Ua lohe paha ʻoe i ka maʻi Sickle Cell . I ka ʻōlelo maʻalahi, he ʻano ia e hoʻopilikia ai i ke ʻano o ka hana ʻana o ko mākou kino i nā hunaola koko ʻulaʻula. ʻIke ʻoe, ʻo kēia mau hunaola koko ʻulaʻula nā mea e lawe ana i ka oxygen ma o ko mākou kino. ʻO ka maʻamau, he mau diski pālahalaha, poepoe, a palupalu kēia mau hunaola. Akā, ʻo kekahi me ka maʻi sickle cell e hoʻomohala i nā hunaola koko ʻulaʻula paʻakikī, ʻano sickle. No laila, hiki i kēia ʻano ʻē ke alakaʻi i nā pilikia olakino he nui, a i ʻole nā ' pilikia '. Akā, mai hopohopo, hiki i kāu kauka ke kōkua i ka mālama ʻana i nā pilikia he nui, a pale aku i kekahi o lākou. E kamaʻilio kākou e pili ana i kēlā me kēia.
ʻEha - ka pilikia maʻamau
ʻO ka pilikia maʻamau a hoʻonāukiuki hoʻi o ka maʻi cell sickle, ʻo ia ka ʻeha . ʻO kēia no ka mea ua paʻa nā cell ʻano sickle i loko o nā kīʻaha koko liʻiliʻi. E noʻonoʻo i ka mea e hana ʻia ke paʻa kahi kaʻa nui i kahi alanui haiki. ʻO ia ka mea e hana ʻia ke ālai kēia mau cell i nā kīʻaha koko.
Hiki ke ʻike pinepine ʻia kēia ʻeha ma ke kua haʻahaʻa, nā wāwae, nā lima, ka ʻōpū, a i ʻole ka umauma. Hiki ke hiki koke mai me he hoʻouka kaua koʻikoʻi (pilikia a hanana paha). I nā poʻe ʻōpio a me nā poʻe ʻelemakule, i kekahi manawa he ʻeha lōʻihi.
ʻO ka maʻamau, ke loaʻa iā ʻoe kahi hōʻeha ʻeha e like me kēia, hiki iā ʻoe ke hoʻomaha me nā lāʻau hōʻeha e like me Paracetamol a i ʻole Ibuprofen . Akā e hoʻomanaʻo, mai hāʻawi i ka aspirin i kekahi ma lalo o 19 makahiki. I kekahi manawa, inā koʻikoʻi ka ʻeha, hiki i ke kauka ke kuhikuhi i kahi lāʻau hōʻeha ikaika mai ka hui opioid. Pono kekahi poʻe e hoʻokomo ʻia i ka haukapila no ka mālama ʻana.
Hiki i kāu kauka ke ʻōlelo i kēia mau ʻōlelo aʻoaʻo e pale aku ai a hōʻemi paha i kēia mau hōʻeha ʻeha:
- E inu i ka wai nui.
- E pale i ka wela nui a me ke anu nui.
- Mai hoʻolōʻihi i ka manawa ma nā wahi kiʻekiʻe, e like me nā wahi mauna.
- Kōkua kahi lāʻau i kapa ʻia ʻo Hydroxyurea i ka hōʻemi ʻana i ke alapine (frequency) o kēia mau hōʻeha ʻeha i nā keiki a me nā pākeke.
Anemia
ʻO kēia kekahi pilikia maʻamau o ka maʻi sickle cell. ʻO kēia kahi e make wikiwiki ai nā hunaola koko ʻulaʻula e like me ka sickle ma mua o nā hunaola maʻamau.. No laila, ʻaʻole hiki i ke kino ke hana i nā ʻāpana hou i ka manawa like me ko lākou make ʻana. ʻO ka hopena, emi ka nui o ka oxygen e hiki aku ana i nā ʻāpana o ke kino, a hiki iā ʻoe ke luhi loa, nāwaliwali, a me ka poniuniu . Hiki iā ʻoe ke ʻike i nā mea e like me ka puʻuwai wikiwiki a me ka paʻakikī o ka hanu ʻana. I loko o kahi keiki, hiki i ka anemia ke hoʻoulu i ka ulu ʻana.
