Ingabe ingane yakho encane ivame ukukhala ngekhanda? Noma ingabe izizwa indikindiki noma ibuthakathaka? Ngezinye izikhathi sicabanga ngalokhu njengesifo esincane esivamile, kodwa uma lezi zimpawu ziqhubeka, kuwumqondo omuhle ukukhathazeka kancane. Ngoba lokhu kungaba izimpawu zesimo esingavamile kodwa esingaba sibi esibizwa ngokuthi i-Hydromyelia esingathinta izingane ezincane. Ngakho-ke, ake sixoxe ngalokhu ngendlela elula namuhla.
Kuyini i-Hydromyelia? Ake sikuqonde kalula.
Kalula nje, i-hydromyelia iwukwanda okungavamile komsele ophakathi, isikhala esingaphakathi komsele womgogodla, phezulu komsele womgogodla ezinganeni ezincane. Cabanga ngale ndlela: kukhona ithubhu elincane elihamba phansi emgogodleni wethu elibizwa ngokuthi umsele ophakathi . Uma lokhu kwanda, kwakha isikhwama esigcwele uketshezi esibizwa ngokuthi i-syrinx .
Lo msele ophakathi uvame ukugcwaliswa ngoketshezi olukhethekile olubizwa ngokuthi uketshezi lwe-cerebrospinal (CSF) . Lolu ketshezi lwe-`(CSF)` luvikela ubuchopho bethu kanye nomgogodla ezingozini ezahlukahlukene, futhi lubanikeza nokudla okunomsoco okudingekayo. Ngakho-ke, lapho lolo `(syrinx)` lwenzeka, lolu ketshezi lwe-`(CSF)` lunganqwabelana futhi lubangele izinkinga ezengeziwe.
Ubani othola i-hydromyelia? Iyiphi ingxenye yobuchopho ethintayo?
Lesi simo, esibizwa ngokuthi i-hydromyelia, senzeka e -ventricle yesine yobuchopho . Lokhu kutholakala phansi kobuchopho, eduze kwe-brainstem . Le ventricle yesine ixhunywe emseleni ophakathi oqhubeka phansi emgogodleni. Lokhu kufana nethangi lamanzi elihlinzeka ngamanzi epayipini.
Lo msele ophakathi uvalwe ngaphakathi uhlobo olukhethekile lweseli olubizwa ngokuthi `amaseli e-ependymal` . Lawa maseli atholakala kuphela kuma-ventricles obuchopho kanye nasemseleni ophakathi womgogodla. Lokhu kubalulekile ukukukhumbula, ngoba kusiza ukuhlukanisa lokhu kwesinye isimo esizoxoxa ngaso kamuva.
Lesi simo (i-Hydromyelia) sivame ukubonakala ezinganeni ezizalwa zinezimo ezithile zobuchopho eziyinkimbinkimbi . Isibonelo:
- (Uhlobo lwe-Chiari malformation II) : Lolu ushintsho oluzalwa nalo (oluzalwa nalo) esakhiweni sobuchopho, ikakhulukazi engxenyeni engezansi yobuchopho.
- (Dandy-Walker syndrome) : Lena futhi inkinga engavamile yokuzalwa eyenzeka ekukhuleni kwengxenye engemuva yobuchopho (i-cerebellum).
- (Hydrocephalus) : Yilokhu okungenzeka ukuthi wake wakuzwa kubizwa ngokuthi "ukuqongelela kwamanzi ebuchosheni." Izingane ezinalesi simo nazo zinamathuba amaningi okuthuthukisa `(Hydromyelia)`.
Akuvamile kakhulu, okusho ukuthi akuvamile kakhulu, lesi simo singavela nasezinganeni ngezinye izizathu. Izizathu ezinjalo zifaka:
- Izimila zobuchopho
- Ukutheleleka kobuchopho, isibonelo, i-encephalitis
- Ukulimala kobuchopho okubuhlungu
Lokhu kuyithinta kanjani inhlalakahle yengane?
Uma leso simila esigcwele uketshezi esikhulume ngaso ekuqaleni, i-`(syrinx)`, iqala ukukhula, ibeka ingcindezi emgogodleni. Cabanga ngakho njengokugcwalisa ibhaluni ngamanzi, futhi njengoba ikhula, isunduza izinto ezizungezile, akunjalo? Yilokho okwenzekayo ngalena. Lokhu kucindezela kubangela ukuthi imizwa ebucayi emgogodleni icindezelwe futhi yonakale . Yilapho kuvela khona izimpawu ezahlukahlukene .
Ingabe i-Hydromyelia ne-Syringomyelia ziyinto efanayo? Uyini umehluko?
