Ngaba wakha wacinga ngendlela intliziyo yethu emangalisayo ngayo? Kodwa ngamanye amaxesha, kwanale ntliziyo inokukhula izifo ngeendlela ezingalindelekanga. Namhlanje siza kuthetha ngesimo somhlaza esingaqhelekanga, kodwa esibi kakhulu. Ukuva oku kunokukwenza uzive usoyika kancinci, kodwa kubaluleke kakhulu ukukwazi oku.
Yintoni le kuthiwa yi-cardiac angiosarcoma?
Ngamafutshane, i-cardiac angiosarcoma sisimila esinobungozi esikhula entliziyweni yakho. Siqala kwimibhobho yegazi entliziyweni yakho. Ukusuka apho, sisasazeka siye kwimisipha yentliziyo.
Amaxesha amaninzi, malunga ne-80% yamatyala, eli thumba lingaqhelekanga likhula kwigumbi eliphezulu lasekunene lentliziyo, elibizwa ngokuba yi-right atrium . Ngamanye amaxesha linokuvela kwigumbi elisezantsi lasekunene, elibizwa ngokuba yi-right ventricle , okanye kwisingxobo esikhuselayo esijikeleze intliziyo, esibizwa ngokuba yi-pericardium . Amaxesha amaninzi, linokuvela kwicala lasekhohlo lentliziyo.
Lo ngumhlaza ohlaselayo kakhulu, osasazeka ngokukhawuleza. Ungawuvala okanye ucinezele iindawo ezibalulekileyo ezijikeleze intliziyo, njengemithambo yegazi kunye neevalvu. Ngenxa yendlela olu hlobo lomhlaza olukhula ngayo, ngamanye amaxesha kunokuba nzima ukuwususa ngokupheleleyo ngotyando.
Ixhaphake kangakanani le sifo?
Enyanisweni, i-cardiac angiosarcoma sisifo esingaqhelekanga kakhulu. Ngokweengxelo zokuhlolwa kwesidumbu, zingaphantsi kwe-0.03% iimeko ze-cardiac neoplasms zokuqala eziye zaxelwa. Ngoko khawucinge, olu hlobo lwe-angiosarcoma lunqabile nangakumbi.
Kodwa, ngokumangalisayo, kwiithumba ezinobungozi ezinokuthi zakheke entliziyweni yomntu omdala, olu lolona hlobo luxhaphakileyo .
Esi sifo sidla ngokufunyanwa kubantu abangaphantsi kweminyaka engama-65 ubudala. Sixhaphake kakhulu kubantu abaphakathi kweminyaka engama-20 ukuya kwengama-40 ubudala. Kuthiwa amadoda anamathuba amabini ukuya kwamathathu okufumana lo mhlaza kunabasetyhini.
Zithini iimpawu zoku?
Iimpawu ze-cardiac angiosarcoma zinokwahluka ngokuxhomekeke kwindawo apho i-tumor ikhoyo. Abanye abantu basenokungabi nazo naziphi na iimpawu ezinkulu ekuqaleni. Nangona kunjalo, kukho ezinye iimpawu eziqhelekileyo ezinokubonakala:
- Ubunzima bokuphefumla (oogqirha bakwabiza oku ngokuba yi-"dyspnea"). Kungavakala ngathi uphefumla kancinci ngokunyuka izinyuko.
- Intlungu yesifuba . Ivakala ngathi iyacinezelwa, ngathi iyacinezelwa.
- Ukudinwa nokudinwa . Ukuziva udiniwe ngalo lonke ixesha ngaphandle kwesizathu.
- Ukulahlekelwa yingqondo ngequbuliso (i-syncope).
- Ukuziva ngathi intliziyo yakho ibetha ngokungacwangciswanga nangokukhawuleza (sikubiza oku ngokuthi "ukubetha kwentliziyo").
Khawucinge nje, kukho umntu oselula ogama linguNalini. Kangangexesha elithile ngoku, ebeziva ediniwe kwaye esifubeni sakhe sixinene kancinci. Wayecinga ukuba mhlawumbi kungenxa yokusebenza kakhulu. Kodwa emva kweentsuku ezimbalwa, waya kugqirha xa wayekufumanisa kunzima ukuphefumla. Mhlawumbi ezi ziimpawu zokuqala zesifo esifana nesi.
