Ingaba umntwana wakho ukhula amaqhuma angaqhelekanga emzimbeni wakhe? Oku kungaba luphawu lweComplex Lymphatic Anomalies (CLA)!

Ngamanye amaxesha siyoyika kakhulu xa sibona utshintsho oluncinci emizimbeni yabantwana bethu, akunjalo? Ingakumbi ukuba asizazi kakuhle ezo zinto. Namhlanje siza kuthetha ngemeko engaqhelekanga kodwa ebaluleke kakhulu ekufuneka siyiqaphele. Oku kubizwa ngokuba yiComplex Lymphatic Anomalies , okanye (CLA) ngamafutshane. Abanye abantu babeyibiza ngokuba yi (Lymphangiomatosis) ngaphambili. Ngoko ke ungaweva omabini la magama.

Okokuqala, masibone ukuba zithini iiComplex Lymphatic Anomalies (CLA)?

Ngamafutshane, iiComplex Lymphatic Anomalies (CLA) zizinto ezingaqhelekanga kodwa ezinokwenzeka ukuba umntwana azalwe nazo apho afumana khona iithumba ezingengobungozi ezibizwa ngokuba yi-lymphatic malformations okanye i-lymphangiomas kwinkqubo ye-lymphatic yomntwana. Ezi thumba zinokukhula zibe ngamathambo omntwana, izicwili ezidityanisiweyo, kunye nezinye izitho zomzimba, nto leyo ebangela umonakalo.

Khawucinge nje, nokuba umntwana wethu unale meko xa ezalwa, uninzi lwexesha iimpawu ziqala ukubonakala xa emdala kancinci, mhlawumbi emva kweminyaka embalwa. Yiyo loo nto ngamanye amaxesha kusiba kudala kakhulu ukuyiqonda le nto.

Ngoko ke, yintoni le nkqubo yeLymphatic?

Kulungile, ngoku mhlawumbi uyazibuza ukuba yintoni inkqubo ye-lymphatic. Ngamafutshane, yinkqubo yokuzikhusela emangalisayo emzimbeni wethu. Ifana namajoni kwilizwe lethu. Le nkqubo ye-lymphatic inceda umzimba wethu ukuba uthintele izifo kwaye uzilwe nazo ukuba ziyazilwa. Yinxalenye ebalulekileyo yenkqubo yethu yokuzikhusela.

Inkqubo ye-lymphatic yenziwe ngenethiwekhi yeetyhubhu ezincinci ezibizwa ngokuba zii-lymphatic vessels, amadlala afana nee-lymph nodes, kunye namalungu afana ne-spleen. Ezi lymphatic vessels zifana neetyhubhu ezincinci. Ziqokelela ulwelo lwe-lymph kwizicubu zomzimba, ziluhluze, zilucoce, zize zilubuyisele egazini. Ayingomsebenzi umangalisayo lo?

Kukho iintlobo ezimbini ze-CLA: ezizimeleyo neziyi-Systemic.

Ii-Complex Lymphatic Anomalies zinokwahlulwa zibe ziintlobo ezimbini eziphambili:

1. Ii-CLA ezizimeleyo: Kulapho iithumba zigcinwa kwindawo enye yomzimba womntwana. Umzekelo, zinokuchaphazela kuphela umngxuma wesifuba. Kwimeko enjalo, imiphunga kunye nezicubu ezithambileyo zesifuba (mediastinum) zichaphazeleka kakhulu.

2. Ii-CLA zeNkqubo: Kule meko, ezi thumba zinokuvela kwiindawo ezininzi emzimbeni womntwana, njengamathambo, esifubeni, nakwisisu.

Ngale ndlela, iimpawu kunye nonyango zinokwahluka ngokuxhomekeke kwindawo echaphazelekileyo.

Ziziphi iintlobo eziphambili ze-Complex Lymphatic Anomalies (CLA)?

Kukho iintlobo ezine eziphambili ze-CLA. Nangona uhlobo ngalunye lunezinye zeempawu ezifanayo, ziimeko ezahlukeneyo. Kwaye utshintsho lwezakhi zofuzo olubangela ezo mpawu nalo lwahlukile.