Inā koʻikoʻi ka anemia, pono paha ke hoʻoili koko . Eia nō naʻe, hiki i nā hoʻoili koko pinepine ke hoʻonui i nā pae hao a hōʻino i ka puʻuwai, ke akepaʻa, a me ka pancreas. No laila, e nānā pinepine kāu kauka i kāu mau pae hao e kōkua i ka mālama ʻana iā lākou. No nā pākeke, hiki i ka lāʻau Hydroxyurea ke kōkua pū me ka anemia.
| Ka pilikia | Nā hōʻailona nui | He aha e hana ai |
|---|---|---|
| Ka Hoʻokaʻawale ʻana o ka Splenic | ʻEha ʻōpū ma ka ʻaoʻao hema, keʻokeʻo, hiamoe nui, puʻuwai wikiwiki. | He pilikia hoʻoweliweli kēia i ke ola. E hele koke i ka ʻOihana Pilikia (ETU) o ka haukapila. |
| ʻO ka maʻi umauma koʻikoʻi | Kuni, pilikia hanu, ʻeha umauma, ʻū. | He kūlana koʻikoʻi loa nō hoʻi kēia. E hele koke i ka Emergency Treatment Unit (ETU) o ka haukapila. |
Nā maʻi a me nā pilikia ʻē aʻe
Hoʻonui ʻia ka maʻalahi i nā maʻi
ʻOi aku ka nui o ka poʻe me ka maʻi sickle cell, ʻoiai nā keiki ʻōpio, e loaʻa i nā maʻi. ʻO kēia no ka mea hōʻino ka maʻi i ka spleen . ʻIke ʻoe, he ʻōkana koʻikoʻi ka spleen e kānana i nā germs e like me ka bacteria mai ko mākou koko. No laila, ke hana pono ʻole ia, hiki i nā maʻi ke komo maʻalahi i ke kino.
He mea nui e loaʻa ka lāʻau lapaʻau no kahi maʻi liʻiliʻi ma mua o ka lilo ʻana i mea koʻikoʻi. Inā loaʻa iā ʻoe a i ʻole kāu keiki ke kuni ma luna o 101°F (38.3°C), e ʻike i ke kauka a i ʻole e hele i ka keʻena pilikia o ka haukapila (ETU) i kēia manawa.
Ka Hoʻokaʻawale ʻana o ka Splenic
He pilikia hoʻoweliweli kēia i ke ola, ʻoiai hoʻi i nā keiki ʻōpio. Hana ʻia kēia i ka wā e ālai ai nā cell sickle i ke kahe koko i ka spleen. Lilo ka spleen i mea pehu a ʻeha. ʻAʻole paha i loaʻa i kekahi mau keiki kekahi mau hōʻailona nui. Eia nō naʻe, hiki i kekahi ke ʻike i nā hōʻailona e like me ka nāwaliwali, ka ʻili keʻokeʻo a me nā lehelehe, ka hiamoe nui, ka ʻeha ma ka ʻaoʻao hema o ka ʻōpū, a me ka puʻuwai wikiwiki . Inā ʻike ʻoe i kēia mau hōʻailona, e hele koke i ka haukapila .
ʻO ka maʻi umauma koʻikoʻi
He kūlana koʻikoʻi loa nō hoʻi kēia. ʻO kēia kahi e ālai ai ka maʻi cell sickle i nā kīʻaha koko i loko o nā māmā. Inā loaʻa iā ʻoe nā hōʻailona e like me ke kuni, ka paʻakikī o ka hanu ʻana, ka ʻeha o ka umauma, a me ke kuni , e hele koke i ka haukapila. Hiki i nā kauka ke hāʻawi iā ʻoe i ka oxygen, nā lāʻau antibiotic, a me ka hoʻoili koko paha.
Nā pilikia lōʻihi ʻē aʻe
Hiki i ka maʻi sickle cell ke hoʻoulu i nā pilikia hou aʻe i ka hala ʻana o ka manawa.
