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He aha ka Spindle Cell Sarcoma? E kamaʻilio maʻalahi kākou e pili ana!

He aha ka Spindle Cell Sarcoma? E kamaʻilio maʻalahi kākou e pili ana!

Ua hopohopo paha ʻoe no kekahi mea ʻē, e like me ka ʻeha a i ʻole ka pehu ʻana i kou mau iwi a i ʻole nā ​​wahi palupalu e like me kou mau ʻiʻo? I kekahi manawa he mea maʻamau kēia mau mea. Akā, i ka manawa kakaikahi, hiki i kēia mau hōʻailona ke hōʻailona o kahi mea koʻikoʻi. No laila, i kēia lā e kamaʻilio mākou e pili ana i kahi ʻano maʻi kanesa i kakaikahi iki, akā he mea nui e ʻike. ʻO ia ka Spindle Cell Sarcoma.

He aha maoli ka Spindle Cell Sarcoma?

I ka ʻōlelo maʻalahi, ʻo Spindle Cell Sarcoma kahi ʻano maʻi kanesa kakaikahi e ulu ana i loko o nā iwi a me nā ʻiʻo palupalu o ko kākou kino. Ua ʻike anei ʻoe ʻo ka 'sarcoma' e pili ana i nā puʻupuʻu cell maʻamau ʻole, a i ʻole nā ​​​​tumors, e ulu ana i loko o kēlā mau iwi a me nā ʻiʻo e pili ana iā lākou?

ʻĀnō, ʻo ka mea kūikawā e pili ana i ka Spindle Cell Sarcoma, ʻo ia ke nānā ʻoe i kēlā mau cell ʻano ʻē ma lalo o kahi microscope, ua like lākou me kahi 'spindle'. He ʻano like ka spindle me ke kukui, me nā ʻaoʻao lahilahi a ʻoi aku ka mānoanoa o waena. ʻO ia ke kumu i loaʻa ai kona inoa.

Ma muli o nā hoʻokolohua lab holomua, ua hiki i nā kauka ke ʻike i nā ʻano sarcoma he 75 a ʻoi. ʻO ka sarcoma cell spindle kekahi o ia ʻano subtype. ʻO ka ʻoiaʻiʻo, hoʻohana ʻia ka huaʻōlelo 'spindle cell sarcoma' e wehewehe i nā sarcomas i hiki ʻole ke hoʻokaʻawale pololei ʻia e kekahi mau hoʻokolohua lab, e like me nā stains a i ʻole nā ​​​​ʻano genetic. No laila, he huaʻōlelo ākea iki ia.

Ma hea kahi e loaʻa pinepine ai kēia mau puʻupuʻu?

ʻO ka Spindle Cell Sarcoma e ulu pinepine ana i loko o nā iwi lōʻihi o ko mākou kino. Eia kekahi laʻana:

  • Kou iwi ʻūhā (`femur`)
  • Iwi ʻūhā (tibia)
  • Iwi lima luna (humerus)

Eia naʻe, ʻaʻole kēia mau wahi wale nō. Loaʻa i kekahi poʻe nā sarcomas spindle cell ma ka pelvis, ke poʻo a me ka ʻāʻī, a me nā ʻāpana ʻē aʻe o ke kino.

He aha nā ʻano nui o ka Spindle Cell Sarcoma?

I kēia manawa, e nānā, hoʻomaka nā sarcomas āpau i nā ʻiʻo palupalu. ʻO ia hoʻi, i nā mea e like me ka momona, nā ʻiʻo, nā kīʻaha koko, nā aʻalolo, a me nā ʻiʻo a puni nā iwi. Hoʻokaʻawale hou nā kauka i nā sarcomas cell spindle ma muli o ke ʻano o ke kelepona kahi e hoʻomaka ai ke kanesa.

Ma ka hoʻomaopopo ʻana i ke ʻano o ke kelepona a me kona mau ʻano ma kēia ʻano, hiki i nā kauka ke loiloi i ka nui o ka laha ʻana o ke kanesa. Kōkua pū kēia iā lākou e ʻike i nā lāʻau lapaʻau maikaʻi loa.

ʻOiai he huaʻōlelo ākea ka 'spindle cell sarcoma', aia kekahi mau ʻano nui:

  • ʻO ka Sarcoma Pleomorphic i hoʻokaʻawale ʻole ʻia:E like me ka inoa e hōʻike nei, ʻo nā pūnaewele i loko o kēia ʻano maʻi kanesa he 'undofferentiated'. ʻO ke ʻano kēia, ʻaʻole maopopo ke ʻano o ke kelepona i hoʻomaka ai ke kanesa. ʻO nā pūnaewele maʻi i loko o ka puʻupuʻu he 'pleomorphic', ʻo ia hoʻi, hele mai lākou i nā ʻano a me nā nui like ʻole. I nā huaʻōlelo ʻē aʻe, he hōʻiliʻili o nā pūnaewele mai nā ʻano like ʻole kahi puʻupuʻu.
  • Fibrosarcoma: Kū mai kēia mau mea mai nā pūnaewele i kapa ʻia ʻo fibroblasts. ʻO nā fibroblasts nā poloka kūkulu nui o nā ʻiʻo hoʻopili i loko o ko mākou kino.
  • Leiomyosarcoma: Hoʻomaka kēia mau mea i loko o nā pūnaewele ʻiʻo laumania. He ʻokoʻa kēia mau mea mai nā pūnaewele i loko o nā ʻiʻo iwi, kahi a mākou e hoʻohana ai e hoʻoneʻe i ko mākou kino a loaʻa ka ikehu. Loaʻa nā pūnaewele ʻiʻo laumania i loko o ko mākou mau ʻōpū o loko, nā lua o ke kino, a me kekahi mau iwi ma ke ʻano he ʻiʻo palupalu.

Pehea ka maʻamau o kēia ʻano?

E like me nā ʻano sarcoma ʻē aʻe, he mea kākaʻikahi loa ka spindle cell sarcoma. ʻO ka ʻoiaʻiʻo, ʻaʻole ia ma mua o 10% o nā maʻi kanesa o ka iwi a me nā ʻiʻo palupalu. E hoʻomanaʻo, he mea kākaʻikahi loa ia ʻaʻole paha e kānalua kāu kauka i kēia ʻano maʻi kanesa i ka wā mua. Pono paha ʻoe e hele i kekahi mau manawa kauka, e ʻike i kekahi mau loea, a loaʻa i kekahi mau hoʻokolohua ma mua o kou loaʻa ʻana o kahi hōʻailona.

Hiki ke ulu ka sarcoma cell spindle i loko o kekahi. Eia nō naʻe, ʻoi aku ka maʻamau i ka poʻe ma luna o 40 mau makahiki. ʻO ka poʻe i loaʻa i ka undifferentiated pleomorphic sarcoma i ʻōlelo ʻia ma mua, ma waena o 60 a me 70 mau makahiki.

He aha nā hōʻailona o kēia?

Hiki ke ʻokoʻa nā hōʻailona o ka spindle cell sarcoma. Aia lākou i ka nui o ka puʻupuʻu, ka helu o nā puʻupuʻu, a me nā iwi (a i ʻole nā ​​​​ʻāpana ʻē aʻe o ke kino) e noho ai nā hunaola kanesa. Eia kekahi mau hōʻailona āu e makaʻala pono ai :

  • ʻEha iwi: Hiki i kēia ʻeha ke mau a hele mai a hele aku. Hiki iā ia ke manaʻo e hou ana kekahi iā ʻoe mai loko mai.
  • Ka haki ʻana o ka iwi ma kahi i hoʻonāwaliwali ʻia e ka maʻi ʻaʻai: Ua kapa ʻia kēia he 'pathological fracture.' Hiki i ka iwi ke haki me ka hāʻule iki ʻana.
  • ʻO ke kaumaha a i ʻole ka pehu ʻana i ke kaomi ʻia ma kahi o ka puʻupuʻu: Aia paha he puʻupuʻu nui e hiki ke paʻa i ka lima.
  • ʻAʻole hiki ke hoʻoneʻe pono i kahi hono i kahi kokoke i ka puʻupuʻu: E noʻonoʻo inā kokoke ke kuli, e paʻakikī ke kūlou a hoʻolōʻihi paha i ke kuli.
  • Luhi: ʻAʻole kēia he luhi maʻamau wale nō. He luhi nui loa ia ʻaʻole e nalo me ka nānā ʻole i ka nui o ka hiamoe a i ʻole ka hoʻomaha āu e loaʻa ai.
  • Malaise: Manaʻo maikaʻi ʻole , me ke kumu ʻole, me he mea lā ʻaʻohe ikaika a hoihoi paha i kekahi mea.

