Ngaba wakha waphawula ukuba amazinyo abanye abantu anombala ongaqhelekanga, mhlawumbi umbala oluhlaza okwesibhakabhaka-ngwevu, okanye umbala otyheli-mdaka? Okanye ngaba unamazinyo abuthathaka kangangokuba ayaphuka okanye aguge nokuba utya into encinci? Usenokucinga ukuba oko kuqhelekile. Nangona kunjalo, oku kusenokubangelwa yimeko engaqhelekanga eyenzeka ngexesha lokukhula kwamazinyo ebizwa ngokuba yi-`(Dentinogenesis Imperfecta)`. Makhe sithethe ngale nto kancinci namhlanje, kulungile?
Yintoni i-`(Dentinogenesis Imperfecta)`? Masiyiqonde ngokulula, akunjalo?
Ngamafutshane, `(Dentinogenesis Imperfecta)` yingxaki eyenzeka xa amazinyo ekhula, oko kukuthi, xa amazinyo ekhula. Okwenzekayo kule meko kukuba amazinyo akho aba buthathaka kakhulu aze aphuke lula . Njengebhisikithi, ukuba uyaphula kancinci, iya kuphuka. Kwakhona, amazinyo abantu abanale meko ayakhanya kancinci. Umbala nawo, njengoko benditshilo ngaphambili , uluhlaza okwesibhakabhaka-ngwevu okanye umthubi-mdaka .
Le meko, ebizwa ngokuba yi-"Dentinogenesis Imperfecta," inokuchaphazela amazinyo akho okuqala kunye namazinyo akho asisigxina . Oku kuthetha ukuba iimpawu zinokuqala ebuntwaneni, okanye zibonakale kamva ebomini.
Ngoku khangela, xa sithatha izinyo, lineeleya ezininzi. Inxalenye ekhazimlayo neyomeleleyo phezulu ibizwa ngokuba yi-`(Enamel)`. Ngaphantsi kwe-`(Enamel)` kukho enye ileya, ebizwa ngokuba yi-`(Dentin)`. Le nxalenye ye-`(Dentin)` yiyo enika izinyo amandla nombala. Okwenzekayo kwi-`(Dentinogenesis Imperfecta)` kukuba inxalenye ye-`(Dentin)` ayiphuhli kakuhle. Kwenzeka ntoni ke ngoko? Ngenxa yokuba i-`(Dentin)` ibuthathaka, i-`(Enamel)` engaphezulu ayincamatheliswanga kakuhle kwizinyo. Yiyo loo nto i-`(Enamel)` ikhawuleza iqhekeke kwaye iguge.
Kubalulekile: `(Dentinogenesis Imperfecta)` yahlukile kwi `(Amelogenesis Imperfecta)`. Kwi `(Amelogenesis Imperfecta)`, `(Enamel)` yezinyo ichaphazeleka ngokuthe ngqo. Kwi `(Dentinogenesis Imperfecta)`, ingxaki ikwi `(Dentin)`.
Kuthiwa le yimeko engaqhelekanga kakhulu. Ngokwesiqhelo, le meko iyenzeka kumntu omnye kubantu abayi-6,000 ukuya kwi-8,000.
Ngaba kukho naziphi na iintlobo ze-`(Dentinogenesis Imperfecta)`?
Ewe, sithetha ngeentlobo ezintathu eziphambili ze-`(Dentinogenesis Imperfecta)`. Masibone ukuba zeziphi.
1. `(Dentinogenesis Imperfecta)` Uhlobo 1 (Uhlobo I): Olu lukhethekile. Kuba olu hlobo lwenzeka kwisifo esibizwa ngokuba yi`(Osteogenesis Imperfecta)`. `(Osteogenesis Imperfecta)` sisifo nje esenza amathambo abe buthathaka kakhulu (isifo samathambo abuthathaka). Ngoko ke, kunye neengxaki zamazinyo, aba bantu banengxaki yamathambo. Isizathu soku kukuba kukho utshintsho oluthile kwi`(Genes)` ye`(COL1A1)` okanye`(COL1A2)` zezakhi zofuzo. Zombini ezi zakhi zofuzo zinceda ekwenzeni iproteni`(Collagen)` emizimbeni yethu.
