Ingabe uke waba nokuqubuka esikhumbeni sakho okungazelelwe okwakungekho ngaphambili, kanye nama-blister alumayo, ngezinye izikhathi agcwele amanzi? Ungase ufune nokwazi ngesimo esibizwa ngokuthi i-bullous pemphigoid. Kuyisifo sesikhumba esingavamile, kodwa kufanelekile ukusazi. Ake sixoxe ngaso ngendlela elula ongayiqonda.
Iyini i-Bullous Pemphigoid? Iluhlobo luni lwesimo?
Kalula nje, i-Bullous Pemphigoid yisifo sesikhumba esingavamile esibangela ukuqubuka okubomvu nokulumayo ebusweni besikhumba, okufana ne-eczema. Ngezinye izikhathi, la maqhuqhuva angakhula abe amaqhuqhuva agcwele uketshezi. Cabanga ngakho njengokulunywa umiyane, kanye namaqhuqhuva amakhulu aluma kakhulu.
Lawa maqhubu angavela endaweni encane yomzimba, noma angasakazeka emzimbeni wonke. Avame ukubonakala ezindaweni lapho isikhumba sigoqeka khona. Isibonelo, ngaphansi kwamakhwapha (i-axilla), esinqeni, noma esiswini. Abanye abantu bangase babe nala maqhubu ezindaweni ezifana nengaphakathi lomlomo, ulimi, umphimbo, umphimbo, noma ngisho namehlo.
Manje ungase uzibuze, "Kungani lokhu kwenzeka?" I-bullous pemphigoid iyisifo sokuzivikela komzimba . Lokhu kusho ukuthi amasosha omzimba wethu, okufanele asivikele, ahlasela ngephutha izicubu ezingaphansi kwesikhumba sethu. Kufana nebutho lethu elihlasela izwe lakithi.
Ubani ongase abe nalokhu? Kuvamile kangakanani?
I-bullous pemphigoid yisimo esivame kakhulu kubantu abangaphezu kweminyaka engama-60. Kodwa-ke, singase sivele nakubantu abasebasha. Nakuba sivame kakhulu emazweni aseNtshonalanga, asivamile kangako emazweni ase-Asia, okungukuthi, engxenyeni yethu yomhlaba.
Lokhu kungenzeka kokubili kwabesilisa nabesifazane, kungakhathaliseki ubulili.
Ingabe kukhona ukuxhumana nezifo zezinzwa?
Yebo, abantu abanezinkinga ezithile zezinzwa kutholakale ukuthi banamathuba amancane okuthuthukisa i-bullous pemphigoid. Lokhu kufaka phakathi:
- Isifo sokulahlekelwa yingqondo
- Isifo sikaParkinson
- Isifo sohlangothi
- Isifo Sokuxhuzula
- I-multiple sclerosis
Lokhu akusho ukuthi wonke umuntu onalezi zimo uzoba ne-bullous pemphigoid. Kodwa-ke, odokotela bathi kungase kube nokuxhumana.
Kuvamile kangangokuthi inani labantu libikwa ukuthi liphakathi kuka-2.4 no-23 ngesigidi. Kodwa-ke, phakathi kwabantu abaneminyaka engu-80 noma ngaphezulu, inani liphakathi kuka-190 no-312 ngesigidi . Lokhu kusho ukuthi amathuba okuba nalesi sifo ayanda njengoba ukhula.
Ingabe i-bullous pemphigoid iyingozi? Ingabe ingaba yingozi empilweni?
Lokhu kungase kuzwakale kusabisa kancane kuwe. Kodwa nansi iqiniso:I-bullous pemphigoid ingaba yingozi empilweni yakho uma unempilo embi noma uma ungayilaphi kahle, ikakhulukazi uma amabhamuza akho ephuka futhi etheleleka. Yingakho sithi kufanele ubonane nodokotela ngokushesha uma ubona noma yini engavamile.
Ziyini izimpawu? Uzibona kanjani?
Izimpawu eziyinhloko ze-bullous pemphigoid ukuvela kwezilonda eziningi ezibomvu ezifana ne-eczema (ama-welts) noma ama-blister agcwele uketshezi (ama-bullae) . Lezi zivame ukubonakala ku:
- Ezandleni
- Emilenzeni
- Esiswini
- Endaweni yesisu
- Ngaphakathi komlomo
Lawa maqhubu avame ukwakheka emaqenjini esikhumba, eduze kwemibimbi yesikhumba. Esikhathini esiningi, awabuhlungu , kodwa uma ephuka, angaba buhlungu futhi abe buhlungu, futhi angaba ngisho nezilonda.