• I-Generalized Lymphatic Anomaly (GLA):Le meko idla ngokuchaphazela amalungu ahlukeneyo omzimba womntwana. Umzekelo, la mathumba anokwenzeka emathanjeni, kwipleyini, esibindini, emiphungeni, nakwizicwili ezithambileyo zesifuba (mediastinum).
• I-Kaposiform Lymphangiomatosis (KLA): Olu lolona hlobo lwe-CLA lubi kakhulu kwaye lusasazeka ngokukhawuleza. Kwi-KLA, imithambo ye-lymphatic ethwala ulwelo lwe-lymph emzimbeni womntwana iyakhula. Oku kubangela ukuba ihlasele kwaye yonakalise amalungu omzimba, amathambo, kunye nezicubu ezimngqongileyo.
• I-Central Conduction Lymphatic Anomaly (CCLA): Abantwana abane-CCLA nabo banemithambo ye-lymph eyandisiweyo. Nangona kunjalo, kwi-CCLA, le mithambo yandisiweyo ifumaneka kakhulu emzimbeni. Oku kunokuchaphazela inkqubo yokugaya ukutya kwaye kuthintele umntwana ekukhupheni ulwelo lwe-lymph ngokufanelekileyo emzimbeni.
• Isifo sikaGorham-Stout (GSD): Esi sifo sikwabizwa ngokuba sisifo sikaGorham, sibangela ukuba amathambo amaninzi anyibilike ngenxa yokwakheka kwemithambo ye-lymphatic ngaphakathi kwamathambo. Sikwabizwa ngokuba "sisifo samathambo esinyamalalayo." Sinokuchaphazela naliphi na ithambo. Nangona kunjalo, abantwana abane-GSD badla ngokuphulukana namathambo kwiimbambo, ekhanda, entanyeni, nasemqolo wesibeleko.

Ixhaphake kangakanani le meko ye-CLA?

Iingxaki zeLymphatic ezintsonkothileyo ngokwenene zizinto ezingaqhelekanga kakhulu . Ngenxa yokuba azixhaphakanga kangako, ngamanye amaxesha kunokuba nzima koogqirha ukuzixilonga ngokuchanekileyo. Ke ngoko, ukuba uneempawu, kubaluleke kakhulu ukubona ingcali ngokukhawuleza.

Yintoni ebangela le CLA?

Oogqirha nabaphandi basazama ukufumanisa ukuba yintoni ebangela i-CLA. Nangona kunjalo, uphando lwakutshanje lubonisa ukuba le meko inokubangelwa kukuguquka kwezakhi zofuzo okuzuzwa ngabazali ukuya ebantwaneni, kunye nokuguquka kwezakhi zofuzo ezenzeka emva kokuzalwa. Oku kuthetha ukuba inxulumene nezakhi zofuzo.

Ngubani osengozini yokufumana i-CLA?

Iingxaki zeLymphatic ezintsonkothileyo zinokuchaphazela nabani na. Ngokukodwa, iimpawu zale meko zihlala zibonakala ebuntwaneni okanye ebusheni. Ngoko ke, nokuba imeko ikhona ekuzalweni, kungathatha ixesha ukuba iimpawu zibonakale.

Ngoko ke, zithini iimpawu ze-CLA?

Iimpawu zingahluka kumntwana ngamnye onesi sifo. Kwakhona, iimpawu ziyahluka ngokuxhomekeke ekubeni leliphi ilungu lomzimba elichaphazelekileyo kwaye linzima kangakanani. Uninzi lwexesha, esi sifo siqhubeka kancinci. Ngenxa yoko, sisenokungazinaki kakhulu ezinye zeempawu, okanye sinokucinga ukuba zibangelwa sisifo esithile.

Ukuba inkqubo yokuphefumla yomntwana wakho ichaphazelekile:

Ngeli xesha, iimpawu ezifana neze-asthma zinokubonakala.

• Ukukhohlela okungapheliyo.
• Ubunzima bokuphefumla (ukuphelelwa ngamandla).
• Ukuphefumla ( isandi sokukhala ) xa uphefumla.

Ukuba inkqubo yamathambo yomntwana wakho ichaphazelekile:

• Intlungu emathanjeni okanye emalungeni.
• Nokuba ukuwa okuncinci kunokubangela ukwaphuka kwamathambo .
• Ukungaziva mnandi kwamalungu omzimba.
• Intlungu okanye ubuthathaka obubangelwa kukucinezelwa kwemithambo-luvo .

