Skip to main content

Iyini i-Lennox-Gastaut Syndrome (LGS)? Ake sixoxe ngayo!

Iyini i-Lennox-Gastaut Syndrome (LGS)? Ake sixoxe ngayo!

Ingabe ingane yakho encane inesifo sokuwa njalo? Ingabe inezinguquko ezinkulu ekufundeni nasekuziphatheni? Uma kunjalo, engizokusho kungaba yinto ebaluleke kakhulu kuwe. Namuhla sizokhuluma nge -Lennox-Gastaut Syndrome , noma (LGS) ngamafuphi, isimo sokuwa esinzima futhi esinzima ukuselapha. Lokhu kungaqala esemncane. Kodwa ungakhathazeki, imithi emisha kanye nokwelashwa sekuyatholakala manje.

Iyini ngempela i-Lennox-Gastaut syndrome (LGS)? Ngubani oyitholayo?

Kalula nje, i-LGS uhlobo olubi kakhulu lwesifo sokuwa oluqala ebuntwaneni, ngokuvamile ngaphambi kweminyaka eyi-10, futhi ikakhulukazi phakathi kweminyaka emi-3 neyi-5. Sivame kakhulu kubafana. Kodwa-ke, akusona isimo esivamile kakhulu. Sithinta cishe umuntu oyedwa kuya kwababili esigidini. Cishe u-1% kuya ku-2% wabo bonke abaguli besifo sokuwa bane-LGS.

Lokhu kuyithinta kanjani imizimba yethu?

Isifo sokuwa yisifo lapho izimpawu zikagesi zobuchopho, noma ulwazi, zidluliselwa khona phakathi kwamaseli. (LGS) uhlobo olubi kakhulu lwesifo sokuwa. Kunezimbangela eziningana:

  • Ku-LGS, kwenzeka izinhlobo ezingaphezu kweyodwa zokuxhuzula. Ezinye zalezi zinhlobo zokuxhuzula cishe zingabangela ukulimala okukhulu enganeni.
  • Lokhu kuquleka kungalimaza ubuchopho uqobo. Izingane ezine-LGS zingaba nomonakalo omkhulu wobuchopho, ubunzima bokufunda, kanye nokubambezeleka kokukhula. Lokhu kusho ukuthi ingane ingalahlekelwa noma ikhohlwe izinto esezifundile kakade, njengokuhamba nokukhuluma. Lesi yisimo esidabukisayo kakhulu.
  • (LGS) ivame ukumelana kakhulu nokwelashwa. Lokhu kusho ukuthi kunzima ukuyilawula ngemithi. Imithi iyindlela yokuqala yokwelapha, kodwa ngokuvamile izinhlobo eziningana zemithi zinikezwa ngesikhathi esisodwa. Ngisho noma zinikezwa, imithi yodwa ayivamile ukumisa ngokuphelele ukuxhuzula.

Ziyini izimpawu ze-(LGS)?

Ingane ene-LGS ingabonisa izimpawu ezahlukahlukene. Ezinye zazo ziyabonakala empilweni yansuku zonke nasemisebenzini, kanti ezinye zibonakala kuphela ngesikhathi sokuwa.

Izinkinga zokufunda nokuziphatha

Kuvamile ukuthi izingane ezine-LGS zibe nezinkinga zokufunda nezinkinga zokuziphatha . Lokhu kungavela ngokushesha ngemva kokuqala kokuquleka, futhi kungaba kubi kakhulu njengoba ukuquleka kuqhubeka. Lezi zinkinga zokufunda nezengqondo zivame ukuhlala isikhathi eside, okusho ukuthi zingaqhubeka zize zibe ngabantu abadala.

Izingane ezine-LGS zinobunzima bokufunda, ukwenza abangane, kanye nokukhulumisana nabanye. Zingase zibe nobunzima bokulawula imizwa yazo. Ezinye izingane zingase zibonise nezimpawu ezifana nezezingane ezine-Autism Spectrum Disorder .

Isigaba sokubanjwa

Ukuquleka ngokuvamile kungenzeka ngezigaba ezintathu:

1. I-Prodrome noma i-aura: Lokhu kuyinto abanye abantu ababhekana nayo ngaphambi kokuba babanjwe yi-seizure, nakuba kungenjalo ngaso sonke isikhathi. Lokhu kungaba umuzwa ongathandeki kancane. Izinguquko embonweni, izinguquko kwezinye izinzwa, noma izinguquko esimweni sengqondo noma ekuziphatheni zingase zenzeke ngalesi sikhathi.

2. Ukuquleka: Yilapho kuvela khona ukuquleka. Lokhu kungahluka kuye ngohlobo lokuquleka (sizoxoxa ngezinhlobo ezahlukene zokuquleka ngezansi).

3. Ukululama ngemva kokuquleka: Lesi yisikhathi ngemva kokuphela kokuquleka. Lesi yisikhathi lapho umuntu ephinde aqonde ngokugcwele.

Izinhlobo zokuxhuzula ezibonakala ku-LGS

Kunezinhlobo eziningana eziyinhloko zokuxhuzula ezitholakala ku-LGS. Izinhlobo ezivame kakhulu zokuxhuzula kanye nemiphumela yazo yilezi ezilandelayo:

  • Ukuquleka kwe-Atonic:
  • Ukulahlekelwa ukulawula/ukuquleka kwemisipha: Lokhu kubizwa nangokuthi "ukuhlaselwa kokuwa" ngoba kuhilela ukulahlekelwa ukulawula ngokuzumayo nokuwa phansi, njengopopi onezintambo eziphukile. Lokhu kuyingozi kakhulu ngoba ingane ayinakho ukulawula lapho iwela futhi ingalimala kakhulu, ngisho nokufa, ekhanda, entanyeni, esifubeni nasemhlane.
  • Ukulahlekelwa yingqondo okuyingxenye: Lokhu kuquleka kungase kungabangela ukulahlekelwa yingqondo ngokuphelele.
  • Isikhathi esifushane: Lokhu kuxhuzula kuhlala isikhathi esifushane kakhulu, njengemizuzwana embalwa.
  • Ukuxhuzula kwe-tonic:
  • Ukuqina/ukuqandisa komzimba wonke: Yilapho yonke imisipha emzimbeni ifinyela ngokuzumayo, okwenza umzimba uqine ngokuphelele sengathi uphenduke itshe.
  • Ukuma okukhethekile: Uma bephansi, imilenze namahlombe abo ephansi, imihlane yabo ingagobeka. Izingalo zinganwetshwa ngaphezu kwamakhanda abo, noma izingalo zingaqiniswa futhi izindololwane zibheke ezinhlangothini, kanti izibhakela zingasondela ezinqeni.
  • Ngokuvamile kwenzeka ngesikhathi sokulala: Lokhu kuvame ukwenzeka ngesikhathi sokulala. Kodwa kungenzeka futhi emini. Uma lokhu kwenzeka ngesikhathi ingane ivukile, kunengozi yokulimala ngoba ingane ingase iwe.
  • Isikhathi esifushane: Lokhu futhi kuthatha imizuzwana embalwa kuya cishe umzuzu.
  • Ukuquleka okungajwayelekile kokungabikho:
  • Amehlo avulekile futhi abheke ngaphandle kolwazi: Kulokhu kubanjwa, ingqondo iyalahleka, kodwa amehlo ahlala evulekile. Ngakho-ke, lokhu kungavame ukuphambaniswa nokuphupha emini, ukuntuleka kokugxila, kanye nomuzwa wokungabi endaweni efanele.
  • Ukunyakaza okuphindaphindiwe: Phakathi nalokhu kuxhuzula, ungase ubone ukunyakaza kwamehlo nomlomo. Kungase kube nokunyakaza kwezandla.
  • Isikhathi esifushane: Lokhu futhi akudluli imizuzwana embalwa.

