Hiki iā ʻoe ke noʻonoʻo e hiki i kahi ʻano maeʻa liʻiliʻi e hoʻomaka ana ma nā wēlau o kou mau manamana wāwae ke pālahalaha mālie i loko o kou kino, e hoʻoulu ai i ka maeʻa ʻana o kou mau lālā a me ka maʻi lolo? He moʻolelo weliweli kēia. Akā ʻo kēia ka ʻoiaʻiʻo o kahi maʻi neurological laha ʻole i kapa ʻia ʻo
Guillain-Barré Syndrome (GBS). Hoʻomohala pinepine ia ma hope o kou hoʻōla ʻana mai kahi ʻōpū maʻamau (e like me ka jaundice) a i ʻole ka maʻi hanu (e like me
ke anu ).
I ka ʻōlelo maʻalahi, he aha ka Guillain-Barré syndrome (GBS)?
I nā huaʻōlelo maʻalahi, ʻo GBS ka manawa e hoʻomaka koke ai ka ʻōnaehana pale o ko mākou kino,
ʻo ia hoʻi ka ʻōnaehana pale , e hoʻouka i ko mākou mau aʻalolo ponoʻī. Ua like ia me ko mākou pūʻali koa ponoʻī e hoʻouka hewa ana i ko mākou poʻe ponoʻī. E noʻonoʻo e like me ko mākou mau aʻalolo e like me nā uea uila. Aia kahi ʻūpā palaki a puni kēia mau uea ma ke ʻano he insulation, ʻeā? Pēlā nō, ua hoʻopuni ʻia ko mākou mau aʻalolo e kahi ʻūpā pale i kapa ʻia ʻo
myelin . Ke ulu ka GBS, hoʻouka kā mākou ʻōnaehana pale i kēlā ʻūpā myelin. Ke hōʻino ʻia kēia ʻūpā, ʻaʻole hiki i nā leka mai ka lolo i nā ʻiʻo pono. ʻO ka hopena, he nāwaliwali nā ʻiʻo, he mae wale, a i kekahi manawa he paralysis piha.
ʻAʻole kēia he maʻi lele a hoʻoilina paha. Eia nō naʻe, he ʻano ia e pono ai ke kōkua lapaʻau koke . No laila, he mea nui loa e ʻimi i ke kōkua lapaʻau i ka wā e ʻike ʻia ai nā hōʻailona mua.
He aha nā ʻano nui o GBS?
Aia kekahi mau ʻano nui o GBS, akā ʻo ke ʻano mua ka mea maʻamau ma Sri Lanka.
| ʻAno maʻi | Kūikawā |
|---|
| ʻO ka polyradiculoneuropathy demyelinating mumū koʻikoʻi (AIDP) | ʻO kēia ke ʻano maʻamau. I kēia ʻano, hoʻomaka ka nāwaliwali o nā ʻiʻo ma nā wāwae a pālahalaha i luna i loko o ke kino. |
| ʻO ka maʻi Miller Fisher (MFS) | He mea maʻamau kēia ma nā ʻāina ʻĀsia. Hoʻomaka mua ia me ka paʻakikī o ka hoʻoneʻe ʻana i nā maka. ʻO ka nalowale o ke kaulike i ka wā e hele ana he hōʻailona nō hoʻi. |
| Nā ʻano AMAN a me AMSAN | ʻOi aku ka maʻamau o kēia ma nā ʻāina e like me Kina a me Iapana. Hiki ke ʻoi aku ka koʻikoʻi o nā hōʻailona ma mua o nā ʻano ʻē aʻe. |
Nā kumu a me nā kumu pilikia no ka hoʻomohala ʻana o GBS
ʻAʻole ʻike ʻia ke kumu kikoʻī o GBS. Eia nō naʻe, manaʻo nā kauka ua hoʻololi kekahi mau maʻi i ke ʻano o kā mākou mau hunaola nerve, e hoʻolilo ana i ka ʻōnaehana pale e kuhihewa iā lākou he mau ʻenemi. Ma kahi o ʻelua hapakolu o ka poʻe i loaʻa iā GBS he maʻi ʻōpū e like me ka maʻi diarrhea a i ʻole kahi maʻi hanu e like me ke anu i kekahi mau lā a i ʻole nā pule ma mua o ka hoʻomaka ʻana o nā hōʻailona neurological.
