba ungenza ntoni ukunciphisa umngcipheko wokosulelwa yi-parvovirus B19. Umzekelo, izinto ezilula ezifana nokuhlala kude neendawo ezinabantu abaninzi kunye nokuhlamba izandla zakho rhoqo kunokubonelela ngokhuseleko oluthile.

Kuza kwenzeka ntoni emva kwale meko? (Ingqikelelo)

Ukuxela kwangaphambili sisiphumo esilindelekileyo kwimeko yakho. Abantu abane-aplastic crisis badla ngokuchacha kwiintsuku ezili-10 ukuya kwezili-14 emva kokuqala unyango. Nangona kunjalo, abanye abantu banokuba neengxaki ze-aplastic crisis eziphindaphindayo. Ke ngoko, kubalulekile ukunikel’ ingqalelo kwiimpawu kwaye ulandele imiyalelo kagqirha wakho.

Ndingazinyamekela njani? / Ndingazinyamekela njani umntwana wam?

Ingxaki ye-Aplastic yenye nje yeengxaki ezininzi ezinokubakho kwizifo zegazi ezifana ne -sickle cell anemia . Usenokungakwazi ukuthintela i-parvovirus B19, kodwa kukho izinto onokuzenza ukuze ugcine impilo yakho iyonke:

• Fumana uhlolo rhoqo: Ngokuhlala unxibelelana rhoqo nogqirha wakho oyintloko, unokuchonga iingxaki ezinkulu zempilo ngaphambi kokuba zenzeke.
• Nciphisa umngcipheko wakho wokosuleleka: Thetha nogqirha wakho malunga neendlela zokuzikhusela kwizifo eziqhelekileyo ezifana nomkhuhlane kunye nomkhuhlane oqhelekileyo.
• Yitya ukutya okunempilo: Yitya ukutya okunesondlo kwaye usele malunga neeglasi ezisi-8-10 zamanzi ngosuku.
• Ukuzilolonga: Ukuzilolonga rhoqo kunokuphucula indlela oziva ngayo kunye nempilo yakho. Kodwa, thatha kancinci, phumla xa uziva udiniwe, kwaye ukhumbule ukusela amanzi amaninzi.

Ezi zinto zinceda ekugcineni amajoni omzimba wakho eqinile kwaye zikuncede uhlale usempilweni ngokubanzi.

Ndifanele ndimbone nini ugqirha?

Ingxaki ye-Aplastic yingxamiseko yezonyango.

Ukuba wena okanye umntwana wakho unengxaki yegazi efana ne -sickle cell anemia , kwaye ufumana utshintsho olukhawulezileyo kwimpilo yakho, njengokuziva ubuthathaka okanye udiniwe kakhulu , kufuneka ubone ugqirha wakho ngoko nangoko, ngaphandle kokulibazisa. Okukhona uqala unyango ngokukhawuleza, kokukhona kungcono.

Ndingayibuza yiphi imibuzo ugqirha?

Ukuba wena okanye umntwana wakho unengxaki yokungakhululeki, ungabuza ugqirha wakho imibuzo efana nale:

• Ndiza kuphola nini mna/umntwana wam?
• Ngawaphi amathuba okuba mna/umntwana wam sibe nengxaki efana nale kwakhona?
• Zeziphi ezinye izinto ekufuneka ndizilumkele ngakumbi xa ndiphila nale meko?

Kubaluleke kakhulu ukubuza imibuzo efana nale nokususa amathandabuzo akho.

Ngaba ingxaki ye-aplastic kunye ne-aplastic anemia ziyafana?

Ewe, nangona zombini ezi meko zinxulunyaniswa nokwehla kwenani leeseli ezibomvu zegazi, kukho umahluko phakathi kwezi zimbini.

Ingxaki ye-Aplastic kukwehla ngequbuliso kwenani leeseli ezibomvu zegazi.

I-Aplastic anemia yimeko ekhula kancinci kancinci ngokuhamba kwexesha. Kule meko, kungekuphela nje iiseli ezibomvu zegazi kodwa nezinye iintlobo zeeseli zegazi (iiseli ezimhlophe zegazi, iiplatelets) zinokuncipha.

Ngamafutshane, i-Aplastic Crisis yingxaki yexeshana, ebukhali. I-Aplastic Anemia yingxaki yexesha elide, enxulumene nomongo wethambo.

Okokugqibela, umyalezo oya ekhaya

Kulungile, ndiyathemba ukuba ngoku uyiqonda ngcono into ebesithetha ngayo namhlanje, i-Aplastic Crisis. Le yingxaki enkulu enokuchaphazela abantu abanezifo zegazi ezifana neSickle Cell Anemia . Okwenzekayo kukuba umongo wakho okanye womntwana wakho ngequbuliso uyeke ukuvelisa iiseli ezibomvu zegazi, nto leyo ebangela i-anemia enzima enokuba yingozi ebomini.

Iingxaki ze-Aplastic zinokuba ngamava oyikisayo kuba iimpawu zinokuvela ngequbuliso kwaye zibe nzima. Ngethamsanqa, oogqirha banokuyinyanga ngokutofelwa igazi namayeza.

Ukuba wena okanye umntwana wakho unesifo segazi esibeka wena okanye umntwana wakho emngciphekweni omkhulu wokuba nengxaki ye-aplastic, buza ugqirha wakho ukuba zeziphi iimpawu ezinokubonisa ingxaki. Usenokungakwazi ukuyithintela ingxaki ye-aplastic, kodwa uya kwazi ukuba wenze ntoni ukuba iyenzeka. Oko kukuqonda yeyona nto ibalulekileyo.

Ingxaki ye- Aplastic, iiseli ezibomvu zegazi, i-Bone Marrow, i-Anemia, i-Parvovirus B19, i-Sickle Cell Anemia