Yebo, la magama amabili azwakala efana kakhulu. Izimpawu nazo zifana kakhulu. Kuzo zombili izimo, i-cyst egcwele uketshezi (ukukhula okufana ne-cyst) kwakheka emgogodleni futhi kuthinta amangqamuzana ezinzwa. Kodwa kuneminye imehluko emincane, kodwa ebaluleke kakhulu phakathi kwala magama amabili. Ake sibone ukuthi iyini?
Mayelana ne-Hydromyelia:
- Lokhu kuthinta kakhulu izinsana nezingane ezincane . Akuvamile kakhulu ukuthi abantu abadala bakuthole lokhu.
- Leso sikhwama (`syrinx`) esigcwele uketshezi sakha ngaphakathi komsele ophakathi womgogodla.
- Ngaphakathi kwaleyo cyst (`syrinx`) kukhona amaseli e-ependymal akhethekile esikhulume ngawo ngaphambili.
Mayelana ne-Syringomyelia:
- Lokhu kuvame ukubonwa kubantu abadala .
- I-cyst yoketshezi (`syrinx`) ikhula ngaphandle komsele ophakathi, okungukuthi, eduze kwayo (kodwa ngaphandle komsele ophakathi) .
- Awekho amaseli e-ependymal ngaphakathi kwalesi simila (`syrinx`).
Lezi zinguquko zibaluleke kakhulu kodokotela ukuze bathole ukuxilongwa okunembile futhi banqume ukwelashwa okufanele kakhulu.
Kungani lokhu kwenzeka nge-hydromyelia? Iyini imbangela?
Uma ngikhuluma iqiniso, abacwaningi basathola ukuthi yini ngempela ebangela lokhu. Okusho ukuthi, kunzima ukusho ngokuqinisekile ukuthi "lena imbangela". Nakuba kutholakale ukuthi ihlotshaniswa nezimo ezifana ne-`(Chiari malformation)` kanye ne-`(Dandy-Walker syndrome)` esikhulume ngazo ngaphambili, kwenziwa ucwaningo olwengeziwe mayelana nokuthi lokho kuxhumana kwenzeka kanjani.
Ziyini izimpawu zalokhu? Ukubona kanjani?
Kwabanye abantwana, i-syrinx incane kakhulu. Uma kunjalo, kungase kungabi nazimpawu , noma noma zikhona, kungase kungabi inkinga enkulu. Ingane ingadlala futhi isebenze ngendlela evamile.
Kodwa-ke, uma i-syrinx inkulu kakhulu, ingacindezela imizwa emgogodleni, okubangela ubuhlungu be-neuropathic . Lobuhlungu bungazwakala ngezindlela ezahlukene:
- Ukuzizwa sengathi kukhona into evuthayo emzimbeni wonke : njengokungathi ivutha.
- Ubuhlungu obungazelelwe, obubukhali, njengokushaywa ugesi noma ukugwazwa ngommese .
- Ukuba ndikindiki : Ngezinye izikhathi ungase ungazizwa isandla noma unyawo lwakho luthinta umzimba wakho.
- Umuzwa wokuzwa izinzipho nezinaliti noma umuzwa wokuthuthumela .
Ngaphezu kwalezi zinhlungu zemizwa, kungase kube nezinye izimpawu:
- Ubuhlungu bekhanda obuvamile : Lokhu akufani nobuhlungu bekhanda obuvamile, kungaba nzima kakhulu.
- Ukulahlekelwa ukuzwela ukushisa nokubanda : Lokhu kuyingozi kancane, njengoba ingane ingathinta into eshisayo ngokungazi bese izishisa, noma ibhekane nomkhuhlane bese iba nezinkinga.
- Ukuqina kwemisipha: Izitho zomzimba ziyaqina futhi kube nzima ukuzigoba.
- I-Scoliosis : Abanye abantwana bangase babe nomgogodla ogobile ohlangothini olulodwa.
- Ubuthakathaka ezingalweni nasemilenzeni : Ingane ingase ikuthole kunzima ukudlala, ukugijima, ukugxuma, futhi ingase ibe nobunzima bokuhamba.
Cabanga ngengane yakho idlala bese ikhala ngokuzumayo ithi, "Mama, isandla sami siyathuthumela, kuzwakala sengathi izintuthwane ziyasidla." Noma, zihlala zithi, "Ngikhathele, imilenze yami izizwa ingasasebenzi." Ungayeki nje izinto ezinjengalezi.
Odokotela bakuthola kanjani lokhu?
Uma ingane yakho inalezi zimpawu, kufanele nakanjani ubonane nodokotela. Udokotela uzokwenza izivivinyo eziningana ukuze anqume ukuthi lokhu kuyi-hydromyelia.