Okubalulekile: Izingane ezine-LGS zingase zibe nokuquleka "ngamaqoqo," okusho ukuthi ukuquleka okuningana kwenzeka ngesikhathi esifushane. Izingane ezingaphezu kwezingxenye ezimbili kwezintathuKuvela isimo esibizwa ngokuthi "Status Epilepticus" . Lesi yisimo esiphuthumayo sezokwelapha esidinga ukwelashwa okuphuthumayo!

Kuyini i-Status Epilepticus?

Lokhu kusho enye yezinto ezimbili:

  • Ukuxhuzula okukodwa, okuhlala isikhathi eside okuhlala phakathi kwemizuzu emi-5 nengama-30.
  • Ukuxhuzula okungaphezu kokukodwa kungakapheli imizuzu engama-30, futhi umuntu akaphinde athole ulwazi oluphelele ngesikhathi salezo zixhuzula.

I-Status epilepticus iyisimo esiphuthumayo sezokwelapha. Siyingozi kakhulu ngoba singabangela ukulimala kwengqondo okungapheli ngisho nokufa.

Ezinye izimpawu kanye nezinhlobo zokuquleka ezihlobene

  • Ukuquleka kwe-Tonic-clonic: Ukuquleka kwe-Tonic-clonic (okwakubizwa ngokuthi "i-grand mal") kuqala ngendlela efanayo nokuquleka kwe-tonic, kodwa kunesigaba esengeziwe. Isigaba se-clonic yilapho umzimba ugxumagxuma, okuyisici esivame kakhulu sokuquleka, kwenzeka. Ukuquleka kwe-Tonic ne-tonic-clonic kuvame ukuthatha imizuzu emibili.
  • Ukunyakaza okusheshayo, okufushane, nokungalawuleki: Ukuxhuzula kwe-myoclonic kuyikunyakaza okungazelelwe nokungalawuleki. Kuthatha imizuzwana embalwa kuphela, kodwa ngezinye izikhathi kungahlala isikhathi eside. Abantu abangenayo i-epilepsy bangaba nalolu hlobo "lwe-myoclonic jerks." Isibonelo, kungabangela ukuxhuzula noma ukuvuka ngokuzumayo ebuthongweni.
  • Izimpawu zokuzwa, zengqondo, noma ezinye: Ukuwa okungaphelele noma okugxile kuthinta ingxenye yomzimba elinganiselwe kuphela.

Yiziphi izimbangela ze-LGS?

Kunezimbangela eziningana ezingaba khona ze-Lennox-Gastaut syndrome. Ezinye zezimbangela zikhona ngaphambi kokuba ingane izalwe. Ezinye zibangelwa izehlakalo ezenzeka ebuntwaneni. Cishe engxenyeni yesine yamacala e-``(LGS)``, akukho sizathu esicacile esingatholakala.

Nazi ezinye zezizathu ezitholakele:

  • Izinkinga zokukhula kobuchopho ngaphambi kokuzalwa.
  • Ukulimala okukhulu ekhanda (ukulimala kobuchopho okubuhlungu noma ukuxhuzula).
  • Izifo ezilimaza ubuchopho, njenge-meningitis noma i-encephalitis.
  • Izifo ze-metabolic ezizuzwe njengefa, isibonelo `(Izifo ze-Mitochondrial)`.
  • Ukulimala kobuchopho okubangelwa ukuntuleka komoya-mpilo ngaphambi noma ngesikhathi sokuzalwa (i-cerebral hypoxia).
  • I-Tuberous sclerosis.
  • Izimila zobuchopho.
  • I-West syndrome (lolu olunye uhlobo lwesifo sokuwa, esingakhula kamuva sibe yi-LGS).

Abacwaningi bathole ukuthi "izinguquko ze-de novo" zivamile kubantu abane-LGS.Igama elithi de novo lisho ukuthi “kusukela ekuqaleni.” Lawa amaphutha ku-‘(DNA)` yomuntu avela ngokuzumayo, ngokungahleliwe. Okusho ukuthi, ukuguquka kwezakhi zofuzo kubangelwa yiphutha ku-‘(DNA)` yesidoda noma iqanda elikhiqize umuntu, kodwa akulona iphutha ku-‘(DNA)` yomzali noma yimuphi.

Kodwa-ke, kungase kube nomthelela wezakhi zofuzo kulesi simo. Cishe abantu abangu-30% abane-LGS banomlando womndeni wesifo sokuwa. Kodwa-ke, kudingeka ucwaningo olwengeziwe ukuze kutholakale ukuthi lokhu kuyisici esingakanani sezakhi zofuzo.

Ingabe lokhu kuyathelelana?

Cha, i-Lennox-Gastaut syndrome ayithelelani. Ayisakazeki isuka komunye umuntu iye komunye. Kodwa-ke, ezinye izifo ezithelelanayo zingabangela ukulimala kobuchopho futhi zibangele "i-LGS". Kodwa-ke, akuwona wonke umuntu onalezo zifo ozoba "ne-LGS".

Itholakala kanjani i-Lennox-Gastaut syndrome (LGS)?

Ukuhlolwa okuningana kuvame ukwenziwa ukuze kutholakale i-LGS, futhi udokotela uzokwenza ukuhlolwa kwezinzwa. Udokotela wezingane angase asole lesi simo ngokusekelwe kulokho abazali abakushoyo ngezimpawu zengane yabo, ikakhulukazi uma ingane inokukhubazeka kokufunda noma izinkinga zokuziphatha.

Yiziphi izivivinyo ezenziwayo ukuze kutholakale lokhu?

