Uyazazi lezi zinto nge-ventricle yesobunxele yenhliziyo yakho? (I-Ventricular Engacindezelwa Ngasohlangothini Lwesobunxele - LVNC) Ake sixoxe!

Namuhla sizokhuluma ngesimo senhliziyo esiyinkimbinkimbi kancane, kodwa esingaba sibaluleke kakhulu. Kungenzeka ukuthi awukaze uzwe ngalokhu ngaphambili. Kubizwa ngokuthi yi-Left Ventricular Non-Compaction (LVNC) njengoba odokotela bekubiza kanjalo. Igama lingase lizwakale njengento enkulu, kodwa ungakhathazeki, masiyigcine ilula.

Ngakho-ke kuyini ukwehluleka kwenhliziyo okungaxinani kwe-ventricular yangakwesobunxele (i-LVNC)?

Kalula nje, lesi yisimo esenzeka lapho igumbi elingezansi ohlangothini lwesobunxele lwenhliziyo yethu, i-Left Ventricle, lingakhuli kahle. Cabanga ngakho, ngokuvamile le ventricle yesobunxele yenhliziyo yethu iyisiqeshana senyama esinamandla kakhulu nesibushelelezi. Yiyona ngxenye eyinhloko epompa igazi emzimbeni wethu wonke. Kodwa kumuntu onale (LVNC), i-ventricle yesobunxele ifana nesiponji, ijiyile kancane, futhi ihlelwe njengenetha. Inemvelo enamagquma, njengengaphakathi lesinkwa.

Lokhu kuvame ukubhekwa njengesifo senhliziyo esizalwa naso. Lokhu kusho ukuthi ungase ube nalesi simo enhliziyweni yakho kusukela ngesikhathi uzalwa . Uma singelashwa kahle, lesi (LVNC) singaholela ezinkingeni ezinkulu zenhliziyo, okungukuthi, isifo senhliziyo.

Lesi simo se-LVNC sithinta kanjani ukusebenza kwenhliziyo?

Manje bheka, i-ventricle yesobunxele yenhliziyo yethu inomsebenzi obaluleke kakhulu. Yilena epompa igazi elinomoya-mpilo elivela emaphashini liye emzimbeni wonke. Njengenjini yamanzi. Kodwa-ke, lapho lesi simo (LVNC) sivela, i-ventricle yesobunxele, efana nesiponji, ayikwazi ukufinyela noma ukuphumula kahle. Okusho ukuthi, inobunzima bokuqinisa nokusunduza igazi phambili, noma ukuphumula nokuligcwalisa ngegazi futhi. Ngakho-ke, umphumela uba ukuthi umsebenzi wokupompa igazi liye emzimbeni wonke awuwenzi kahle . Yingakho izinkinga ezahlukahlukene ziqala ukuvela.

Kungavamile kangakanani lesi simo esibizwa ngokuthi i-LVNC?

Empeleni lesi yisimo esingavamile. Ngokusho kochwepheshe bezokwelapha, cishe abantu abayishumi nambili kuphela kwabayisigidi abatholakala benalesi simo minyaka yonke. Kodwa-ke, inani langempela lingase libe phezulu kakhulu . Isizathu siwukuthi abanye abantu ababonisi zimpawu. Bese bengayi kudokotela, ngakho-ke abatholi ukuxilongwa.

Ziyini izimpawu ze-LVNC?

Lokhu kuyinto ebaluleke kakhulu. Abanye abantu bangase bangakhombisi zimpawu . Kodwa-ke, abanye bangaba nezinkinga ezinkulu zenhliziyo. Isibonelo, ukufa kwenhliziyo ngokuzumayo kungenzeka. Cishe izingxenye ezimbili kwezintathu zabantu abane-LVNC basengozini yokuthola ukwehluleka kwenhliziyo .