He aha ke kumu o ka sarcoma cell spindle?

E like me nā maʻi kanesa ʻē aʻe a pau, hoʻomaka ka spindle cell sarcoma i ka wā e lilo ai nā pūnaewele olakino i mea ʻino. Ulu kēia mau pūnaewele ʻino ma waho o ke kaohi, e hana ana i nā puʻupuʻu. Hiki i kēia mau puʻupuʻu ke hōʻino i nā ʻiʻo olakino a puni. ʻO ka mea weliweli loa, hiki i kēia mau pūnaewele kanesa ke haki aku mai ka puʻupuʻu mua a laha ma ke kino holoʻokoʻa, e hōʻino ana i nā ʻiʻo a me nā ʻōpū ʻē aʻe. ʻO kēia ka mea a mākou e kapa nei he metastasis, a i ʻole ka maʻi kanesa metastatic.

Akā, eia kekahi mea e ʻike ai. ʻO ka maʻamau, he mea maikaʻi nā pūnaewele spindle (ke ulu pono lākou). Hoʻokumu ʻia nā pūnaewele spindle ma kahi i hōʻino ʻia ai nā ʻiʻo. No laila, ʻo ka loaʻa ʻana o nā pūnaewele spindle he hōʻailona ia e ho'ōla ana kou ʻeha. Nalo kēia mau pūnaewele i ka wā e ho'ōla ai ka ʻeha.

Eia nō naʻe, i loko o ka sarcoma cell spindle, ke hoʻomau nei kēia mau cell spindle i ka ulu a me ka hoʻonui ʻana. ʻAʻole i loaʻa i nā kānaka ʻepekema kahi kumu kikoʻī hoʻokahi e lilo ai kēia mau cell i mea ʻino.

Eia nō naʻe, ua ʻike nā kānaka noiʻi e hiki i kekahi mau hoʻololi ʻana o ka genetic ke hoʻonui i ka pilikia o ke kanaka i ka loaʻa ʻana o kēia maʻi kanesa. ʻO ka 'mutation' he hewa ia i loko o kā mākou mau genes, ka ʻōnaehana e haʻi i kā mākou mau cell pehea e hana ai. I ke ʻano o ka spindle cell sarcoma, he mau hoʻoilina pinepine kēia mau hoʻololi ʻana, ʻo ia hoʻi hiki iā lākou ke holo i loko o nā ʻohana.

He aha nā kumu pilikia e hoʻonui ai i ka pilikia o ka loaʻa ʻana o kēia maʻi kanesa?

Aia kekahi mau kumu e hiki ai ke hoʻonui i ka pilikia o ka loaʻa ʻana o ka spindle cell sarcoma. E nānā kākou i ko lākou ʻano:

  • ʻO ka Infarction o ka iwi: ʻO kēia ka wā e make ai ka ʻiʻo iwi no ka mea ʻaʻole lawa ke koko. E like me kou ʻike, pono ka ʻiʻo iwi i ke koko e ola ai, ʻo ia ka mea a ka oxygen e hana ai.
  • ʻO Fibrous Dysplasia: Ma kēia kūlana, ua pani ʻia nā ʻiʻo iwi olakino e nā ʻiʻo e like me ka iwi fibrous. Hoʻonui kēia i ka pilikia o nā haki a (kākaʻikahi loa) hiki ke alakaʻi i ka ulu ʻana o fibrosarcomas.
  • Osteomyelitis: He maʻi kēia e hoʻopilikia ai i ka ʻiʻo huʻa i loko o kekahi mau iwi, i kapa ʻia ʻo ka iwi iwi. Hiki ke hana kēia inā hele ka bacteria a i ʻole nā ​​​​germs ʻē aʻe mai kou koko a i ka iwi a hoʻopilikia i nā cell ma laila.
  • ʻO ka maʻi o Paget o ka iwi: He kūlana lōʻihi kēia (mau). Hoʻonāwaliwali ia i nā iwi a haki maʻalahi. Hiki i kēia ke hoʻonui i ka pilikia o ka loaʻa ʻana o ka maʻi ʻaʻai iwi, me ka spindle cell sarcoma.
  • Ma hope o ka loaʻa mua ʻana o ka radiation therapy no ka maʻi kanesa:Hoʻohana ka lāʻau lapaʻau radiation i nā kukuna ikehu kiʻekiʻe (pinepine nā kukuna X-ikehu kiʻekiʻe) e luku i nā hunaola kanesa. I ka manawa kākaʻikahi, ua ulu nā sarcomas cell spindle ma nā wahi i mālama ʻia me ka radiation. Ke hana ʻia kēia, ulu pinepine ka sarcoma i kekahi mau makahiki ma hope o ka lāʻau lapaʻau (ʻehiku a iwakālua mau makahiki). Akā e hoʻomanaʻo, ʻaʻole i hiki i ka 1% o ka poʻe i loaʻa ka lāʻau lapaʻau radiation ke loaʻa i kēia ʻano kanesa e pili ana i ka radiation.

He aha nā pilikia o ka spindle cell sarcoma?

ʻOi aku ka maʻalahi o kēia maʻi kanesa i kou mau iwi e haki (haʻihaʻi) ma kahi o ka puʻupuʻu. Ke haki ka iwi, hiki i nā hunaola kanesa mai ka puʻupuʻu ke hele i nā wahi kokoke.

Eia nō naʻe, aia nō ka hoʻopaʻapaʻa e pili ana inā he ʻokoʻa kēia ʻano haki iwi i ka prognosis holoʻokoʻa (ʻo ia hoʻi, ka hopena paha) o ke kanesa, a inā paha e pili wale ana ka hopena i ka laha mamao o ke kanesa (metastatic spread).

Pehea e ʻike ʻia ai ka spindle cell sarcoma?

Ma mua o ka hiki ʻana i kāu kauka ke ʻike a hoʻonohonoho i ke ʻano o kou maʻi ʻaʻai, pono paha ʻoe e loaʻa i kekahi mau hoʻokolohua a me nā kaʻina hana. ʻO ke ʻano o ke ʻano o ka maʻi ʻaʻai e hiki ai i nā kauka ke hoʻokaʻawale i ke koʻikoʻi o ke kanesa ma muli o ka nui o ka puʻupuʻu, kona wahi, a inā ua pālahalaha. I ke ʻano o ke ʻano o ka maʻi ʻaʻai iwi, nānā pū lākou inā he 'kiʻekiʻe' a 'haʻahaʻa' paha ka puʻupuʻu. ʻOi aku ka nui o nā cell ʻano ʻē o nā puʻupuʻu kiʻekiʻe. ʻOi aku ka nui o ko lākou ulu ʻana a pālahalaha koke.

ʻO ka hapa nui o nā sarcomas cell spindle he kiʻekiʻe ke ʻano.

Nā hoʻokolohua kiʻi

ʻOiai ʻaʻole hiki i nā hoʻokolohua kiʻi ke haʻi i ke ʻano o ke kanesa, hiki iā lākou ke hōʻike i ka nui a me kahi o ka puʻupuʻu. Hiki iā lākou ke hōʻike inā ua pālahalaha ke kanesa ma ʻō aku o ka puʻupuʻu mua.

