Cabanga nje ungakwazi ukulawula izingalo noma imilenze yakho. Izitho zomzimba wakho ziyanyakaza ngokungazikhetheli, njengokungathi othile uyadansa. Empeleni lesi yisimo abanye abantu ababhekana naso. Umuntu obona lokhu angase acabange ukuthi uyadansa nje. Igama elithi Chorea livela egameni lesiGreki elisho "umdanso". Kodwa kumuntu ohlushwa yilokhu, akulula kangako. Ake sifunde kabanzi ngakho namuhla.
Iyini ngempela iChorea?
Kalula nje, i-Chorea iyisifo sokunyakaza. Ibangelwa ukungasebenzi kahle kwe-basal ganglia, uhlelo lwezinzwa oluphakathi olutholakala ekujuleni kobuchopho olulawula ukunyakaza. Lokhu kubangela ukunyakaza okungazikhetheli kwezandla, izinyawo, nobuso okwenzeka ngaphandle kokulawula kwethu.
Lokhu kunyakaza kungaba kuncane kakhulu ngezinye izikhathi, njengokujika emuva naphambili. Abanye abantu bacabanga ukuthi lokhu kumane kuwukusabela kokwethuka. Kodwa ngezinye izikhathi kungaba ukunyakaza okunobudlova nokusheshayo okugeleza kusuka kwenye ingxenye yomzimba kuya kwenye.
Yiziphi izimpawu eziyinhloko zalesi sifo?
Kunezimpawu eziningana ezithile odokotela abazisebenzisayo ukuxilonga i-Chorea. Lezi zingaba uphawu lokuthi ungase ube nalesi simo.
| Isibonakaliso | Kuchazwe kalula |
|---|---|
| Ukubamba kwencekukazi yobisi | Laba bantu banenkinga yokugcina imisipha iqinile. Isibonelo, uma ubamba isandla sabo, ngeke basibambe ngokuqinile, kodwa bazosicindezela futhi basikhulule njengokungathi bayasenga. |
| Ulimi olufana noJack-in-the-box | Lapho ecelwa ukuba akhiphe ulimi lwakhe, ngokuzumayo uyalukhipha bese elubuyisela ngaphakathi. Kufana nokugxumela ithoyizi ebhokisini. Lokhu kubizwa nangokuthi ulimi lukaHarlequin. |
| Ukuhamba okuhlukile | Abantu abane-chorea banendlela ehlukile yokuhamba. Udokotela wezinzwa angasithola lesi simo ngokubheka le ndlela yokuhamba. |
Ezinye izinhlobo ze-chorea
Ngaphezu kwezinhlobo eziyinhloko ze-chorea, kunezinye izinkinga eziningana zokunyakaza ezihambisana nayo.
- I-Athetosis: Lolu uhlobo lwe-chorea olusebenza kancane. Lapha, ukunyakaza kuba yinto enyakazayo nejiyile.
- I-Choreoathetosis: Lokhu kuyinhlanganisela ye -Chorea kanye ne-Athetosis. Lapha ukunyakaza kwenzeka ngesivinini esimaphakathi kanye namandla.
- I-Ballism/i-Ballismus: Lolu uhlobo lwe-chorea olushesha kakhulu nolunobudlova. Kubonakala sengathi othile uphonsa izingalo nemilenze yakhe.
Ziyini izimbangela ze-chorea?
Njengoba sixoxile ngaphambili, impande yalokhu yingxenye yobuchopho ebizwa ngokuthi i-basal ganglia. Ososayensi bakholelwa ukuthi i-chorea yenzeka lapho le ngxenye ithola ikhemikhali eliningi kakhulu elibizwa ngokuthi i-dopamine, elisiza ekusebenzeni kwezinzwa. I-Dopamine ibalulekile emizimbeni yethu, kodwa uma iba ningi kakhulu, ingabangela izinkinga ezinjengalezi.
Imbangela eyinhloko neyaziwa kakhulu ye-chorea yisifo sikaHuntington . Lesi yisifo esizuzwa njengefa.
Kodwa-ke, kungaba nezinye izizathu eziningi zalokhu, ezinye zazo ezingavamile kakhulu.
- Umkhuhlane we-rheumatic: Ezinye izingane zingase zibe nesimo sesikhashana se-chorea uma ziba nomkhuhlane we-rheumatic ngemva kokutheleleka komphimbo (strep throat) noma umkhuhlane obomvu.
- Izifo ezihlasela umzimba : Lesi simo singavela kubantu abanezifo ezifana ne-lupus.
- Ukulimala kobuchopho: I-Chorea ingabangelwa yizimo ezifana nomdlavuza wobuchopho noma isifo sohlangothi.
- Ukuphazamiseka kwama-hormone kanye nokuphazamiseka kwe-metabolic: Lokhu kungabangelwa nayizimo ezifana ne-hypothyroidism.