Ukuba umhlaza ngandlela thile usasazeke ngaphaya kwentliziyo uye kwezinye iindawo zomzimba, ezinye iimpawu zinokuvela, ezinje nge -anemia , okanye ukwehla kobunzima ngendlela engachazekiyo .
Kutheni kusenzeka into efana nale? Zithini izizathu?
Akukho sizathu sicacileyo nesicacileyo sokuphuhliswa kwe-cardiac angiosarcoma, kodwa oogqirha bakholelwa ukuba izinto ezithile zinokudlala indima.
- Kukholelwa ukuba abantu abaneenguqu kwiijini zabo , njengejini yePOT1, banamathuba amaninzi okufumana lo mhlaza.
- Enye into enokwenzeka kukuba abantu abafumene unyango lwe-radiation kwindawo yesifuba njengonyango lomnye umhlaza besebancinci banokuba semngciphekweni omkhulu wokufumana esi sifo kamva ebomini.
Zithini izinto ezibangela umngcipheko?
Kukho nezinye izinto ezininzi ezinokubangela umngcipheko onokuchaphazela uphuhliso lwesi sifo:
- Ekubeni ndifumene unyango lwe-radiation njengonyango lomnye umhlaza ngaphambili.
- Ukuchanabeka kwiikhemikhali ezithile ezinokubangela umhlaza.
- Kwabo banemeko ebizwa ngokuba yi-lymphedema, ekukudumba kwenkqubo ye-lymphatic .
Ziziphi iingxaki ezinokubakho zesi sifo?
Ngenxa yokuba i-cardiac angiosarcoma yimeko enzima, inokukhokelela kwiingxaki ezahlukeneyo.
- Ukusilela kwentliziyo : Ukungakwazi kwentliziyo ukupompa igazi ngokufanelekileyo.
- Ukuvaleka kwe-Vena cava : Ukuvaleka komthambo oyintloko othwala igazi ukusuka emzimbeni ongaphezulu ukuya entliziyweni.
- Ukuphazamiseka kwesantya sentliziyo (arrhythmia) : Utshintsho olungaqhelekanga kwintliziyo.
- Ukuphuma kwegazi entliziyweni : Ulwelo olufana nolwelo oluzalisa ingxowa ejikeleze intliziyo.
- I-Cardiac tamponade : Ukuqokelelana kolwelo okukhankanyiweyo kubeka uxinzelelo entliziyweni.
- Ukubuyela kwevalvu yentliziyo: Igazi livuza umva ngeevalvu zentliziyo ngaphandle kokuvala kakuhle.
- Uxinzelelo oluthintela ukuhamba kwegazi: Imeko embi kakhulu ebangelwa kukuphazamiseka kokuhamba kwegazi.
Ukuva konke oku kusenokukukhathaza kancinci, kodwa kubalulekile ukuzazi ezi zinto.
Sifunyaniswa njani esi sifo?
Ugqirha uza kwenza uvavanyo oluninzi ukuqinisekisa ukuba unaso na esi sifo okanye awunaso.
- I-echocardiogram yeTransthoracic `(i-echocardiogram yetransthoracic)`: Oku kufana nokuhlolwa kwentliziyo nge-ultrasound. Luvavanyo olungenabuhlungu olwenziwa kumphezulu wesifuba.
- I-Transesophageal echocardiogram : Oku kuquka ukufaka umbhobho omncinci kwi-esophagus ukuze ubone intliziyo ngokucacileyo.
- I-CT scan (i-computed tomography - i-CT scan) : Oku kunokuvelisa imifanekiso eneenkcukacha zentliziyo kunye neendawo ezingqongileyo.
- I-MRI yentliziyo (i-magnetic resonance imaging) : Isebenzisa intsimi yemagnethi kunye namaza erediyo ukuvelisa imifanekiso eneenkcukacha zentliziyo.
- Iskeni se-Positron emission tomography (PET) : Oku kunceda ekuchongeni iiseli ezisebenzayo, ezifana neeseli zomhlaza.