Kulungile, ake sibone ukuthi hlobo luni lwezimpawu umuntu one-(LVNC) angase azibonise:

Izimpawu ezivame ukubonakala:

• Kungakheka amahlule egazi . Lawa ayingozi kakhulu, ngoba uma la mahlule eya ebuchosheni noma emaphashini, kungaba yinkinga enkulu.
• Ungase ube nobunzima bokuphefumula ngenkathi ulele embhedeni.
• Ukuquleka .
• Ukushaya kwenhliziyo - Lokhu kungazwakala sengathi isigubhu sishaya ngaphakathi esifubeni, noma sengathi inhliziyo iyagijima.
• Ukungakwazi ukuzivocavoca, ukuphelelwa umoya ngisho noma umatasa kancane (i-Dyspnea) .
• Isigqi senhliziyo esingajwayelekile (i-Arrhythmia) .
• Ukuvuvukala kwemilenze (i-Lymphedema) - ikakhulukazi emaqakaleni.
• Ukuphelelwa umoya / Ukuphelelwa umoya - Ukuzizwa sengathi uphelelwa umoya ngisho noma ungenza umzamo omncane.

Kungani lesi simo se-LVNC senzeka? Ziyini izimbangela?

Esikhathini esiningi, lesi simo (LVNC) sibangelwa ushintsho lwezakhi zofuzo (ukuguqulwa kwezakhi zofuzo) olwenzeka ngaphambi kokuba uzalwe. Lokhu kuyinto eyinkimbinkimbi kakhulu. Lolu shintsho lwezakhi zofuzo lungenzeka ngokungahleliwe, okusho ukuthi ngaphandle kwesizathu, noma lungazuzwa kubazali bakho. Lokho kusho ukuthi kungaba yinto eyenzeka emindenini. Cabanga nje, eminye imindeni inezinga eliphezulu lalolu hlobo lwesifo senhliziyo.

Futhi, iphesenti elincane kakhulu labesifazane lingase libe ne-LVNC okokuqala ngesikhathi sokukhulelwa ngaphandle kwesizathu esibonakalayo. Odokotela bacabanga ukuthi lokhu kungenzeka ngenxa yokucindezeleka okwengeziwe emisipheni yenhliziyo ngesikhathi sokukhulelwa. Kwabanye besifazane, lezi zimpawu ziyaphela ngemva kokubeletha. Kodwa kwabanye, i-LVNC ingaba nemiphumela yesikhathi eside.

Odokotela bakuthola kanjani lesi simo se-LVNC?

Udokotela uzokwenza izivivinyo eziningana ukuze anqume ukuthi unalesi simo "(LVNC) noma cha. Ake sibheke ukuthi ziyini:

• I-Echocardiogram: Lokhu kubheka ukuthi inhliziyo yakho ihambisa igazi kahle kangakanani, ukuthi ama-valve asebenza kahle kangakanani, nokuthi ngabe kukhona yini izinkinga ngama-valve. Kufana nokuskena kwenhliziyo nge-ultrasound. Yilapho uqala ukubona khona isimo se-ventricle yesobunxele esinjenge-sponge.
• I-Electrocardiogram (ECG): Lokhu kulinganisa ukusebenza kukagesi kwenhliziyo yakho. Kungabona noma yiziphi izinkinga ngesigqi senhliziyo yakho.
• Ukuhlolwa okukhethekile kwezithombe: Lokhu kufaka phakathi ukuskena kwe-CT yenhliziyo kanye nokuskena kwe-magnetic resonance (MRI). Lokhu kungabonisa isakhiwo senhliziyo, njengokuthi inhliziyo yenziwe kanjani kanye nobukhulu bezindonga zayo. Ku-LVNC, ukubukeka okufana nesiponji kubonakala ngokucacile kulezi ziskena.
• I-Coronary angiogram: Lokhu kuhlola ukuthi igazi ligeleza kanjani emithanjeni yenhliziyo ehambisa igazi enhliziyweni, nokuthi ngabe kukhona yini ukuvinjelwa. Ngezinye izikhathi lokhu kuhlolwa kungadingeka futhi ukuze kunqunywe ezinye izimo zenhliziyo.

