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Umuthi omusha wokulawula i-ALS? (i-Sodium Phenylbutyrate; i-Taurursodiol) Ake sifunde ngakho!

MBBS

Medically reviewed by MBBS — Updated on Jul 16, 2026 · 5 min read

Umuthi omusha wokulawula i-ALS? (i-Sodium Phenylbutyrate; i-Taurursodiol) Ake sifunde ngakho!
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Uma wena noma othandekayo wakho ene-Amyotrophic Lateral Sclerosis (ALS), siyazi ukuthi kungaba nzima kangakanani. Ukuphila nalesi sifo, esinciphisa kancane kancane amangqamuzana ezinzwa alawula imisipha yethu, akulula. Ngakho-ke namuhla sizokhuluma ngomuthi ongasiza ekulawuleni nasekunciphiseni ukuwohloka kwalezi zimpawu. Lo muthi ubizwa ngokuthi i-Sodium Phenylbutyrate; i-Taurursodiol.

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Kwenzekani ngempela ngalo muthi?

Okokuqala, ake sikuqonde lokhu. Lo muthi awulona ikhambi eliphelele le-ALS. Kodwa wenza into ebaluleke kakhulu. Lo muthi okwenziwa yilo muthi ukuvikela amangqamuzana ezinzwa alimele yilesi sifo. Ngale ndlela, unganciphisa ukuqhubeka kwezimpawu. Kalula nje, lo muthi usiza ekunikezeni isiguli impumuzo ethile futhi ulawule inkambo yesifo ngezinga elithile.

Odokotela bangase batuse lokhu nakwezinye izimo zezokwelapha, ngakho-ke uma unemibuzo ngalokhu, kungcono ukukhuluma nodokotela wakho bese uxazulula lezo zinkinga.

Izinto okufanele uzitshele udokotela wakho ngaphambi kokuthatha imithi

Ngaphambi kokuqala lo muthi, kubaluleke kakhulu ukunikeza udokotela wakho incazelo ephelele yesimo sakho sempilo. Qiniseka ukuthi uyamtshela uma unezinye zezimo ezingezansi.

Ukugula noma esinye isimo Kungani kufanele ngazise udokotela ?
Isifo sesibindi Ngoba isibindi sibalulekile ekususeni imithi emzimbeni.
Isifo sezinso Ngoba izinso zihlunga umuthi.
Isifo senhliziyo (ukwehluleka kwenhliziyo) Lomuthi uqukethe i-sodium, engathinta inhliziyo.
Umfutho wegazi ophakeme Ngoba i-sodium ingakhuphula umfutho wegazi.
Isifo senyongo Ngoba ezinye zezithako ezikulo muthi zingathinta inyongo.
Isifo se-pancreatic Ngoba kungathinta ukusebenza kwe-pancreatic.
Izinkinga zamathumbu Ngoba imiphumela emibi efana nesifo sohudo ingase ivele.
Ukungezwani neminye imithi, ukudla noma izinto Ukuze ugweme ukubangela ukusabela kokungezwani komzimba.
Ukukhulelwa noma ukuzama ukukhulelwa Ukuqaphela imiphumela engaba khona embungwini.
Ukuncelisa Qaphela ukuthi kungenzeka ukuthi umuthi udluliselwe enganeni ngobisi lwebele.

Ngingawusebenzisa kanjani umuthi?

Kubaluleke kakhulu ukwazi ukuthi ungawusebenzisa kanjani lo muthi ngendlela efanele.

  • Indlela Yokuthatha: Lona umuthi ophuzwayo. Zama ukuwuthatha ngesikhathi esifanayo nsuku zonke, njengoba nje udokotela wakho ekuyalele.
  • Ukulungiselela: Beka impuphu evela ephaketheni lomuthi engilazini yamanzi afudumele ekamelweni (cishe ama-240 ml). Bese uvuselela kahle ukuze incibilike.
  • Ukuphuza nini: Phuza lokhu ekuqaleni kokudla noma kanye nokudla okulula . Ungakudli esiswini esingenalutho.
  • Ukuyeka: Qhubeka uthatha umuthi uma nje udokotela wakho ekutshelile. Ungayeki phakathi nendawo.

Qaphela: Uma ucabanga ukuthi usuthathe lo muthi omningi kakhulu, okungukuthi, ukudlula ngokweqile, shayela ngokushesha i-National Poisons Information Centre e-Colombo National Hospital noma uye e-Emergency Treatment Unit (ETU) yesibhedlela esiseduze. Phatha lokhu njengesimo esiphuthumayo.

Okunye, lo muthi unikezwe wena kuphela. Ungalokothi uwuhlanganyele nanoma ubani omunye, noma ngabe lowo muntu unezimpawu ezifanayo nezakho.

Yini okufanele uyenze uma uphuthelwa umthamo wemithi?

