Ngaba ngamanye amaxesha uziva uphelelwa ngumphefumlo, okanye uzive ungaqhelekanga esifubeni sakho? Kusenokwenzeka ukuba uxinzelelo olungaphakathi kwimithambo yegazi emiphungeni yakho luphezulu kancinci. Le yimeko ekhethekileyo ebizwa ngokuba yi-`(Chronic Thromboembolic Pulmonary Hypertension)` okanye `(CTEPH)`. Ungakhathazeki, siza kuthetha ngale nto ngokulula, ngendlela onokuyiqonda.
Yintoni le `(CTEPH)`? Masiqonde kakuhle!
Ngamafutshane, i-CTEPH kukunyuka okungaqhelekanga koxinzelelo lwegazi ngaphakathi kwemithambo yegazi emincinci emiphungeni. Kufana noxinzelelo olungaphakathi kumbhobho wamanzi. Kodwa esona sizathu siphambili soku kukuba ukhe waba negazi elijiyileyo emiphungeni yakho ngaphambili (sikubiza oku ngokuba yi-Pulmonary Embolism) kwaye i-clot ayinyibiliki kakuhle . Kulapho olu xinzelelo lunyuka khona.
Ngubani onokuthi abe nethuba elingcono lokuphuhlisa i-CTEPH?
Oku kubaluleke kakhulu. I-CTEPH yenzeka kuphela kubantu abanembali ye-pulmonary embolism . Ukuba unoxinzelelo oluphezulu emiphungeni yakho kodwa ungenawo amahlwili egazi, isenokungabi yi-CTEPH, kodwa yimeko eyahlukileyo. Ngoko ke kubalulekile ukuqonda lo mahluko.
Ixhaphake kangakanani le meko?
I-CTEPH yimeko engaqhelekanga . Umzekelo, kwilizwe elifana ne-United States, kuphela malunga nama-5,000 amatyala amatsha axelwayo minyaka le. Nangona kunjalo, ekubeni ngamanye amaxesha ingachongwa ngokufanelekileyo, inani linokuba phezulu kakhulu. Ke ngoko, kubaluleke kakhulu ukuqaphela iimpawu.
Luhlobo luni lwempembelelo olunokuba nayo i-CTEPH kwimpilo yakho?
Xa uxinzelelo olukwimiphunga yakho lusanda, ingakumbi kwimeko ye-CTEPH, icala lasekunene lentliziyo yakho liva uxinzelelo olukhulu . Khawuthelekelele, intliziyo yakho kufuneka isebenze nzima ukupompa igazi liye emiphungeni yakho. Okwenzekayo kukuba elinye igazi elingenaoksijini liyanamathela entliziyweni yakho kwaye lithathe ixesha elide ukuya emiphungeni yakho. Oku kunokubangela ukuba umzimba wakho ube namanqanaba aphantsi eoksijini. Le yimeko embi kakhulu, akunjalo?
Kutheni le nto `(CTEPH)` iphuhla? Zithini izizathu?
Eyona nto iphambili kukuba amahlwili egazi ayenzeka kwimithambo yegazi emincinci emiphungeni awanyibiliki kakuhle. Xa oku kusenzeka , izicubu ezifana nezibazi zenzeka apho kwakukho amahlwili khona. Olu qhekeko lubangela ukuba imithambo yegazi inciphe, njengombhobho wamanzi uvaleka. Njengoko olu qhekeko lukhula, uxinzelelo nalo luyanda.
Ziziphi izinto ezibangela umngcipheko wokuphuhlisa i-CTEPH?
Kukho izinto ezinobungozi ezinokubangela uphuhliso lwe-`(CTEPH). Makhe sijonge ukuba zeziphi:
- Ukuba nohlobo lwegazi olungelulo uhlobo O.
- Ukuba nosulelo emathanjeni (i-Osteomyelitis).
- Ezinye iintlobo zomhlaza.
- Izifo zamathumbu ezingapheliyo, umzekelo, iimeko ezifana `(Isifo samathumbu esivuthayo)`.