- Imithi ethile: I-Chorea ingenzeka njengomphumela ongemuhle wemithi ethile, ikakhulukazi leyo esetshenziselwa isifo sikaParkinson .
Ake sifunde ngokuxilongwa kanye nokwelashwa.
Into yokuqala udokotela ayenzayo ukubona izimpawu zakho.Inselele iwukuthola imbangela yalesi sifo , okungasizwa ukuskena kobuchopho (ukuhlolwa kwezithombe) kanye nokuhlolwa kwegazi.
Futhi, udokotela wakho uzobuza nakanjani ngayo yonke imithi oyithathayo njengamanje, njengoba ngezinye izikhathi lokhu kungabangelwa umuthi.
Uma imbangela isitholakele, udokotela wakho uzonquma ukuthi udinga ukwelashwa noma cha. Kwezinye izimo, ikakhulukazi uma kubangelwa umuthi, isimo se-chorea sizophela sodwa uma umuthi umisiwe noma ushintshiwe. Ngaphandle kwalokho, imbangela eyisisekelo yalesi simo izokwelashwa.
Kunemithi engasiza ekulawuleni lokhu kunyakaza okungalawuleki. Le mithi ivame ukusebenza ngokuvimbela isenzo se-dopamine ebuchosheni. Nakuba ukuhlinzwa kobuchopho kanye nokuvuselelwa kobuchopho okujulile (i-DBS) kusetshenziswa njengokwelapha, ayivamile ukusetshenziswa ngenxa yokuthi kungenzeka kube nezinkinga.
Isifo sikaHuntington kanye neChorea
Uma sikhuluma nge-chorea, asikwazi ukuzibamba ngaphandle kokukhuluma ngesifo sikaHuntington. Lesi yimbangela eyaziwa kakhulu ye-chorea. Kodwa yisifo esingavamile kakhulu, esithinta umuntu oyedwa kuphela kwabayi-10,000 noma abangu-20,000.
Lesi sifo sihlukile kwezinye izimbangela ngoba asinalo ikhambi elithile futhi lesi sifo siyaqhubeka ngokuhamba kwesikhathi futhi siholela ekufeni . Lesi sifo senzeka lapho izingxenye ze-basal ganglia ebuchosheni zibhujiswa.
I-chorea ivame ukuqala phakathi kweminyaka engama-35 nengama-40. Nakuba izinkinga zengqondo nazo ziqala ngesikhathi esifanayo, azibonakali kahle ezigabeni zokuqala.
Uhlangothi lwezakhi zofuzo lwesifo sikaHuntington
Ngenxa yokuthi kuyisifo esizuzwa njengefa, ingane ezelwe ngumama noma ubaba onesifo sikaHuntington inethuba elingu-50% lokuthola lesi sifo. I-gene enephutha eliyimbangela yatholakala ososayensi ngo-1993.
Namuhla, ulwazi mayelana nalesi sifo lungatholakala ngokuhlolwa kwezakhi zofuzo .
- Uma unezimpawu, qiniseka ukuthi yisifo sikaHuntington.
- Uma othile emndenini wakho (abazali, izihlobo) enalesi sifo, thola ukuthi nawe uzosithola yini lesi sifo esikhathini esizayo.
- Thola ukuthi ingane esibelethweni inalesi sifo ngesikhathi sokukhulelwa (ukuhlolwa kwangaphambi kokubeletha).
Kodwa ngaphambi kokwenza ukuhlolwa kofuzo okunjalo, kubaluleke kakhulu ukufuna iseluleko sofuzo mayelana nendlela yokubhekana nemiphumela. Ngoba lesi yisinqumo esizothinta impilo yakho. Ngakho-ke, kufanele ukhulume nodokotela onolwazi ngakho futhi ucabange ngokucophelela ngaphambi kokwenza ukuhlolwa okunjalo.
Umlayezo Wokuya Nawe Ekhaya
- I-Chorea yisifo sokunyakaza esenzeka ngaphandle kokulawulwa nguwe. Sibangelwa inkinga ebuchosheni.
- Lokhu kungabangelwa imithi, izifo ezizuzwe njengefa (njengesifo sikaHuntington), kanye nezinye izimo zezokwelapha.
- Uma wena noma othile omaziyo enalezi zimpawu, ungalibali ukubona udokotela ofanelekayo, ikakhulukazi udokotela wezinzwa .
- Ukuhlonza lesi sifo ngendlela efanele kuyisinyathelo sokuqala sokwelashwa okufanele.
- Uma kukhona ukusolakala kwesifo esizuzwe njenge-Huntington's, kubaluleke kakhulu ukufuna ukwelulekwa ngofuzo ngaphambi kokuhlolwa ngofuzo.











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