Kumkhathaza kangakanani umama noma ubaba uma bebheka umntwana osanda kuzalwa bese bebona ushintsho oluthile emzimbeni wabo? Ngezinye izikhathi, ngisho nento engavamile kakhulu, ingathinta ingane yethu futhi isenze sizizwe sidabuke kakhulu. Namuhla, sizokhuluma ngesimo esingavamile ukuzwakala ngaso, kodwa okubaluleke kakhulu ukusazi. Lokhu sikubiza ngokuthi (i-Urogenital Sinus).
Kuyini lokhu (i-Urogenital Sinus)? Ake sikuqonde kalula?
Kalula nje, i-Urogenital Sinus iyisici esizalwa naso ohlelweni lomchamo kanye nohlelo lokuzala lowesifazane. Manje, bheka, ngokuvamile umntwana wesifazane unezimbobo ezintathu zokungcola ukuze aphume emzimbeni: enye yi-rectum, lapho kuphuma khona indle, enye yimbobo ye-urethral, lapho kuphuma khona umchamo, kanti eyesithathu yi - vagina . Kodwa-ke, umntwana one-Urogenital Sinus unezimbobo ezimbili. Enye yi-rectum, lapho kuphuma khona indle, kanti enye iyimbobo evamile ye-urethra kanye ne-vagina. Lokhu kusho ukuthi umchamo uphuma futhi uxhumeke ne-vagina usuka endaweni efanayo.
Lesi simo (i-Urogenital Sinus) senzeka ngezigaba zokuqala zokukhula kwengane. Cabanga nje, isikhathi esifushane kakhulu esigabeni sengane, zonke izinhlelo ezintathu - umgudu wamathumbu (i-rectum), umgudu wangasese (isitho sangasese sowesifazane), kanye nomgudu womchamo (isitho sangasese sowesifazane) - konke kuxhunywe emgodini owodwa kanye nomgodi. Lokhu sikubiza ngokuthi ( i-Cloaca ). Njengoba ingane ikhula, lezi zinhlelo ezintathu ziyahlukana futhi zakha izikhala ezintathu ezihlukene (isitho sangasese sowesifazane, i-urethra , kanye ne-anus). Kodwa ngezinye izikhathi, ngesizathu esithile, umgudu womchamo kanye nohlelo lokuzala - ikakhulukazi i-urethra kanye nesitho sangasese sowesifazane - azihlukani kahle, kodwa ziyaqhubeka nokugcina imbobo eyodwa. Leyo mbobo evamile ibizwa ngokuthi (i-Urogenital Sinus). Abanye abantu babiza lokhu nangokuthi (i-Persistent Urogenital Sinus - PUGS).
Yini evame ukubangela i-Urogenital Sinus?
Ngesikhathi sokukhula okuvamile, le ndawo (ebizwa ngokuthi i-Urogenital Sinus) kamuva izoba yi-urethra kanye nesikhumba esizungeze umgodi wesitho sangasese sowesifazane (i-vulvar vestibule). I-urethra yipayipi lapho umchamo uphuma khona emzimbeni wakho. Isikhumba esizungeze umgodi wesitho sangasese sowesifazane (i-vulvar vestibule) yisikhumba esingaphakathi kwe-labia, phakathi kwe-urethra kanye nomgodi wesitho sangasese sowesifazane.
Ikuphi i-Urogenital Sinus emzimbeni?
Lokhu (i-Urogenital Sinus) kuxhunywe ku-urethra kanye nesitho sangasese sowesifazane.
Ingabe zikhona izinhlobo ze-Urogenital Sinus?
Yebo, kunezinhlobo ezimbili eziyinhloko ze-Urogenital Sinus. Ukuhlonza lokhu kubaluleke kakhulu ekuhleleni ukwelashwa.
