Ingaba isisu somntwana wakho sishwabene? Ngaba yiPrune Belly Syndrome? Masiqaphele oku.

Xa ujonga umntwana wakho osandul’ ukuzalwa, ngaba ukhe waphawula ukuba ulusu lwesisu sakhe lushwabene njenge-prune? Okanye isisu sakhe sibonakala sikhulu ngokungaqhelekanga? Kuqhelekile ukuba nawuphi na umama okanye utata oyike xa ebona ezi zinto. Kodwa oku kungaba luphawu lwesifo esingaqhelekanga esibizwa ngokuba yiPrune Belly Syndrome. Ungakhathazeki, siza kuthetha ngayo yonke into ngokucacileyo nangokulula.

Yintoni iPrune Belly Syndrome?

Ngamafutshane, iPrune Belly Syndrome yimeko engaqhelekanga kakhulu ebakho xa umntwana ezalwa (ezalwa). Eli gama livela kwinto yokuba ulusu olusesiswini lwaba bantwana lubonakala lushwabene kwaye lufana neprune. Oku kubangelwa zizinto ezintathu eziphambili.

1. Izihlunu zesisu ezibuthathaka okanye ezingekhoyo: Izihlunu zesisu zomntwana azikakhuli ngokupheleleyo, nto leyo ebangela ukuba ulusu lwesisu lubonakale lugobile kwaye lushwabene.

2. Amasende angathotywanga: Kumakhwenkwe, amasende awazange ehle emzimbeni aye kwi-scrotum apho afanele ukuba khona.

3. Iingxaki zenkqubo yomchamo: Kukho iingxaki ngendlela inkqubo yomchamo yomntwana, oko kukuthi, izintso kunye nesinyi, eyenzeka ngayo.

Ukongeza kwezi ngxaki zintathu ziphambili, le meko inokuchaphazela nezinye iindawo zomzimba womntwana. Umzekelo, intliziyo, imiphunga, amathumbu, kunye nenkqubo yamathambo zinokuchaphazeleka. Oku kukwabizwa ngokuba yiTriad Syndrome okanye iEagle-Barrett Syndrome.

Ixhaphake kangakanani le meko?

Le yimeko engaqhelekanga kakhulu. Ichaphazela malunga nenye kwiintsana ezisandul’ ukuzalwa ezingama-30,000 ukuya kuma-40,000. Okumangalisa kakhulu kukuba ama-95% amatyala ale meko axelwa kubafana .

Ziziphi iimpawu eziphambili zesi sifo?

Kukho iimpawu ezingaphezu kwama-50 zePrune Belly Syndrome. Nangona kunjalo, ezi mpawu zinokwahluka kumntwana ngamnye. Ugqirha wakho uza kumxilonga umntwana wakho aze enze uvavanyo olufunekayo ukuqinisekisa imeko.

Makhe sijonge ezinye zeempawu eziphambili eziqhele ukubonwa.

Kutheni oku kusenzeka? Yintoni unobangela?

Abaphandi abakafumani sizathu soku okwangoku, kodwa kukho iingcamango ezininzi ezibonisa ukuba isenokuba yimbangela.

• Iingxaki zesinyi: Abanye abantu bakholelwa ukuba le meko ibangelwa kukungaqheleki kwesinyi okuvela ngelixa umntwana ekhula esibelekweni. Umchamo awukwazi ukuhamba kakuhle kwaye uqokelelana, nto leyo ebangela ukuba isinyi, umchamo kunye nezintso zidumbe. Njengoko isinyi sikhula, sibeka uxinzelelo kwizihlunu zesisu, nto leyo ebangela ukuba ziphele.
• Ingxaki yokukhula kwemisipha: Abanye bakholelwa ukuba isizathu esiphambili kukuba izihlunu zesisu somntwana azikhuli kakuhle.
• Izizathu zofuzo: Kukholelwa ukuba le meko inokuba nefuthe kwimfuza, njengoko ibonwa nakubantakwabo. I-Prune Belly Syndrome ikwabonakala nakubantwana abaneengxaki zofuzo ezifana neTrisomy 18 (Edwards syndrome) kunye neDown syndrome (Trisomy 21).

Ziziphi iingxaki ezinokwenzeka ngenxa yale meko?

Zininzi iziphumo ebezingalindelekanga kunye neengxaki ezihambisana nePrune Belly Syndrome. Iyahluka ukusuka kusana ukuya kusana. Ezi zezona ngxaki ziphambili ezinokubonwa.