Izivivinyo ezisetshenziswa kakhulu yilezi:

  • I-Electroencephalogram (EEG): Lokhu kuhilela ukubeka ama-electrode amaningana ekhanda ngejeli yokuhambisa umoya ukuze kulinganiswe umsebenzi kagesi wobuchopho. I-EEG ibalulekile ekuxilongeni i-LGS ngoba ikhombisa iphethini kagesi ehlukile kumaza obuchopho.
  • I-Magnetic Resonance Imaging (MRI): Lokhu kusebenzisa i-magnet enamandla kanye nekhompyutha ukuthatha izithombe ezicacile zangaphakathi komzimba, ikakhulukazi ubuchopho. Lokhu kusiza kakhulu ekutholeni izinkinga zokukhula kobuchopho.
  • Ukuhlolwa kwelebhu: Lokhu kuhlolwa kuhlola igazi nomchamo ukuze kubonakale ukuthi zikhona yini ezinye izimbangela zokuquleka. Kubheka izinto ezifana ne-chemistry yegazi, ama-enzyme esibindi, kanye nokusebenza kwezinso. Nakuba lokhu kuhlolwa kungenakukwazi ukuxilonga i-LGS ngokuphelele, kungasiza ekususeni ezinye izimo ezingase zifane ne-LGS.
  • Ukuhlolwa kofuzo: Lokhu kungasiza ekunqumeni ukuthi ngabe kunezimo ezizuzwe njengefa ezingabangela i-LGS, noma ukuthi kukhona yini ukuguquka okuzenzakalelayo.

Ngaphezu kwalokho, kungase kwenziwe ezinye izivivinyo ukuze kukhishwe izimo ezifanayo. Udokotela wakho uzokutshela okwengeziwe ngalokhu.

Kungelashwa kanjani lokhu? Ingabe kungelapheka?

Kunezindlela eziningana zokwelapha i-LGS. Kodwa-ke, lesi simo sinzima kakhulu ukuselapha. Ezimweni eziningi, ukwelashwa okukodwa noma okuhlanganisiwe kungasetshenziswa:

  • Imithi
  • Ukwelashwa ngokudla
  • Ukuhlinzwa kobuchopho noma amadivayisi afakwe

Imithi

I-Lennox-Gastaut syndrome ivame ukumelana kakhulu nemithi. Yingakho kunzima ukuyiphatha. Ezimweni eziningi, kudingeka imithi eminingi. Esinye isici esiyinkimbinkimbi ukuthi eminye imithi yokulwa nokuquleka, elawula ezinye izinhlobo zokuquleka, ingandisa ukuvama kwezinye izinhlobo zokuquleka.

Uma lesi simo singamelani nokwelashwa, odokotela bangase bazame ukuvimbela izinhlobo ezithile zokuquleka noma ukunciphisa ukuvama kwazo. Isibonelo, ukuquleka kwe-atonic kubaluleke kakhulu ukuvimbela, njengoba kuhlotshaniswa nengozi ephezulu yokulimala ngenxa yokuwa.

Ukwelashwa ngokudla

Kubantu abaningi abanesifo sokuwa esinzima, ukushintsha ukudla kungasiza ekunciphiseni ukuvama kokuwa noma ukukuyekise ngokuphelele. Ukudla okune-ketogenic kwesifo sokuwa – ukudla okunamaprotheni amaningi namafutha kanye nama-carbohydrate aphansi – kuvame ukunconywa odokotela. Kungaba inketho enhle uma imithi ingasebenzanga.

Nakuba ukudla kwe-ketogenic kuyindlela ethandwayo yokwelapha isifo sokuwa esibi kakhulu, kunezinkinga ezimbalwa. Lokhu kudla kusebenza kuphela uma ukulandele ngqo. Lokhu kungenxa yokuthi ukudla ama-carbohydrate amaningi kakhulu, njengoshukela nokudla okunesitashi, kungabangela ukuxhuzula. Kodwa-ke, okunye ukudla okuguquliwe nakho kungasiza. Uma unesithakazelo, udokotela wakho angakusiza uzame okunye kwalokhu kudla.

Ukuhlinzwa kobuchopho kanye namadivayisi afakwe

Kwezinye izimo, ikakhulukazi uma ezinye izindlela zokwelapha zingasebenzi, ukuhlinzwa kuyindlela engcono kakhulu. Nazi ezinye izinhlobo zokuhlinzwa:

  • Ukukhuthazwa Kwemizwa Yesigubhu (i-VNS): Lokhu kuhilela ukufaka idivayisi emzimbeni ehambisa ugesi omncane emthanjeni we-cranial we-10th, i-vagus nerve - exhunywe ngqo ebuchosheni. Lo mshini unganciphisa ukuvama kanye nobunzima bokuxhuzula. Ngokuhamba kwesikhathi, imiphumela yawo iyanda. Lokhu kusho ukuxhuzula okumbalwa kanye nokuxhuzula okungekubi kakhulu. Ukufaka le divayisi kuyinqubo elungisekayo, enezingozi eziphansi kanye nesikhathi esifushane sokululama, ngakho-ke kuvame ukucatshangelwa ngaphambi kokuhlinzwa okukhulu.
  • I-Corpus callosotomy: I-corpus callosum iyingxenye yobuchopho esebenza njengebhuloho phakathi kwezingxenye zesobunxele nesokudla. Lapho i-corpus callosum inqanyulwa, izimpawu ezingavamile ezibangela ukuxhuzula ziyeka ukubuya nokubuya. Lokhu kunganciphisa ukuvama kokuxhuzula, noma kumise ngisho nokuxhuzula okukhulu, okukhubaza ngokuphelele ukuxhuzula.
  • I-Hemispherectomy `(Ukususwa kwe-Hemispher)`:Lokhu kuhilela ukususa uhlangothi olulodwa lobuchopho ngokuhlinzwa. Nakuba lokhu kungase kubonakale kuyingozi kakhulu, ochwepheshe bangakusebenzisa ukuvimba ukuquleka okungalawuleki. Kamuva, ukwelashwa ngokomzimba kungasiza ubuchopho ukuba bujwayele ushintsho. Ubuchopho buzihlela kabusha, bese ingxenye esele ithatha imisebenzi yengxenye esusiwe.
  • Ukususwa: Ukuphazamiseka kwesakhiwo ebuchosheni ngezinye izikhathi kungabangela i-LGS. Uma odokotela bengathola ukungajwayelekile okunjalo, bangase bakwazi ukususa izicubu zobuchopho ezonakele noma ezigulayo futhi bamise ukuxhuzula. Kodwa-ke, ngoba ku-LGS, umsebenzi wokuxhuzula usezindaweni ezingaphezu kweyodwa zobuchopho, lokhu ngokuvamile akuyona inketho ephumelela kakhulu ye-LGS.

Izinkinga/imiphumela emibi yokwelashwa

Izinkinga zokwelashwa ziqondene ngqo nokwelashwa ngakunye. Ngakho-ke, kungcono ukukhuluma nodokotela wakho ngezinkinga nemiphumela emibi yokwelashwa okutholayo wena noma ingane yakho. Udokotela angakunikeza ulwazi olufanele isimo sakho, izimo zakho, kanye nezinye izimo zezokwelapha.