2. `(Dentinogenesis Imperfecta)` Uhlobo 2 (Uhlobo II): Olu hlobo luxhaphake kakhulu kunamazinyo asisigxina.Ixhaphake kakhulu kumazinyo omntwana. Aba bantu badla ngokuba nezinye izifo ezimbalwa ezidluliselwa kwilifa. Nangona kunjalo, kufunyenwe ukuba ngamanye amaxesha kukho ithuba lokulahlekelwa kukuva ngenxa yokwaluphala .
3. `(Dentinogenesis Imperfecta)` Uhlobo 3 (Uhlobo III): Olu lolona hlobo lungaqhelekanga . Luchaphazela amazinyo asisigxina ngaphezu kwamazinyo omntwana. Abaphandi baxele ukuba olu hlobo luchaphazela kakhulu abantu bomnombo wamaJuda ababizwa ngokuba yi`(Ashkenazi Jewish)`, nakwiintsapho ezininzi ezihlala emazantsi eMaryland.
Zithini iimpawu ze-`(Dentinogenesis Imperfecta)`? Ungayibona njani?
Njengoko benditshilo ngaphambili, iimpawu eziphambili kukutshintsha kombala kunye namazinyo abuthathaka nabuthathaka . Amazinyo adla ngokukhanya, abe nombala otyheli-mdaka okanye oluhlaza-ngwevu .
Ngaphandle koko, ungabona nezinye iimpawu ezifana nezi:
- Ukulahlekelwa ngamazinyo omntwana emva kwexesha: Amazinyo omntwana aphuma emva kwexesha kunesiqhelo.
- I-Enamel Hypoplasia: Oku kuthetha ukuba umaleko we-enamel ongaphezulu kwamazinyo ulahlekile ngokwaneleyo.
- Ukungashukumi Kwamalungu: Abanye abantu banokugoba amalungu abo, njengeminwe neengqiniba zabo, ngokugqithisileyo.
- Ukuzalwa Kwamazinyo: Oku kuthetha ukuzalwa ungenamazinyo athile.
- I-enamel yamazinyo ebuthathaka: I-enamel ibuthathaka kwaye iyaphela ngokukhawuleza.
Khawucinge nje, ukuba amazinyo omntwana omncinci anombala ongaqhelekanga, anombala oluhlaza okwesibhakabhaka, okanye aqhekeka lula, ngokuqinisekileyo ufanele ukhathazeke ngawo.
Kutheni le nto `(Dentinogenesis Imperfecta)` isenzeka? Yintoni unobangela?
Isizathu esiphambili soku kukutshintsha kwezakhi zofuzo zethu. Ngokukodwa, utshintsho kwizakhi zofuzo olubizwa ngokuba yi-`(DSPP) ` lubangela i-`(Dentinogenesis Imperfecta). Le `(DSPP)` gene inika imiyalelo yokwenza i-`(Dentin)`, umaleko ophakathi wamazinyo ethu. Ngoko ke xa kukho ingxaki ngale zakhi zofuzo, i-`(Dentin)` ayiveli kakuhle.
Olu tshintsho lwemfuza lunokufunyanwa kubazali , okanye lunokwenzeka ngokungacwangciswanga .
Abo bane-Dentinogenesis Imperfecta type 1, njengoko benditshilo ngaphambili, bane-mutations kwi-COL1A1 okanye kwi-COL1A2 genes. Ezi zi-mutations ze-genetic ezifanayo nezibonwayo kwabo bane-Osteogenesis Imperfecta (isifo esibangela amathambo abuthathaka).
Oogqirha bayixilonga njani le nto?