Ungakhathazeki. Uma uphuthelwa umthamo, thatha ngokushesha nje lapho ukhumbula. Kodwa uma sekuyisikhathi somthamo wakho olandelayo, yeqa umthamo ophuthelwe bese uthatha umthamo wakho olandelayo ngesikhathi esihleliwe. Ungalokothi uthathe umthamo ophindwe kabili ukuze ubuyisele umthamo ophuthelwe.

Eminye imithi engase ihlangane nalo muthi

Eminye imithi oyithathayo ingase ihlangane nalo muthi. Ngakho-ke, kubalulekile ukutshela udokotela wakho ngayo yonke imithi oyithathayo. Ikakhulukazi uma uthatha noma yimuphi wale mithi elandelayo:

  • Ama-antacid athile
  • I-Cholestyramine
  • I-Colesevelam
  • I-Colestipol
  • I-Cyclosporine
  • I-Probenecid

Lolu hlu aluphelele. Kubalulekile ukutshela udokotela wakho ngayo yonke imithi oyithathayo, okuhlanganisa imithi kadokotela kanye nemithi engabhalwanga ngudokotela, amavithamini, imithi yamakhambi, kanye nemithi yendabuko. Kubalulekile futhi ukutshela udokotela wakho uma ubhema, uphuza utshwala, noma usebenzisa ezinye izidakamizwa.

Yimiphi imiphumela emibi engaba khona?

Njenganoma yimuphi umuthi, lo ungabangela imiphumela emibi. Eminye yayo iyingozi, eminye yayo ivamile.

Uhlobo lomphumela ongemuhle Izimpawu
Imiphumela emibi okufanele ibikwe kudokotela wakho ngokushesha
Ukusabela kokungezwani komzimbaUkuqubuka kwesikhumba, ukulunywa, ukuvuvukala kobuso, izindebe, ulimi noma umphimbo, ubunzima bokuphefumula.
Imiphumela emibi evamile okufanele ibikwe kudokotela uma iqhubeka noma ikhathaza
Uhudo Ukuqunjelwa.
Isicanucanu Ukuzizwa sengathi uhlanza.
Ubuhlungu besisu Ubuhlungu besisu noma ukungakhululeki.

Lolu hlu aluhlanganisi yonke imiphumela emibi engaba khona. Uma uhlangabezana nanoma yini engavamile ngaphezu kwale, funa iseluleko sezokwelapha.

Ngingawugcina kanjani umuthi? Ngingawususa kanjani?

  • Indawo Yokugcina: Gcina lo muthi kude nezingane nezilwane ezifuywayo . Kungcono ukuwugcina ezingeni lokushisa legumbi (phakathi kwama-degree Celsius angu-20 no-25). Ungasebenzisi umuthi ophelelwe yisikhathi.
  • Ukulahlwa: Uma ulahla imithi ephelelwe yisikhathi noma engasadingeki, kubalulekile ukwenza kanjalo ngokuphephile. Hlola imiyalelo esephaketheni lemithi. Uma ithi kuphephile ukuyilahla kudoti, khipha imithi esitsheni bese uyixuba nento efana nodoti wekati, inhlabathi, noma ikhofi esetshenzisiwe. Bese ubeka ingxube esikhwameni esivalwe kahle bese uyilahla kudoti. Uma ungaqiniseki, cela iseluleko kudokotela wakho.

Umlayezo Wokuya Nawe Ekhaya

  • Lo muthi (i-Sodium Phenylbutyrate; i-Taurursodiol) awuphilisi i-ALS, kodwa uyasiza ekunciphiseni izinga lapho izimpawu ziba zimbi khona.
  • Njalo thatha umuthi wakho kanye nokudla, njengoba kuyalelwe udokotela wakho.
  • Yazisa udokotela wakho ngayo yonke eminye imithi oyithathayo kanye nanoma yiziphi ezinye izimo zezokwelapha onazo (ikakhulukazi isibindi, izinso, noma isifo senhliziyo).
  • Uma kuvela izimpawu zokusabela kokungezwani komzimba (ukuqubuka kwesikhumba, ukuvuvukala), funa iseluleko sezokwelapha ngokushesha.
  • Uma uphuza ngokweqile, hamba ngokushesha e-National Poison Information Center noma eMnyangweni Wezimo Eziphuthumayo wesibhedlela esiseduze (i-ETU).
  • Lo muthi ungowakho wedwa. Ungalokothi wabelane ngawo nabanye.
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Yini okufanele uyenze uma uphuthelwa umthamo wemithi?

Ungakhathazeki. Uma uphuthelwa umthamo, thatha ngokushesha nje lapho ukhumbula. Kodwa uma sekuyisikhathi somthamo wakho olandelayo, yeqa umthamo ophuthelwe bese uthatha umthamo wakho olandelayo ngesikhathi esihleliwe. Ungalokothi uthathe umthamo ophindwe kabili ukuze ubuyisele umthamo ophuthelwe.

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