Ngizozizwa ngingcono isikhathi esingakanani ngemva kokwelashwa? Kuzothatha isikhathi esingakanani ukululama?

Isikhathi sokululama ngemva kokwelashwa siyahlukahluka kakhulu kuye ngezindlela zokwelapha ezisetshenzisiwe kanye nesimo sakho sonke. Udokotela wakho ungumuntu ongcono kakhulu ukukutshela ngqo ukuthi yini ongayilindela nokuthi kuzothatha isikhathi esingakanani ukululama.

Ingabe i-Lennox-Gastaut syndrome (LGS) ingavinjelwa?

Ezimweni eziningi, i-LGS ayisona isimo esingavinjelwa. Futhi ingozi yokuyithola ayinakuncishiswa. Okuwukuphela komehluko ukuvimbela ukulimala kwekhanda nobuchopho okungabangelwa yi-LGS. Okuwukuphela kwendlela yokuvimbela lesi simo ukuthi singenzeki ukuba izingane zakho zigqoke izigqoko zokuzivikela ezivunyiwe neziqinisekisiwe.

Yini okufanele ngiyilindele uma mina noma ingane yami sinalesi simo?

I-Lennox-Gastaut syndrome yisimo esivame ukuba nemiphumela emibi kakhulu. Izingane eziningi ezinalesi simo ziba nokukhubazeka kokufunda kanye nokulimala kobuchopho okuhlala njalo okunciphisa amakhono azo engqondo. Futhi, ngenxa yokuthi ukuquleka kwe-atonic (ukuhlaselwa ngamaconsi) kuvamile, futhi kuvame ukuholela ekuweni, izingane ezinalesi simo zisengozini enkulu yokulimala.

Lesi simo kunzima futhi ukwelapha. Izingane eziningi ezinaso zidinga ukunakekelwa okukhethekile impilo yazo yonke ngoba azikwazi ukuzinakekela. Kodwa-ke, abanye abantu abanalesi simo banomonakalo omncane wobuchopho, okusho ukuthi bangaphila ngokuzimela.

Ihlala isikhathi esingakanani (i-LGS)?

Ngaphandle kokuthi kunikezwe ukwelashwa kokuqeda ngokuphelele ukuxhuzula (okuyinto engavamile kakhulu), i-LGS iyisimo sokuphila konke.

Iyini ikusasa lalesi simo?

Izingozi ezinkulu ze-Lennox-Gastaut syndrome ukulimala kobuchopho ngenxa yokuxhuzula okungalawuleki, noma ngenxa yokuwa okubangelwa ukuxhuzula. Ngenxa yalezo zingozi, izinga lokufa kwabantu abane-"LGS" phakathi neminyaka eyi-10 yokutholakala benalesi sifo liphakathi kuka-3% no-7%.

Kwezinye izimo, izinqubo zezokwelapha zingamisa ukuquleka okubangelwa yi-LGS. Lokhu kuyayimisa le nkinga, kodwa akukwazi ukulungisa umonakalo ebuchosheni obubangelwe ukuquleka kwangaphambilini.

Ngizinakekela kanjani mina? / Ngimnakekela kanjani ingane yami?

Uma wena noma othandekayo wakho ene-LGS, kubaluleke kakhulu ukulandela imiyalelo kadokotela wakho ngqo. Lokhu kufaka phakathi:

  • Ukuthatha imithi njengoba kuyalelwe.
  • Ukuya kudokotela njengoba kunconyiwe.
  • Ukuqapha ukuquleka nokugwema izinto ezibangela ukuquleka noma izimo ezingase zibangele ukuquleka.

Kufanele ngimbone nini udokotela?

Udokotela wakho noma wengane yakho uzokutshela ukuthi uze uzobona udokotela wakho uma kudingeka. Kufanele futhi ubone udokotela wakho uma izimpawu zakho zokuxhuzula zishintsha kakhulu noma uma zithinta indlela yakho evamile yansuku zonke kanye nemisebenzi.

Kufanele ngiye nini e-Emergency Treatment Unit (ETU) ?

Uma wena noma ingane yakho ninesithuthwane noma isithuthwane esiningi esihlangabezana nezindinganiso zesimo esiphuthumayo sezokwelapha esibizwa ngokuthi i-status epilepticus , kufanele niye egumbini lezimo eziphuthumayo esibhedlela esiseduze. Lokhu kusho ukuthi ezimweni ezilandelayo:

  • Uma ukuxhuzula okukodwa kuthatha imizuzu emi-5 kuya kwengama-30.
  • Uma kwenzeka ukuxhuzula okubili noma ngaphezulu kungakapheli imizuzu engama-30 futhi umuntu engabuyi ebuthongweni obuphelele ngesikhathi sokuxhuzula.

Umlayezo Wokuya Nawe Ekhaya

I-Lennox-Gastaut syndrome (LGS) iwuhlobo olubi kakhulu lwesifo sokuwa esiqala ekuqaleni. Ivame ukuba nomthelela omkhulu, ngezinye izikhathi impilo yonke empilweni yengane. Nakuba kunzima ukwelapha, imithi emisha, ukuhlinzwa, kanye nokwelashwa kungasiza ekunciphiseni ubucayi besimo futhi kunciphise ukusabalala kwesifo. Akuvamile, ukwelashwa kungasiqeda ngokuphelele lesi simo. Kodwa-ke, kudingeka ucwaningo olwengeziwe ukuze kutholakale ukuthi lesi simo singelashwa noma selapheke noma cha. Uma ingane yakho inanoma yiziphi zalezi zimpawu, kungcono ukubona udokotela ngokushesha okukhulu.


I- Lennox-Gastaut syndrome, i-LGS, isifo sokuwa, ukuquleka, izingane, izinkinga zobuchopho, izifo zezinzwa

Frequently Asked Questions (FAQ)

Kuyini i-Status Epilepticus?

Lokhu kusho enye yezinto ezimbili:

Yiziphi izivivinyo ezenziwayo ukuze kutholakale lokhu?

Izivivinyo ezisetshenziswa kakhulu yilezi:

Iyini ikusasa lalesi simo?

Izingozi ezinkulu ze-Lennox-Gastaut syndrome ukulimala kobuchopho ngenxa yokuxhuzula okungalawuleki, noma ngenxa yokuwa okubangelwa ukuxhuzula. Ngenxa yalezo zingozi, izinga lokufa kwabantu abane-"LGS" phakathi neminyaka eyi-10 yokutholakala benalesi sifo liphakathi kuka-3% no-7%.

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

Awekho amazwana athunyelwe okwamanje. Faka amazwana akho lapha okokuqala ngqa.