Ukuba wena okanye umntwana wakho unezinye zezi mpawu, kufuneka niqale nibone ugqirha wamazinyo . Uza kuqala enze uvavanyo lomzimba aze abuze ukuba kukho umntu kusapho lwakho okhe waba nazo na ezi mpawu..
Ukongeza, ukuba ukrokrela ukuba une-Dentinogenesis Imperfecta, kunokwenziwa ezi mvavanyo zilandelayo ukuqinisekisa imeko:
- Ukuthatha ii-X-ray zamazinyo.
- Mhlawumbi ungenza i-CT scan .
Ngokujonga le mifanekiso, ugqirha unokufumana umbono olungileyo ngemeko yangaphakathi yamazinyo, uhlobo lwe-"Dentin".
Ngamanye amaxesha, ugqirha wakho unokucebisa uvavanyo lwemfuza ukuze kufunyaniswe ukuba loluphi utshintsho kwi-DNA yakho olubangela i-dentinogenesis imperfecta.
Zithini iindlela zokunyanga oku? (Unyango)
Eyona nto iphambili kunyango lwe-Dentinogenesis Imperfecta kukuqinisa amazinyo abuthathaka . Oogqirha bamazinyo basebenzisa iindlela ezahlukeneyo zokubuyisela amazinyo kwimeko yawo efanelekileyo.
Umzekelo:
- Izizaliso: Zalisa izikhewu kunye nemingxunya emazinyweni.
- IiVeneers: Ezi ziigobolondo ezibhityileyo ezibekwa ngaphambili kwezinyo. Zinokuphucula ukubonakala kwezinyo.
- Izithsaba: Isithsaba sifana nesigqubuthelo esibekwa phezu kwezinyo. Sigquma lonke izinyo size siliqinise.
Olu nyango lusebenzisa izinto ezinombala wamazinyo, ukuze ugcine uncumo lwakho luhle.
Xa une-Dentinogenesis Imperfecta, amathuba okuba ulahlekelwe ngamazinyo njengoko ukhula. Ukuba ulahlekelwa ngamazinyo, ungawatshintsha ngee -dental implants okanye amazinyo okufakelwa .
Luhlobo luni lwethemba onokuba nalo ngelixa uphila nale meko? (Imbono)
Indlela ocinga ngayo ixhomekeke kwizinto ezininzi:
- Ubudala bakho xa wafunyaniswa une-HIV.
- Uqale unyango ngokukhawuleza kangakanani.
- Loluphi uhlobo lwe-Dentinogenesis Imperfecta onalo?
Into ebalulekileyo kukuba i-Dentinogenesis Imperfecta ayinyangeki . Nangona kunjalo, ngononophelo olufanelekileyo lwamazinyo kunye nemikhwa emihle yokucoca umlomo, unokunceda ekuthinteleni umonakalo ongakumbi kumazinyo akho kwaye uwagcine eqinile. Okukhona imeko ifunyaniswa kwaye inyangwa ngokukhawuleza, kokukhona iziphumo ziba ngcono.
Ngaba i-Dentinogenesis Imperfecta ingathintelwa?
Ngelishwa, i-Dentinogenesis Imperfecta ayinakuthintelwa kuba ibangelwa lutshintsho lwemfuza esingenakukwazi ukululawula. Nangona kunjalo, ukuqala unyango ngokukhawuleza kunokunciphisa umonakalo wexesha elide kumazinyo.
Ndingawanyamekela njani amazinyo am? (Ukuzinyamekela)
Ukuba une-`(Dentinogenesis Imperfecta)`, ucoceko lomlomo olulungileyo lubalulekile.Kubalulekile ukuyigcina ikwimeko entle. Ukuze unciphise ukubola kwamazinyo nomonakalo, yenza oku kulandelayo:
- Buza ugqirha wakho wamazinyo malunga nonyango lwe-fluoride ukuqinisa amazinyo akho.
- Hlamba amazinyo akho kabini okanye kathathu ngemini ngebrashi yamazinyo ethambileyo kunye ne -fluoride toothpaste .