  • Nā kukuna X: Hiki i nā kukuna X ke hōʻike i nā puʻupuʻu a i ʻole nā ​​​​​​mea ʻē aʻe i loko o kou mau iwi. Hiki i kahi kukuna X-ray umauma ke ʻike inā ua pālahalaha ke kanesa i nā māmā. Hoʻolaha pinepine ka metastatic spindle cell sarcoma i nā māmā ma mua.
  • MRI Scan: Hoʻohana ka MRI i kahi magnet nui, nā nalu lekiō, a me ke kamepiula e kiʻi i nā kiʻi o nā mea i loko o ke kino. ʻAʻole e like me nā kukuna X, hiki i ka MRI ke hōʻike i nā ʻiʻo palupalu me nā kikoʻī nui. He mea pono loa kēia no nā kauka e ʻike i nā puʻupuʻu ʻiʻo palupalu a lākou e manaʻo nei he sarcomas paha.
  • Nā Kiʻi CT: Hoʻohana nā kiʻi CT i nā kukuna X a me kahi kamepiula e hana i nā kiʻi ʻekolu-dimensional (3D) o nā iwi a me nā ʻiʻo palupalu. I ke ʻano o ka spindle cell sarcoma, hiki i nā kiʻi CT ke hōʻike inā ua pālahalaha ke kanesa i nā ʻiʻo palupalu. ʻOi aku ka maikaʻi o lākou no ka ʻike ʻana i nā haki a i ʻole nā ​​​​wahi i nāwaliwali ai nā iwi.
  • Nā Scan PET: Hoʻohana nā scan PET i kahi mea i kapa ʻia he tracer e ʻike i nā hunaola kanesa ma ke kino holoʻokoʻa. Hiki iā lākou ke kōkua i ka ʻike ʻana i ka sarcoma spindle cell metastasized. Hiki paha iā ʻoe ke loaʻa i kahi scan PET e ʻike ai pehea e hana ai kāu lāʻau. Eia naʻe, ʻaʻole hoʻohana ʻia nā scan PET no nā ʻano sarcoma āpau. Na kāu kauka e hoʻoholo inā kūpono kahi scan PET iā ʻoe.

Nā hoʻāʻo koko

ʻAʻohe hoʻāʻo koko kikoʻī e hiki ke ʻike i ka spindle cell sarcoma. Eia nō naʻe, hāʻawi nā hoʻāʻo koko i ka ʻike koʻikoʻi e pili ana i kou olakino, a he mea nui i kāu kauka ke ʻike i kēlā ʻike. Ma keʻano laulā, hiki i nā hoʻāʻo koko ke hāʻawi i ka ʻike e pili ana i nā mea e like me:

  • Kou mau hunaola koko
  • Hana o ke kino
  • Nā pae enzyme (nā enzymes he mau kemika e kōkua i nā ʻōpū e hoʻokō i nā kaʻina hana koʻikoʻi)

Biopsy

ʻO ke ala maikaʻi loa e ʻike pono ai inā he maʻi kanesa kahi puʻupuʻu, ʻo ia ka hana ʻana i kahi biopsy. ʻO ia wale nō ke ala e ʻike ai i ke ʻano o ke kanesa a me kona ʻano. I ka wā o ka biopsy, lawe ke kauka i kahi hāpana o ka ʻiʻo mai ka puʻupuʻu a hoʻouna aku i kahi keʻena hoʻokolohua e nānā i nā ʻāpana.

Loaʻa i ka hapa nui o ka poʻe me ka spindle cell sarcoma kahi biopsy nila. Hoʻomāʻū nā kauka i ka ʻiʻo a puni ka puʻupuʻu a laila hoʻohana i kahi nila liʻiliʻi a hakahaka e lawe i kahi laʻana. No ke kōkua ʻana i ke kauka e ʻike pono i kahi o kou kino e hoʻokomo ai i ka nila, pono paha ʻoe i kahi X-ray a i ʻole CT scan.

Pehea e mālama ʻia ai ka spindle cell sarcoma?

ʻO ka lāʻau lapaʻau āu e loaʻa ai e pili ana i kou olakino, kahi, ka nui, ke ʻano, a me nā mea ʻē aʻe. Pili nō hoʻi ia i ka loaʻa ʻana o ka lāʻau lapaʻau no ka manawa mua a i ʻole inā ua hoʻi hou mai ke kanesa ma hope o ka lāʻau lapaʻau (recurrent).

ʻoki kino

ʻO ka pahuhopu o ke ʻoki ʻana, ʻo ia ka wehe ʻana i ka puʻupuʻu me ka mālama ʻana i ka nui o kou iwi e like me ka hiki. Inā hiki ke wehe ʻia nā koena āpau o ke kanesa i loko o ka puʻupuʻu mua a me nā puʻupuʻu lua, hiki ke ho'ōla ʻia ke kanesa. Eia nō naʻe, i ka wā e pālahalaha ai ke kanesa ma ʻō aku o ka puʻupuʻu mua, ʻoi aku ka paʻakikī o ka wehe loa ʻana.

Kemoterapia

ʻO ka Chemotherapy kahi lāʻau lapaʻau e hoʻohana ana i nā lāʻau lapaʻau e pepehi i nā hunaola kanesa ma ke kino holoʻokoʻa. Hiki ke hāʻawi ʻia iā ʻoe i ka chemotherapy ma mua o ke ʻoki ʻana e hoʻēmi i ka puʻupuʻu a maʻalahi ka wehe ʻana. A i ʻole, hiki ke hāʻawi ʻia iā ʻoe i ka chemotherapy e pepehi i nā hunaola kanesa i koe ma hope o ke ʻoki ʻana. Hoʻohana ʻia ka Chemotherapy ma ke ʻano he 'mālama palliative'. ʻOiai ʻaʻole hiki ke ho'ōla i ka kanesa, hiki i ka chemotherapy ke pepehi i nā hunaola kanesa e hōʻemi i nā hōʻailona e like me ka ʻeha iwi.

Ua hāʻawi ʻia i nā kānaka he nui ka hui pū ʻana o nā lāʻau chemotherapy e hoʻomaikaʻi ai i ka lāʻau. Ma muli o ka loaʻa ʻana o ka lāʻau lapaʻau no ka manawa mua, ʻaʻole pane maikaʻi i kekahi o nā lāʻau chemo, a inā ua hoʻi mai ke kanesa ma hope o ke komo ʻana i ka "remission," hiki ke hāʻawi ʻia iā ʻoe nā lāʻau chemo like ʻole. ʻO ke "Remission" ʻo ia hoʻi ua maikaʻi a nalowale paha ke kanesa ma hope o ka lāʻau lapaʻau.

Hoʻōla Pāhawewe

Hoʻohana ka External Beam Radiation Therapy (EBRT) i kahi mīkini e kuhikuhi i nā kukuna X i ka puʻupuʻu e pepehi i nā hunaola kanesa. Inā ʻaʻole hiki iā ʻoe ke hana ʻoki kino, hiki ke hāʻawi ʻia ka radiation therapy e luku i ka puʻupuʻu. I kekahi manawa, ʻaʻole hiki i ke kauka lapaʻau ke hiki i ka puʻupuʻu ma ke ʻoki kino. Hiki ke hohonu loa i loko o ka ʻiʻo a kokoke loa paha i nā ʻōpū koʻikoʻi e wehe palekana ʻia. I kēlā mau hihia, hiki ke hāʻawi ʻia iā ʻoe ka radiation therapy.

E like me ka chemotherapy, hiki i ka radiation therapy ke hōʻemi i nā hōʻailona inā ʻaʻole hiki ke ho'ōla ʻia ke kanesa.

He aha nā pilikia a i ʻole nā ​​hopena ʻaoʻao o ka lāʻau lapaʻau?

He mea maʻamau ka loaʻa ʻana o nā hopena ʻaoʻao mai ka chemotherapy a me ka radiation therapy i ka wā o ka mālama ʻana i ka maʻi kanesa. Hiki ke hoʻomau kēia mau mea no kekahi manawa ma hope o ka pau ʻana o ka mālama ʻana. He mea nui e nīnau i kāu kauka e pili ana i nā hopena ʻaoʻao hiki ke loaʻa, ma muli o ka mālama ʻana āu e loaʻa nei.

Āhea wau e ʻike ai i kaʻu kauka?