- Poho o ka iwi (Avascular Necrosis): Ke ʻoki ʻia ke kahe o ke koko i nā hono nui (e like me ka ʻūhā), hoʻomaka ka make ʻana o nā ʻiʻo iwi. He mea maʻamau kēia i nā poʻe ʻōpio a me nā poʻe ʻelemakule. Hiki i nā lāʻau ʻeha ke hāʻawi i ka hōʻoluʻolu, akā pono paha kekahi poʻe i ke ʻoki ʻana.
- ʻO ka hōʻino ʻana i nā kino ʻē aʻe: ʻO nā pilikia me nā maka, ka puʻuwai, nā puʻupaʻa, a me ke akepaʻa e piʻi aʻe ka pilikia no nā ʻōpū koko a me ka hahau ʻana. ʻO ia ke kumu e nānā mau ai kāu kauka i ka hana o kēia mau kino.
Ka Hoʻoili ʻana o ka Iwi Momona a me nā Lapaʻau Hou
No ka poʻe e ʻike pinepine ana i nā pilikia koʻikoʻi, hiki ke noʻonoʻo ʻia kahi lāʻau i kapa ʻia he hoʻoili iwi iwi . Pili kēia i ka hoʻololi ʻana i nā pūnaewele iwi iwi e hana ana i nā cell sickle me nā pūnaewele olakino. Hiki i kēia ke ho'ōla loa i ka maʻi.
Akā, ʻaʻole kēia he mea hiki i nā kānaka a pau ke hana. Pono ʻoe e ʻimi i kahi mea hāʻawi olakino e kūlike ana i kou ʻiʻo. Eia kekahi, inā he pilikia kou me nā ʻōpū e like me ka puʻuwai a i ʻole nā puʻupaʻa, hiki ke pilikia kēia ʻoki kino. Pono paha ʻoe e noho ma ka haukapila no ka manawa lōʻihi. I kekahi manawa, ʻaʻole paha e holomua kēia lāʻau lapaʻau. No laila, pono ka ʻohana e kamaʻilio pono me ke kauka a hoʻoholo inā kūpono kēia lāʻau lapaʻau iā lākou.
Eia kekahi, aia nā lāʻau lapaʻau hou, e like me Crizanlizumab, hiki ke kōkua i ka hōʻemi ʻana i nā hōʻeha ʻeha. E nīnau i kāu kauka e pili ana i kēia mau mea.
Leka Lawe-Home
- ʻO ka maʻi ʻeha cell sickle kahi maʻi genetic e hoʻololi i ke ʻano o nā hunaola koko ʻulaʻula. Hiki i kēia ke hana i nā pilikia koʻikoʻi e like me ka ʻeha, ka anemia, a me ka hōʻino ʻana o nā kino.
- Inā ʻike ʻoe i nā hōʻailona e like me ka ʻeha nui, ke kuni, ka paʻakikī o ka hanu ʻana, a i ʻole ka mae wale loa, e ʻimi koke i ke kōkua lapaʻau a i ʻole e hele i ka Emergency Treatment Unit (ETU) o ka haukapila.
- Hiki ke hoʻomalu ʻia nā pilikia he nui ma ka inu ʻana i ka wai he nui, ka mālama ʻana i kahi nohona olakino, a me ka lawe ʻana i nā lāʻau lapaʻau (e like me Hydroxyurea) e like me ke kauoha a kāu kauka.
- No nā keiki, he mea nui loa ka pale ʻana i nā maʻi ma o ka loaʻa ʻana o nā lāʻau pale āpau i ka manawa kūpono a me ka hāʻawi ʻana iā lākou i nā lāʻau antibiotic i kēlā me kēia lā.
- Inā he mau nīnau a hopohopo paha kāu e pili ana i kou kūlana a i ʻole ke kūlana o kāu keiki, e kūkākūkā mau me kāu kauka. Hiki iā ʻoe ke ola me ka holomua me ka maʻi me ka makaʻu ʻole, ma ka ʻike ʻia ʻana.











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