Xa sithetha nogqirha ngexesha lokukhulelwa, ngamanye amaxesha sidibana namagama esingazange siweve, okanye iimeko zonyango ezingaqhelekanga. Kuqhelekile ukuba noloyiko olukhulu kunye nexhala ngamaxesha anjalo. Namhlanje siza kuthetha ngesinye seziphene ezingaqhelekanga nezinzulu zokuzalwa. Le meko siyibiza ngokuba yi-Ectopia Cordis. Musa ukoyika xa usiva oku. Masiqonde yonke into ngale nto ngokulula, nganye nganye.
Yintoni kanye kanye i-Ectopia Cordis?
Ngamafutshane, i-Ectopia Cordis iyenzeka xa umntwana ezalwa enentliziyo yonke okanye inxalenye yayo ingaphandle komzimba wakhe. Le yimeko engaqhelekanga kakhulu. Khawucinge nje, le meko yenzeka kwiintsana ezisibhozo kuphela kwizigidi ezizelweyo kwihlabathi liphela.
Ngenxa yokuba esi sisifo esibi kakhulu, uninzi lweentsana ezizalwa zine-Ectopia Cordis zifela esibelekweni okanye kwiintsuku ezintathu emva kokuzalwa. Nangona kunjalo, kukho icala elinika ithemba kweli bali. Amaqela ezonyango anobuchule oogqirha, abahlengikazi, iingcali zonyango lomzimba kunye nezinye iingcali ziye zakwazi ukugcina ezinye iintsana ezizalwa zinesi sifo ziphila iiveki, kwaye ngamanye amaxesha kwaneminyaka.
Yintoni isizathu soku?
Inyaniso kukuba, iingcali azikafumani sizathu siqinisekileyo sale nto, kodwa zineengcinga ezimbalwa.
- Iingxaki zokukhula: Enye ingcamango kukuba njengoko umntwana ekhula esibelekweni , kwenzeka utshintsho emzimbeni oluphazamisana nokukhula okuqhelekileyo komntwana. Umzekelo, iibhanti ze-fibrous zakha kwi-sac egcwele ulwelo (i-amniotic sac) ejikeleze umntwana, nto leyo enokuthintela ukukhula komntwana.
- Ingxaki yokukhula kwesifuba: Enye ingcamango kukuba isifuba somntwana asikhuli kakuhle. Oku kuthintela intliziyo ukuba ingahambi iye kwindawo yayo efanelekileyo ngaphakathi kwesifuba. Oku kunokukhokelela kwi-Ectopia Cordis kunye nezinye iziphene zentliziyo.
- Ukudibana nezinye izifo: I-Ectopia cordis idla ngokubonakala kunye nezinye iziphene zokuzalwa ezenzeka kumgca ophakathi womzimba. Umzekelo, inxulunyaniswa neziphene kwi-sternum, i-pericardium, kunye nodonga lwesisu. Inganxulunyaniswa neemeko ze-chromosome ezifana neTrisomy 18 kunye ne-Turner syndrome.
- Izizathu zofuzo : Enye ingcamango yakutshanje kukuba ezinye iimveku azinazo i-gene ethile ebizwa ngokuba yi-``(BMP2)''. Le gene ibalulekile ekuphuhlisweni kakuhle kwentliziyo kunye nomphambili wesifuba. Ngoko ke bakholelwa ukuba ukungabikho kwayo kusenokuba yimbangela.
Ziziphi iimpawu ezinokuchongwa?
Uphawu oluphambili nolucacileyo lwe-Ectopia Cordis kukuba intliziyo ingaphandle komzimba. Nangona kunjalo, aba bantwana banokuba nezinye iziphene eziphakathi komgca womzimba (umgca osuka entloko uye ezantsi).
| Ezinye iingxaki eziboniweyo | Ingcaciso elula |
|---|---|
| Uqhekeko lwentloko | Ukuba nomqolo okanye uqhekeko olufana nobuso. |
| Umlebe/inkalakahla ecacileyo | Ukuba nomngxuma emlonyeni ongasentla okanye emlonyeni. |
| Imiphunga ayikhuliswanga ngokupheleleyo | Imiphunga yomntwana ayikakhuli ngokwaneleyo. |
| I-Scoliosis | Ukuba ne-curvature okanye i-scoliosis yomqolo. |
| Umngxuma kuDonga oluKhulu | Umngxuma ongaqhelekanga kwi-diaphragm, umsipha owahlula isifuba nesisu. |
Oogqirha bayixilonga njani le nto?
Kwiimeko ezininzi, ukuba umntwana wakho une-Ectopia Cordis, inokubonwa ngexesha lokuhlolwa kwe-ultrasound rhoqo ngexesha lokukhulelwa. Inokubonwa kwangethuba kwi-trimester yokuqala yokukhulelwa. Kusenokufuneka uphinde wenze umjikelo wokuhlolwa kwe-ultrasound ukuqinisekisa ukuxilongwa. Iziphumo zezi mvavanyo zibaluleke kakhulu kuwe ukuze uthathe isigqibo sokuba uza kwenza ntoni ngokulandelayo.