E haʻi aku kāu kauka iā ʻoe i ka pinepine o kou pono e hele mai no ka mālama ʻana, a i ʻole e loaʻa nā hoʻokolohua e ʻike ai inā ke ola nei ke kanesa i ka "remission." He nui ka poʻe me ke kanesa e ola nei i ka remission e pono e hele pinepine i ke kauka i nā pae mua. Ke noho lōʻihi ʻoe me ka ʻole o ke kanesa, e emi ana ka nui o nā manawa hoʻopaʻa e nānā no ka hoʻi hou ʻana.

He aha ke ʻano o ka lāʻau lapaʻau e pono ai iaʻu?

Ma muli o ka nui o ka iwi i pono ai ke kauka lapaʻau e wehe, pono paha ʻoe i nā kaʻina hana hou aʻe. Kōkua kēia mau kaʻina hana i ka mālama ʻana i ka hana o ka iwi. No ka laʻana, pono paha ʻoe i kahi kāpili iwi. ʻO ka kāpili iwi e pili ana i ka hoʻololi ʻana i ka ʻiʻo i wehe ʻia me ka ʻiʻo mai kahi ʻāpana ʻē aʻe o kou kino a i ʻole mai kahi mea hāʻawi. Pono paha ʻoe i kahi lālā hana. Pono paha ʻoe i nā lāʻau lapaʻau hou aʻe e kōkua iā ʻoe e hoʻomaʻamaʻa i kēia mau loli.

He aha nā nīnau e pono iaʻu e nīnau aku i kaʻu kauka e pili ana i ka spindle cell sarcoma?

Eia kekahi mau nīnau koʻikoʻi e nīnau aku i kāu kauka:

  • Aia i hea ke kanesa?
  • He aha ke kahua/pae o ka maʻi kanesa?
  • Pehea ka hopena o kēlā pae/māka i kaʻu hoʻolālā lapaʻau?
  • He aha nā hopena ʻaoʻao lapaʻau e pono iaʻu ke manaʻo?
  • Hiki ke ho'ōla ʻia koʻu maʻi kanesa?
  • He aha nā pahuhopu o ka mālama ʻana?
  • Hiki iā ʻoe ke hoʻohui iaʻu i nā lawelawe mālama palliative e kōkua iaʻu e hoʻomanawanui i kaʻu maʻi kanesa?

Hiki ke ho'ōla ʻia ka spindle cell sarcoma? Pehea ke koʻikoʻi o ia mea?

Inā hiki ke wehe ʻia nā koena āpau o ke kanesa, hiki i nā kauka ke ho'ōla i ka spindle cell sarcoma. ʻOi aku ka maʻalahi o ka ho'ōla ʻana i ka spindle cell sarcoma i pālahalaha ʻole ma mua o kona wahi mua. Eia nō naʻe, he mea paʻakikī loa ka mālama ʻana i nā sarcoma i pālahalaha. ʻAʻole hiki ke ho'ōla pinepine ʻia nā Metastatic Spindle Cell Sarcomas.

ʻO kēia ʻano maʻi kanesa he 'kiʻekiʻe' pinepine. ʻO ke ʻano kēia e ulu koke ana a laha koke. Ma hope o ka hoʻomaha ʻana, ʻoi aku ka nui o ka hoʻi ʻana mai, i kekahi manawa ma kahi like me ka puʻupuʻu mua, i kekahi manawa ma kahi ʻē aʻe.

Akā e hoʻomanaʻo, ʻokoʻa kēlā me kēia hōʻailona maʻi kanesa. Hiki i kāu kauka ke haʻi iā ʻoe i ka hopena kūpono o ka lāʻau lapaʻau (prognosis) ma muli o ke ʻano kikoʻī o ka maʻi kanesa āu i loaʻa ai, kona pae, kou olakino holoʻokoʻa, kāu pane i ka lāʻau lapaʻau, a me nā ʻano kumu like ʻole. ʻO kāu kauka ke kanaka maikaʻi loa e aʻo iā ʻoe pehea e hoʻopilikia ai kēia hōʻailona iā ʻoe.

Nā mea e pono ai kākou e hoʻomanaʻo mai kēia moʻolelo (Leka Lawe-Home)

Hiki i ka ʻike ʻia ʻana me ka Spindle Cell Sarcoma ke lilo i mea hopohopo. Hiki i ke kūlana ke hoʻoluhi a hoʻoluhi ʻole iā ʻoe. He ikaika pinepine nā lāʻau lapaʻau, a hiki iā ʻoe ke kū i nā pilikia e like me ka hoʻomaʻamaʻa ʻana i kahi hoʻopili iwi a i ʻole kahi lālā hana.

No laila, he mea nui loa ka loaʻa ʻana o kahi kamaʻilio pololei a wehe ʻia me kāu kauka mai ka hoʻomaka ʻana. Ma kēia ala, hiki iā ʻoe ke hoʻomaopopo i kāu hōʻailona, ​​​​ka nui o ka hiki ke ho'ōla ʻia kou maʻi ʻaʻai, nā pahuhopu o kāu mālama ʻana, a me nā hoʻololi o ke ʻano o ka nohona āu e pono ai e hana i ka wā o ka mālama ʻana a me ka hoʻōla ʻana.

He maʻi kanesa koʻikoʻi ka Spindle cell sarcoma a ulu wikiwiki hoʻi. Eia nō naʻe, aia nā lāʻau lapaʻau e hiki ke kāohi i kona ulu ʻana a, i kekahi mau hihia, e hoʻōla loa iā ia. E kamaʻilio me kāu kauka e pili ana i kāu mea e manaʻo ai. Mai haʻalele i ka manaʻolana. He mea nui loa ka hahai ʻana i nā ʻōlelo aʻoaʻo lapaʻau kūpono a me ka noho maikaʻi ʻana i kēia hakakā.

👩🏽‍⚕️ Nā nīnau hou aku (FAQs)

💬 He maʻi ʻaʻai lolo anei ka Spindle Cell Sarcoma?

ʻAʻole! Hoʻomaka nā maʻi kanesa maʻamau (Carcinomas) mai ka ʻili (nā ʻiʻo) o nā ʻōpū o ke kino. Akā, ʻo 'Sarcoma' kahi ʻano maʻi kanesa e kū mai ana mai nā ʻiʻo, ka momona, nā aʻalolo, ke cartilage a me nā iwi (nā ʻiʻo hoʻohui) e kākoʻo ana i ko kākou kino. Loaʻa i kēia maʻi kanesa kona inoa no ka mea ua like kona mau ʻāpana me kahi 'spindle' ke nānā ʻia ma lalo o kahi microscope.

💬 He aha nā hōʻailona o kēia maʻi kanesa e ulu ana i loko o nā ʻiʻo o ko kākou mau lima a me nā wāwae?

Hoʻomaka pinepine kēia maʻi ʻaʻai ma nā ʻiʻo hohonu o nā wāwae a me nā lima (Extremities). I nā pae mua, ʻaʻohe ʻeha. Manaʻo ka mea maʻi iā ia me he puʻupuʻu nui ʻole (e ulu ana) ma lalo o ka ʻili o ka lima a i ʻole ka wāwae. Aia wale nō ke ulu ka puʻupuʻu a kaomi i kahi aʻalolo kokoke e hoʻomaka ai e hōʻeha nui.

💬 He aha ke ʻano lapaʻau nui no kēia maʻi kanesa?

ʻO ka lāʻau lapaʻau nui a maikaʻi loa no kēia, ʻo ia ka hana ʻoki ʻana i ka wā hikiwawe loa, e wehe loa ana i ka puʻupuʻu a me nā ʻiʻo olakino e hoʻopuni ana (excision ākea). Ma hope o kēlā, hāʻawi ʻia ka radiation a i ʻole chemo e luku i nā hunaola kanesa i koe.


ʻO ka Spindle Cell Sarcoma, Spindle Cell Sarcoma, Kanesa, Kanesa Iwi, Kanesa ʻIʻo Palupalu, Puʻupuʻu, Nā Hōʻailona, ​​Lapaʻau

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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He aha ka Spindle Cell Sarcoma? E kamaʻilio maʻalahi kākou e pili ana!