1. Ukuhlangana okuphansi/okuphansi: Kulolu hlobo, i-urethra kanye nesitho sangasese sowesifazane kuhlangana eduze kakhulu nomnyango wangaphandle womzimba, okungukuthi, phansi. Ngakho-ke, lo mzila ovamile umfushane kakhulu. Kulokhu, i-urethra kanye nesitho sangasese sowesifazane kufana kakhulu ngobukhulu kanye nendawo evamile. Lesi yisimo esingesibi kangako.
2. Ukuhlangana okuphezulu / Ukuhlangana okuphezulu: Kulesi simo, i-urethra kanye nesitho sangasese sowesifazane kuhlangana kude nomnyango wangaphandle womzimba, okungukuthi, phezulu. Khona-ke le ndlela evamile inde kakhulu. Lolu hlobo lokuhlangana okuphezulu luyimbi kakhulu. Ngoba, ezinye izinkinga zingavela ngalokhu. Isibonelo, i-anus ingatholakala phambili kakhulu kunokujwayelekile emzimbeni.
Kungavamile kangakanani lesi simo (se-Urogenital Sinus)?
I-Urogenital Sinus yisimo esingavamile kakhulu . Uma sikhuluma nje, sithinta cishe izingane ezisanda kuzalwa ezingu-0.6 kwezingu-10,000.
Ziyini izimpawu ze-Urogenital Sinus?
Izimpawu ze-Urogenital Sinusitis zingahluka kuye ngokuthi isimo sibucayi kangakanani. Ezinye zezimpawu ezisobala kakhulu zifaka:
- Ukuba nomthombo owodwa kuphela wokukhipha indle kanye nomunye umthombo ovamile esithweni sangasese sowesifazane kanye ne-urethra.
- Ukuvuvukala kwesitho sangasese sowesifazane ngenxa yokuqongelela komchamo. Lokhu kubizwa nangokuthi (i-Hydrocolpos).
- Isitho sangasese sowesifazane singase sivalwe ngendlela engavamile.
- Ngezinye izikhathi kungase kungabikho nhlobo isitho sangasese sowesifazane.
- Isibeletho, ama-ovari, noma amashubhu e-fallopian awakhuli kahle.
Yiziphi izimbangela ze-Urogenital Sinus?
Uma sikhuluma iqiniso, ngisho nochwepheshe bezokwelapha bakuthola kunzima ukukhomba imbangela eqondile ye-Urogenital Sinus.
Kwezinye izimo, lokhu kungahlotshaniswa nesimo esibizwa ngokuthi i-Congenital Adrenal Hyperplasia (CAH). I-CAH iyiqembu lezifo zofuzo. Uma une-CAH, eyodwa noma zombili izindlala zakho ze-adrenal azikhiqizi i-enzyme edingekayo ukwenza ama-hormone. Lokhu kungabangela ukuthi izitho zobulili zikhule ngendlela engavamile. I-CAH ingathinta noma ubani, kodwa amantombazane anamathuba amaningi okuba nezitho zobulili ezingavamile.
Isimo esibizwa ngokuthi i-virilization singabangela ne-urogenital sinusitis. I-virilization yilapho umfana enama-hormone amaningi kakhulu wesilisa (ama-androgen) emzimbeni wakhe. Ama-Androgen yiwo asiza umzimba ukuthi ukhule, futhi athinta nezinto ezifana nokujula kwezwi, izinwele zomzimba, kanye nokukhula kwemisipha.
Isifo se-Urogenital Sinus sitholakala kanjani?
(Urogenital Sinus) kubaluleke kakhulu ekunqumeni ukuthi singayelapha kanjani leso simo. Lokhu kungathinta hhayi nje kuphela izitho zangasese zengane yakho, kodwa futhi nokukhula kwayo konke kanye nentuthuko.
Ngezinye izikhathi, odokotela bangasithola lesi simo (i-Urogenital Sinus) ngesikhathi sokuhlolwa kwe-ultrasound ngenkathi umntwana esesesibelethweni. Kodwa-ke, ngokuvamile, odokotela basithola ngesikhathi sokuhlolwa kokuqala ngokomzimba ngemva kokuzalwa komntwana. Bangase benze ukuhlolwa kwegazi ukuze bafunde kabanzi ngempilo yomntwana iyonke kanye nezinkinga zofuzo.