Yiziphi izindlela zokwelapha lesi simo se-LVNC?

Ukwelashwa kwe-LVNC kuyahlukahluka kuye ngezimpawu zakho. Akuwona wonke umuntu ophathwa ngendlela efanayo. Isibonelo, uma unesifo senhliziyo, udokotela wakho angase akunike imithi efana nalokhu:

• Ama-inhibitors e-Angiotensin-converting enzyme (ACE inhibitors): Isibonelo, i-benazepril (Lotensin®) noma i-lisinopril (Prinivil®, Zestril®) noma i-sacubitril-valsartan (Entresto®) (ama-inhibitors e-angiotensin-neprilysin). Lawa asebenza ngokuphumula nokuvula imithambo yegazi yakho (imithambo yegazi nemithambo yegazi) ukuze kube lula ukuthi igazi ligeleze kuyo. Lokhu kunciphisa umthwalo womsebenzi enhliziyweni.
• Ama-Beta-blocker: Isibonelo, i-metoprolol (Lopressor®, Toprol XL®) noma i-atenolol (Tenormin®). Lawa avimba ama-hormone athile (isb. i-adrenaline), ehlisa umfutho wegazi futhi elawula izinga lokushaya kwenhliziyo.
• I-Digoxin (Digoxin®, Lanoxin®): Lokhu kulawula ukushaya kwenhliziyo yakho, kwandisa kancane amandla okupompa kwenhliziyo yakho, futhi kuthuthukisa ukujikeleza kwegazi.
• Ama-diuretics noma "amaphilisi amanzi": Lawa asebenza ngokubangela ukuthi umzimba ukhiphe usawoti namanzi amaningi ngomchamo. Lokhu kunciphisa ukuvuvukala futhi kunciphisa umthwalo womsebenzi enhliziyweni.

Ngezinye izikhathi, uma kunengozi yokuma kwenhliziyo ngokuzumayo, udokotela angase ancome ukufakwa kwedivayisi ebizwa ngokuthi i-Implantable Cardioverter Defibrillator (ICD) ngaphansi kwesikhumba senhliziyo. Lena idivayisi encane esebenza ngebhethri. Ithola isigqi esisheshayo, esisongela ukuphila enhliziyweni futhi ilethe ukushaqeka kukagesi enhliziyweni ukuze kubuyiselwe isigqi esijwayelekile. Ezimweni ezimbi kakhulu, uma ezinye izindlela zokwelapha zingaphumeleli, kungadingeka ukufakelwa kwenhliziyo .

Ingabe lesi simo se-LVNC singalapheka ngokuphelele? Ingabe singaguqulwa?

Cha. Okwamanje akukho ukwelashwa kwe-LVNC . Okusho ukuthi, akunakuguqulwa. Kodwa ungakhathazeki. Ukwelashwa kungathuthukisa ikhwalithi yempilo yakho futhi kunciphise izinkinga ezingabangelwa yisifo senhliziyo . Futhi, njengoba ngishilo ngaphambili, ezimweni ezimbi kakhulu, kungadingeka ukufakelwa inhliziyo.

Singakugwema kanjani lesi simo se-LVNC?

Ayikho indlela yokuvimbela i-LVNC. Lokhu kungenxa yokuthi ivame ukubangelwa izici zofuzo. Kodwa-ke, uma une-gene mutation ebangela lesi simo, noma uma ucabanga ukuthi ungaba nayo (isibonelo, uma othile emndenini wakho enalesi simo), ukuhlolwa kofuzo kungaba usizo kakhulu.Umeluleki wezakhi zofuzo uzochaza imiphumela yokuhlolwa kwakho kuwe nomndeni wakho. Bazokusiza uqonde ukuthi kusho ukuthini ukuba ne-LVNC nokuthi iyini ingozi yakho yokuyidlulisela ezinganeni zakho.

Ingabe zikhona ezinye izimo zezokwelapha ezihlobene nalesi simo se-LVNC?