He aha ka Spindle Cell Sarcoma? E kamaʻilio maʻalahi kākou e pili ana!

Ua hopohopo paha ʻoe no kekahi mea ʻē, e like me ka ʻeha a i ʻole ka pehu ʻana i kou mau iwi a i ʻole nā ​​wahi palupalu e like me kou mau ʻiʻo? I kekahi manawa he mea maʻamau kēia mau mea. Akā, i ka manawa kakaikahi, hiki i kēia mau hōʻailona ke hōʻailona o kahi mea koʻikoʻi. No laila, i kēia lā e kamaʻilio mākou e pili ana i kahi ʻano maʻi kanesa i kakaikahi iki, akā he mea nui e ʻike. ʻO ia ka Spindle Cell Sarcoma.

He aha maoli ka Spindle Cell Sarcoma?

I ka ʻōlelo maʻalahi, ʻo Spindle Cell Sarcoma kahi ʻano maʻi kanesa kakaikahi e ulu ana i loko o nā iwi a me nā ʻiʻo palupalu o ko kākou kino. Ua ʻike anei ʻoe ʻo ka 'sarcoma' e pili ana i nā puʻupuʻu cell maʻamau ʻole, a i ʻole nā ​​​​tumors, e ulu ana i loko o kēlā mau iwi a me nā ʻiʻo e pili ana iā lākou?

ʻĀnō, ʻo ka mea kūikawā e pili ana i ka Spindle Cell Sarcoma, ʻo ia ke nānā ʻoe i kēlā mau cell ʻano ʻē ma lalo o kahi microscope, ua like lākou me kahi 'spindle'. He ʻano like ka spindle me ke kukui, me nā ʻaoʻao lahilahi a ʻoi aku ka mānoanoa o waena. ʻO ia ke kumu i loaʻa ai kona inoa.

Ma muli o nā hoʻokolohua lab holomua, ua hiki i nā kauka ke ʻike i nā ʻano sarcoma he 75 a ʻoi. ʻO ka sarcoma cell spindle kekahi o ia ʻano subtype. ʻO ka ʻoiaʻiʻo, hoʻohana ʻia ka huaʻōlelo 'spindle cell sarcoma' e wehewehe i nā sarcomas i hiki ʻole ke hoʻokaʻawale pololei ʻia e kekahi mau hoʻokolohua lab, e like me nā stains a i ʻole nā ​​​​ʻano genetic. No laila, he huaʻōlelo ākea iki ia.

Ma hea kahi e loaʻa pinepine ai kēia mau puʻupuʻu?

ʻO ka Spindle Cell Sarcoma e ulu pinepine ana i loko o nā iwi lōʻihi o ko mākou kino. Eia kekahi laʻana:

  • Kou iwi ʻūhā (`femur`)
  • Iwi ʻūhā (tibia)
  • Iwi lima luna (humerus)

Eia naʻe, ʻaʻole kēia mau wahi wale nō. Loaʻa i kekahi poʻe nā sarcomas spindle cell ma ka pelvis, ke poʻo a me ka ʻāʻī, a me nā ʻāpana ʻē aʻe o ke kino.

He aha nā ʻano nui o ka Spindle Cell Sarcoma?

I kēia manawa, e nānā, hoʻomaka nā sarcomas āpau i nā ʻiʻo palupalu. ʻO ia hoʻi, i nā mea e like me ka momona, nā ʻiʻo, nā kīʻaha koko, nā aʻalolo, a me nā ʻiʻo a puni nā iwi. Hoʻokaʻawale hou nā kauka i nā sarcomas cell spindle ma muli o ke ʻano o ke kelepona kahi e hoʻomaka ai ke kanesa.

Ma ka hoʻomaopopo ʻana i ke ʻano o ke kelepona a me kona mau ʻano ma kēia ʻano, hiki i nā kauka ke loiloi i ka nui o ka laha ʻana o ke kanesa. Kōkua pū kēia iā lākou e ʻike i nā lāʻau lapaʻau maikaʻi loa.

ʻOiai he huaʻōlelo ākea ka 'spindle cell sarcoma', aia kekahi mau ʻano nui:

  • ʻO ka Sarcoma Pleomorphic i hoʻokaʻawale ʻole ʻia:E like me ka inoa e hōʻike nei, ʻo nā pūnaewele i loko o kēia ʻano maʻi kanesa he 'undofferentiated'. ʻO ke ʻano kēia, ʻaʻole maopopo ke ʻano o ke kelepona i hoʻomaka ai ke kanesa. ʻO nā pūnaewele maʻi i loko o ka puʻupuʻu he 'pleomorphic', ʻo ia hoʻi, hele mai lākou i nā ʻano a me nā nui like ʻole. I nā huaʻōlelo ʻē aʻe, he hōʻiliʻili o nā pūnaewele mai nā ʻano like ʻole kahi puʻupuʻu.
  • Fibrosarcoma: Kū mai kēia mau mea mai nā pūnaewele i kapa ʻia ʻo fibroblasts. ʻO nā fibroblasts nā poloka kūkulu nui o nā ʻiʻo hoʻopili i loko o ko mākou kino.
  • Leiomyosarcoma: Hoʻomaka kēia mau mea i loko o nā pūnaewele ʻiʻo laumania. He ʻokoʻa kēia mau mea mai nā pūnaewele i loko o nā ʻiʻo iwi, kahi a mākou e hoʻohana ai e hoʻoneʻe i ko mākou kino a loaʻa ka ikehu. Loaʻa nā pūnaewele ʻiʻo laumania i loko o ko mākou mau ʻōpū o loko, nā lua o ke kino, a me kekahi mau iwi ma ke ʻano he ʻiʻo palupalu.

Pehea ka maʻamau o kēia ʻano?

E like me nā ʻano sarcoma ʻē aʻe, he mea kākaʻikahi loa ka spindle cell sarcoma. ʻO ka ʻoiaʻiʻo, ʻaʻole ia ma mua o 10% o nā maʻi kanesa o ka iwi a me nā ʻiʻo palupalu. E hoʻomanaʻo, he mea kākaʻikahi loa ia ʻaʻole paha e kānalua kāu kauka i kēia ʻano maʻi kanesa i ka wā mua. Pono paha ʻoe e hele i kekahi mau manawa kauka, e ʻike i kekahi mau loea, a loaʻa i kekahi mau hoʻokolohua ma mua o kou loaʻa ʻana o kahi hōʻailona.

Hiki ke ulu ka sarcoma cell spindle i loko o kekahi. Eia nō naʻe, ʻoi aku ka maʻamau i ka poʻe ma luna o 40 mau makahiki. ʻO ka poʻe i loaʻa i ka undifferentiated pleomorphic sarcoma i ʻōlelo ʻia ma mua, ma waena o 60 a me 70 mau makahiki.

He aha nā hōʻailona o kēia?

Hiki ke ʻokoʻa nā hōʻailona o ka spindle cell sarcoma. Aia lākou i ka nui o ka puʻupuʻu, ka helu o nā puʻupuʻu, a me nā iwi (a i ʻole nā ​​​​ʻāpana ʻē aʻe o ke kino) e noho ai nā hunaola kanesa. Eia kekahi mau hōʻailona āu e makaʻala pono ai :

  • ʻEha iwi: Hiki i kēia ʻeha ke mau a hele mai a hele aku. Hiki iā ia ke manaʻo e hou ana kekahi iā ʻoe mai loko mai.
  • Ka haki ʻana o ka iwi ma kahi i hoʻonāwaliwali ʻia e ka maʻi ʻaʻai: Ua kapa ʻia kēia he 'pathological fracture.' Hiki i ka iwi ke haki me ka hāʻule iki ʻana.
  • ʻO ke kaumaha a i ʻole ka pehu ʻana i ke kaomi ʻia ma kahi o ka puʻupuʻu: Aia paha he puʻupuʻu nui e hiki ke paʻa i ka lima.
  • ʻAʻole hiki ke hoʻoneʻe pono i kahi hono i kahi kokoke i ka puʻupuʻu: E noʻonoʻo inā kokoke ke kuli, e paʻakikī ke kūlou a hoʻolōʻihi paha i ke kuli.
  • Luhi: ʻAʻole kēia he luhi maʻamau wale nō. He luhi nui loa ia ʻaʻole e nalo me ka nānā ʻole i ka nui o ka hiamoe a i ʻole ka hoʻomaha āu e loaʻa ai.
  • Malaise: Manaʻo maikaʻi ʻole , me ke kumu ʻole, me he mea lā ʻaʻohe ikaika a hoihoi paha i kekahi mea.