- Ukuba ngumfazi. (Abafazi banamathuba amaninzi kunamadoda okufumana le meko.)
- Usulelo lwezicubu zentliziyo olubangelwa yi-pacemaker.
- Wena okanye umntu okwintsapho yakho unembali yeengxaki zokunqamana kwegazi, ezifana ne-Antiphospholipid Syndrome.
- Ekubeni sele isusiwe i-spleen ngaphambili (i-Splenectomy).
- Ukuthatha unyango lokutshintshwa kwehomoni ye-thyroid.
Ayizizo zonke ezi zinto ezichaphazela wonke umntu, kodwa zichongiwe njengezinto ezibangela umngcipheko.
Zithini iimpawu ze-`(CTEPH)`?
Umntu one-CTEPH unokufumana iimpawu ezifana nezi:
- Ukuziva iintlungu zesifuba okanye ukuxinana .
- Ukukhohlela igazi (oku kungaqhelekanga).
- Ukutshintsha kombala oluhlaza okwesibhakabhaka kweminwe kunye neenzwane (iCyanosis).
- Ndiziva ndinesizungu .
- I-Syncope.
- Ndiziva ndidiniwe kakhulu (`Ukudinwa`) .
- Ukuziva ngathi isifuba sakho siyabetha ngamandla, oku sikubiza ngokuba yi-"Heart Palpitations".
- Ubunzima bokuphefumla , ingakumbi xa usenza into okanye uhamba.
- Ukudumba kwemilenze, okubangelwa kukuqokelelwa kwamanzi emzimbeni (i-edema).
Musa ukucinga ukuba une-CTEPH kuba nje unenye okanye ezimbini zezi mpawu. Kodwa ukuba ezi mpawu ziyaqhubeka, kungcono ukubona ugqirha.
Sifunyaniswa njani esi sifo `(CTEPH)`?
Xa ubona ugqirha, angaqala enze iimvavanyo zokujonga i-CTEPH, ezifana nezi:
- Uvavanyo olujonga umoya ophumayo kunye nokuhanjiswa kwegazi emiphungeni (`(Iskeni yomoya ophumayo emiphungeni - iskeni ye-V/Q)`).
- I-"Pulmonary Angiogram" luvavanyo olujonga ukuba igazi liqhekekile okanye linciphile na kwimithambo yegazi yemiphunga.
- Uvavanyo Lokusebenza Kwemiphunga.
- I-Transthoracic Echocardiogram (TTE) ifana ne-ultrasound scan yentliziyo.
Emva kwezi mvavanyo zokuqala, kunokufuneka ezinye iimvavanyo ukuqinisekisa ukuxilongwa kwe-CTEPH nokufumanisa ubukhali bayo. Ezi zingabandakanya:
- I-Right Heart Catheterization luvavanyo olulinganisa uxinzelelo ngokufaka umbhobho omncinci kwicala lasekunene lentliziyo.
- Hlola imithambo yegazi emiphungeni usebenzisa iindlela eziphambili zokuthatha imifanekiso ezifana ne-CT Pulmonary Angiography (CTPA) okanye i-Digital Subtraction Angiography.
- Iskeni ye-MRI.
- ``Uvavanyo loxinzelelo lomzimba'' olujonga ukusebenza kwentliziyo ngexesha lokuzilolonga.
Olu vavanyo luvumela oogqirha ukuba baqinisekise ukuba une-CTEPH na kwaye ukwinqanaba elingakanani na.
Ziziphi iindlela zonyango ze-`(CTEPH)`?
Unyango lwe-CTEPH ludla ngokubandakanya utyando okanye inkqubo efanayo. Kukho iindlela ezimbini eziphambili:
1. Utyando lwe-Pulmonary Endarterectomy : Olu lutyando oluvulelekileyo. Kule nkqubo, amahlwili egazi amadala kunye nezicubu ezixineneyo ezinamathele kwimithambo yemiphunga ziyasuswa ngotyando. Oku kwenziwa ukuzama ukubuyisela ukuhamba kwegazi emiphungeni.