Yebo. Ngezinye izikhathi lesi simo esibizwa ngokuthi (LVNC) singabonakala njengengxenye yezinye izimo zofuzo (ama-syndromes). Lezi ziyinkimbinkimbi kakhulu, kodwa odokotela baphinde bacabangele lezi zimo lapho bexilonga (LVNC). Nazi izibonelo ezimbalwa:

• I-Barth syndrome
• I-Noonan syndrome
• I-Roifman syndrome
• Isifo sikaToriello Carey

Liyini ikusasa lomuntu one-LVNC? Liyini izinga lokuphila elilindelekile?

Umbono womuntu one-LVNC ungahluka. Uhlukahluka kumuntu nomuntu. Ngokwelashwa okuhle, izimpawu zingalawulwa , futhi abanye abantu baphila isikhathi eside sokuphila.

I-LVNC yisimo esingaba yingozi, kodwa akuhlali kunjalo . Iningi labantu abane-LVNC abafi ngenxa yalesi sifo. Into ebaluleke kakhulu ukubona udokotela wenhliziyo njalo bese uhlolwa . Angakusiza ukuphatha impilo yenhliziyo yakho futhi anciphise ingozi yezinkinga.

Uma mina noma ingane yami ine-LVNC, yimiphi imibuzo okufanele ngiyibuze udokotela?

Uma wena noma ingane yakho ninayo (i-LVNC), noma uma ninezinkinga, kuwumqondo omuhle ukubuza udokotela wakho imibuzo efana nale:

• Yini okungenzeka kakhulu ukuthi iyimbangela yesifo se-LVNC sengane yami/yengane yami? (okungukuthi, ingabe kuyizakhi zofuzo noma okunye)
• Ingabe uncoma ukuhlolwa kofuzo kwe-LVNC? Uma kunjalo, kungabaluleka yini kwamanye amalungu omndeni?
• Yiziphi izivivinyo mina/ingane yami okudingeka ngizihlole ukuze ngithole i-LVNC? Yini engingayilindela kuzo?
• Yiziphi izindlela zokwelapha ze-LVNC? Yikuphi ukwelashwa okungcono kakhulu kimi/enganeni yami? Ingabe kukhona imiphumela emibi kulezi zindlela zokwelapha?
• Uma mina noma ingane yami sihlaselwa yisifo senhliziyo ngokuzumayo, yiziphi izimpawu? Yini okufanele ngiyenze ngokushesha?

Le mibuzo izokusiza ukuthi uxoxe ngayo nodokotela wakho futhi uthole ukuqonda okungcono ngesimo sakho.

Ngakho-ke, yiziphi izinto ezibaluleke kakhulu okudingeka sizikhumbule kule ndaba?

Inhliziyo engasebenzi kahle ye-ventricular yesobunxele (LVNC) iyisifo senhliziyo esingavamile, esivame ukuzalwa naso. Lokhu kwenzeka lapho i-ventricle yesobunxele yenhliziyo ingakhuli kahle. Esikhundleni sokuba yisicubu esibushelelezi nesiqinile, iba nkulu futhi ibe yi-sponge. Lokhu kubangela ukuthi inhliziyo ingapompi igazi kahle.

Uma une-(LVNC),Into ebaluleke kakhulu ukubona udokotela wenhliziyo njalo bese ulandela iseluleko sakhe. Nakuba kungekho ikhambi lalokhu, ukwelashwa udokotela wakho akunikezayo kunganciphisa ingozi yakho yezinkinga futhi kuthuthukise ikhwalithi yokuphila kwakho. Kubalulekile ukungesabi bese uthola ukwelashwa okufanele . Khumbula, awuwedwa, futhi odokotela bakhona ukukusiza.

Isifo senhliziyo, i-ventricle yesobunxele, i-LVNC, izimpawu zesifo senhliziyo, ukwehluleka kwenhliziyo, izifo zofuzo, ukwelashwa kwesifo senhliziyo