Udokotela wakho kungenzeka ukuthi ukutshelile ukuthi ungase ube nesifo esibizwa ngokuthi i-myopathy. Kuvamile ukuthi kube nemibuzo eminingi engqondweni yakho uma uzwa lokho. Iyini ngempela i-myopathy? Ingabe kuyinto okufanele uyesabe? Ingabe ikhona indlela yokwelapha? Ake sixoxe ngayo kalula nangokucacile.
Kalula nje, iyini i-myopathy?
I-Myopathy igama elivamile elinikezwa iqembu lezifo ezithinta imisipha yamathambo emizimbeni yethu. Lezi zifo zilimaza futhi zibuthakathaze imicu yemisipha emisipheni yethu. Lesi simo singaba khona lapho sizalwa noma sikhule kamuva ekuphileni.
Manje ungase uzibuze ukuthi iyini imisipha yamathambo. Kulula kakhulu. Yimisipha enamathele emathanjeni ethu futhi esingayilawula futhi sinyakaze ngendlela esifuna ngayo. Cabanga ngakho, uma uphakamisa ingalo, ugoba umlenze, uhamba, ukhuluma... le misipha yamathambo iyasiza kukho konke lokhu. Inani elikhulu lemisipha emzimbeni wethu lingelalolu hlobo. Ngakho-ke lapho kuvela i-myopathy, ngisho nokwenza le misebenzi yansuku zonke kungaba nzima.
Yiziphi izinhlobo eziyinhloko ze-myopathies?
I-Myopathies ingahlukaniswa ngezigaba ezimbili eziyinhloko: ezizuzwe njengefa nezitholwe ngofuzo. Ake sibheke lezi zinhlobo ngokwehlukana.
| Uhlobo lwe-myopathy | Incazelo elula |
|---|---|
| 1. I-Myopathies Ezuzwe Njengefa Izinhlobo ezizuzwe kubazali ngokuguqulwa kwezakhi zofuzo. | |
| I-Myopathies Yokuzalwa | Lokhu kuvame ukubonakala njengezimpawu enganeni encane noma enganeni. Amakhono okunyakaza komzimba njengokukhasa nokuhamba angase aphuze. Zonke imisipha yamathambo emzimbeni zivame ukuthinteka, futhi isimo asibi sibi ngokuhamba kwesikhathi. |
| I-Mitochondrial Myopathies | Kubangelwa ukukhubazeka ku-mitochondria, "izindawo zamandla" zamaseli ethu ezikhiqiza amandla. Ngaphezu kobuthakathaka bemisipha, kungathinta nenhliziyo, ubuchopho, kanye nesistimu yokugaya ukudla. Izibonelo zifaka phakathi i-Kearns-Sayre syndrome , i-MELAS , kanye ne -MERRF . |
| I-Muscular Dystrophies | Kulezi zimo, ubuthakathaka bemisipha bukhula kancane kancane ngokuhamba kwesikhathi. Lesi simo sibangelwa ukuwohloka kwezicubu zemisipha ngenxa yokukhubazeka kwamaprotheni asekela izicubu zemisipha. |
| I-Metabolic Myopathies | Lesi yisimo lapho kuba khona ubuthakathaka bemisipha obungazelelwe ngesikhathi sokuzivocavoca noma ukucindezeleka kwemisipha. Lesi simo sibangelwa ukukhubazeka kwezakhi zofuzo ezikhiqiza ama-enzyme athile. |
| 2. I-Myopathies Etholakale Izinhlobo ezenzeka kamuva ekuphileni ngenxa yezimbangela zangaphandle. | |
| I-Autoimmune/Inflammatory Myopathy | Kubangelwa inkinga ngesimiso sethu somzimba sokuzivikela ehlasela imisipha. |
| I-Myopathy Enobuthi | Kungabangelwa ubuthi obuthile (isib. utshwala obuningi) noma imithi ethile. |
| I-Endocrine Myopathy | Zibangelwa izinkinga ohlelweni lwe-endocrine, olulawula ama-hormone emzimbeni wethu. Lokhu kungabangelwa izifo ze-thyroid noma izindlala ze-adrenal. |
| I-Myopathy Ethelelanayo | Ubuthakathaka bemisipha ngenxa yokutheleleka ngegciwane, amagciwane, izimuncagazi, noma isikhunta. |
| I-Myopathy Yesifo Esibucayi Eyunithi Yokunakekelwa Okujulile | Kungenzeka ngesikhathi sokwelashwa egunjini lokunakekelwa okujulile (ICU). Kucatshangwa ukuthi kubangelwa ukuba sesimweni esifanayo isikhathi eside. Kuthinta kakhulu imisipha esiza ekuphefumuleni. |
Yiziphi izimpawu ezivamile ze-myopathy?
Uphawu oluyinhloko oluvame kakhulu kuzo zonke izinhlobo ze-myopathy ubuthakathaka bemisipha . Lokhu kuvame ukuzwakala ezingalweni ezingaphezulu, emahlombe nasemathangeni. Ngaphezu kwalokho, izimpawu ezifana nalezi:
- Ukuqaqamba kwemisipha nokuqina kwayo
- Ukuqaqamba kwemisipha
- Amandla aphansi
- Ukuzizwa ukhathele ngokushesha ngisho nangemva kokwenza imisebenzi emincane
Ngenxa yalobu buthakathaka bemisipha, ngisho nemisebenzi elula yansuku zonke njengokugqoka, ukugeza, ukukama izinwele zakho, ukukhuphuka izitebhisi, nokuvuka embhedeni kungaba yinselele.