Udokotela angase acele ukuhlolwa okwengeziwe ukuqinisekisa ukuxilongwa noma ukufunda kabanzi mayelana nobukhulu be-Urogenital Sinus. Lokhu kungafaka:
- I-Ultrasound: Lokhu kusebenzisa amaza omsindo avame kakhulu ukuthatha ividiyo noma izithombe zezitho zomzimba ezingaphakathi emzimbeni. Lokhu kungabonisa izinkinga ngezinso zengane yakho, esinyeni, esithweni sangasese sowesifazane kanye ne-rectum. Kungaphinde kubone ukuthi ingane yakho inomchamo oqongelelekile esithweni sangasese sowesifazane (hydrocolpos).
- I-genitogram yokubuyisela emuva: Lolu futhi uhlobo lokuhlolwa kwezithombe. Kulolu vivinyo, udokotela ufaka idayi ekhethekile ku-urethra/isitho sangasese sowesifazane bese ethatha i-X-ray. Lolu dayi luvumela usayizi, ukuma, kanye nendawo yezicubu nezitho zomzimba ukuthi kubonakale ngokucacile.
- Ukuhlolwa Kokuqagela Ukuzwakala Kwamagnetic (MRI): I-MRI isebenzisa i-magnet, amaza omsakazo, kanye nekhompyutha ukuthatha izithombe ezicacile zomzimba. Lokhu kunganikeza izithombe ezinemininingwane eminingi ze-Urogenital Sinus. I-MRI ingasetshenziswa futhi ukuhlola noma yiziphi izinkinga ngesinqe somntwana kanye nomgogodla.
- I-Endoscopy: I-endoscopy isebenzisa ithubhu elincane, elide (i-endoscope) elinokukhanya kanye nekhamera kolunye uhlangothi. Le endoscope ifakwa ku-urethra/isitho sangasese sowesifazane ukuze kubhekwe ukwakheka komzimba ngaphakathi.
Indlela yokwelapha i-Urogenital Sinus?
Ukuphela kwendlela yokwelapha isimo se-Urogenital Sinus ukwenza ukuhlinzwa ukuze kuhlukaniswe isitho sangasese somntwana wakho kanye ne-urethra. Ngezinye izikhathi, ikakhulukazi ezinganeni ezinesifo sofuba (ngenxa ye-Congenital Adrenal Hyperplasia (CAH)) futhi ezitholakale zine-Disordered Sexual Development (DSD), kungaba nemibono exubile mayelana nokwenza ukuhlinzwa. Ngakho-ke, ngaphambi kokuhlinzwa, kufanele ukhulume ngokuningiliziwe nethimba lezokwelapha elilapha ingane yakho. Leli thimba livame ukufaka:
- Udokotela ogxile ezifweni zesistimu yomchamo kanye nesistimu yokuzala ((Urologist)).
- I-endocrinologist udokotela ogxile ezifweni ezihlobene nohlelo lwe-endocrine. Uhlelo lwakho lwe-endocrine yilona olwenza futhi lukhiphe ama-hormone.
Ukuhlinzwa kuvame ukwenziwa phakathi nonyaka wokuqala womntwana . Lokhu kuhlinzwa kwenziwa udokotela wezifo zomchamo.
Uma une-Urogenital Sinus ephansi, udokotela we-Urologist uvame ukwenza ukuhlinzwa okubizwa ngokuthi i-Flap vaginoplasty. Kulokhu, bakha izikhala ezimbili ezihlukene ngaphandle komzimba - enye yesitho sangasese sowesifazane, kanti enye ye-urethra.