Uketshezi olungaphakathi kwe-blister lungase lucwebe noma lube negazi kancane. Isikhumba esizungeze i-blister singase sibe sijwayelekile noma sishintshe umbala (obomvu, onsomi, onsundu, noma umbala omnyama kancane kunesikhumba sakho).
Izindaba ezinhle ukuthi lokhu kuqubuka kanye nama-blister cishe akunakwenzeka ukuthi kubangele izibazi.
Kungani kuvela i-bullous pemphigoid? Ziyini izimbangela?
Njengoba sishilo ngaphambili, i-bullous pemphigoid yisifo esibangelwa ukungasebenzi kahle kwesimiso somzimba sokuzivikela. Kodwa-ke, odokotela nabacwaningi abakasitholi isizathu esiqondile sokuthi kungani isimiso sethu somzimba sokuzivikela sisabela ngale ndlela.
Eminye imithi ingabangela noma ibhebhethekise lesi simo. Isibonelo, umuthi wesifo sikashukela i-alogliptin. Ukukhanya kwe-Ultraviolet (UV) kanye nemisebe ye-ionizing evela elangeni nakho kungadala noma kubhebhethekise lesi simo.
Ingabe ukudla neziphuzo ezithile kungakwandisa lokhu?
Lona umbuzo abantu abaningi abawubuzayo. Eqinisweni, odokotela abanabo ubufakazi obucacile besayensi bokufakazela ukuthi kukhona ukuxhumana phakathi kokudla kanye ne-bullous pemphigoid. Abanye abantu bathi izimpawu zabo zithuthukile lapho beyeka ukudla okuthile ekudleni kwabo. Kodwa-ke, abukho ubufakazi obuqinile bokufakazela lokhu okwamanje.
Uma une-bullous pemphigoid, khuluma nodokotela wakho mayelana nokuthi ukuyeka ukudla neziphuzo ezithile kungasiza yini. Angase akutshele ukuthi ugcine ijenali yokudla . Ungabe usubona ukuthi ukudla okuthile kwenza izimpawu zakho zibe zimbi kakhulu. Uma ubona ukuthi ziyaba njalo, ungakuqeda kancane kancane lokho kudla bese ubona ukuthi lokho kuyasiza yini.
Ingabe lesi yisifo esithathelwanayo?
Cha, i-bullous pemphigoid ayithelelani. Ayikwazi ukusabalala komunye umuntu ngokuthintana kwesikhumba nesikhumba. Ngakho ungakhathazeki ngayo.
Udokotela ukuxilonga kanjani lokhu ngokunembile?
Uma uya kudokotela, uzoqala ahlole izindawo ezithintekile zesikhumba sakho. Bese bezokubuza imibuzo ethile. Isibonelo:
- "Lezi zimpawu zaqala nini?"
- "Ingabe ubomvu noma igazi emaqakaleni akho?"
- "Ingabe ubunomkhuhlane?"
- "Ingabe usuqalile imithi emisha?"
Ngemva kokubuza imibuzo efana nale, udokotela ufinyelela esiphethweni esiyisisekelo ngokusekelwe ezimpendulweni ozinikezayo.
Yiziphi izivivinyo ezenziwayo ngalokhu?
Ukuqinisekisa ukuxilongwa, udokotela wakho angase akuncome ukuthi wenze lezi zivivinyo:
- Ukuhlolwa kwegazi: Inaliti encane isetshenziswa ukuthatha isampula yegazi emthanjeni osengalweni yakho bese uyithumela elabhorethri ukuze ihlolwe.
- Ukuhlolwa kwesikhumba: Lokhu kuhilela ukuthatha ingxenye encane yesikhumba sakho bese uyithumela elabhorethri ukuze iyohlolwa. Lena ngokuvamile yindlela kuphela yokuqinisekisa imbangela eqondile yalesi simo.
Yiziphi izindlela zokwelapha ezingcono kakhulu?
Ezimweni ezincane ze-bullous pemphigoid, ukwelashwa okungcono kakhulu ukufaka ama-corticosteroid creams noma amafutha ngqo ezindaweni ezithintekile.
Kodwa-ke, ezimweni eziphakathi kuya kwezinzima , udokotela wakho angakunika amaphilisi e-corticosteroid omlomo, njenge-prednisone , ngaphezu kokhilimu we-corticosteroid. Bangakunikeza nezinye izidakamizwa zokulawula amasosha omzimba ezingasiza ekunciphiseni ukusetshenziswa kwama-steroid. Isibonelo, izidakamizwa ezifana ne-dapsone, i-mycophenolate mofetil, i-azathioprine, i-methotrexate, noma i-chlorambucil.
Uma ungakwazi ukuthatha ama-corticosteroids noma eminye imithi yokuvimbela amasosha omzimba, udokotela wakho angase akunike amaphilisi abizwa ngokuthi i-tetracycline noma i-doxycycline .