Ezinye izinhlobo ze-myopathy nazo zinezimpawu ezithile. Isibonelo, ekuwohlokeni kwemisipha, ubuthakathaka bemisipha bukhula kancane kancane. Lobu buthakathaka buvame ukuqala ebusweni, ezinqeni nasemahlombe.
I-myopathy itholakala kanjani?
Ngenxa yokuthi kunezifo eziningi ezithinta imizwa nemisipha emizimbeni yethu, kudingeka izivivinyo eziningana ukuze kutholakale ngokunembile i-myopathy. Udokotela wakho angase ancome okukodwa noma ngaphezulu kwalokhu kuhlolwa.
| Igama lokuhlolwa | Kalula nje... |
|---|---|
| Ukuhlolwa Kwezakhi Zofuzo | Basebenzisa isampula yegazi noma yamathe ukuhlola ukuthi kukhona yini iphutha ezizakhini zakho zofuzo. |
| Ukuhlolwa Kwezakhi Zofuzo Ze-Biochemical | Igazi, umchamo, noma uketshezi lomgogodla kuyahlolwa ukuze kubhekwe ukungasebenzi kahle kwama-enzyme. |
| I-CT Scan (i-Computerized Tomography) | Kuthathwa uchungechunge lwe-X-ray ukuze kudalwe isithombe esiphelele se-3D samathambo, imithambo yegazi, nezicubu ezithambile. |
| Ukubhoboza kwe-Lumbar | Inaliti encane ifakwa phakathi kwamathambo amabili angemuva ongezansi bese kuthathwa uketshezi lomgogodla (i-CSF) bese kuhlolwa. |
| Ukuskena kwe-MRI (Umfanekiso Wokuqabulana Kwamagnetic) | Kusetshenziswa insimu enamandla yamagnetic kanye namagagasi omsakazo ukuthola izithombe ezinemininingwane yezitho zomzimba, izicubu kanye nohlaka lwamathambo. |
| I-Biopsy Yezinzwa Nemisipha | Ukuze kuhlolwe, ingxenye encane yezicubu isuswa ngokuhlinzwa emsipheni noma emsipheni ofanele bese ithunyelwa elabhorethri. |
| Izifundo Zokuqhuba Imizwa | Ama-electrode anamathele esikhumbeni, avuselela imizwa futhi alinganise isivinini lapho izimpawu zikagesi zihamba khona kuzo. Lokhu kusiza ekunqumeni ukuthi kunenkinga yini ngemizwa. |
| I-Electromyography (EMG) | Ama-electrode amancane afakwa emisipheni futhi umsebenzi kagesi ulinganiswa njengoba imisipha ifinyela futhi ihamba. Lokhu kungasiza futhi ekunqumeni ukuthi inkinga isemisipheni ngokwayo. |
Yiziphi izindlela zokwelapha i-myopathy?
Ukwelashwa kwe-myopathy kuncike ngokuphelele ohlotsheni lwe-myopathy onayo.
Ayikho ikhambi lezinkinga eziningi ze-myopathies ezizuzwe njengefa . Kodwa-ke, izimpawu zingalawulwa futhi impilo ingenziwa ibe lula ngokwelashwa okufana nokwelashwa ngokomzimba . Ezinye izinhlobo, njenge- Duchenne muscular dystrophy kanye nesifo se-Pompe, nazo zingelashwa ngemithi.
I-myopathies etholakele ivame ukwelashwa ngokwelapha imbangela eyisisekelo . Isibonelo, i-endocrine myopathy iphathwa ngokuqinisa amazinga ama-hormone. Kuye ngokuthi isimo sibucayi kangakanani, ukwelashwa ngokomzimba kungadingeka futhi kulezi zimo.
Okubaluleke kakhulu, udokotela wakho uzonquma uhlelo lokwelapha olungcono kakhulu lwesimo sakho, ngakho-ke vuleka futhi uthembeke kuye nganoma yini.
Umlayezo Wokuya Nawe Ekhaya
- I-Myopathy akuyona isifo sezinzwa, kodwa yisifo esithinta imisipha .
- Kunezinhlobo eziningi zalokhu; ezinye zikhona lapho zizalwa, kanti ezinye zikhula kamuva ekuphileni.
- Uphawu oluyinhloko ubuthakathaka bemisipha, okungenza izinto ezifana nokuhamba nokuphakamisa kube nzima.
- Kungadingeka ukuhlolwa okuhlukahlukene, njengokuhlolwa kwegazi, ukuskena, kanye ne-biopsies, ukuze kutholakale ngokunembile lesi sifo.
- Ukwelashwa kuncike ohlotsheni lwe-myopathy onayo, ngakho-ke xhumana nodokotela wakho njalo ukuze uthole iseluleko esifanele.











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