ʻO nā kīʻaha koko liʻiliʻi i hohola ʻia ma ko kākou kino a pau, ua like ia me nā paipu e lawe ana i ka wai. ʻO kēia nā mea e lawe ana i ke koko i nā wahi a pau o ko kākou kino. No laila, he aha ka mea e hana ai inā hōʻino kekahi mea i kēia mau kīʻaha koko? I kēia lā, e kamaʻilio ana kākou e pili ana i kahi maʻi hiki ke koʻikoʻi, a ʻo ia hoʻi kahi maʻi i kapa ʻia ʻo Fibrinoid Necrosis . Mai makaʻu, e hoʻomaopopo maʻalahi kākou i kēia.
He aha ka necrosis fibrinoid?
I ka ʻōlelo maʻalahi, ʻo ka fibrinoid necrosis ka hōʻino ʻia ʻana o nā paia o loko o nā kīʻaha koko liʻiliʻi i loko o ko kākou kino, ʻoiai hoʻi nā aʻa liʻiliʻi . E noʻonoʻo e like me ka pahū ʻana o kahi paipu wai. Ke hōʻino ʻia nā kīʻaha koko ma kēia ʻano, hiki iā lākou ke haki, ʻeha , kahe ke koko, a hiki i ka palapū i loko o ke kino.
ʻO ke ʻano o ka huaʻōlelo "necrosis" ʻo ia hoʻi ka make ʻana o nā cell . ʻO ia hoʻi ka make ʻana o nā cell ma muli o kahi ulia, ʻeha, a i ʻole ka nalowale ʻana o ke koko. He ʻano like ka fibrinoid necrosis, ʻo ia hoʻi ka make ʻana o nā cell i loko o nā paia o nā kīʻaha koko.
Pehea e kū mai ai kēia kūlana?
Me he mea lā he mea paʻakikī iki kēia, akā e noʻonoʻo e pili ana i kēia ʻano. Loaʻa iā mākou kahi ʻōnaehana pale ma ko mākou kino. Ua like ia me ka mana pale i loko o ko mākou kino. ʻO kēia ʻōnaehana ka mea e pale ai iā mākou mai nā maʻi . Akā i kekahi manawa lilo kēia ʻōnaehana pale i mea hana nui a huikau paha.
I ka fibrinoid necrosis, lilo ka ʻōnaehana pale i mea hana nui a hoʻokuʻu i kekahi mau mea. Hoʻopili kēia mau mea i nā paia o loko o ko mākou mau kīʻaha koko. A laila aia ka mumū , ʻo ia hoʻi ka pehu a me ka ʻulaʻula. ʻO kēia mumū ke kumu o ka make ʻana o nā cell i loko o nā paia o nā kīʻaha koko. I nā huaʻōlelo ʻē aʻe, me he mea lā e hoʻouka ana kā mākou mau pale ponoʻī i kā mākou mau cell ponoʻī.
He aha ke kumu o ka necrosis fibrinoid?
ʻO kēlā me kēia kūlana e hiki ke hōʻino i nā kīʻaha koko e hiki ke hana i kēia. Aia kekahi mau kumu nui e kōkua ai:
- Ke koko kiʻekiʻe loa: Ua kapa ʻia kēia ʻo (Malignant Hypertension) a i ʻole (Hypertensive Crisis) . ʻO ka maʻamau, pono ke koko o ke kanaka olakino ma lalo o 130/80 mmHg. Eia nō naʻe, i kēia kūlana i kapa ʻia ʻo (Malignant Hypertension), piʻi ke koko i 180/120 mmHg a ʻoi aku paha. Ke hana ʻia kēia, ʻo kā mākouHiki ke hana ʻia ka necrosis fibrinoid ma ka hōʻino ʻana i nā kīʻaha koko e lawe ana i ke koko i nā ʻōkana koʻikoʻi e like me ka puʻuwai , ka lolo, a me nā puʻupaʻa. He pilikia koʻikoʻi loa kēia a pono e mālama koke ʻia e ke kauka.
- Nā maʻi Autoimmune : E like me ka mea i ʻōlelo ʻia ma mua, ʻo ia nā maʻi kahi e hoʻouka ai kā mākou ʻōnaehana pale ponoʻī i ko mākou kino ponoʻī. Eia kekahi laʻana:
- (ʻO ka ʻArthritis Rheumatoid )
- (Lupus) (Maʻi Lupus - hoʻopilikia i nā ʻōpū he nui e like me ka ʻili, nā hono, nā puʻupaʻa)
- (Rheumatic Fever - kahi kūlana e hiki ke hana ma hope o ka maʻi ʻāʻī a hoʻopilikia i ka puʻuwai)
- Preeclampsia: He kūlana kēia e ulu ai kekahi mau makuahine i ka wā hāpai. Hōʻike ʻia e ke koko kiʻekiʻe a me nā hōʻailona ʻē aʻe.