- Ukufakwa kwe-catheter kwintliziyo : Uvavanyo apho ityhubhu encinci idluliselwa entliziyweni ngemithambo yegazi ukuze kulinganiswe uxinzelelo kwaye kuthathwe iisampuli.
- I-biopsy yentliziyo : Kuthathwa iqhekeza elincinci lesicubu entliziyweni lize lihlolwe nge-microscope ukuqinisekisa umhlaza.
Iphathwa njani?
Unyango lwesi sifo lunzima kancinci. Iindlela eziphambili zonyango zezi:
- Utyando : Ukuba kunokwenzeka, ukususa ithumba ngokupheleleyo kunika ithuba elihle lokusinda . Nangona kunjalo, ukuba umhlaza usasazeke kwezinye iindawo zentliziyo, kunokuba nzima ukuwususa ngokupheleleyo. Kubaluleke kakhulu ukukhetha ugqirha onamava ngezi thumba zingaqhelekanga.
- Unyango lweKhemotherapy : Oku kunokunceda ukunciphisa iimpawu kwaye kuncede abanye abantu baphile ixesha elide.
- Unyango lwemisebe : Kwezinye iimeko, oku kunokunceda ukuphucula imeko.
Ngaba iingxaki zingavela ngenxa yonyango?
Ewe, ezinye iindlela zonyango zinokubangela iingxaki, ingakumbi emva kotyando:
- Ukopha.
- Ukungahambi kakuhle kwesingqisho sentliziyo (arrhythmia).
- Ubuthathaka ekusebenzeni kwentliziyo.
Yiyo loo nto oogqirha beceba unyango emva kokucinga ngako konke oku.
Yintoni onokuyilindela ngesi sifo?
Ukuthetha inyani, le yimeko enzima kancinci.
Kwanasemva konyango , ithumba lingabuya . Rhoqo, xa kufunyaniswa ukuba i-cardiac angiosarcoma isasazeka (i-metastasized) nakwezinye iindawo, ezifana nesibindi, imiphunga, kunye nengqondo. Ngamanye amaxesha, inokusasazeka nasemathanjeni nakwiindlala ze-adrenal. Yiyo loo nto ukunyanga lo mhlaza nokusindisa ubomi kunzima.
Iyintoni imbonakalo yesifo? (Imbonakalo)
Kubuhlungu ukutsho oku, kodwa ingqikelelo yesifo sentliziyo i-angiosarcoma ayilunganga kangako . Esi sifo sinamandla kakhulu kwaye sisasazeka kwizicwili ezingqongileyo.
Umyinge wobomi bomntu onesi sifo uphakathi kweenyanga ezili-10 ukuya kwezili-16.Yindlela ebalwa ngayo loo nto. Ngaphandle kotyando, nokuba kukho ezinye iindlela zonyango, uninzi lwabantu luphila phakathi kweenyanga ezili-9 neli-12. Ezinye iingqikelelo zithi eli xesha linokuba lifutshane njengeenyanga ezi-5 okanye ngaphantsi.
Yi -14% kuphela yabantu abafunyaniswe bene-cardiac angiosarcoma abasaphila emva kweminyaka emihlanu befunyaniswe ukuba banayo. I-cardiac angiosarcoma esasazeke (eyasasazeka) kwezinye iindawo zomzimba idla ngokubulala.
Kuqhelekile ukuba uzive ulusizi kwaye usoyika xa usiva into efana nale. Nangona kunjalo, ukwazi olu lwazi kuya kukunceda uthethe noogqirha bakho kwaye uqonde ukuba zeziphi iindlela ezilungileyo onokuzisebenzisa.
Ngaba zikho iindlela zokunciphisa le ngozi?
Nangona kungekho ndlela yokukuphepha ngokupheleleyo oku, zikho izinto onokuzama ukuzinciphisa.
- Kubalulekile ukunciphisa ukuvezwa kwiikhemikhali ezinokubangela umhlaza.
- Ukuba unesifo semfuza esikubeka emngciphekweni omkhulu wolu hlobo lomhlaza, thetha nogqirha wakho ngaso. Emva koko, unokukwazi ukufumana uvavanyo olunokusibona kwangethuba isifo.