Uma unesimo esinamajoyinti aphezulu (i-Urogenital Sinus), udokotela (Urologist) uvame ukwenza ukuhlinzwa okubizwa ngokuthi i-Pull-through vaginoplasty). Lokhu kuwukuhlinzwa okuyinkimbinkimbi kancane. Kulokhu, udokotela (Urologist) uhlukanisa isitho sangasese sowesifazane nomgodi ovamile, adale ohlukile, bese evala lowo mgodi ovamile. Ngemuva kwalokho, umchamo uyaqhubeka nokugeleza uphuma endaweni lapho kwakukhona khona umgodi ovamile.
Kwezinye izimo ze-high-jointed (Urogenital Sinus), udokotela (Urologist) angenza inqubo ebizwa ngokuthi (Urogenital mobilization) kanye ne-(Flap vaginoplasty). Ngesikhathi (Urogenital mobilization), bazokwenza okulandelayo:
- I-rectum ihlukene.
- I-urethra kanye nesitho sangasese sowesifazane kuyahlukaniswa futhi kuhlanganiswe ndawonye bese kulethwa e-perineum.
- I-rectum ixhunywe ku-sphincter yendunu .
- Ngemuva kwalokho kwenziwa (i-flap vaginoplasty).
Ezinye izingane zingadinga nokuhlinzwa okubizwa ngokuthi i-Clitoroplasty kanye/noma i-Labiaplasty. I-Clitoroplasty ihilela ukubumba kabusha izicubu ukuze kwakheke i-clitoris evamile. Udokotela ohlinzayo uzama ukulondoloza imizwa eminingi ngangokunokwenzeka ukuze ingane ibe nokuphila kocansi okunempilo lapho ikhula. I-Labiaplasty ihilela ukubumba kabusha i-labia, okuyizindebe ezizungeze isitho sangasese sowesifazane.
Kuthatha isikhathi esingakanani ukuthi umntwana alulame ngemva kokwelashwa nge-Urogenital Sinus?
Ingane yakho kuzodingeka ihlale esibhedlela izinsuku ezimbalwa ngemva kokuhlinzwa (kwe-Urogenital Sinus). Ubuhlungu kufanele buqale ukuncipha phakathi nesonto, futhi ingane kufanele ilulame ngokuphelele phakathi nenyanga. Kodwa-ke, kuye ngokuthi i-Urogenital Sinus yengane yakho inzima kangakanani, udokotela wengane yakho uzokunikeza umbono ocacile ngalokhu.
Ingabe i-Urogenital Sinus ingavinjelwa?
Uma othile emndenini wakho enesifo esibizwa ngokuthi i-Congenital Adrenal Hyperplasia (CAH), futhi ukhulelwe noma uzama ukukhulelwa, kubalulekile ukukhuluma nodokotela wakho. Ukuze uvimbele i-Urogenital Sinus, ama-hormone anganikezwa ngaphambi kokubeletha.
Yini okufanele ngiyilindele uma ingane yami ine-Urogenital Sinus?
Umphumela wengane yakho uncike ngobukhulu be-urogenital sinus yayo. Umgomo wokuhlinzwa ukunikeza ingane yakho ukusebenza okuvamile kanye nokubukeka kwezitho zangasese. Iningi lezingane ezihlinzwayo liyakwazi ukuchama ngendlela evamile ngemva kokululama.
Njengoba umntwana ekhula, isitho sangasese sowesifazane singaba sincane (i-vaginal stenosis) futhi sibe sifushane. Lokhu kungabangela izinkinga ngesikhathi socansi lwesitho sangasese sowesifazane.
Ingane enesifo se-Urogenital Sinus ayimvimbeli ukuthi akhulelwe. Kodwa-ke, uma ukuhlinzwa bekubanzi kakhulu, kungaba ngcono ukwenza ukuhlinzwa ngokuhlinzwa (C-section) ngesikhathi sokubeletha. Udokotela wakho uzoxoxa ngalokhu nengane yakho ngesikhathi esifanele.
Ngingayinakekela kanjani ingane yami?
