Ke ʻeha mau nei kou kino a me kou ʻūlū ʻana? E kamaʻilio kākou e pili ana i ka CIDP (CIDP)

I kekahi manawa loaʻa iā mākou ka ʻūlū ma kekahi lima a i ʻole ka wāwae, a nalo wale ia ma hope o kekahi manawa, ʻeā? Akā e noʻonoʻo, inā e nalowale mālie kou mau lima a me kou mau wāwae i ka ikaika, hoʻomaka e manaʻo he mae, a piʻi mālie ke ʻano ma luna o ʻelua mahina? ʻO kēia kekahi o nā hōʻailona nui o kahi maʻi neurological laha ʻole i kapa ʻia ʻo CIDP (Chronic Inflammatory Demyelinating Polyneuropathy) . ʻOiai he paʻakikī iki ka inoa, e hoʻomaopopo maʻalahi kākou. ʻOiai he maʻi laha ʻole kēia, he mea nui loa ia no nā mea a pau e ʻike i kēia.

I ka ʻōlelo maʻalahi, he aha ka CIDP?

He kūlana lōʻihi ka CIDP e kū mai ana i ka wā e hoʻouka hewa ai kā mākou ʻōnaehana pale (ka ʻōnaehana e pale ai iā mākou mai ka maʻi ) i ko mākou mau aʻalolo ponoʻī. ʻO ke kikoʻī, hōʻino ia i ka uhi pale a puni nā aʻalolo (i kapa ʻia ʻo myelin ). E noʻonoʻo i kēia uhi e like me ka ʻūpā plastik a puni kahi uea uila . Ke hōʻino ʻia kēia ʻūpā, ʻaʻole hoʻouna pono nā aʻalolo i nā leka i ka lolo a me nā ʻāpana ʻē aʻe o ke kino. ʻO ia ke kumu o nā hōʻailona e like me ka nāwaliwali a me ka numbness i nā lālā.

ʻOiai hiki ke loaʻa kēia maʻi i kēlā me kēia makahiki, ʻoi aku ka maʻamau i waena o nā pākeke a me nā kāne.

He aha ka ʻokoʻa ma waena o ka CIDP a me ka Guillain-Barre syndrome (GBS)?

Ua lohe paha ʻoe i ka maʻi Guillain-Barre ( GBS ). Hoʻopilikia kēia mau maʻi ʻelua i nā aʻalolo a he like nā hōʻailona. Akā, aia nā ʻokoʻa maopopo ma waena o nā mea ʻelua.

• ʻO Guillain-Barre Syndrome (GBS): Hoʻomaka koke kēia i kekahi mau lā ma hope o kahi maʻi, e like me ka ʻeha o ka ʻōpū. Akā me ka mālama ʻana, ʻoi aku ka maʻalahi o ka hoʻōla koke ʻana.
• CIDP: He kūlana lōʻihi kēia e ulu ana i nā mahina me ka ʻole o ka pilina me kekahi maʻi. ʻAʻole hiki i ka GBS ke holomua i CIDP me ka ʻole o ka mālama ʻia.

He aha nā hōʻailona o CIDP?

ʻAʻole like nā hōʻailona o ka CIDP no kēlā me kēia kanaka. Hiki ke ʻokoʻa lākou ma muli o ke ʻano o ka CIDP āu e loaʻa ai. Ma keʻano laulā, hiki iā ʻoe ke ʻike i ka luhi nui, ka mae ʻana, a me ka ʻeha. Hiki i kēia ke hoʻolohi i kāu mau reflexes a nāwaliwali kou mau lima a me kou mau wāwae.