- (Subacute Bacterial Endocarditis): He maʻi bacteria kēia o ka uhi o loko o ka puʻuwai.
- Vasculitis: I ka ʻōlelo maʻalahi, he mumū ia o nā kīʻaha koko, ʻo ia hoʻi ka pehu ʻana. ʻO nā hiʻohiʻona o kēia:
- (Polyarteritis Nodosa)
- (IgA Vasculitis) (i ʻike mua ʻia ʻo Henoch-Schönlein purpura)
I kēia manawa ua maopopo paha iā ʻoe ʻaʻole i hoʻokumu ʻia kēia ʻano maʻi e hoʻokahi wale nō kumu, akā hiki ke pili pū me nā maʻi like ʻole.
He aha nā hōʻailona o kēia maʻi?
Ma muli o ka hōʻino ʻana o ka fibrinoid necrosis i nā kīʻaha koko, ʻo ke kahe koko ka hōʻailona nui . Hiki ke hana ʻia kēia ma nā ʻano like ʻole:
- Nā ʻāʻī koko.
- Koko i loko o ka ʻōpala (ʻeleʻele a ʻulaʻula paha).
- Koko i loko o ka mimi - kapa mākou i kēia (Hematuria) .
- ʻO ka palapū ma nā wahi like ʻole o ke kino (me he mea lā ua palapū ʻia me ka ʻole o ka pā ʻia ma kahi ʻē).
- Ke kahe ʻana o ke koko i loko o ke kino (ʻaʻole ʻike ʻia kēia mai waho mai, akā hiki ke hoʻomaopopo ʻia mai nā hōʻailona ʻē aʻe).
- Kokoke ka ihu.
Inā he koko kou e like me kēia, mai hoʻowahāwahā . He mea nui loa ka ʻimi ʻana i ke aʻo lapaʻau.
He aha nā pilikia e hiki ke loaʻa mai ka Fibrinoid Necrosis?
ʻO nā pilikia e kū mai ana mai kēia kūlana e hilinaʻi pinepine ʻia i ka maʻi kumu i hoʻokumu ai. E noʻonoʻo, no ka laʻana:
- ʻO ka mea a mākou i kamaʻilio ai (Malignant Hypertension) , ʻo ia hoʻi, inā loaʻa ka fibrinoid necrosis i loko o nā kīʻaha koko o nā puʻupaʻa ma muli o ke koko kiʻekiʻe, hiki iā ia ke alakaʻi i ka hāʻule ʻana o ka puʻupaʻa .
- Inā hiki mai kēia ʻano ma muli o kahi maʻi e like me lupus , hiki ke loaʻa nā ʻeha ʻili a me nā maʻi puʻuwai.
ʻO ia hoʻi, ʻaʻole i hoʻoholo wale ʻia nā pilikia e ka necrosis fibrinoid, akā, e ka maʻi kumu hoʻi.
Pehea e ʻike ʻia ai kēia maʻi? (Diagnosis)
Ke make nā pūnaewele, hoʻokuʻu lākou i kahi mea i kapa ʻia ʻo fibrin . ʻO kēia mea i kapa ʻia ʻo fibrin ka hōʻike nui e ʻike ai i kēia maʻi.
ʻO nā pathologists , he poʻe loea i ka ʻike ʻana i nā maʻi, lawe lākou i kahi hāpana o nā ʻiʻo i hōʻino ʻia a nānā iā ia ma lalo o kahi microscope. A laila hiki iā lākou ke ʻike inā ua waiho ʻia kēia mea (Fibrin).
ʻO ka lawe ʻana i kahi hāpana ʻiʻo ua kapa ʻia he biopsy . ʻOkoʻa ke ʻano o ka hana ʻana i kēia biopsy ma muli o ka wahi o ka maʻi:
- Nā biopsies ʻili: Hiki ke ʻoki ʻia kahi papa lahilahi o ka ʻili mai ka ʻili o ka ʻili, a i ʻole e lawe ʻia kahi ʻāpana liʻiliʻi me kahi mea hana kūikawā (mea hana punch). I kekahi manawa hiki ke hana ʻia kahi ʻoki liʻiliʻi e lawe i kahi hāpana mai kahi hohonu.
- Nā biopsies kūloko: No ka lawe ʻana i kahi hāpana ʻiʻo mai kahi ʻōkana i loko o ke kino, hoʻohana nā kauka i kahi nila a i ʻole kahi mea hana i kapa ʻia he endoscope . He ʻōmole lahilahi ka endoscope me kahi kāmela a me nā mea hana liʻiliʻi ma kekahi ʻaoʻao. Hiki ke hoʻokomo ʻia kēia i loko o ke kino e lawe i kahi hāpana ʻiʻo.