Engeza amazwana akho

Sicela ubale: 2 + 4 =
Iyini i-Lennox-Gastaut Syndrome (LGS)? Ake sixoxe ngayo!
Izifo NezimoJulayi 16, 2026

Iyini i-Lennox-Gastaut Syndrome (LGS)? Ake sixoxe ngayo!

Ingabe ingane yakho encane inesifo sokuwa njalo? Ingabe inezinguquko ezinkulu ekufundeni nasekuziphatheni? Uma kunjalo, engizokusho kungaba yinto ebaluleke kakhulu kuwe. Namuhla sizokhuluma nge -Lennox-Gastaut Syndrome , noma (LGS) ngamafuphi, isimo sokuwa esinzima futhi esinzima ukuselapha. Lokhu kungaqala esemncane. Kodwa ungakhathazeki, imithi emisha kanye nokwelashwa sekuyatholakala manje.

Iyini ngempela i-Lennox-Gastaut syndrome (LGS)? Ngubani oyitholayo?

Kalula nje, i-LGS uhlobo olubi kakhulu lwesifo sokuwa oluqala ebuntwaneni, ngokuvamile ngaphambi kweminyaka eyi-10, futhi ikakhulukazi phakathi kweminyaka emi-3 neyi-5. Sivame kakhulu kubafana. Kodwa-ke, akusona isimo esivamile kakhulu. Sithinta cishe umuntu oyedwa kuya kwababili esigidini. Cishe u-1% kuya ku-2% wabo bonke abaguli besifo sokuwa bane-LGS.

Lokhu kuyithinta kanjani imizimba yethu?

Isifo sokuwa yisifo lapho izimpawu zikagesi zobuchopho, noma ulwazi, zidluliselwa khona phakathi kwamaseli. (LGS) uhlobo olubi kakhulu lwesifo sokuwa. Kunezimbangela eziningana:

  • Ku-LGS, kwenzeka izinhlobo ezingaphezu kweyodwa zokuxhuzula. Ezinye zalezi zinhlobo zokuxhuzula cishe zingabangela ukulimala okukhulu enganeni.
  • Lokhu kuquleka kungalimaza ubuchopho uqobo. Izingane ezine-LGS zingaba nomonakalo omkhulu wobuchopho, ubunzima bokufunda, kanye nokubambezeleka kokukhula. Lokhu kusho ukuthi ingane ingalahlekelwa noma ikhohlwe izinto esezifundile kakade, njengokuhamba nokukhuluma. Lesi yisimo esidabukisayo kakhulu.
  • (LGS) ivame ukumelana kakhulu nokwelashwa. Lokhu kusho ukuthi kunzima ukuyilawula ngemithi. Imithi iyindlela yokuqala yokwelapha, kodwa ngokuvamile izinhlobo eziningana zemithi zinikezwa ngesikhathi esisodwa. Ngisho noma zinikezwa, imithi yodwa ayivamile ukumisa ngokuphelele ukuxhuzula.

Ziyini izimpawu ze-(LGS)?

Ingane ene-LGS ingabonisa izimpawu ezahlukahlukene. Ezinye zazo ziyabonakala empilweni yansuku zonke nasemisebenzini, kanti ezinye zibonakala kuphela ngesikhathi sokuwa.

Izinkinga zokufunda nokuziphatha

Kuvamile ukuthi izingane ezine-LGS zibe nezinkinga zokufunda nezinkinga zokuziphatha . Lokhu kungavela ngokushesha ngemva kokuqala kokuquleka, futhi kungaba kubi kakhulu njengoba ukuquleka kuqhubeka. Lezi zinkinga zokufunda nezengqondo zivame ukuhlala isikhathi eside, okusho ukuthi zingaqhubeka zize zibe ngabantu abadala.

Izingane ezine-LGS zinobunzima bokufunda, ukwenza abangane, kanye nokukhulumisana nabanye. Zingase zibe nobunzima bokulawula imizwa yazo. Ezinye izingane zingase zibonise nezimpawu ezifana nezezingane ezine-Autism Spectrum Disorder .

Isigaba sokubanjwa

Ukuquleka ngokuvamile kungenzeka ngezigaba ezintathu:

1. I-Prodrome noma i-aura: Lokhu kuyinto abanye abantu ababhekana nayo ngaphambi kokuba babanjwe yi-seizure, nakuba kungenjalo ngaso sonke isikhathi. Lokhu kungaba umuzwa ongathandeki kancane. Izinguquko embonweni, izinguquko kwezinye izinzwa, noma izinguquko esimweni sengqondo noma ekuziphatheni zingase zenzeke ngalesi sikhathi.

2. Ukuquleka: Yilapho kuvela khona ukuquleka. Lokhu kungahluka kuye ngohlobo lokuquleka (sizoxoxa ngezinhlobo ezahlukene zokuquleka ngezansi).

3. Ukululama ngemva kokuquleka: Lesi yisikhathi ngemva kokuphela kokuquleka. Lesi yisikhathi lapho umuntu ephinde aqonde ngokugcwele.

Izinhlobo zokuxhuzula ezibonakala ku-LGS

Kunezinhlobo eziningana eziyinhloko zokuxhuzula ezitholakala ku-LGS. Izinhlobo ezivame kakhulu zokuxhuzula kanye nemiphumela yazo yilezi ezilandelayo:

  • Ukuquleka kwe-Atonic:
  • Ukulahlekelwa ukulawula/ukuquleka kwemisipha: Lokhu kubizwa nangokuthi "ukuhlaselwa kokuwa" ngoba kuhilela ukulahlekelwa ukulawula ngokuzumayo nokuwa phansi, njengopopi onezintambo eziphukile. Lokhu kuyingozi kakhulu ngoba ingane ayinakho ukulawula lapho iwela futhi ingalimala kakhulu, ngisho nokufa, ekhanda, entanyeni, esifubeni nasemhlane.
  • Ukulahlekelwa yingqondo okuyingxenye: Lokhu kuquleka kungase kungabangela ukulahlekelwa yingqondo ngokuphelele.
  • Isikhathi esifushane: Lokhu kuxhuzula kuhlala isikhathi esifushane kakhulu, njengemizuzwana embalwa.
  • Ukuxhuzula kwe-tonic:
  • Ukuqina/ukuqandisa komzimba wonke: Yilapho yonke imisipha emzimbeni ifinyela ngokuzumayo, okwenza umzimba uqine ngokuphelele sengathi uphenduke itshe.
  • Ukuma okukhethekile: Uma bephansi, imilenze namahlombe abo ephansi, imihlane yabo ingagobeka. Izingalo zinganwetshwa ngaphezu kwamakhanda abo, noma izingalo zingaqiniswa futhi izindololwane zibheke ezinhlangothini, kanti izibhakela zingasondela ezinqeni.
  • Ngokuvamile kwenzeka ngesikhathi sokulala: Lokhu kuvame ukwenzeka ngesikhathi sokulala. Kodwa kungenzeka futhi emini. Uma lokhu kwenzeka ngesikhathi ingane ivukile, kunengozi yokulimala ngoba ingane ingase iwe.
  • Isikhathi esifushane: Lokhu futhi kuthatha imizuzwana embalwa kuya cishe umzuzu.
  • Ukuquleka okungajwayelekile kokungabikho:
  • Amehlo avulekile futhi abheke ngaphandle kolwazi: Kulokhu kubanjwa, ingqondo iyalahleka, kodwa amehlo ahlala evulekile. Ngakho-ke, lokhu kungavame ukuphambaniswa nokuphupha emini, ukuntuleka kokugxila, kanye nomuzwa wokungabi endaweni efanele.
  • Ukunyakaza okuphindaphindiwe: Phakathi nalokhu kuxhuzula, ungase ubone ukunyakaza kwamehlo nomlomo. Kungase kube nokunyakaza kwezandla.
  • Isikhathi esifushane: Lokhu futhi akudluli imizuzwana embalwa.