Ukuba inkqubo yokwetyisa yomntwana wakho ichaphazelekile:

• Ukudumba kwesisu kunye nentlungu yesisu .
• I-anemia kunye nokudinwa okungapheliyo.
• Urhudo.
• Ukutya akunancasa.
• Isicaphucaphu nokuhlanza.
• Ukunciphisa umzimba ngaphandle kwesizathu.

Ukuba inkqubo yomchamo yomntwana wakho ichaphazelekile:

• Igazi kumchamo (i-hematuria).
• Intlungu emqolo.
• Uxinzelelo lwegazi oluphezulu ebantwaneni.

Ukuba umntwana wakho unenye okanye ngaphezulu kwezi mpawu, nceda ufumane ingcebiso kugqirha. Ezi azizo iimpawu ze-CLA, kodwa kubalulekile ukuba ahlolwe.

Oogqirha bayixilonga njani le meko ye-CLA?

Ngenxa yokuba i-CLA yimeko engaqhelekanga kwaye iimpawu zayo zahlukile, ngamanye amaxesha kunokuba nzima koogqirha ukufumanisa imeko echanekileyo. Ekubeni idla ngokuchaphazela imiphunga namathambo abantwana, ugqirha womntwana wakho unokuyalela iimvavanyo ezifana nezi:

• I-Bronchoscopy: Ukujonga usulelo okanye ezinye iingxaki kwindlela yomoya.
• Uvavanyo lokusebenza kwephaphu: Linganisa ukuba imiphunga yakho isebenza kakuhle kangakanani.
• I-MRI yomzimba wonke: Ukujonga izinto ezifana namalungu omzimba achaphazelekileyo, izilonda zamathambo, okanye ulwelo esiswini.
• Ii-X-reyi: Ukujonga ngakumbi amathambo abonakala erhaneleka okanye enzakeleyo kwi-MRI. Ii-X-reyi zesifuba zinokujonga nokungahambi kakuhle kwemiphunga.

Ngamanye amaxesha oogqirha bathatha isampuli encinci yee-lymph nodes kunye nezicubu (i-biopsy) baze bayihlole phantsi kwe-microscope. Nangona olu vavanyo lunokufumanisa ngokuqinisekileyo i-CLA, ngamanye amaxesha lunokubangela iingxaki, ezifana nokuqokelelwa kolwelo lwe-lymph olujikeleze imiphunga (chylothorax). Ngenxa yoku, oogqirha badla ngokuxhomekeka kuvavanyo olungenazintsholongwane ukuze benze uxilongo.

Iphathwa njani i-CLA?

Ngenxa yokuba i-CLA inokuchaphazela iindawo ezininzi zomzimba womntwana, oogqirha basebenzisana, oko kukuthi, basebenzisa indlela eyahlukeneyo yokucwangcisa unyango olufanelekileyo kumntwana. Xa unyanga i-CLA, eyona nto iphambili kukulawula iimpawu zomntwana. Ukuze wenze oku, ungenza izinto ezinje:

• Ukufakelwa kwamathambo: Ukonzakala kwamathambo kwiimeko ezifana ne-GSD.
• Ukutya okuneproteni ephezulu okanye ukutya okunesondlo ngemithambo yegazi (isondlo esipheleleyo se-parenteral okanye i-TPN).
• Unyango lweSclerotherapy: Ukunciphisa okanye ukucima iithumba okanye imithambo ye-lymph.
• Utyando: Ukususa iithumba okanye ukufaka iityhubhu ezincinci (ii-shunt) ukuze kube lula ukuhamba kolwelo lwe-lymph.
• Unyango ngemitha okanye i-chemotherapy: Ukunciphisa iithumba ezingezizo umhlaza (ezi zisetyenziswa kuphela kwiimeko ezinzima kakhulu nezisongela ubomi).

Kutshanje, kuye kwasetyenziswa iindlela zonyango ezijolise kwiinguqu zemfuza ezibangela le meko. Ezi ndlela zonyango zikwabonakalisiwe ukuba zisebenza njengonyango lokuqala lwe-CLA.

Ngaba i-Complex Lymphatic Anomalies (CLA) ingathintelwa?

Ngelishwa, akukho . I-CLA iyenzeka ngexesha lokukhulelwa, kwaye isizathu esichanekileyo asaziwa. Ngoko ke, akukho nto ubunokuyenza ukuthintela umntwana wakho ukuba angabi nale meko.