Ngezinye izikhathi, uma lokhu kwelashwa kungalawuli lesi sifo (amacala abangela ukungezwani komzimba), udokotela angase futhi ancome ukwelashwa okufana ne -Rituximab noma i-IVIG infusion (uketshezi olufakwa emthanjeni) .
Into ebaluleke kakhulu ukuthi, ungasebenzisi noma yimuphi umuthi ngaphandle kokubonisana nodokotela. Nguye ozonquma ukwelashwa okungcono kakhulu kwesimo sakho.
Ingabe kukhona izindlela zokwelapha ezingenziwa ekhaya?
Azikho izindlela zokwelapha zasekhaya ezithile ze-bullous pemphigoid. Kodwa-ke, kunezinto ezithile ongazenza ukusiza ekunciphiseni izimpawu zakho nokunikeza impumuzo ethile.
Ngama-blister esikhumbeni:
- Gqoka izingubo ezithambile nezikhululekile ezenziwe ngemicu yemvelo (isib. ukotini).
- Ungahlali elangeni isikhathi eside kakhulu. Uma uphuma, gqoka isithako sokuvikela ilanga.
- Gcina amanxeba noma izilonda zakho zihlanzekile ngokuzigeza ngensipho namanzi alwa namagciwane. Ngemva kokwenza lokhu, faka ukhilimu we-antiseptic emanxebeni bese uwamboza ngebhandeji elinganamatheli. Lokhu kungasiza ekuvimbeleni ukutheleleka.
- Uma une-bullous pemphigoid emilenzeni yakho, gwema ukuma noma ukuhamba isikhathi eside.
- Faka i-moisturizer, ukhilimu, uwoyela kakhukhunathi, noma ibhotela le-shea ukuze ugcine isikhumba sakho simanzi.
Uma unezilonda emlonyeni:
Uma unezilonda ze-bullous pemphigoid emlonyeni wakho, lawa macebiso angakusiza ukuvimbela izinkinga zokudla okunempilo futhi unciphise ezinye zezimpawu zakho:
- Yidla ukudla okuthambile, njengesobho, ukudla okucoliwe, ama-pudding, kanye ne-applesauce.
- Uma udla ukudla okushisayo, linda kuze kuphole ngaphambi kokudla.
- Gwema ukudla ukudla okuqinile nokubukhali (isib. ama-chips, okusanhlamvu, ama-breadcrumbs, imifino eluhlaza kanye nezithelo).
- Gwema ukudla ukudla okune-asidi ephezulu (isib. i-chili, i-salsa, ama-lime, utamatisi).
- Gwema ukuphuza utshwala.
Ngizozizwa ngingcono nini uma sengiqale ukwelashwa?
Kufanele uqale ukuzizwa ungcono zingakapheli izinsuku ezimbalwa uqale ukwelashwa. Kodwa-ke, lokhu kungahluka kumuntu nomuntu.
Ingabe ikhona indlela yokuvimbela lokhu ukuthi kungenzeki?
Ngeshwa, odokotela nabacwaningi abakayazi indlela yokuvimbela ukukhula kwe-bullous pemphigoid.
Kuzokwenzekani uma ngithola lesi sifo? Kuzokwenzekani esikhathini esizayo?
I-bullous pemphigoid ivame ukuba ngcono ngokwayo phakathi neminyaka emihlanu. Isabela kahle ekwelashweni. Kodwa-ke, ngezinye izikhathi lesi sifo singavuka futhi ngezinye izikhathi singaphela. Ngesikhathi sokululama, ungase ukwazi ukuyeka ukwelashwa (ngeseluleko sikadokotela wakho).
Uma amabhamuza akho eqhuma futhi etheleleka, usengozini yokuthola isimo esisongela ukuphila esibizwa ngokuthi i-sepsis . Ngakho-ke, kubaluleke kakhulu ukunakekela amabhamuza akho.
Yiziphi izikhathi ezinhle kakhulu zokuya kudokotela?
Uma unezimbobo ezingachazeki , bonana nodokotela ngokushesha okukhulu. Njengoba kushiwo ngaphambili, kungcono ukuthola ukuxilongwa nokwelashwa ngokushesha okukhulu.
Imibuzo ebalulekile okufanele uyibuze udokotela wakho
Uma uya kudokotela, kungaba usizo ukubuza le mibuzo:
- "Ungasho kanjani ukuthi ngine-bullous pemphigoid?"
- "Uma ngingenayo i-bullous pemphigoid, yisiphi esinye isifo sesikhumba engingaba naso?"
- "Ngingazilawula kanjani izimpawu zami?"