Okubalulekile: Izingane ezine-LGS zingase zibe nokuquleka "ngamaqoqo," okusho ukuthi ukuquleka okuningana kwenzeka ngesikhathi esifushane. Izingane ezingaphezu kwezingxenye ezimbili kwezintathuKuvela isimo esibizwa ngokuthi "Status Epilepticus" . Lesi yisimo esiphuthumayo sezokwelapha esidinga ukwelashwa okuphuthumayo!

Kuyini i-Status Epilepticus?

Lokhu kusho enye yezinto ezimbili:

  • Ukuxhuzula okukodwa, okuhlala isikhathi eside okuhlala phakathi kwemizuzu emi-5 nengama-30.
  • Ukuxhuzula okungaphezu kokukodwa kungakapheli imizuzu engama-30, futhi umuntu akaphinde athole ulwazi oluphelele ngesikhathi salezo zixhuzula.

I-Status epilepticus iyisimo esiphuthumayo sezokwelapha. Siyingozi kakhulu ngoba singabangela ukulimala kwengqondo okungapheli ngisho nokufa.

Ezinye izimpawu kanye nezinhlobo zokuquleka ezihlobene

  • Ukuquleka kwe-Tonic-clonic: Ukuquleka kwe-Tonic-clonic (okwakubizwa ngokuthi "i-grand mal") kuqala ngendlela efanayo nokuquleka kwe-tonic, kodwa kunesigaba esengeziwe. Isigaba se-clonic yilapho umzimba ugxumagxuma, okuyisici esivame kakhulu sokuquleka, kwenzeka. Ukuquleka kwe-Tonic ne-tonic-clonic kuvame ukuthatha imizuzu emibili.
  • Ukunyakaza okusheshayo, okufushane, nokungalawuleki: Ukuxhuzula kwe-myoclonic kuyikunyakaza okungazelelwe nokungalawuleki. Kuthatha imizuzwana embalwa kuphela, kodwa ngezinye izikhathi kungahlala isikhathi eside. Abantu abangenayo i-epilepsy bangaba nalolu hlobo "lwe-myoclonic jerks." Isibonelo, kungabangela ukuxhuzula noma ukuvuka ngokuzumayo ebuthongweni.
  • Izimpawu zokuzwa, zengqondo, noma ezinye: Ukuwa okungaphelele noma okugxile kuthinta ingxenye yomzimba elinganiselwe kuphela.

Yiziphi izimbangela ze-LGS?

Kunezimbangela eziningana ezingaba khona ze-Lennox-Gastaut syndrome. Ezinye zezimbangela zikhona ngaphambi kokuba ingane izalwe. Ezinye zibangelwa izehlakalo ezenzeka ebuntwaneni. Cishe engxenyeni yesine yamacala e-``(LGS)``, akukho sizathu esicacile esingatholakala.

Nazi ezinye zezizathu ezitholakele:

  • Izinkinga zokukhula kobuchopho ngaphambi kokuzalwa.
  • Ukulimala okukhulu ekhanda (ukulimala kobuchopho okubuhlungu noma ukuxhuzula).
  • Izifo ezilimaza ubuchopho, njenge-meningitis noma i-encephalitis.
  • Izifo ze-metabolic ezizuzwe njengefa, isibonelo `(Izifo ze-Mitochondrial)`.
  • Ukulimala kobuchopho okubangelwa ukuntuleka komoya-mpilo ngaphambi noma ngesikhathi sokuzalwa (i-cerebral hypoxia).
  • I-Tuberous sclerosis.
  • Izimila zobuchopho.
  • I-West syndrome (lolu olunye uhlobo lwesifo sokuwa, esingakhula kamuva sibe yi-LGS).

Abacwaningi bathole ukuthi "izinguquko ze-de novo" zivamile kubantu abane-LGS.Igama elithi de novo lisho ukuthi “kusukela ekuqaleni.” Lawa amaphutha ku-‘(DNA)` yomuntu avela ngokuzumayo, ngokungahleliwe. Okusho ukuthi, ukuguquka kwezakhi zofuzo kubangelwa yiphutha ku-‘(DNA)` yesidoda noma iqanda elikhiqize umuntu, kodwa akulona iphutha ku-‘(DNA)` yomzali noma yimuphi.

Kodwa-ke, kungase kube nomthelela wezakhi zofuzo kulesi simo. Cishe abantu abangu-30% abane-LGS banomlando womndeni wesifo sokuwa. Kodwa-ke, kudingeka ucwaningo olwengeziwe ukuze kutholakale ukuthi lokhu kuyisici esingakanani sezakhi zofuzo.

Ingabe lokhu kuyathelelana?

Cha, i-Lennox-Gastaut syndrome ayithelelani. Ayisakazeki isuka komunye umuntu iye komunye. Kodwa-ke, ezinye izifo ezithelelanayo zingabangela ukulimala kobuchopho futhi zibangele "i-LGS". Kodwa-ke, akuwona wonke umuntu onalezo zifo ozoba "ne-LGS".

Itholakala kanjani i-Lennox-Gastaut syndrome (LGS)?

Ukuhlolwa okuningana kuvame ukwenziwa ukuze kutholakale i-LGS, futhi udokotela uzokwenza ukuhlolwa kwezinzwa. Udokotela wezingane angase asole lesi simo ngokusekelwe kulokho abazali abakushoyo ngezimpawu zengane yabo, ikakhulukazi uma ingane inokukhubazeka kokufunda noma izinkinga zokuziphatha.

Yiziphi izivivinyo ezenziwayo ukuze kutholakale lokhu?