ʻO ka hōʻailona nui a me ka hōʻailona mua i ʻike ʻia, ʻo ia ka piʻi mālie ʻana o ka nui o nā uaua ma luna o ʻelua mahina a ʻoi aʻe paha.Ka nāwaliwali o nā ʻiʻo . Hoʻopilikia kēia nāwaliwali i nā ʻaoʻao ʻelua o ke kino. ʻOi aku ka kikoʻī:

• Nā pūhaka a me nā ʻūhā
• Nā poʻohiwi a me nā lima luna
• Nā lima
• Nā wāwae

Ma waho aʻe o kēia hōʻailona nui, hiki ke ʻike ʻia nā hōʻailona ʻē aʻe:

• ʻAtrophy o nā ʻiʻo: Hoʻēmi nā ʻiʻo a lilo i mea liʻiliʻi.
• Paresthesia: He manaʻo o ka ʻūlū a i ʻole ke kani ʻana ma nā manamana lima.
• Paʻakikī ke hele wāwae: Ka nalowale o ke kaulike a me ka hiki ʻole ke hele pono.
• ʻEha neuropathic: ʻEha nui i hoʻokumu ʻia e nā pilikia me ka ʻōnaehana nerve.
• Nā pane nāwaliwali (Nā pilikia o ke aʻalolo hohonu): Ke kuʻi ke kauka i ke kuli me ka hāmare liʻiliʻi, nalowale ka pane, me he mea lā e kīkoʻo ʻia ana ka wāwae.

I ka hapanui pinepine, hiki ke loaʻa ka pilikia i ka moni ʻana (dysphagia) a me ka ʻike pālua manawa pōkole (diplopia).

Aia kekahi mau ʻano CIDP like ʻole?

ʻAe, hiki ke hoʻokaʻawale ʻia ʻo CIDP i kekahi mau ʻano nui e pili ana i nā hōʻailona. E hāʻawi kēia papa ʻike iā ʻoe i kahi manaʻo maopopo.

Eia kekahi, hoʻokaʻawale nā ​​​​kauka i ka maʻi i ʻekolu mau māhele e pili ana i ke ʻano o kāna hana:

• Holomua: E ʻoi aʻe ka ʻino o nā hōʻailona i ka hala ʻana o ka manawa.
• Hoʻi hou: ʻIke ʻia nā hōʻailona, ​​​​nalo, a ʻike hou ʻia.
• Monophasic: Hoʻokahi wale nō manawa e loaʻa ai ka maʻi i ke ola. Hoʻopau ʻia ma hope o 1-3 mau makahiki.

He aha ke kumu o ka CIDP? He mea laha paha ia?

ʻAʻole maopopo ke kumu kikoʻī o CIDP, akā ua ʻike mākou ua hoʻokumu ʻia e ka mumū o nā aʻalolo a me nā aʻa aʻalolo. E like me ka mea i ʻōlelo ʻia ma mua, hōʻino kēia i ka ʻupena myelin a puni nā aʻalolo.

Pehea e hana ʻia ai ka hōʻailona?

ʻAʻohe hoʻāʻo kikoʻī no CIDP. No laila, e nīnau mua kāu kauka e pili ana i kāu mau hōʻailona (i ka wā i hoʻomaka ai, pehea kou manaʻo), a laila e hana i kahi hoʻokolohua kino a paipai i kekahi mau hoʻokolohua e ʻike pono i ka mea hewa me kou mau aʻalolo a kāpae i nā kūlana ʻē aʻe.

Hiki i kēia mau hoʻokolohua ke komo pū me:

• Nā hoʻāʻo koko a me ka mimi.
• Ke aʻo ʻana i ke alakaʻi ʻana o nā aʻalolo a me ka Electromyogram (EMG): Ke nānā nei kēia mau mea i ka hōʻino ʻia o nā aʻalolo a me ka ʻupena myelin.
• ʻO ka puncture lumbar: Lawe ʻia kahi liʻiliʻi o ka wai mai ke kaula kuamoʻo e nānā i nā pae protein kiʻekiʻe, kahi mea maʻamau i ka CIDP.
• ʻO ka biopsy nerve: Lawe ʻia kahi ʻāpana liʻiliʻi o ke kino mai kahi aʻalolo a nānā ʻia ma lalo o kahi microscope.
• MRI scan: Hiki ke nānā no ka pehu ʻana o nā aʻa o ke aʻalolo.

He aha nā koho lapaʻau?

He nui ka poʻe e pono ai ka lāʻau lapaʻau. ʻO ka wikiwiki o ka hoʻomaka ʻana o ka lāʻau lapaʻau, ʻoi aku ka maikaʻi o ka manawa e ho'ōla piha ai.