- "Yimiphi imithi ongincoma yona?"
- "Ingabe leyo mithi inemiphumela emibi?"
- "Yini enye okufanele ngiyenze ukuze ngithuthukise izimpawu zami?"
- "Kuyoze kube nini nginalesi simo se-pemphigoid esinobugovu?"
- "Ingabe kufanele ngibone udokotela wesikhumba noma omunye uchwepheshe?"
Uyini umehluko phakathi kwe-Bullous Pemphigoid ne-Pemphigus Vulgaris?
Zombili lezi zifo zibangela amabhamuza esikhumbeni ngenxa yokungasebenzi kahle kwesimiso somzimba sokuzivikela. I-Pemphigus vulgaris inezimpawu ezifanayo neze-bullous pemphigoid. Kodwa-ke, i-pemphigus vulgaris ivame ukuqala emangqamuzaneni angaphakathi emlonyeni. Bambalwa kakhulu abantu abakha amabhamuza esikhumbeni. Futhi, amabhamuza e-pemphigus vulgaris abuthakathaka kakhulu kunamabhamuza e-bullous pemphigoid.
Uma kuvela ama-blister e-pemphigus vulgaris, avame ukuba ukuguguleka, hhayi ama-blister angaphuki njengase-bullous pemphigoid. Uma une-pemphigus vulgaris, izendlalelo eziphezulu zesikhumba sakho zizohlukana kalula nezendlalelo ezingezansi ngokucindezela okuncane noma ukuhlikihla (lokhu kubizwa ngokuthi uphawu lwe-Nikolsky) .
Nakuba cishe wonke umuntu one-bullous pemphigoid enemiphumela yesikhumba, cishe ingxenye yesithathu (33%) yabo ikhula amabhamuza emlonyeni .
Ekugcineni, umyalezo okufanele uwuthathe uye nawo ekhaya
Kulungile, ngakho-ke sesikhulume kakhulu nge-bullous pemphigoid. Nazi ezinye zezinto ezibaluleke kakhulu okufanele uzikhumbule:
- I-bullous pemphigoid yisifo esingavamile, esibangelwa amasosha omzimba esibangela amabhamuza noma izilonda esikhumbeni.
- Lokhu akuthelelani.
- Kuvame kakhulu ukwenzeka kubantu abadala, kodwa kungenzeka nakubantu abasha.
- Uma isikhumba sakho siqhuma noma siluma ngaphandle kwesizathu, thintana nodokotela ngokushesha.
- Ngokwelashwa okufanele, lokhu kungalawulwa kahle, futhi ngokuhamba kwesikhathi, kungenzeka ukuthi umuntu alulame ngokuphelele.
- Ama-blister angaba yingozi uma etheleleka, ngakho-ke kubaluleke kakhulu ukuwagcina ehlanzekile.
Uma unalezi zimpawu, ungesabi. Ngokulandela iseluleko sezokwelapha, ungalulama ngokushesha.
👩🏽⚕️ Imibuzo eyengeziwe (ama-FAQ)
💬 Ingabe i-Bullous Pemphigoid iyisifo sesikhumba?
Cha. Lesi yisifo esingavamile sokuzivikela komzimba esibangela ukuthi amasosha omzimba wakho ahlanye futhi ahlasele izicubu zesikhumba sakho. Lokhu kubangela ukuthi kwakheke amabhamuza amakhulu, agcwele uketshezi (ama-bullae) phakathi kwesikhumba kanye nongqimba olungaphansi.
💬 Ingabe lokhu kwenzeka kakhulu kubantu abadala?
Yebo. Lesi sifo sivame ukwenzeka kubantu abaneminyaka engaphezu kwengu-60, ikakhulukazi labo abaneminyaka engaphezu kwengu-80. Lawa maqhubu angavela ezandleni, ezinyaweni, nasesiswini, futhi ngezinye izikhathi emlonyeni (ulwelwesi lwamafinyila).
💬 Yini engingayenza ngalokhu? Ingabe kuzolulama kalula?
Lesi sifo sibangela ukulunywa kakhulu kwesikhumba. Njengokwelashwa, odokotela banikeza ama-steroid anamandla (ama-Corticosteroids - isibonelo: i-Prednisolone) ngesimo samaphilisi noma okhilimu. Le mithi kufanele isetshenziswe njalo izinyanga noma iminyaka, kodwa lesi sifo singalawulwa kahle ngemithi.
I- Bullous Pemphigoid, Izifo zesikhumba, Ama-blister amanzi, Ama-blister alumayo, Izifo zokuzivikela komzimba, Izifo zesikhumba, Isifo sokuzivikela komzimba, Ama-blister esikhumba











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