Izivivinyo ezisetshenziswa kakhulu yilezi:

  • I-Electroencephalogram (EEG): Lokhu kuhilela ukubeka ama-electrode amaningana ekhanda ngejeli yokuhambisa umoya ukuze kulinganiswe umsebenzi kagesi wobuchopho. I-EEG ibalulekile ekuxilongeni i-LGS ngoba ikhombisa iphethini kagesi ehlukile kumaza obuchopho.
  • I-Magnetic Resonance Imaging (MRI): Lokhu kusebenzisa i-magnet enamandla kanye nekhompyutha ukuthatha izithombe ezicacile zangaphakathi komzimba, ikakhulukazi ubuchopho. Lokhu kusiza kakhulu ekutholeni izinkinga zokukhula kobuchopho.
  • Ukuhlolwa kwelebhu: Lokhu kuhlolwa kuhlola igazi nomchamo ukuze kubonakale ukuthi zikhona yini ezinye izimbangela zokuquleka. Kubheka izinto ezifana ne-chemistry yegazi, ama-enzyme esibindi, kanye nokusebenza kwezinso. Nakuba lokhu kuhlolwa kungenakukwazi ukuxilonga i-LGS ngokuphelele, kungasiza ekususeni ezinye izimo ezingase zifane ne-LGS.
  • Ukuhlolwa kofuzo: Lokhu kungasiza ekunqumeni ukuthi ngabe kunezimo ezizuzwe njengefa ezingabangela i-LGS, noma ukuthi kukhona yini ukuguquka okuzenzakalelayo.

Ngaphezu kwalokho, kungase kwenziwe ezinye izivivinyo ukuze kukhishwe izimo ezifanayo. Udokotela wakho uzokutshela okwengeziwe ngalokhu.

Kungelashwa kanjani lokhu? Ingabe kungelapheka?

Kunezindlela eziningana zokwelapha i-LGS. Kodwa-ke, lesi simo sinzima kakhulu ukuselapha. Ezimweni eziningi, ukwelashwa okukodwa noma okuhlanganisiwe kungasetshenziswa:

  • Imithi
  • Ukwelashwa ngokudla
  • Ukuhlinzwa kobuchopho noma amadivayisi afakwe

Imithi

I-Lennox-Gastaut syndrome ivame ukumelana kakhulu nemithi. Yingakho kunzima ukuyiphatha. Ezimweni eziningi, kudingeka imithi eminingi. Esinye isici esiyinkimbinkimbi ukuthi eminye imithi yokulwa nokuquleka, elawula ezinye izinhlobo zokuquleka, ingandisa ukuvama kwezinye izinhlobo zokuquleka.

Uma lesi simo singamelani nokwelashwa, odokotela bangase bazame ukuvimbela izinhlobo ezithile zokuquleka noma ukunciphisa ukuvama kwazo. Isibonelo, ukuquleka kwe-atonic kubaluleke kakhulu ukuvimbela, njengoba kuhlotshaniswa nengozi ephezulu yokulimala ngenxa yokuwa.

Ukwelashwa ngokudla

Kubantu abaningi abanesifo sokuwa esinzima, ukushintsha ukudla kungasiza ekunciphiseni ukuvama kokuwa noma ukukuyekise ngokuphelele. Ukudla okune-ketogenic kwesifo sokuwa – ukudla okunamaprotheni amaningi namafutha kanye nama-carbohydrate aphansi – kuvame ukunconywa odokotela. Kungaba inketho enhle uma imithi ingasebenzanga.

Nakuba ukudla kwe-ketogenic kuyindlela ethandwayo yokwelapha isifo sokuwa esibi kakhulu, kunezinkinga ezimbalwa. Lokhu kudla kusebenza kuphela uma ukulandele ngqo. Lokhu kungenxa yokuthi ukudla ama-carbohydrate amaningi kakhulu, njengoshukela nokudla okunesitashi, kungabangela ukuxhuzula. Kodwa-ke, okunye ukudla okuguquliwe nakho kungasiza. Uma unesithakazelo, udokotela wakho angakusiza uzame okunye kwalokhu kudla.

Ukuhlinzwa kobuchopho kanye namadivayisi afakwe

Kwezinye izimo, ikakhulukazi uma ezinye izindlela zokwelapha zingasebenzi, ukuhlinzwa kuyindlela engcono kakhulu. Nazi ezinye izinhlobo zokuhlinzwa:

  • Ukukhuthazwa Kwemizwa Yesigubhu (i-VNS): Lokhu kuhilela ukufaka idivayisi emzimbeni ehambisa ugesi omncane emthanjeni we-cranial we-10th, i-vagus nerve - exhunywe ngqo ebuchosheni. Lo mshini unganciphisa ukuvama kanye nobunzima bokuxhuzula. Ngokuhamba kwesikhathi, imiphumela yawo iyanda. Lokhu kusho ukuxhuzula okumbalwa kanye nokuxhuzula okungekubi kakhulu. Ukufaka le divayisi kuyinqubo elungisekayo, enezingozi eziphansi kanye nesikhathi esifushane sokululama, ngakho-ke kuvame ukucatshangelwa ngaphambi kokuhlinzwa okukhulu.
  • I-Corpus callosotomy: I-corpus callosum iyingxenye yobuchopho esebenza njengebhuloho phakathi kwezingxenye zesobunxele nesokudla. Lapho i-corpus callosum inqanyulwa, izimpawu ezingavamile ezibangela ukuxhuzula ziyeka ukubuya nokubuya. Lokhu kunganciphisa ukuvama kokuxhuzula, noma kumise ngisho nokuxhuzula okukhulu, okukhubaza ngokuphelele ukuxhuzula.
  • I-Hemispherectomy `(Ukususwa kwe-Hemispher)`:Lokhu kuhilela ukususa uhlangothi olulodwa lobuchopho ngokuhlinzwa. Nakuba lokhu kungase kubonakale kuyingozi kakhulu, ochwepheshe bangakusebenzisa ukuvimba ukuquleka okungalawuleki. Kamuva, ukwelashwa ngokomzimba kungasiza ubuchopho ukuba bujwayele ushintsho. Ubuchopho buzihlela kabusha, bese ingxenye esele ithatha imisebenzi yengxenye esusiwe.
  • Ukususwa: Ukuphazamiseka kwesakhiwo ebuchosheni ngezinye izikhathi kungabangela i-LGS. Uma odokotela bengathola ukungajwayelekile okunjalo, bangase bakwazi ukususa izicubu zobuchopho ezonakele noma ezigulayo futhi bamise ukuxhuzula. Kodwa-ke, ngoba ku-LGS, umsebenzi wokuxhuzula usezindaweni ezingaphezu kweyodwa zobuchopho, lokhu ngokuvamile akuyona inketho ephumelela kakhulu ye-LGS.

Izinkinga/imiphumela emibi yokwelashwa

Izinkinga zokwelashwa ziqondene ngqo nokwelashwa ngakunye. Ngakho-ke, kungcono ukukhuluma nodokotela wakho ngezinkinga nemiphumela emibi yokwelashwa okutholayo wena noma ingane yakho. Udokotela angakunikeza ulwazi olufanele isimo sakho, izimo zakho, kanye nezinye izimo zezokwelapha.