ʻO kekahi o nā kumu nui e hiki ke kōkua i ka GBS:- ʻO ka bacteria Campylobacter: ʻO kēia bacteria, ka mea i hoʻoili ʻia ma o ka moa i moʻa pono ʻole ʻia, ua manaʻo ʻia ʻo ia ke kumu nui o GBS .
- Maʻi palū
- Maʻi COVID -19
- ʻO ka maʻi Cytomegalovirus
- ʻO ka maʻi Epstein-Barr
- ka maʻi Zika
- Hepatitis A , B, C a me E
- ka maʻi HIV
- ʻO kekahi mau ʻoki kino a i ʻole nā ulia pōpilikia
- I nā hihia kakaikahi, kekahi mau lāʻau pale (e like me nā lāʻau pale COVID-19 Johnson & Johnson a me AstraZeneca)
ʻAʻole nā kānaka a pau i loaʻa i kēia maʻi e loaʻa iā lākou ka GBS. Hoʻokahi wale nō i loko o ka miliona o ka poʻe i pilikia.
He aha nā hōʻailona e pono ai ʻoe e makaʻala?
Hiki ke ʻike koke ʻia nā hōʻailona o GBS, i kekahi manawa e lilo i mea koʻikoʻi i loko o kekahi mau hola a i ʻole mau lā.
| Hōʻailona | Wehewehena |
|---|
| Māʻule | He ʻano ʻūlili e like me nā nalo e kolo ana ma kou mau manamana wāwae, nā kuʻekuʻe wāwae, nā manamana lima, a me nā pulima lima. |
| Nāwaliwali o nā ʻiʻo | He manaʻo ola ʻole e hoʻomaka ana ma nā wāwae a laha mālie i nā ʻāpana o luna o ke kino. |
| Paʻakikī ka hele wāwae | Ua nalowale koʻu kaulike i ka wā e hele ana a he paʻakikī iaʻu ke piʻi i nā alapiʻi. |
| Nā loli o ka helehelena | Lilo i mea paʻakikī ke ʻōlelo, nau i ka meaʻai, a me ke ale ʻana. Hiki iā ʻoe ke ʻike i hoʻokahi a ʻelua paha mau mea ma nā maka ʻelua (ʻike pālua). |
| ʻEha nui | He ʻeha hou, ʻeha hou i nā ʻiʻo o ke kino. Hiki ke ʻoi aku ka ʻino o kēia ʻeha, ʻoi aku hoʻi i ka pō. |
| Nā hiʻohiʻona ʻē aʻe | Hoʻonui ʻia ka helu o ka puʻuwai, ke koko kiʻekiʻe a haʻahaʻa, ka hiki ʻole ke kaohi i ka mimi a me ka ʻōpala, ka paʻakikī o ka hanu ʻana. |
He mea nui loa: Inā manaʻo koke ʻoe ua maʻi ʻoe a lilo i mea ʻino aʻe i loko o kekahi mau hola, a inā pilikia ʻoe i ka hanu ʻana a i ʻole ke ale ʻana, e hele koke i ka ʻOihana Pōpilikia (ETU) o ka haukapila. ʻAʻole kēia he mea e hoʻopaneʻe ai.
Pehea e ʻike ai ke kauka i kēia maʻi?
Ma muli o ka like o nā hōʻailona o GBS me nā maʻi neurological ʻē aʻe, e holo ke kauka i kekahi mau hoʻokolohua e hōʻoia i ʻaʻohe maʻi ʻē aʻe.
- Ke nīnau nei iā ʻoe: Ke nīnau nei i nā mea e like me pehea a me ka wā i hoʻomaka ai kāu mau hōʻailona, a inā he mau maʻi hou kāu.
- Hoʻāʻo ʻōnaehana nerve: Hoʻāʻo kēia i kou ikaika o nā ʻiʻo, ka hele ʻana, ke kaulike, a me nā reflexes.
- ʻO ke kī ʻana o ka iwi kuamoʻo / lumbar puncture: ʻO kēia ke komo ʻana i kahi nila lahilahi loa i loko o kou kua haʻahaʻa a lawe i kahi liʻiliʻi o ke wai a puni kou kaula iwi kuamoʻo (wai cerebrospinal) a hoʻouna aku i kahi lab no ka hoʻāʻo ʻana. Inā kiʻekiʻe nā pae protein i loko o kēia wai, he hōʻailona ia o GBS.
- Nā hoʻokolohua hana neurological:
- Electromyography (EMG): Pili kēia i ke kau ʻana i nā electrodes e like me ke nila maikaʻi i loko o nā ʻiʻo e ana i ka hana aʻalolo.