• Ukuqhinwa: Ubunzima bokuphuma kwendle ngenxa yemisipha yesisu ebuthathaka.
• Ukukhubazeka kwamathambo: izinto ezifana nokuphuma kwesinqe, ukungabikho kwezandla, iminwe, okanye iinzwane.
• Izifo zomchamo: Ukuvela rhoqo kwezifo zomchamo (UTIs).
• Ukungazali okanye umhlaza: Ukungawehlisi amasende kunokukhokelela ekungazali okanye emngciphekweni womhlaza kwixesha elizayo.
• Ukukhula okunciphileyo kwemiphunga: Imiphunga ayiphuhli kakuhle (i-pulmonary hypoplasia).
• Ukungasebenzi kakuhle kwezintso okungapheliyo: Le yeyona ngxaki inzima kakhulu.

Ungayixilonga njani le meko?

Kwiimeko ezininzi, le meko inokubonwa kwangethuba ngexesha lokuhlolwa kwe-ultrasound (i-fetal ultrasound) oye wayifumana ngexesha lokukhulelwa kwakho. Olu vavanyo luvumela ugqirha ukuba abone usana:

• Ukungasebenzi kakuhle kwamathambo okanye imisipha
• Iingxaki zentliziyo
• Uphuhliso oluphantsi lwemiphunga
• Iingxaki zenkqubo yokugaya ukutya
• Isinyi sidumbile.
• Izintso ziyakhula.

Emva kokuba umntwana ezelwe, ugqirha usenokucinga ukuba umntwana unale meko ngokumjonga nje. Ukuqinisekisa loo ngxaki, kunokwenziwa uvavanyo oluninzi, olufana nolu:

• Uvavanyo lwegazi
• Iskeni ye-ultrasound
• I-X-reyi
• Iskeni ye-CT
• Iskeni ye-MRI
• I-voiding cystourethrogram (VCUG) - Oku kuquka ukufaka ulwelo olukhethekileyo kwisinyi kunye nokuthatha ii-X-ray ngelixa umntwana echama ukujonga ukusebenza kwenkqubo yomchamo.

Iphathwa njani?

Unyango lwale meko luyahluka kumntwana ngamnye. Iqela leengcali liza kusebenzisana ukuze lenze isicwangciso sonyango esifanelekileyo kumntwana. Oku kuya kuthathela ingqalelo izinto ezininzi, kuquka ubudala bomntwana, imeko yempilo, ubukhali bemeko, kunye neminqweno yabazali.

• Iimeko ezingembi kangako: Abanye abantwana abaneempawu ezingezizo ezinzulu kangako banokungenelwa zii -antibiotics zodwa ukuthintela okanye ukunyanga usulelo lomchamo.
• Utyando: Nangona kunjalo, abantwana abaninzi baya kufuna utyando oluninzi ukulungisa udonga lwesisu, amalungu esini, isinyi, kunye nezinye iindawo zenkqubo yomchamo.

Nazi ezinye zeentlobo eziphambili zotyando ezenziwayo:

• I-Vesicostomy: Kuvulwa umngxuma omncinci ngesisu ungene kwisinyi, nto leyo evumela umchamo ukuba uphume kuwo.
• I-Orchiopexy: Amasende athotywa ngotyando emzimbeni aze abekwe kwisinqe.
• I-Cystoplasty: Utyando lokucoca umzimba:Utyando oluntsonkothileyo oluyakha kwakhona ngokupheleleyo isinyi.

Kwezinye iimeko ezinzima, umntwana usenokufuna ukufakelwa izintso .

Liza kuba njani ikamva laba bantwana?

Ulindelo lobomi lwaba bantwana luxhomekeke kubukhulu besifo. Okubuhlungu kukuba, phakathi kwe-10% kunye ne-25% yabantwana abazalwa benesi sifo bafela esibelekweni okanye bafe ngenxa yeengxaki kwiiveki zokuqala zobomi.

Nangona kunjalo, malunga nama-40% abantwana abanePrune Belly Syndrome basebenza kakuhle kwizintso kwaye banokuphila ubomi obuqhelekileyo.

Abanye abangama-30% baya kufuna ukufakelwa izintso ngaxa lithile ebomini babo.

Ngawaphi amaxesha afanelekileyo okubonana nogqirha?

Abantwana abanePrune Belly Syndrome basengozini enkulu yosulelo lwendlela yomchamo (UTIs), ngoko ke ukuba ubona naziphi na iimpawu zosulelo lwendlela yomchamo, fowunela ugqirha wakho ngokukhawuleza.

Ukongeza, funa ingcebiso kagqirha ukuba umntwana wakho unenye ingxaki yokuchama okanye ubonisa naziphi na ezinye iimpawu ezingaqhelekanga. Kubaluleke kakhulu ukumsa umntwana wakho kuvavanyo lwezonyango ubuncinane kanye ngonyaka .

Ukunyamekela umntwana ozelwe enale meko kunokuba nzima. Kodwa khumbula, awuwedwa. Ukusebenza nogqirha kunye neqela leengcali ezinolwazi ngale meko kunokukunika wena nomntwana wakho amandla kunye nolwalathiso abaludingayo.