Nā ʻano lāʻau lapaʻau

• Corticosteroids: ʻO kēia nā lāʻau lapaʻau steroid e hōʻemi i ka mumū a kaohi i ka hana o ka ʻōnaehana pale.
• Immunotherapy: Hoʻōki kēia mau lāʻau lapaʻau i ka ʻōnaehana pale mai ka hoʻouka ʻana i ka myelin.
• ʻO Biologics: Hoʻohana ʻia nā lāʻau lapaʻau e like me Vyvgart, kahi papa lāʻau lapaʻau hou i ʻāpono ʻia nei, no kēia kumu.

Nā lāʻau lapaʻau kūikawā

• ʻO ka immunoglobulin intravenous (IVIG): Hāʻawi ʻia ʻoe i kahi inikini o kahi ʻano antibodies i hoʻohuihui ʻia mai ke koko o ka poʻe olakino. Kōkua kēia i ka kaohi ʻana i ka hana hewa ʻana o kāu ʻōnaehana pale.
• Hoʻololi Plasma (PE): Pili kēia i ka lawe ʻana i kou koko, hoʻouna ʻana ma o kahi mīkini kūikawā, wehe ʻana i ka plasma koko e loaʻa ana nā antibodies ʻino, a laila hoʻihoʻi hou i ke koko maʻemaʻe i loko o kou kino.
• Hoʻoili pūnaewele kumu: Ma kēia lāʻau lapaʻau kakaʻikahi loa, hoʻoili ʻia nā pūnaewele kumu olakino e "hoʻonohonoho hou" i ka ʻōnaehana pale.

Nā lāʻau lapaʻau kākoʻo ʻē aʻe

• Hoʻōla kino: He mea kōkua nui kēia i ka loaʻa hou ʻana o ka ikaika nalowale, ka hele wāwae, a me ka hoʻomaikaʻi ʻana i ke kaulike.
• ʻO ka hoʻōla hana: Ke aʻo aku nei iā ʻoe pehea e hana maʻalahi ai i nā hana o kēlā me kēia lā me ka nānā ʻole i kou kūlana.
• Hoʻoikaika kino a me ka ʻai: Hiki i ka hoʻoikaika kino kūpono ke kōkua iā ʻoe e noho ikaika. Akā, pono e hana ʻia ka hoʻoikaika kino ma lalo o ka nānā ʻana a kāu kauka a mea hoʻoponopono kino paha. Hiki i ka ʻai kaulike ke kōkua i ka pale ʻana i ka piʻi ʻana o ke kaumaha pono ʻole.

Ke noho nei me CIDP a me ka nānā ʻana

Ke loaʻa iā ʻoe kahi hōʻailona CIDP, hiki iā ʻoe ke manaʻo ua kaumaha ʻoe. He mea maʻamau kēlā. He mea nui e noho mau me kāu kauka a kamaʻilio e pili ana i kāu mau hōʻailona a me ka lāʻau lapaʻau.

He mea nui loa hoʻi e ʻimi i ke kōkua loea e hoʻokele i ka ʻeha a loaʻa ka hōʻoluʻolu noʻonoʻo. ʻO kou ʻohana, nā hoaaloha, a me kāu hui lapaʻau he kumu ikaika nui ia nou ma kēia huakaʻi.

No ke ʻano o ka nānā ʻana, pili ia i kou mau makahiki, ke ʻano o ka maʻi, pehea e hoʻomaka mua ai ka mālama ʻana, a pehea e pane ai kou kino i ka mālama ʻana.ʻO ka nūhou maikaʻi, me ka mālama ʻana, e ola ana ma kahi o 90% o ka poʻe. Hiki i kekahi poʻe ke ʻike i ka hoʻi hou ʻana o nā hōʻailona. Eia nō naʻe, ʻaʻole hoʻopōkole pinepine ka CIDP i ka manaʻolana ola.

CIDP, neuropathy, numbness, nāwaliwali o nā ʻiʻo, myelin, Guillain-Barre syndrome, immunotherapy, nā maʻi autoimmune, CIDP sinhala