He aha ke kumu o ka sarcoma cell spindle?

E like me nā maʻi kanesa ʻē aʻe a pau, hoʻomaka ka spindle cell sarcoma i ka wā e lilo ai nā pūnaewele olakino i mea ʻino. Ulu kēia mau pūnaewele ʻino ma waho o ke kaohi, e hana ana i nā puʻupuʻu. Hiki i kēia mau puʻupuʻu ke hōʻino i nā ʻiʻo olakino a puni. ʻO ka mea weliweli loa, hiki i kēia mau pūnaewele kanesa ke haki aku mai ka puʻupuʻu mua a laha ma ke kino holoʻokoʻa, e hōʻino ana i nā ʻiʻo a me nā ʻōpū ʻē aʻe. ʻO kēia ka mea a mākou e kapa nei he metastasis, a i ʻole ka maʻi kanesa metastatic.

Akā, eia kekahi mea e ʻike ai. ʻO ka maʻamau, he mea maikaʻi nā pūnaewele spindle (ke ulu pono lākou). Hoʻokumu ʻia nā pūnaewele spindle ma kahi i hōʻino ʻia ai nā ʻiʻo. No laila, ʻo ka loaʻa ʻana o nā pūnaewele spindle he hōʻailona ia e ho'ōla ana kou ʻeha. Nalo kēia mau pūnaewele i ka wā e ho'ōla ai ka ʻeha.

Eia nō naʻe, i loko o ka sarcoma cell spindle, ke hoʻomau nei kēia mau cell spindle i ka ulu a me ka hoʻonui ʻana. ʻAʻole i loaʻa i nā kānaka ʻepekema kahi kumu kikoʻī hoʻokahi e lilo ai kēia mau cell i mea ʻino.

Eia nō naʻe, ua ʻike nā kānaka noiʻi e hiki i kekahi mau hoʻololi ʻana o ka genetic ke hoʻonui i ka pilikia o ke kanaka i ka loaʻa ʻana o kēia maʻi kanesa. ʻO ka 'mutation' he hewa ia i loko o kā mākou mau genes, ka ʻōnaehana e haʻi i kā mākou mau cell pehea e hana ai. I ke ʻano o ka spindle cell sarcoma, he mau hoʻoilina pinepine kēia mau hoʻololi ʻana, ʻo ia hoʻi hiki iā lākou ke holo i loko o nā ʻohana.

He aha nā kumu pilikia e hoʻonui ai i ka pilikia o ka loaʻa ʻana o kēia maʻi kanesa?

Aia kekahi mau kumu e hiki ai ke hoʻonui i ka pilikia o ka loaʻa ʻana o ka spindle cell sarcoma. E nānā kākou i ko lākou ʻano:

  • ʻO ka Infarction o ka iwi: ʻO kēia ka wā e make ai ka ʻiʻo iwi no ka mea ʻaʻole lawa ke koko. E like me kou ʻike, pono ka ʻiʻo iwi i ke koko e ola ai, ʻo ia ka mea a ka oxygen e hana ai.
  • ʻO Fibrous Dysplasia: Ma kēia kūlana, ua pani ʻia nā ʻiʻo iwi olakino e nā ʻiʻo e like me ka iwi fibrous. Hoʻonui kēia i ka pilikia o nā haki a (kākaʻikahi loa) hiki ke alakaʻi i ka ulu ʻana o fibrosarcomas.
  • Osteomyelitis: He maʻi kēia e hoʻopilikia ai i ka ʻiʻo huʻa i loko o kekahi mau iwi, i kapa ʻia ʻo ka iwi iwi. Hiki ke hana kēia inā hele ka bacteria a i ʻole nā ​​​​germs ʻē aʻe mai kou koko a i ka iwi a hoʻopilikia i nā cell ma laila.
  • ʻO ka maʻi o Paget o ka iwi: He kūlana lōʻihi kēia (mau). Hoʻonāwaliwali ia i nā iwi a haki maʻalahi. Hiki i kēia ke hoʻonui i ka pilikia o ka loaʻa ʻana o ka maʻi ʻaʻai iwi, me ka spindle cell sarcoma.
  • Ma hope o ka loaʻa mua ʻana o ka radiation therapy no ka maʻi kanesa:Hoʻohana ka lāʻau lapaʻau radiation i nā kukuna ikehu kiʻekiʻe (pinepine nā kukuna X-ikehu kiʻekiʻe) e luku i nā hunaola kanesa. I ka manawa kākaʻikahi, ua ulu nā sarcomas cell spindle ma nā wahi i mālama ʻia me ka radiation. Ke hana ʻia kēia, ulu pinepine ka sarcoma i kekahi mau makahiki ma hope o ka lāʻau lapaʻau (ʻehiku a iwakālua mau makahiki). Akā e hoʻomanaʻo, ʻaʻole i hiki i ka 1% o ka poʻe i loaʻa ka lāʻau lapaʻau radiation ke loaʻa i kēia ʻano kanesa e pili ana i ka radiation.

He aha nā pilikia o ka spindle cell sarcoma?

ʻOi aku ka maʻalahi o kēia maʻi kanesa i kou mau iwi e haki (haʻihaʻi) ma kahi o ka puʻupuʻu. Ke haki ka iwi, hiki i nā hunaola kanesa mai ka puʻupuʻu ke hele i nā wahi kokoke.

Eia nō naʻe, aia nō ka hoʻopaʻapaʻa e pili ana inā he ʻokoʻa kēia ʻano haki iwi i ka prognosis holoʻokoʻa (ʻo ia hoʻi, ka hopena paha) o ke kanesa, a inā paha e pili wale ana ka hopena i ka laha mamao o ke kanesa (metastatic spread).

Pehea e ʻike ʻia ai ka spindle cell sarcoma?

Ma mua o ka hiki ʻana i kāu kauka ke ʻike a hoʻonohonoho i ke ʻano o kou maʻi ʻaʻai, pono paha ʻoe e loaʻa i kekahi mau hoʻokolohua a me nā kaʻina hana. ʻO ke ʻano o ke ʻano o ka maʻi ʻaʻai e hiki ai i nā kauka ke hoʻokaʻawale i ke koʻikoʻi o ke kanesa ma muli o ka nui o ka puʻupuʻu, kona wahi, a inā ua pālahalaha. I ke ʻano o ke ʻano o ka maʻi ʻaʻai iwi, nānā pū lākou inā he 'kiʻekiʻe' a 'haʻahaʻa' paha ka puʻupuʻu. ʻOi aku ka nui o nā cell ʻano ʻē o nā puʻupuʻu kiʻekiʻe. ʻOi aku ka nui o ko lākou ulu ʻana a pālahalaha koke.

ʻO ka hapa nui o nā sarcomas cell spindle he kiʻekiʻe ke ʻano.

Nā hoʻokolohua kiʻi

ʻOiai ʻaʻole hiki i nā hoʻokolohua kiʻi ke haʻi i ke ʻano o ke kanesa, hiki iā lākou ke hōʻike i ka nui a me kahi o ka puʻupuʻu. Hiki iā lākou ke hōʻike inā ua pālahalaha ke kanesa ma ʻō aku o ka puʻupuʻu mua.