Ziziphi iingxaki ezinokubakho ze-CLA?

I-CLA inokubeka umntwana wakho emngciphekweni ngenxa yezi zinto zilandelayo:

• I-Ascites: Ukuqokelelana kolwelo esiswini.
• Ukuqhekeka kwamathambo.
• I-Chylothorax kunye neChylopericardium: Ingqokelela yolwelo olufana nobisi (chyle) oluqulethe ulwelo lwe-lymph kunye namafutha kwi-membrane egubungela imiphunga (pleura) okanye ingxowa ejikeleze intliziyo (pericardium).
• Imiphunga ephukileyo/i-pneumothorax.
• Ukungasebenzi kakuhle kwesibindi.
• Ukukhubazeka komzimba.
• Ukuphuma kwegazi kwintliziyo.
• Ukuphuma kwegazi kwimithambo yegazi kunye nokudumba kwemithambo yegazi ebangelwa yintliziyo.

Ezinye zezi ngxaki zinokuba yingozi kakhulu, ngoko ke kubalulekile ukuba uqaphele iimpawu kwaye ulandele imiyalelo kagqirha wakho.

Liyintoni ikamva lomntu one-CLA?

Akukho nyango lwe-Complex Lymphatic Anomalies (CLA). Ikamva lomntwana wakho lixhomekeke ekubeni zeziphi iinkqubo zomzimba ezichaphazelekileyo kunye nokuba iimpawu zinzima kangakanani.

Ukuqhekeka kwemithambo yegazi ye-Pleural yeyona nto ibangela ukufa phakathi kwabantu abane-CLA. Nangona kunjalo, ngonyango olufanelekileyo nokulawulwa, umntwana unokuncedwa ukuba aphile ubomi obuqhelekileyo.

Ndifanele ndimbone nini ugqirha?

Ukuba umntwana wakho unenye yezi mpawu, bonana nogqirha ngokukhawuleza:

• Intlungu esiswini okanye emathunjini.
• Ukuba kukho igazi kumchamo.
• Ukukhohlela okungapheliyo, ukuphefumla nzima, okanye ubunzima bokuphefumla.
• Ukucaphuka okungachazekiyo, ukudinwa, okanye ukwehla kobunzima.

Ukuba unayo nayiphi na kwezi, nceda ubone ugqirha ngokukhawuleza.

Ndingayibuza ntoni ugqirha?

Usenokubuza ugqirha womntwana wakho imibuzo efana nale:

• Ngawaphi amalungu omzimba womntwana wam achaphazeleke yile meko?
• Ziziphi iindlela zonyango ezikhoyo kumntwana wam?
• Ngaba umntwana wam udinga utyando?
• Ngaba kufuneka ndiqaphele iimpawu zeengxaki?

Kubaluleke kakhulu ukubuza le mibuzo nokuqonda kakuhle imeko.

Okokugqibela, ndimele ndithi...

Xa ufumanisa ukuba umntwana wakho une-CLA (lymphangiomatosis), kuyinto eqhelekileyo ukuziva usoyika kwaye ukhathazekile malunga nendlela oku kuya kuyichaphazela ngayo impilo yakhe kunye nekamva lakhe. Uninzi lwethu lusenokuba aluzange luve ngesi sifo ngaphambili. Kwaye akukho nto ubunokuyenza ukuyithintela.

Inyathelo lokuqala lokunceda umntwana wakho kukwazi kakuhle ngesi sifo, iimpawu zaso, kunye nonyango lwaso. Bona ugqirha ogxile kwizifo zenkqubo ye-lymphatic. Bangaphendula imibuzo yakho baze banike unyango oluthile olufunekayo kumntwana wakho.

Nangona kungekho nyango lwe-CLA, unyango olufanelekileyo kunye nolawulo lunokunceda umntwana wakho aphile ubomi obonwabisayo nobunempilo. Ngoko ke, hlala uqinile kwaye wenze konke okusemandleni akho kumntwana wakho.

` Iingxaki zeLymphatic ezintsonkothileyo, iLymphangiomatosis, Izifo zeLymphatic System, iiTumors zobuntwana, iOsteomalacia, Iimpawu zePulmonary, Izifo ezingaqhelekanga zobuntwana