Pehea e mālama ai? (Lapaʻau)
ʻO kaʻoiaʻiʻo, ʻaʻohe lāʻau lapaʻau maʻamau no ka fibrinoid necrosis. Eia nō naʻe, hiki i nā kauka ke kāohi i ke kahe ʻana o ke koko . Aia ia i ka wahi a me ke ʻano o ke kahe ʻana o ke koko.
Eia kekahi, ʻo ka mea nui loa, ʻo ia ka mālama ʻana i ka maʻi kumu i hoʻoulu ai i ka fibrinoid necrosis .
Eia kekahi laʻana, inā ʻo ke koko kiʻekiʻe ke kumu, hāʻawi ʻia ka lāʻau lapaʻau e kāohi iā ia. Inā he pilikia ia me ka ʻōnaehana pale, aia nā lāʻau lapaʻau e kāohi iā ia a hoʻōki i ka hōʻino hou ʻana i nā kīʻaha koko.
No laila, ʻo ka manaʻo nui o ka mālama ʻana, ʻo ia ka mālama ʻana i ke kumu kumu o ka maʻi .
Pehea e pale ai iā ʻoe iho mai ka necrosis fibrinoid? (Kāohi ʻana)
Ma mua o ka ho'āʻo ʻana e pale loa iā ʻoe iho mai kēia, ʻo ka mea maikaʻi loa hiki iā ʻoe ke hana, ʻo ia ke hōʻemi i ka pilikia o ka hoʻomohala ʻana i nā kūlana kumu e hoʻokumu ai.
- E ʻike pinepine i kāu kauka no nā nānā kino. Ma kēlā ala, inā he pilikia olakino, hiki ke ʻike ʻia a mālama ʻia ma mua o ka lilo ʻana i mea koʻikoʻi.
- Inā loaʻa iā ʻoe kahi maʻi e hiki ai ke hoʻoulu i kēia (e like me ke koko kiʻekiʻe, ka maʻi diabetes, ka maʻi autoimmune), e hahai pololei i nā ʻōlelo a kāu kauka . E lawe i kāu mau lāʻau lapaʻau i ka manawa kūpono a mālama i kou nohona e like me ke kauoha.
He aha ka wā e hiki mai ana no kekahi me kēia maʻi? (Wānana)
Pili maoli kēia i ke koʻikoʻi o ke kūlana kumu i hoʻokumu ai i ka necrosis fibrinoid. Hiki i kekahi mau kūlana ke ola a pau, hoʻemi i ke ʻano o ke ola, a hiki ke alakaʻi i ka make mua.
Eia kekahi laʻana, inā ʻaʻole mālama koke ʻia ke kūlana i ʻōlelo ʻia ma luna (Malignant Hypertension) , hiki ke hoʻemi ʻia ke ola o ka mea maʻi a hiki i ʻelua mau makahiki. No laila he mea nui e ʻimi i ke kōkua lapaʻau i ka wā e ʻike ʻia ai nā hōʻailona.
Āhea ʻoe e ʻike ai i ke kauka?
Inā ʻike ʻoe ua hōʻino ʻia nā kīʻaha koko, a i ʻole inā loaʻa iā ʻoe kekahi o nā hōʻailona i ʻōlelo ʻia ma mua (ʻoiai ke kahe koko i wehewehe ʻole ʻia), he mea nui e ʻike i ke kauka no ka nānā pono ʻana.
Ma ka hahai pono ʻana i ka hoʻolālā lapaʻau a kāu kauka e hāʻawi ai iā ʻoe, hiki iā ʻoe ke kaohi i kou kūlana a pale i nā pōʻino hou aʻe.
ʻO ka fibrinoid necrosis kahi maʻi e hōʻino ai i nā kīʻaha koko. Hiki i nā maʻi ke koʻikoʻi, no laila pono ka nānā pono ʻana e ke kauka. Ma ka ʻike pinepine ʻana i kāu kauka, hiki iā ʻoe ke mālama maikaʻi i kou olakino a pale i nā pilikia mai nā maʻi kumu.
Leka Lawe-Home
- ʻO ka necrosis fibrinoid ka hōʻino ʻia ʻana o nā kīʻaha koko liʻiliʻi.
- ʻO nā kumu nui o kēia, ʻo ia nā kūlana e like me ke koko kiʻekiʻe a me nā maʻi autoimmune.
- ʻO ka hōʻailona nui nā ʻano kahe koko like ʻole.
- Pono paha kahi biopsy e ʻike ai i ka maʻi.
- Hoʻokomo mua ʻia ka lāʻau lapaʻau i ke kumu kumu.
- He mea nui loa e ʻimi i ke kōkua lapaʻau inā loaʻa iā ʻoe nā hōʻailona a i ʻole nā kumu pilikia, no ka mea, hiki ke lilo i mea koʻikoʻi inā hoʻowahāwahā ʻia.
Manaʻolana wau he mea pono kēia ʻike iā ʻoe. E ola kino!











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