Ngizozizwa ngingcono isikhathi esingakanani ngemva kokwelashwa? Kuzothatha isikhathi esingakanani ukululama?

Isikhathi sokululama ngemva kokwelashwa siyahlukahluka kakhulu kuye ngezindlela zokwelapha ezisetshenzisiwe kanye nesimo sakho sonke. Udokotela wakho ungumuntu ongcono kakhulu ukukutshela ngqo ukuthi yini ongayilindela nokuthi kuzothatha isikhathi esingakanani ukululama.

Ingabe i-Lennox-Gastaut syndrome (LGS) ingavinjelwa?

Ezimweni eziningi, i-LGS ayisona isimo esingavinjelwa. Futhi ingozi yokuyithola ayinakuncishiswa. Okuwukuphela komehluko ukuvimbela ukulimala kwekhanda nobuchopho okungabangelwa yi-LGS. Okuwukuphela kwendlela yokuvimbela lesi simo ukuthi singenzeki ukuba izingane zakho zigqoke izigqoko zokuzivikela ezivunyiwe neziqinisekisiwe.

Yini okufanele ngiyilindele uma mina noma ingane yami sinalesi simo?

I-Lennox-Gastaut syndrome yisimo esivame ukuba nemiphumela emibi kakhulu. Izingane eziningi ezinalesi simo ziba nokukhubazeka kokufunda kanye nokulimala kobuchopho okuhlala njalo okunciphisa amakhono azo engqondo. Futhi, ngenxa yokuthi ukuquleka kwe-atonic (ukuhlaselwa ngamaconsi) kuvamile, futhi kuvame ukuholela ekuweni, izingane ezinalesi simo zisengozini enkulu yokulimala.

Lesi simo kunzima futhi ukwelapha. Izingane eziningi ezinaso zidinga ukunakekelwa okukhethekile impilo yazo yonke ngoba azikwazi ukuzinakekela. Kodwa-ke, abanye abantu abanalesi simo banomonakalo omncane wobuchopho, okusho ukuthi bangaphila ngokuzimela.

Ihlala isikhathi esingakanani (i-LGS)?

Ngaphandle kokuthi kunikezwe ukwelashwa kokuqeda ngokuphelele ukuxhuzula (okuyinto engavamile kakhulu), i-LGS iyisimo sokuphila konke.

Iyini ikusasa lalesi simo?

Izingozi ezinkulu ze-Lennox-Gastaut syndrome ukulimala kobuchopho ngenxa yokuxhuzula okungalawuleki, noma ngenxa yokuwa okubangelwa ukuxhuzula. Ngenxa yalezo zingozi, izinga lokufa kwabantu abane-"LGS" phakathi neminyaka eyi-10 yokutholakala benalesi sifo liphakathi kuka-3% no-7%.

Kwezinye izimo, izinqubo zezokwelapha zingamisa ukuquleka okubangelwa yi-LGS. Lokhu kuyayimisa le nkinga, kodwa akukwazi ukulungisa umonakalo ebuchosheni obubangelwe ukuquleka kwangaphambilini.

Ngizinakekela kanjani mina? / Ngimnakekela kanjani ingane yami?

Uma wena noma othandekayo wakho ene-LGS, kubaluleke kakhulu ukulandela imiyalelo kadokotela wakho ngqo. Lokhu kufaka phakathi:

  • Ukuthatha imithi njengoba kuyalelwe.
  • Ukuya kudokotela njengoba kunconyiwe.
  • Ukuqapha ukuquleka nokugwema izinto ezibangela ukuquleka noma izimo ezingase zibangele ukuquleka.

Kufanele ngimbone nini udokotela?

Udokotela wakho noma wengane yakho uzokutshela ukuthi uze uzobona udokotela wakho uma kudingeka. Kufanele futhi ubone udokotela wakho uma izimpawu zakho zokuxhuzula zishintsha kakhulu noma uma zithinta indlela yakho evamile yansuku zonke kanye nemisebenzi.

Kufanele ngiye nini e-Emergency Treatment Unit (ETU) ?

Uma wena noma ingane yakho ninesithuthwane noma isithuthwane esiningi esihlangabezana nezindinganiso zesimo esiphuthumayo sezokwelapha esibizwa ngokuthi i-status epilepticus , kufanele niye egumbini lezimo eziphuthumayo esibhedlela esiseduze. Lokhu kusho ukuthi ezimweni ezilandelayo:

  • Uma ukuxhuzula okukodwa kuthatha imizuzu emi-5 kuya kwengama-30.
  • Uma kwenzeka ukuxhuzula okubili noma ngaphezulu kungakapheli imizuzu engama-30 futhi umuntu engabuyi ebuthongweni obuphelele ngesikhathi sokuxhuzula.

Umlayezo Wokuya Nawe Ekhaya

I-Lennox-Gastaut syndrome (LGS) iwuhlobo olubi kakhulu lwesifo sokuwa esiqala ekuqaleni. Ivame ukuba nomthelela omkhulu, ngezinye izikhathi impilo yonke empilweni yengane. Nakuba kunzima ukwelapha, imithi emisha, ukuhlinzwa, kanye nokwelashwa kungasiza ekunciphiseni ubucayi besimo futhi kunciphise ukusabalala kwesifo. Akuvamile, ukwelashwa kungasiqeda ngokuphelele lesi simo. Kodwa-ke, kudingeka ucwaningo olwengeziwe ukuze kutholakale ukuthi lesi simo singelashwa noma selapheke noma cha. Uma ingane yakho inanoma yiziphi zalezi zimpawu, kungcono ukubona udokotela ngokushesha okukhulu.


I- Lennox-Gastaut syndrome, i-LGS, isifo sokuwa, ukuquleka, izingane, izinkinga zobuchopho, izifo zezinzwa

Frequently Asked Questions (FAQ)

Kuyini i-Status Epilepticus?

Lokhu kusho enye yezinto ezimbili:

Yiziphi izivivinyo ezenziwayo ukuze kutholakale lokhu?

Izivivinyo ezisetshenziswa kakhulu yilezi:

Iyini ikusasa lalesi simo?

Izingozi ezinkulu ze-Lennox-Gastaut syndrome ukulimala kobuchopho ngenxa yokuxhuzula okungalawuleki, noma ngenxa yokuwa okubangelwa ukuxhuzula. Ngenxa yalezo zingozi, izinga lokufa kwabantu abane-"LGS" phakathi neminyaka eyi-10 yokutholakala benalesi sifo liphakathi kuka-3% no-7%.

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

Awekho amazwana athunyelwe okwamanje. Faka amazwana akho lapha okokuqala ngqa.

Engeza amazwana akho

Sicela ubale: 2 + 4 =