Wake wezwa ngesimo esibizwa ngokuthi i-hemophilia ? Lesi yisimo esingavamile kodwa esibucayi kakhulu. Kalula nje, yisimo lapho igazi lingavimbi kahle emizimbeni yethu. Lokhu kusho ukuthi ngisho nokulimala okuncane, ukuwa, noma ukusikeka ngezinye izikhathi kungabangela ukopha okukhulu. Ngezinye izikhathi, ukopha okuzenzekelayo kungenzeka ngaphandle kwesizathu esicacile.
Kuyini ngempela i-hemophilia?
Cabanga nje ukuthi uma sopha igazi, imizimba yethu ineqembu elincane labasebenzi abasebenza ukulimisa. Sibiza laba basebenzi ngokuthi 'izici'. Empeleni lezi yizinhlobo ezikhethekile zamaprotheni. Lezi zici ziyahlangana ukuze zakhe ihlule legazi futhi zimise ukopha kwegazi.
Kunezinhlobo ezimbili eziyinhloko ze-hemophilia:
- I-Hemophilia A: Laba bantu abanayo iphrotheni eyanele ebizwa ngokuthi i-factor VIII , edingekayo ukuze igazi lijiye.
- I-Hemophilia B : Laba bantu abanayo iphrotheni ebizwa ngokuthi i-factor IX .
Lokhu kuvame ukwelashwa udokotela wakho ekunikeza i-deficiency factor ngemithambo yegazi. Ukwelashwa kokuvimbela ukopha kubizwa ngokuthi “ukuvimbela ukopha,” kanti ukwelashwa lapho ukopha kwenzeka kubizwa ngokuthi “uma kudingeka.”
Kodwa, kunenkinga encane lapha...
Kwabanye iziguli, umzimba uqala ukusebenza ngokumelene nalezi zinto esizinikeza ngokugoma. Njengokungathi ucabanga ukuthi ziyisitha bese uzihlasela. Lokhu sikubiza ngokuthi ukwakheka “kwama-inhibitors” . Uma lokhu kwenzeka, amandla okwelashwa kwezinto esizinikezayo ayancishiswa. Ngakho-ke, ukwelapha abantu abanalezi zinhlobo ‘zama-inhibitors’ kuyinkimbinkimbi kakhulu.
Kwenzekani ngalo muthi omusha obizwa ngokuthi i-Alhemo?
I-Alhemo(concizumab-mtci) umuthi omusha ovunyelwe ukunciphisa noma ukuvimbela ukopha, ikakhulukazi ezigulini ezine-hemophilia A noma i-hemophilia B ezine-'inhibitors' okukhulunywe ngayo ngaphambilini.
Kalula nje, imizimba yethu ngokwemvelo ineprotheni evimbela igazi ekujiyeni. Ibizwa ngokuthi i-TFPI (Tissue Factor Pathway Inhibitor) . Cabanga ngayo 'njenge-traffic cop' emizimbeni yethu; ilawula inqubo yokujiya kwegazi. Lokho okwenziwa yi-Alhemo kuphazamisa kancane umsebenzi walo 'mjovi' obizwa nge-TFPI. Ngemuva kwalokho, umzimba wandisa ukukhiqizwa kwesinye isici esisiza ukujiya kwegazi (i-factor Xa), futhi ikhono lokwenza ama-blood clots liyathuthuka. Lokhu kunciphisa kakhulu ingozi yokopha.
Ungayisebenzisa kanjani i-Alhemo?
I-Alhemo iwumjovo wansuku zonke ongaphansi kwesikhumba . Iza ngepeni eligcwaliswe kusengaphambili, ngakho-ke kulula kakhulu ukuyisebenzisa. Uma udokotela wakho enquma ukuthi ungazinika lo mjovo ekhaya, uzokukhombisa ngqo ukuthi ungakwenza kanjani.
- Umthamo: Umthamo ophakeme kancane (umthamo wokulayisha) unikezwa ngosuku lokuqala lokwelashwa. Ngemuva kwalokho, kufanele uthathe umthamo wokunakekela onqunyiwe nsuku zonke. Umthamo unqunywa ngokusekelwe esisindweni sakho, ngakho-ke kufanele utshele udokotela wakho uma isisindo sakho sishintsha.
- Ukuhlolwa: Emasontweni amane ngemuva kokuqala ukwelashwa, uzobe uhlolwa igazi ukuze kuhlolwe ukuthi inani lomuthi emzimbeni wakho lilungile yini. Ngokusekelwe emiphumeleni, udokotela wakho angase alungise umthamo wakho.
- Izindawo zokugoma: Umuthi wokugoma unikezwa esiswini (amasentimitha angu-2 azungeze inkaba) noma ethangeni. Ungajovi endaweni efanayo nsuku zonke, kodwa shintsha indawo. Ungajovi ezindaweni ezibuhlungu, eziphukile, ezibomvu, ezine-eczema, noma ezinezibazi .