1. Ukuhlolwa kwemizwa : Okokuqala, udokotela uzohlola ingane kahle. Uzokubuza ngezimpawu zengane nokuthi zinzima kangakanani. Uzobheka indlela ingane ehamba ngayo, egijima ngayo, egxuma ngayo, ephakamisa futhi yehlisa ngayo imilenze yayo, amandla emisipha kanye nezinzwa.
2. I-MRI scan : Lena yindlela ebaluleke kakhulu nenembile yokuxilonga lesi sifo. I-MRI scan ingathatha izithombe ezinemininingwane zomgogodla nobuchopho. Lokhu kungabona ngokucacile ukuthi kukhona yini i-cyst (syrinx) ewuketshezi, ukuthi inkulu kangakanani, nokuthi kukhona yini okunye ukukhubazeka emgogodleni.
3. I-Electromyography (EMG) : Lokhu kuhlolwa kungenziwa ngezinye izikhathi. Kunganikeza umbono wokusebenza kwezinzwa nemisipha. Ikakhulukazi, kungasiza ukuhlukanisa lokhu kwezinye izimo ezifana ne-Syringomyelia.
Ingabe i-cyst encane ingaba yi-hydromyelia?
Yebo, lo mbuzo ubalulekile. Ngisho noma i-MRI ikhombisa i-cyst encane kakhulu, mhlawumbe efana ne-slit, ku-ventricle yesine, lokho kungaba yi-Hydromyelia. Ngisho noma i-cyst incane kakhulu, isengadala izimpawu .Ngakho-ke, ukuze kutholakale futhi kutholakale ngokunembile ngisho nezimila ezincane njengalezi, kudingeka udokotela onolwazi ochwepheshe bezinzwa.
Yiziphi izindlela zokwelapha lokhu? (Ukwelashwa)
Ukwelashwa kwe-hydromyelia kuncike ezimpawini zengane kanye nobunzima bazo. Akuzona zonke izingane ezinikezwa ukwelashwa okufanayo.
- Izimpawu ezincane noma ezingenazo nhlobo : Uma ingane yakho inezimpawu ezimbalwa kakhulu, noma ingenazo nhlobo izimpawu, kungase kungadingeki ukwelashwa . Kodwa-ke, udokotela uzoqhubeka nokuqapha ingane yakho ukuze abone ukuthi kukhona yini izinguquko.
- Izimpawu eziphazamisayo : Uma izimpawu ezifana nokuqina kwemisipha kanye nobuthakathaka ziphazamisa imisebenzi yansuku zonke yengane yakho, ukwelashwa ngokomzimba kunganikeza impumuzo enkulu. Uchwepheshe wezokwelapha ngokomzimba uzofundisa ingane yakho izivivinyo kanye namasu okuqinisa imisipha afanele ingane yakho.
- Izimpawu ezimaphakathi nezinzima : Uma izimpawu zinzima, okusho ukuthi ingane izwa ubuhlungu obukhulu nokungakhululeki, ukuhlinzwa kuvame ukudingeka .
Ingabe ngidinga ukuhlinzwa? Hlobo luni lokuhlinzwa?
Uma izimpawu zinkulu, ukuhlinzwa kuvame ukuba yisisombululo esingcono kakhulu. Lokhu kuhilela ukufaka i-shunt ukusiza ubuchopho bengane ukukhipha i-CSF (uketshezi lomgogodla) ngokwemvelo.
Le 'shunt' iyinto ethambile kakhulu, efana nethubhu encane. Idala indlela yokuthi uketshezi oluningi lwe-'CSF' oluqongelele 'ku-ventricle yesine' lugeleze luye kwenye ingxenye yomzimba (ngokuvamile umgodi wesisu). Lokhu kunciphisa ingcindezi ngaphakathi kwe-'syrinx' futhi kunciphisa izimpawu.
Lokhu kuhlinzwa kwe-shunt kwenziwa udokotela ohlinza izinzwa. Kunganciphisa okwesikhashana noma unomphela izimpawu . Kodwa-ke, ezinye izingane zingadinga i-shunt engaphezu kweyodwa ngesikhathi sokuphila kwazo, noma zingadinga ukuhlinzwa ukuze kulungiswe i-shunt ekhona.
Ayikho indlela yokuvimbela lokhu ukuthi kungenzeki?
Ngeshwa, imbangela eqondile ye-hydromyelia ayaziwa, ngakho-ke okwamanje ayikho indlela eqondile yokuyivimbela . Njengoba sishilo ngaphambili, ivame ukuhlotshaniswa nezinye izimo zokuzalwa (ezikhona lapho kuzalwa), ngakho-ke uma lezo zimo eziyisisekelo zingenakuvinjelwa, kunzima ukuvimbela nalesi.