Uzinyamekela njani?
Izinto ezisisiseko ozenzayo xa usempilweni zibaluleke ngakumbi xa ulwa nomhlaza.
- Ukutya ukutya okunesondlo kunika umzimba amandla owadingayo.
- Ukuba uziva udiniwe ngenxa yonyango, kubaluleke kakhulu ukuba uphumle ngokwaneleyo .
- Zama izinto ezifana neyoga, ukucamngca, kunye nokuzilolonga ngokuphefumla ukuze uphumze ingqondo yakho.
- Kukwangumbono olungileyo ukujoyina iqela lenkxaso (nokuba likwi-intanethi) apho unokwabelana khona ngeemvakalelo zakho.
Ukhathalelo lwe-hospice lunokukunceda uhlale ukhululekile ekupheleni kobomi bakho.
Ndifanele ndimbone nini ugqirha?
Ungalibali ukubona ugqirha wakho rhoqo xa udibana naye. Nangona kunjalo, nxibelelana nogqirha wakho ngoko nangoko ukuba:
- Ukuba iimpawu zakho ziyavela kwakhona.
- Ukuba iimpawu ziya zisiba mandundu.
- Ukuba ufuna uncedo ngemiphumo emibi evela kunyango.
Ufanele uye nini kwigumbi likaxakeka?
Ukuba unale mpawu, funa unyango olungxamisekileyo ngoko nangoko:
- Ukuba unengxaki enkulu yokuphefumla .
- Ukuba ufumana iintlungu eziqatha esifubeni .
- Ukuba ukhe wasebenzisa i-chemotherapy, uba nomkhuhlane okanye ezinye iimpawu zosulelo (umz., ukubanda, isilonda esibonakala ngathi siyadumba).
Yeyiphi imibuzo omele uyibuze ugqirha wakho?
Ngenxa yokuba i-cardiac angiosarcoma sisifo esingaqhelekanga, kunokuba nzima ukufumana ulwazi oluninzi ngaso. Ungabuza ugqirha wakho imibuzo efana nale:
- "Ingaba lo mhlaza usasazeke nakwamanye amalungu omzimba wam?"
- "Ndingenza utyando?"
- "Xa ujonga ezi scan, ngaba kubonakala ngathi lonke ithumba lingasuswa?"
- "Undicebisa ukuba ndinyangwe ngoluphi uhlobo lonyango?"
- "Iyintoni imbono yomntu okwimeko endikuyo?"
Ekubeni abantu abaninzi bengazange beve nge-cardiac angiosarcoma, kunokuba nzima ukuchazela usapho lwakho nabahlobo bakho imeko yakho. Musa ukoyika ukubuza ugqirha wakho ngayo nantoni na ongayiqondiyo. Sebenzisa naziphi na izixhobo kunye neenkonzo ezikhoyo kuwe ukunceda. Ukuba imbono yakho ayilunganga, thetha nomntu omthembayo malunga neemfuno zakho. Ukuthetha nomcebisi kunye nokulungiselela iinkonzo ze-hospice kunokukunceda uzive ukhululekile ngakumbi.
Okokugqibela, izinto ekufuneka uzikhumbule
I-Cardiac Angiosarcoma ngumhlaza ongaqhelekanga kwaye unzima. Kubalulekile ukuqaphela oku nokuqaphela iimpawu. Okukhona ifunyanwa ngokukhawuleza, kokukhona inokuthi inyangwe.
- Lo ngumhlaza ongaqhelekanga kodwa onzima.
- Ukuba kuvela iimpawu, funa ingcebiso kagqirha ngoko nangoko.
- Thetha ngokukhululekileyo nogqirha wakho malunga nonyango kunye neziphumo zalo.
- Musa ukuthandabuza ukufuna intuthuzelo yengqondo kunye nenkxaso.
Ndiyathemba ukuba olu lwazi luluncedo kuwe. Hlala usempilweni!
Umhlaza wentliziyo , i-angiosarcoma, isifo sentliziyo, iimpawu zomhlaza, unyango lomhlaza, impilo yentliziyo, umhlaza ongaqhelekanga











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