  • Nā kukuna X: Hiki i nā kukuna X ke hōʻike i nā puʻupuʻu a i ʻole nā ​​​​​​mea ʻē aʻe i loko o kou mau iwi. Hiki i kahi kukuna X-ray umauma ke ʻike inā ua pālahalaha ke kanesa i nā māmā. Hoʻolaha pinepine ka metastatic spindle cell sarcoma i nā māmā ma mua.
  • MRI Scan: Hoʻohana ka MRI i kahi magnet nui, nā nalu lekiō, a me ke kamepiula e kiʻi i nā kiʻi o nā mea i loko o ke kino. ʻAʻole e like me nā kukuna X, hiki i ka MRI ke hōʻike i nā ʻiʻo palupalu me nā kikoʻī nui. He mea pono loa kēia no nā kauka e ʻike i nā puʻupuʻu ʻiʻo palupalu a lākou e manaʻo nei he sarcomas paha.
  • Nā Kiʻi CT: Hoʻohana nā kiʻi CT i nā kukuna X a me kahi kamepiula e hana i nā kiʻi ʻekolu-dimensional (3D) o nā iwi a me nā ʻiʻo palupalu. I ke ʻano o ka spindle cell sarcoma, hiki i nā kiʻi CT ke hōʻike inā ua pālahalaha ke kanesa i nā ʻiʻo palupalu. ʻOi aku ka maikaʻi o lākou no ka ʻike ʻana i nā haki a i ʻole nā ​​​​wahi i nāwaliwali ai nā iwi.
  • Nā Scan PET: Hoʻohana nā scan PET i kahi mea i kapa ʻia he tracer e ʻike i nā hunaola kanesa ma ke kino holoʻokoʻa. Hiki iā lākou ke kōkua i ka ʻike ʻana i ka sarcoma spindle cell metastasized. Hiki paha iā ʻoe ke loaʻa i kahi scan PET e ʻike ai pehea e hana ai kāu lāʻau. Eia naʻe, ʻaʻole hoʻohana ʻia nā scan PET no nā ʻano sarcoma āpau. Na kāu kauka e hoʻoholo inā kūpono kahi scan PET iā ʻoe.

Nā hoʻāʻo koko

ʻAʻohe hoʻāʻo koko kikoʻī e hiki ke ʻike i ka spindle cell sarcoma. Eia nō naʻe, hāʻawi nā hoʻāʻo koko i ka ʻike koʻikoʻi e pili ana i kou olakino, a he mea nui i kāu kauka ke ʻike i kēlā ʻike. Ma keʻano laulā, hiki i nā hoʻāʻo koko ke hāʻawi i ka ʻike e pili ana i nā mea e like me:

  • Kou mau hunaola koko
  • Hana o ke kino
  • Nā pae enzyme (nā enzymes he mau kemika e kōkua i nā ʻōpū e hoʻokō i nā kaʻina hana koʻikoʻi)

Biopsy

ʻO ke ala maikaʻi loa e ʻike pono ai inā he maʻi kanesa kahi puʻupuʻu, ʻo ia ka hana ʻana i kahi biopsy. ʻO ia wale nō ke ala e ʻike ai i ke ʻano o ke kanesa a me kona ʻano. I ka wā o ka biopsy, lawe ke kauka i kahi hāpana o ka ʻiʻo mai ka puʻupuʻu a hoʻouna aku i kahi keʻena hoʻokolohua e nānā i nā ʻāpana.

Loaʻa i ka hapa nui o ka poʻe me ka spindle cell sarcoma kahi biopsy nila. Hoʻomāʻū nā kauka i ka ʻiʻo a puni ka puʻupuʻu a laila hoʻohana i kahi nila liʻiliʻi a hakahaka e lawe i kahi laʻana. No ke kōkua ʻana i ke kauka e ʻike pono i kahi o kou kino e hoʻokomo ai i ka nila, pono paha ʻoe i kahi X-ray a i ʻole CT scan.

Pehea e mālama ʻia ai ka spindle cell sarcoma?

ʻO ka lāʻau lapaʻau āu e loaʻa ai e pili ana i kou olakino, kahi, ka nui, ke ʻano, a me nā mea ʻē aʻe. Pili nō hoʻi ia i ka loaʻa ʻana o ka lāʻau lapaʻau no ka manawa mua a i ʻole inā ua hoʻi hou mai ke kanesa ma hope o ka lāʻau lapaʻau (recurrent).

ʻoki kino

ʻO ka pahuhopu o ke ʻoki ʻana, ʻo ia ka wehe ʻana i ka puʻupuʻu me ka mālama ʻana i ka nui o kou iwi e like me ka hiki. Inā hiki ke wehe ʻia nā koena āpau o ke kanesa i loko o ka puʻupuʻu mua a me nā puʻupuʻu lua, hiki ke ho'ōla ʻia ke kanesa. Eia nō naʻe, i ka wā e pālahalaha ai ke kanesa ma ʻō aku o ka puʻupuʻu mua, ʻoi aku ka paʻakikī o ka wehe loa ʻana.

Kemoterapia

ʻO ka Chemotherapy kahi lāʻau lapaʻau e hoʻohana ana i nā lāʻau lapaʻau e pepehi i nā hunaola kanesa ma ke kino holoʻokoʻa. Hiki ke hāʻawi ʻia iā ʻoe i ka chemotherapy ma mua o ke ʻoki ʻana e hoʻēmi i ka puʻupuʻu a maʻalahi ka wehe ʻana. A i ʻole, hiki ke hāʻawi ʻia iā ʻoe i ka chemotherapy e pepehi i nā hunaola kanesa i koe ma hope o ke ʻoki ʻana. Hoʻohana ʻia ka Chemotherapy ma ke ʻano he 'mālama palliative'. ʻOiai ʻaʻole hiki ke ho'ōla i ka kanesa, hiki i ka chemotherapy ke pepehi i nā hunaola kanesa e hōʻemi i nā hōʻailona e like me ka ʻeha iwi.

Ua hāʻawi ʻia i nā kānaka he nui ka hui pū ʻana o nā lāʻau chemotherapy e hoʻomaikaʻi ai i ka lāʻau. Ma muli o ka loaʻa ʻana o ka lāʻau lapaʻau no ka manawa mua, ʻaʻole pane maikaʻi i kekahi o nā lāʻau chemo, a inā ua hoʻi mai ke kanesa ma hope o ke komo ʻana i ka "remission," hiki ke hāʻawi ʻia iā ʻoe nā lāʻau chemo like ʻole. ʻO ke "Remission" ʻo ia hoʻi ua maikaʻi a nalowale paha ke kanesa ma hope o ka lāʻau lapaʻau.

Hoʻōla Pāhawewe

Hoʻohana ka External Beam Radiation Therapy (EBRT) i kahi mīkini e kuhikuhi i nā kukuna X i ka puʻupuʻu e pepehi i nā hunaola kanesa. Inā ʻaʻole hiki iā ʻoe ke hana ʻoki kino, hiki ke hāʻawi ʻia ka radiation therapy e luku i ka puʻupuʻu. I kekahi manawa, ʻaʻole hiki i ke kauka lapaʻau ke hiki i ka puʻupuʻu ma ke ʻoki kino. Hiki ke hohonu loa i loko o ka ʻiʻo a kokoke loa paha i nā ʻōpū koʻikoʻi e wehe palekana ʻia. I kēlā mau hihia, hiki ke hāʻawi ʻia iā ʻoe ka radiation therapy.

E like me ka chemotherapy, hiki i ka radiation therapy ke hōʻemi i nā hōʻailona inā ʻaʻole hiki ke ho'ōla ʻia ke kanesa.

He aha nā pilikia a i ʻole nā ​​hopena ʻaoʻao o ka lāʻau lapaʻau?

He mea maʻamau ka loaʻa ʻana o nā hopena ʻaoʻao mai ka chemotherapy a me ka radiation therapy i ka wā o ka mālama ʻana i ka maʻi kanesa. Hiki ke hoʻomau kēia mau mea no kekahi manawa ma hope o ka pau ʻana o ka mālama ʻana. He mea nui e nīnau i kāu kauka e pili ana i nā hopena ʻaoʻao hiki ke loaʻa, ma muli o ka mālama ʻana āu e loaʻa nei.

Āhea wau e ʻike ai i kaʻu kauka?