Odokotela bengane yakho bazokutshela ukuthi ungayiphatha kanjani kangcono. Ubukhali be-(Urogenital Sinus) kanye nemiphumela yokuhlinzwa kuzonquma ukuthi uzoqhubeka kanjani uyinakekela.
Kufanele ngimbone nini udokotela?
Ngemva kokuhlinzwa, ingane yakho kuzodingeka ibe nezikhathi zokulandelela njalo ukuqinisekisa ukuthi umzimba wayo ululama kahle futhi usebenza njengoba kulindelekile. Qiniseka ukuthi uya kuzo zonke lezi zikhathi zokuhlangana.
Uma ubona noma yiziphi izimpawu ezintsha, njengokungakwazi ukuzibamba ngomchamo, khuluma nodokotela wezingane noma udokotela we-urologist wengane yakho.
Yimiphi imibuzo okufanele ngiyibuze udokotela wengane yami?
Nazi ezinye imibuzo ongayibuza udokotela wakho:
- Hlobo luni lwe-Urogenital Sinus ingane yami enalo?
- Yikuphi ukuhlinzwa okuncomayo?
- Kunconywa ukuhlinzwa eneminyaka emingaki?
- Ingabe ingane yami izozwa ubuhlungu, noma ingabe isizwa ubuhlungu kakade?
- Ingabe ingane izodinga ukuhlinzwa okwengeziwe njengoba ikhula?
- Ulindele ukuthi ingane yakho ibe nezinkinga nge-urethra noma isitho sayo sangasese sowesifazane njengoba ikhula?
- Ingabe lokhu kuzothinta umjikelezo wokuya esikhathini kwengane yami?
- Ingabe lokhu kuzothinta ikhono lami lokukhulelwa umntwana?
- Ingabe ingane yami izokwazi ukubeletha ngokuphephile?
Okubalulekile: Ungesabi ukubuza udokotela wakho noma yimiphi imibuzo onayo, kungakhathaliseki ukuthi mincane kangakanani. Unelungelo lokwazi konke ngokucacile.
Kuyini i-Urogenital Disorder ngokujwayelekile?
Isifo Sokuchama Kwesitho Sokuzala yinoma yisiphi isimo esithinta uhlelo lwakho lomchamo kanye nohlelo lokuzala. Ezinye izibonelo zifaka:
- Izimila ezingembi.
- I-Hernia.
- Izifo Ezithathelwana Ngocansi (ama-STI).
- Umdlavuza ofana nomdlavuza wesinyi, umdlavuza wesibeletho, noma umdlavuza wesibeletho.
- I-Interstitial cystitis/bladder pain syndrome (IC/BPS).
Okokugcina, izinto okufanele uzikhumbule (Umyalezo Wokuya Ekhaya)
Kuvamile ukuzizwa ushaqekile futhi wesaba uma uthola ukuthi ingane yakho ine-Urogenital Sinus. Kodwa khumbula, lesi simo singelashwa ngokuhlinzwa ukuze kuhlukaniswe i-urethra yengane yakho kanye nesitho sangasese sowesifazane. Lokhu kusho ukuthi ingane yakho kufanele ikwazi ukuchama ngokukhululeka.Njengoba ekhula, kufanele futhi abe sesikhathini sakhe. Kodwa-ke, ngezinye izikhathi, njengoba ekhula, angase azizwe engakhululekile ngesikhathi socansi lwesitho sangasese sowesifazane.
Into ebalulekile ukuthi, akudingeki ubhekane nalezi zinto wedwa. Khuluma nodokotela wengane yakho. Bangaphendula yonke imibuzo yakho, banciphise ukwesaba kwakho, futhi bakusize uthole ukwelashwa okungcono kakhulu nokunakekelwa kwengane yakho.
I- Urogenital sinus, ama-PUGS, ukukhubazeka kokuzalwa, uhlelo lomchamo, uhlelo lokuzala, ukuhlinzwa, impilo yengane











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