- Haʻawina hoʻoili aʻalolo: Ke ana nei kēia i ka wikiwiki o ka hele ʻana o nā impulses aʻalolo ma ke kau ʻana i nā electrodes ma ka ʻili a me ka hoʻouna ʻana i kahi au uila liʻiliʻi. Hoʻolohi ʻia kēia wikiwiki i ka GBS.
- MRI scan: Loaʻa paha iā ʻoe kahi MRI scan o kou lolo a i ʻole ka iwi kuamoʻo.
He aha nā lāʻau lapaʻau?
Inā ua ʻike ʻia ʻoe me GBS, pono ʻoe e hoʻomaka koke i ka lāʻau lapaʻau. E mālama pinepine ʻia ʻoe ma ka ʻāpana mālama koʻikoʻi (ICU) o kahi haukapila. ʻElua mau lāʻau lapaʻau nui: 1.
Hoʻololi plasma / Plasmapheresis: Hoʻokomo ʻia kou koko i loko o kahi mīkini kūikawā, a hoʻokaʻawale ʻia ka ʻāpana wai o kou koko (plasma). Loaʻa i kēia plasma nā antibodies e hōʻino i nā aʻalolo. Hoʻopau ka mīkini i kēia mau antibodies maikaʻi ʻole a hoʻihoʻi i nā hunaola koko maikaʻi i loko o kou kino. 2.
Immunoglobulin therapy: Hāʻawi ʻia iā ʻoe kahi nui o nā antibodies maikaʻi i lawe ʻia mai nā poʻe olakino ma o kahi hopena saline. Hoʻemi kēia mau antibodies maikaʻi i ka hana o nā antibodies maikaʻi ʻole i loko o kou kino. Ma waho aʻe o kēia mau lāʻau lapaʻau nui, e hāʻawi ʻia ʻoe i nā mea ʻeha, nā mea hoʻokahe koko, a inā pono, e hānai ʻia ʻoe ma o kahi paipu no ka mea ʻaʻole hiki iā ʻoe ke ale i ka meaʻai.
Inā paʻakikī ka hanu ʻana, pono paha ʻoe e hoʻopili ʻia no kekahi manawa i kahi ventilator. I kou wā e hoʻōla ai, pono ʻoe e hana i ka hoʻomaʻamaʻa ikaika me ke kōkua o ka hoʻōla kino a me ka hoʻōla hana.
Pehea lā ke ʻano o ka hoʻōla hou ʻana a me ka wā e hiki mai ana?
Hiki ka maʻi i kona kiʻekiʻe loa he 2-3 mau pule ma hope o ka hoʻomaka ʻana o nā hōʻailona. Ma hope o kēlā, hoʻomaka mālie ka hoʻōla ʻana.
- Ma kahi o 80% o nā maʻi e hiki ke hele me ke kōkua ʻole i loko o 6 mau mahina.
- Ma kahi o 60% o nā maʻi e hoʻi hou i ka ikaika piha o nā ʻiʻo i loko o hoʻokahi makahiki.
- Hiki ke lōʻihi ka ho'ōla ʻana ma waena o 6-12 mau mahina, a no kekahi poʻe hiki ke lōʻihi a hiki i 3 mau makahiki.
ʻOi aku ka wikiwiki o ke ola ʻana o nā keiki me GBS ma mua o nā pākeke. Ke hoʻōla piha ʻia ʻoe mai GBS, hiki iā ʻoe ke ola i kahi ola maʻamau.
Leka Lawe-Home
- Inā he maneʻo kou a he manaʻo nāwaliwali paha e hoʻomaka ana ma kou mau wāwae a pālahalaha i kou kino, mai hoʻowahāwahā iā ia.
- Inā hele pū kēia mau hōʻailona me ka paʻakikī o ka hanu ʻana a i ʻole ke ale ʻana, he pilikia olakino ia. E hele koke i ka ʻOihana Pilikia o ka haukapila (ETU).
- He maʻi laha ʻole ka GBS akā he maʻi koʻikoʻi paha. Eia nō naʻe, inā hoʻomaka mua ʻia ka mālama ʻana, hiki i ka hapa nui o ka poʻe ke hoʻōla piha.
- Mai hopohopo. Inā loaʻa iā ʻoe kēia mau hōʻailona, e ʻike koke i kāu kauka no ka ʻōlelo aʻo.
ʻO Guillain-Barré Syndrome, GBS, neuropathy, hemohemo wāwae, hemohemo, ʻōnaehana pale, myelin
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