E haʻi aku kāu kauka iā ʻoe i ka pinepine o kou pono e hele mai no ka mālama ʻana, a i ʻole e loaʻa nā hoʻokolohua e ʻike ai inā ke ola nei ke kanesa i ka "remission." He nui ka poʻe me ke kanesa e ola nei i ka remission e pono e hele pinepine i ke kauka i nā pae mua. Ke noho lōʻihi ʻoe me ka ʻole o ke kanesa, e emi ana ka nui o nā manawa hoʻopaʻa e nānā no ka hoʻi hou ʻana.

He aha ke ʻano o ka lāʻau lapaʻau e pono ai iaʻu?

Ma muli o ka nui o ka iwi i pono ai ke kauka lapaʻau e wehe, pono paha ʻoe i nā kaʻina hana hou aʻe. Kōkua kēia mau kaʻina hana i ka mālama ʻana i ka hana o ka iwi. No ka laʻana, pono paha ʻoe i kahi kāpili iwi. ʻO ka kāpili iwi e pili ana i ka hoʻololi ʻana i ka ʻiʻo i wehe ʻia me ka ʻiʻo mai kahi ʻāpana ʻē aʻe o kou kino a i ʻole mai kahi mea hāʻawi. Pono paha ʻoe i kahi lālā hana. Pono paha ʻoe i nā lāʻau lapaʻau hou aʻe e kōkua iā ʻoe e hoʻomaʻamaʻa i kēia mau loli.

He aha nā nīnau e pono iaʻu e nīnau aku i kaʻu kauka e pili ana i ka spindle cell sarcoma?

Eia kekahi mau nīnau koʻikoʻi e nīnau aku i kāu kauka:

  • Aia i hea ke kanesa?
  • He aha ke kahua/pae o ka maʻi kanesa?
  • Pehea ka hopena o kēlā pae/māka i kaʻu hoʻolālā lapaʻau?
  • He aha nā hopena ʻaoʻao lapaʻau e pono iaʻu ke manaʻo?
  • Hiki ke ho'ōla ʻia koʻu maʻi kanesa?
  • He aha nā pahuhopu o ka mālama ʻana?
  • Hiki iā ʻoe ke hoʻohui iaʻu i nā lawelawe mālama palliative e kōkua iaʻu e hoʻomanawanui i kaʻu maʻi kanesa?

Hiki ke ho'ōla ʻia ka spindle cell sarcoma? Pehea ke koʻikoʻi o ia mea?

Inā hiki ke wehe ʻia nā koena āpau o ke kanesa, hiki i nā kauka ke ho'ōla i ka spindle cell sarcoma. ʻOi aku ka maʻalahi o ka ho'ōla ʻana i ka spindle cell sarcoma i pālahalaha ʻole ma mua o kona wahi mua. Eia nō naʻe, he mea paʻakikī loa ka mālama ʻana i nā sarcoma i pālahalaha. ʻAʻole hiki ke ho'ōla pinepine ʻia nā Metastatic Spindle Cell Sarcomas.

ʻO kēia ʻano maʻi kanesa he 'kiʻekiʻe' pinepine. ʻO ke ʻano kēia e ulu koke ana a laha koke. Ma hope o ka hoʻomaha ʻana, ʻoi aku ka nui o ka hoʻi ʻana mai, i kekahi manawa ma kahi like me ka puʻupuʻu mua, i kekahi manawa ma kahi ʻē aʻe.

Akā e hoʻomanaʻo, ʻokoʻa kēlā me kēia hōʻailona maʻi kanesa. Hiki i kāu kauka ke haʻi iā ʻoe i ka hopena kūpono o ka lāʻau lapaʻau (prognosis) ma muli o ke ʻano kikoʻī o ka maʻi kanesa āu i loaʻa ai, kona pae, kou olakino holoʻokoʻa, kāu pane i ka lāʻau lapaʻau, a me nā ʻano kumu like ʻole. ʻO kāu kauka ke kanaka maikaʻi loa e aʻo iā ʻoe pehea e hoʻopilikia ai kēia hōʻailona iā ʻoe.

Nā mea e pono ai kākou e hoʻomanaʻo mai kēia moʻolelo (Leka Lawe-Home)

Hiki i ka ʻike ʻia ʻana me ka Spindle Cell Sarcoma ke lilo i mea hopohopo. Hiki i ke kūlana ke hoʻoluhi a hoʻoluhi ʻole iā ʻoe. He ikaika pinepine nā lāʻau lapaʻau, a hiki iā ʻoe ke kū i nā pilikia e like me ka hoʻomaʻamaʻa ʻana i kahi hoʻopili iwi a i ʻole kahi lālā hana.

No laila, he mea nui loa ka loaʻa ʻana o kahi kamaʻilio pololei a wehe ʻia me kāu kauka mai ka hoʻomaka ʻana. Ma kēia ala, hiki iā ʻoe ke hoʻomaopopo i kāu hōʻailona, ​​​​ka nui o ka hiki ke ho'ōla ʻia kou maʻi ʻaʻai, nā pahuhopu o kāu mālama ʻana, a me nā hoʻololi o ke ʻano o ka nohona āu e pono ai e hana i ka wā o ka mālama ʻana a me ka hoʻōla ʻana.

He maʻi kanesa koʻikoʻi ka Spindle cell sarcoma a ulu wikiwiki hoʻi. Eia nō naʻe, aia nā lāʻau lapaʻau e hiki ke kāohi i kona ulu ʻana a, i kekahi mau hihia, e hoʻōla loa iā ia. E kamaʻilio me kāu kauka e pili ana i kāu mea e manaʻo ai. Mai haʻalele i ka manaʻolana. He mea nui loa ka hahai ʻana i nā ʻōlelo aʻoaʻo lapaʻau kūpono a me ka noho maikaʻi ʻana i kēia hakakā.

👩🏽‍⚕️ Nā nīnau hou aku (FAQs)

💬 He maʻi ʻaʻai lolo anei ka Spindle Cell Sarcoma?

ʻAʻole! Hoʻomaka nā maʻi kanesa maʻamau (Carcinomas) mai ka ʻili (nā ʻiʻo) o nā ʻōpū o ke kino. Akā, ʻo 'Sarcoma' kahi ʻano maʻi kanesa e kū mai ana mai nā ʻiʻo, ka momona, nā aʻalolo, ke cartilage a me nā iwi (nā ʻiʻo hoʻohui) e kākoʻo ana i ko kākou kino. Loaʻa i kēia maʻi kanesa kona inoa no ka mea ua like kona mau ʻāpana me kahi 'spindle' ke nānā ʻia ma lalo o kahi microscope.

💬 He aha nā hōʻailona o kēia maʻi kanesa e ulu ana i loko o nā ʻiʻo o ko kākou mau lima a me nā wāwae?

Hoʻomaka pinepine kēia maʻi ʻaʻai ma nā ʻiʻo hohonu o nā wāwae a me nā lima (Extremities). I nā pae mua, ʻaʻohe ʻeha. Manaʻo ka mea maʻi iā ia me he puʻupuʻu nui ʻole (e ulu ana) ma lalo o ka ʻili o ka lima a i ʻole ka wāwae. Aia wale nō ke ulu ka puʻupuʻu a kaomi i kahi aʻalolo kokoke e hoʻomaka ai e hōʻeha nui.

💬 He aha ke ʻano lapaʻau nui no kēia maʻi kanesa?

ʻO ka lāʻau lapaʻau nui a maikaʻi loa no kēia, ʻo ia ka hana ʻoki ʻana i ka wā hikiwawe loa, e wehe loa ana i ka puʻupuʻu a me nā ʻiʻo olakino e hoʻopuni ana (excision ākea). Ma hope o kēlā, hāʻawi ʻia ka radiation a i ʻole chemo e luku i nā hunaola kanesa i koe.


ʻO ka Spindle Cell Sarcoma, Spindle Cell Sarcoma, Kanesa, Kanesa Iwi, Kanesa ʻIʻo Palupalu, Puʻupuʻu, Nā Hōʻailona, ​​Lapaʻau

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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