Liyini ikusasa lomntwana one-Hydromyelia? (Isibikezelo)
Lona umbuzo omkhulu kunayo yonke umzali anayo. Kunzima ukusho noma yini ecacile ngekusasa lomntwana one-`(Hydromyelia)`, ngoba kuyahlukahluka kuye ngengane.
- Ezinganeni ezincane kakhulu, izimpawu ziyaphela zodwa, ngaphandle kokwelashwa, noma zizinze ezingeni elifanayo . Kodwa lokhu kungathatha iminyaka.
- Izingane eziningi zithola impumuzo enkulu ezimpawini zazo ngemva kokuba ne-shunt. Kodwa-ke , ngezinye izikhathi izimpawu zingaphinde zibuye . Okusho ukuthi, isifo esidala singabuya ngemva kwesikhashana.
- Ngakho-ke, kubaluleke kakhulu ukuqhubeka nokubona udokotela kanye nokuhlolwa kwengane yakho (izivivinyo ze-neurological) kanye, uma kudingeka, ne-MRI scan. Lokhu kuzosiza ekutholeni kusenesikhathi uma izimpawu zibuya noma uma kunenkinga nge-shunt.
Injani impilo yansuku zonke yengane ene-Hydromyelia?
Indlela lesi simo esithinta ngayo impilo yansuku zonke yengane incike ngokuphelele ekutheni izimpawu zimbi kangakanani.
- Uma izimpawu zincane kakhulu , ingane ingenza imisebenzi yayo yansuku zonke njengokujwayelekile. Kungase kube nokungakhululeki okuncane, kodwa kungase kungabi yinkinga ngaso sonke isikhathi.
- Kodwa uma kunezimpawu eziphakathi kuya kwezinzima, impilo ingaba yinselele encane enganeni nasemndenini :
- Ubuhlungu : Lokhu kungafika kudlule kungazelelwe. Njengoba ungeke wazi ukuthi kuzofika nini noma kanjani, ingane ingaba novalo njalo futhi ingakhululeki.
- Ukuqina kwemisipha noma ubuthakathaka : Lokhu kungenza kube nzima ngengane ukunyakaza, ukudlala, ukukhasa, ukuhamba, nokwenza umsebenzi wesikole. Bangase bagweme imisebenzi abayijabulelayo nezinye izingane.
- Ubuhlungu bekhanda : Ubuhlungu bekhanda obuhlala bukhona bungabangela ingane ukuba ithukuthele, ingahlaliseki, futhi iphuthelwe umsebenzi wesikole.
Abazali badinga isineke esikhulu, ukuqonda, kanye namandla okunakekela ingane efana nale. Kubaluleke kakhulu ukulandela imiyalelo kadokotela, ukwenza izinto ezifana nokwelashwa ngokomzimba ngendlela efanele, nokunikeza ingane ukwesekwa kwengqondo.
Izinto ezibaluleke kakhulu okudingeka sizikhumbule (Umyalezo Wokuya Ekhaya)
Kulungile, ngakho-ke, kusukela kulokho esikhulume ngakho, lezi yizinto ezibaluleke kakhulu okudingeka uzikhumbule:
- I-Hydromyelia yisimo esingavamile kodwa esikhathazayo lapho kwakheka khona isikhwama esigcwele uketshezi (i-syrinx) emseleni ophakathi womgogodla ezinganeni ezincane.
- Njengoba imbangela eqondile yalokhu ingaziwa, ayikho indlela yokukuvimbela.
- Izimpawu ziyahlukahluka kuye ngengane. Eziyinhloko ukuvuvukala, ukungazweli, ubuthakathaka ezithweni, ikhanda elibuhlungu, kanye nokungakwazi ukuzwa ukushisa/ukubanda.
- Lesi sifo singatholakala ngokunembile kuphela nge-MRI scan.
- Ukwelashwa kuncike ezimpawini. Abanye abantu bangase bangadingi ukwelashwa, abanye bangadinga ukwelashwa ngokomzimba, kanti abanye bangadinga ukuhlinzwa kwe-shunt.
- Into ebaluleke kakhulu ukuthi uma usola ukuthi ingane yakho inesinye salezi zimpawu, ungesabi futhi uthintane nodokotela ofanelekayo ngokushesha, ikakhulukazi udokotela wezinzwa. Ukutholwa kusenesikhathi kungasiza kakhulu ekuhlinzekeni ingane ngokwelashwa okudingekayo nokuthuthukisa ikhwalithi yempilo yayo.
Uma uneminye imibuzo mayelana nalokhu, qiniseka ukuthi ukhuluma nodokotela wakho. Ngithemba ukuthi lolu lwazi luzokusiza!
'I-Hydromyelia, intambo yomgogodla, ubuchopho, i-cyst yoketshezi, i-syrinx, i-CSF, izifo zezingane, izifo zezinzwa, ukuhlinzwa kwe-shunt

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