Ukuba ugqiba ekubeni uqhubeke nokukhulelwa kwakho, ugqirha wakho uya kujonga ukukhula komntwana wakho ngokusondeleyo. Oku kungabandakanya i-MRI ( magnetic resonance imaging).Kuza kusetyenziswa uvavanyo lwe- )` kunye ne- `(Echocardiography)`. I-Echocardiography luvavanyo olukhethekileyo olusebenzisa amaza esandi ukuthatha imifanekiso eneenkcukacha zentliziyo.
Oogqirha bakwahlula le meko ngokwendawo ebekwe kuyo intliziyo.
| Indawo apho intliziyo ikhoyo | Intsingiselo | Ubuninzi |
|---|---|---|
| Isifuba | Kufuphi neembambo kunye ne-sternum esifubeni, ngaphezulu kwesisu. | Malunga ne-64% |
| I-Thoracoabdominal | Kwinxalenye esezantsi yesifuba, ngasesiswini. | Malunga ne-18% |
| Isisu | Kwindawo yesisu. | Malunga ne-15% |
| Umlomo wesibeleko | Ubunzima kwindawo yentamo, ukuya emgogodleni. | Malunga ne-3% |
Ukuxilongwa nge-Ectopia Cordis kukwenza uxinezeleke kakhulu kusapho. Kubaluleke kakhulu ukuhlala uqinile engqondweni ngexesha elinje.
Zithini iindlela zonyango zoku?
Xa sithetha ngeendlela zonyango , into yokuqala ekufuneka sicinge ngayo kukhuseleko lomntwana. Ke ngoko, indlela ekuphela kwayo yokubeleka umntwana kukuhlinzwa (C-section). Leyo yeyona ndlela ilungileyo yokukhupha umntwana ngaphandle kokonakalisa intliziyo ngaphandle.
Emva kokuzalwa, umntwana wakho usenokufuna uncedo olongezelelekileyo lokuphefumla. Ukuze benze oku, oogqirha baza kufaka ityhubhu yeplastiki eguquguqukayo kumbhobho womoya womntwana wakho ukuqinisekisa ukuhamba komoya. Basenokufaka nolwelo olukhethekileyo ngetyhubhu egubungela imiphunga ukuze incede ifunxe ioksijini ngcono.
Injongo ephambili yokunyanga i-Ectopia Cordis kukuvala ngotyando umngxuma osesifubeni, ukufaka intliziyo esifubeni kwakhona, nokulungisa naziphi na ezinye iziphene zentliziyo. Olu tyando alusoloko lwenziwa ngaxeshanye. Lwenziwa ngamanqanaba aliqela.
Umngeni wokuqala nowona mkhulu kukufaka intliziyo esifubeni esincinci kunesiqhelo. Emva kokuba ugqirha ekwenzile oko, utshintsha ithambo lesifuba (sternum). Kwimeko ezinje, ukufakelwa intliziyo akusoloko kuyindlela.
Yintoni "iComfort Care"?
Kwezinye iimeko, utyando luyingozi kakhulu kwaye amathuba okuphumelela aphantsi kakhulu. Kwiimeko ezinjalo, ugqirha wakho uza kuthetha nawe malunga nokhetho olubizwa ngokuba yi-"Comfort Care."
Injongo kukunciphisa iintlungu nokubandezeleka umntwana akufumanayo nokumvumela ukuba aphile ubomi bakhe bonke ngoxolo nangoxolo. Olu luhlobo olukhethekileyo lokhathalelo olujolise ekunikeni intuthuzelo kumntwana nakusapho ngeli xesha linzima, endaweni yokumnyanga nokumphilisa.
Umyalezo Wokuya Ekhaya
- I-Ectopia Cordis sisifo esingaqhelekanga nesinzima sokuzalwa apho intliziyo yomntwana ifumaneka ngaphandle komzimba.
- Nangona unobangela woku ungekafunyanwa, kukholelwa ukuba iingxaki ezenzeka ngexesha lokukhula komntwana esibelekweni sikanina kunye nezinto ezibangela ufuzo zinegalelo koku.
- Ukuxilongwa kudla ngokwenziwa ngexesha lokukhulelwa ngokusebenzisa ii-ultrasound scans.
- Nangona utyando olunzima kakhulu oluquka amanyathelo aliqela lwenziwa njengonyango, ayingomntwana wonke onokukwazi ukwenza utyando.
- Ukuxilongwa okunje ngumceli mngeni onzima kakhulu kusapho. Ke ngoko, kubalulekile ukuxoxa ngazo zonke iindlela, kuquka utyando kunye "noNcedo oluNgcolisayo," nogqirha wakho ngokukhululekileyo kwaye wenze isigqibo esifanelekileyo kumntwana wakho kunye nosapho lwakho.
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