- Nciphisa ukutya okuneswekile, okune-asidi.
- Hlamba umlomo wakho nge-fluoride mouth hlamba kube kanye ngemini.
- Ndwendwela ugqirha wamazinyo rhoqo ukuze uhlolwe kwaye ucoceke .
Yintoni elungileyo ukuyitya nokusela xa une-`(Dentinogenesis Imperfecta)`?
Eyona nto ingcono onokuyenza kukukhetha ukutya neziselo ezineswekile encinci kunye ne-asidi . Oku kuthetha ukunciphisa iziselo ezifana nesoda, iziqhamo ze-citrus ezifana neelayimu, kunye nesosi yetumato kangangoko unako. Kukwangumbono olungileyo ukunciphisa ukutya okufuna ukuhlafunwa kwaye okuqinileyo okanye okukrwada .
Nazi ezinye zokutya ezilungileyo onokuzitya kumntu one-`(Dentinogenesis Imperfecta):`
- Intlanzi ebhakiweyo
- Iintlobo zeeCasseroles
- Imifuno ephekiweyo
- I-oatmeal
- Ipasta enesosi esekwe kukhrimu
- Amaqanda aqhuqhiwe
- Iismoothies
Oku kukutya okulula ukukutya kwaye akubangeli monakalo mkhulu emazinyweni akho.
Ndifanele ndimbone nini ugqirha?
Ukuba wena okanye umntwana wakho nibona nantoni na engaqhelekanga okanye eyahlukileyo ngamazinyo akhe, kungcono ukuxelela ugqirha wakho ngoko nangoko . Khumbula, iimpawu ze-DGI zinokuvela nangaliphi na ixesha. Ukuba amazinyo okuqala omntwana wakho abonakala eluhlaza okwesibhakabhaka, ngwevu, okanye emdaka , qiniseka ukuba ubona ugqirha wamazinyo wabantwana ukuze akunike iingcebiso.
Yeyiphi imibuzo omele uyibuze ugqirha?
Ukuba ufunyaniswe une-Dentinogenesis Imperfecta, ungabuza ugqirha wakho imibuzo efana nale:
- Luhlobo luni lwe-`(DGI)` endinalo?
- Luhlobo luni lonyango endiludingayo?
- Luza kuthatha ixesha elingakanani unyango? Luza kuthatha ixesha elingakanani unyango?
- Ndifanele ndihlambe amazinyo kangaphi?
- Ngawaphi amanyathelo okuthintela endinokuwathatha ukunciphisa ukuguguleka nokonakala kwamazinyo?
Ekugqibeleni kukho into... (Umyalezo oya nawo ekhaya)
Ukuba namazinyo abuthathaka, aqhekeka lula kuyacaphukisa kakhulu. Kuyadinisa kakhulu ukuba uqaphele rhoqo xa usitya. Xa une-`(Dentinogenesis Imperfecta)`, usenokuba neentloni ngokubonakala kwamazinyo akho. Ngenxa yesi sizathu, usenokungafuni ukujongana noluntu.
Kodwa khumbula, awuwedwa.Kukho oogqirha abanokukunceda. Banokucebisa unyango lokuqinisa amazinyo akho, ukuphucula uncumo lwakho, nokukhulisa ukuzithemba kwakho. Ngoko ke, ungakhathazeki nganto, kwaye ulandele icebiso likagqirha wakho.
Ngokufumanisa esi sifo kwasekuqaleni, ukufumana unyango olufanelekileyo, nokulandela imikhwa emihle yokucoca umlomo, ungaphila ubomi obusempilweni nobonwabisayo nangona unesifo `(Dentinogenesis Imperfecta).'
` i-dentinogenesis imperfecta, izifo zamazinyo, amazinyo abuthathaka, ukutshintsha kombala wamazinyo, izifo zemfuza, impilo yamazinyo, amazinyo omntwana











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