Into ebaluleke kakhulu ukuthi, ungayeki ukuthatha lo muthi ngaphandle kokukhuluma nodokotela wakho. Ukuze uvimbele ukuphuma kwegazi, kubaluleke kakhulu ukuthatha umuthi ngesikhathi esifanele nsuku zonke.
| Uma kungakapheli amasonto amane okuqala | Shayela udokotela wakho ngokushesha bese ucela iseluleko. |
| Uma uphuthelwa umthamo ngemva kokuqala umthamo wokunakekela | Yithathe ngokushesha nje lapho ukhumbula. Yithathe ngesikhathi sakho esivamile ngosuku olulandelayo. |
| Uma uphuthelwa imithandazo emibili kuya kweyisithupha (2-6) | Uma ukhumbula, thatha ukudla okubili ngesikhathi esisodwa. Kusukela ngosuku olulandelayo, thatha ukudla okukodwa njengokujwayelekile. |
| Uma imithandazo eyisikhombisa (7) noma ngaphezulu iphuthelwe | Shayela udokotela wakho ngokushesha. Kuzodingeka uphinde uthathe 'umthamo wokulayisha' omusha. |
Yiziphi imiphumela emibi? Ungabhekana kanjani nayo?
Njenganoma yimuphi umuthi, i-Alhemo ingaba nemiphumela emibi.
Imiphumela emibi evamile
Ngenxa yokuthi lokhu kungumjovo, kungase kube nokusabela okuncane endaweni yomjovo . Isibonelo:
- Ukudumba, ukubomvu, ukulunywa, noma ukopha okuncane endaweni yokujova.
- Ukuze usize ngalokhu, ungabeka i-compress epholile endaweni.
- Lokhu kungancishiswa futhi ngokushintsha indawo yomjovo nsuku zonke.
- Ungaphuzi imithi yokubulala izinhlungu noma eminye imithi ngaphandle kokubonisana nodokotela wakho.
Imiphumela emibi kakhulu - qaphela kakhulu ngalokhu!
Kodwa-ke, kukhona into eyodwa ebaluleke kakhulu okufanele uyiqaphele: kukhona ingozi engavamile kakhulu yokwakheka kwamahlule egazi (thrombosis) emithanjeni yegazi .
Lezi zandla, imilenze, amaphaphu, inhliziyo enamaqhubu egaziNoma kungakheka emithanjeni ezindaweni ezifana nobuchopho. Uma ulungiselela noma yikuphi ukuhlinzwa, kufanele utshele nodokotela wakho ngakho.
Uma uhlangabezana nanoma yiziphi izimpawu ezilandelayo, funa iseluleko sezokwelapha ngokushesha ngaphandle kokulibala:
- Ukushaya kwenhliziyo
- Ubuhlungu besifuba noma ukuqina
- Ubunzima bokuphefumula
- Ubunzima bokukhuluma, izinguquko embonweni
- Ubuhlungu noma ukuvuvukala emilenzeni
Uma uhlangabezana nanoma yiziphi zalezi zimpawu, xhumana nodokotela wakho ngokushesha, noma uye egumbini lezimo eziphuthumayo esibhedlela esiseduze (i-ETU). Lokhu kubaluleke kakhulu.
Uthola kanjani umuthi okhethekile onjengalona?
I-Alhemo akuyona imithi ongayithenga ekhemisi elivamile. Lena uhlobo 'lomuthi okhethekile'. Kunenqubo ekhethekile yokuthola le mithi.
Ngemva kokuba udokotela wakho ekunike umuthi, uzothintwa yikhemisi ekhethekile. Yibo abazokunikeza imininingwane yokuthi umuthi ungathunyelwa kanjani ekhaya lakho. Kungase kudingeke futhi uthole imvume kusengaphambili enkampanini yakho yomshuwalense. Ummeleli wenkampani eyenza umuthi angase akwazi ukusiza ngale nqubo. Udokotela wakho uzokuqondisa kukho konke lokhu.
Umlayezo Wokuya Nawe Ekhaya
- I-Hemophilia iwukuntuleka kwenqubo yokujiya kwegazi.
- I-Alhemo iwumjovo wansuku zonke onikezwa ukulawula ukopha, ikakhulukazi ezigulini esezithuthukise 'ama-inhibitor' okwelapha nge-factor.
- Ungalokothi uyeke ukuthatha lo muthi ngaphandle kweseluleko sikadokotela wakho. Njalo thatha umthamo owunikeziwe.
- Qaphela ingozi enkulu yokuqhekeka kwegazi. Uma uhlangabezana nezimpawu ezifana nobuhlungu besifuba noma ubunzima bokuphefumula, iya kudokotela noma ku-ETU ngokushesha.
- Njengoba lo umuthi okhethekile, khuluma nodokotela wakho mayelana nenqubo yokuwuthola futhi uqiniseke ukuthi uyawuqonda kahle.
💬 Comments (0)
Awekho amazwana athunyelwe okwamanje. Faka amazwana akho lapha okokuqala ngqa.
Engeza amazwana akho