2. ``(I-Pulmonary Balloon Angioplasty)``: Kule nto, ibhaluni encinci incamatheliswa esiphelweni sombhobho omde (i-catheter), odluliselwa kumthambo wegazi onciphileyo emiphungeni. Ibhaluni iyavuthelwa ukuze ityhale izicubu zesilonda ecaleni, ikwandise umthambo wegazi kwakhona.
Ukukhetha enye yezi ndlela zimbini kusekelwe kwizinto ezininzi, ezifana nemeko yesigulane kunye nendawo apho igazi liqhekeke khona.
Ngaba zikho ezinye iindlela zonyango?
Ewe, abanye abantu basenokungakwazi ukwenza olu tyando. Kwabo bantu, okanye abo baqhubeka benoxinzelelo emiphungeni yabo emva kotyando, ipilisi ebizwa ngokuba yi-`(Riociguat)` inokunikwa. Eli liyeza elinikwa uxinzelelo lwegazi oluphezulu emaphaphu. Oku kunceda ekunciphiseni iimpawu.
Ngaba i-CTEPH ingathintelwa?
I-CTEPH yingxaki yezinye iimeko ezininzi zempilo. Ezinye izinto esingenakuzilawula. Kodwa eyona nto ibalulekileyo onokuyenza kukunyamekela imiphunga yakho kakuhle . Oko kuthetha ukuba ukuyeka ukutshaya nokuba kude necuba kubaluleke kakhulu.
Iyintoni imbono yezigulane ezine-CTEPH?
Ezi zezona ndaba zimnandi! Utyando lwe-Pulmonary Endarterectomy kunye ne-Pulmonary Balloon Angioplasty zinokunyanga ngokupheleleyo i-CTEPH . Abantu abaninzi abafumana olu nyango bafumana iziphumo ezintle kakhulu.
Nangona kunjalo, nangona ezi ziphumo zintle, ezinye izigulana zinokuba noxinzelelo oluthile lwengqondo, ixhala, kunye nokudakumba. Oku kunokuba yinyani ngakumbi kwabo bangafanelekiyo kunyango olukhankanyiweyo apha ngasentla. Ukuba uhlangabezana naluphi na kwezi ngxaki zengqondo, thetha nogqirha wakho. Banokumamela iinkxalabo zakho baze bakucebise unyango oluya kukunceda uzive ungcono.
Zeziphi izinto ezibalulekileyo ekufuneka uzazi xa uhlala ne-`(CTEPH)`?
- Kuza kufuneka uthathe amayeza okunciphisa igazi ubomi bakho bonke .
- Ukuba usela amayeza afana neWarfarin, kunokufuneka unciphise ukutya okuthile (okufana nesoya kunye nebroccoli, ezityebileyo kwi-vitamin K). Buza ugqirha wakho ngale nto.
- Ukuzilolonga okulula , njengokuhamba, kunokunceda abantu abaninzi ukuba bafumane amandla kwakhona baze bahlale besempilweni. Ugqirha wakho angacebisa nenkqubo yokuzilolonga ejongiweyo (ukuvuselelwa kwepulmonary).
Okokugqibela, khumbula oku.
I-Chronic Thromboembolic Pulmonary Hypertension (CTEPH) yimeko engaqhelekanga apho uxinzelelo lwegazi kwimithambo yegazi yemiphunga lunyuka, kodwa sisifo esinokunyangwa ukuba sifunyenwe kwangethuba kwaye sinyangwa ngokufanelekileyo . Ukuba unayo nayiphi na kwezi mpawu, ungathandabuzi ukufuna ingcebiso kagqirha. Khumbula, ngonyango olufanelekileyo, uninzi lwabantu lunokuphila kakuhle. Ngoko ke ungoyiki. Landela imiyalelo kagqirha wakho ngononophelo, kwaye uya kukwazi ukuphila ngokukhawuleza!
"I-CTEPH, Uxinzelelo lwegazi oluphezulu, Amahlwili egazi, Ubunzima bokuphefumla, Isifo sentliziyo, Ukuvaleka kwemithambo yegazi, Uxinzelelo lwegazi oluphezulu











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