Sɔntɛnde, yu kin fil taya ɔ taya? Ɔ yu dɔn ɛva mek dɔktɔ put stetɔskɔp na yu chɛst ɛn se sɔntin lɛk, "Mmm... a yɛri smɔl strenj sawnd (murmur) de kɔmɔt na yu at"? Di tin we kin mek dis apin kin bi smɔl chenj na yu at we dɛn bɔn yu wit. Nɔ wɔri, tide wi de tɔk bɔt wan kɔmɔn kɔndishɔn we dɛn kɔl Bicuspid Aortic Valve.
Fɔ tɔk am simpul wan, wetin na dis Bicuspid Aortic Valve?
Okay, mek wi ɔndastand dis dis we. Fo men valv dɛn de na wi at. Dɛn tin ya tan lɛk get dɛn we de opin na wan say nɔmɔ. Fɔ dɛn wan ya, di wan we de sɛn blɔd to di aorta, we na di men blɔd vesel we de kɛr blɔd we gɛt ɔksijɛn frɔm di at to di wan ol bɔdi, dɛn kɔl am di aorta valv. nכmal wan, pan hεlty pכsin, dis aorta valv gεt tri sכm sכm flap dεm (cusps כ liflet dεm). Dɛn tri flap ya kin opin ɛn lɔk fayn fayn wan fɔ kɔntrol di we aw blɔd de flɔ. Bɔt pan pɔsin we gɛt wan sik we dɛn kɔl
bicuspid aortic valve, dis valv
gɛt tu flap dɛn instead fɔ gɛt tri . Dis na wan sik we dɛn bɔn wit. So, bikɔs na tu flap nɔmɔ de, dis valv kin gɛt smɔl prɔblɛm fɔ opin ɛn lɔk fayn fayn wan. dis kin mek tu men prכblεm: 1.
Aortic Stenosis (narrowing of the valve): Bikɔs di valv nɔ de opin fayn, na smɔl ples nɔmɔ de fɔ di at fɔ pɔmp blɔd to di bɔdi. Dis kin mek di at wok tranga wan. 2.
Aortic Regurgitation (bakflɔ ɔf blɔd): Bikɔs di valv nɔ de lɔk fayn, sɔm pan di blɔd we dɛn pɔmp to di bɔdi de lik bak insay di at. Yu nɔ go gɛt ɛni sayn fɔ lɔng tɛm. Bɔt as tɛm de go, dis ɛkstra strɛs kin mek yu at gɛt prɔblɛm.
Aw siriɔs dis tin de apin?
Nɔto ɔlman we gɛt Bicuspid Aortic Valve go gɛt big prɔblɛm. Bɔt lɛk wan pan ɔl tri pipul dɛn go gɛt prɔblɛm dɛn as tɛm de go. Na dat mek
i impɔtant fɔ de chɛk-ap ɔltɛm ɛn du mɛdikal tɛst if yu dɔktɔ tɛl yu se yu gɛt dis sik. I nɔ kin bɔku lɛk aw yu kin tink. I de afɛkt 1% to 2% pan di pipul dɛm na di wɔl. I kin tu tɛm bak pan man dɛn pas uman dɛn. Pipul wae gɛt sɔm kayn jɛnɛtik sik lɛk Turner syndrome, dɛnsɛf kin gɛt bɔrku risk. Di bɛst pat na dat, wit di advans mɛdikal tɛknɔlɔji tide, yu kin no dis sik ɛn di chenj dɛn we i kin chenj we nɔ klia bifo yu ivin notis di sayn dɛm. Ɛn if yu gɛt di rayt tritmɛnt, yu go ebul fɔ liv ful layf, gɛt wɛlbɔdi, ɛn lɔng layf.
Wetin na di sayn dɛm fɔ dis?
Bɔrku pipul nɔr kin gɛt ɛni sayn fɔ lɔng tɛm. Bɔt as di valv de wok fayn, di sayn dɛn kin bigin fɔ sho. pan yכŋ pikin dεm εn bεlε pikin dεm, if di kכndyushכn rili bad, di sayn dεm lεk bluish/pale kכla na di skin (`
cyanosis` ) εn i at fכ it כ fכ gεt wet kin apin sכm tεm afta dεn bכn am. De sayn dɛm wae dɛn kin si pan big pipul dɛm na:
| Di sayn we de sho se di sik de | Tɔk bɔt |
|---|
| Taya | Dis na de sayn wae kin pasmak: yu kin fil taya pasmak ivin afta yu dɔn du smɔl wok. |
| Chest pen ɔ diskɔmfɔt | Filin fɔ prɛshɔ we di at gɛt fɔ wok tranga wan. |
| Diziz ɔ fɔdɔm . | I kin apin we di bren nɔ gɛt bɛtɛ blɔd. |
| Palpitations (fɔ fil lɛk se yu at de bit fast) . | At nɔ kin bit ɔltɛm ɔ i kin bit kwik kwik wan. |
| Shot we yu de blo | Fɔ blo shɔt, mɔ we yu de du ɛksɛsayz ɔ waka. |
Yu kin tray fɔ du sɔntin we smɔl. Kɔmpia di wok we yu kin du insay wan de tide wit di wok we yu bin dɔn du siks mɔnt bifo dis tɛm. Yu kin fil taya kwik kwik wan naw? Yu nid mɔ tɛm fɔ rɛst? If na so i bi, dat kin bi sayn fɔ sho se yu at de wok tranga wan. Tɔk to yu dɔktɔ bɔt ɛni chenj lɛk dis.
Wetin kin mek dis apin? Yu tink se na frɔm dɛn gret gret granpa dɛn?
di ekzak kכz fכ dis `Aortic valve` dεn nכ fכnshכn yet. dis na sכmtin we de apin we di pikin in at de divεlכp we di bεlε de bigin. Dis kכndyushכn
kin rכn na famili dεm to sכm tεm (hereditary) . Dat min se, if pɔrsin na yu fambul wae de nia yu (mama, papa, brɔda ɛn sista, pikin) gɛt dis sik, yu kin gɛt sɔm risk bak. So, if ɛnibɔdi na yu famili gɛt dis kayn at valv sik, i rili impɔtant fɔ tɛl yu dɔktɔ bɔt am. Dɔn, if i want, dɛn kin tɛst yu bak.
Us prɔblɛm dɛn kin apin if dɛn nɔ trit am?
If dɛn nɔ trit am di rayt tɛm, siriɔs prɔblɛm dɛn kin apin.
- di at we de wok fayn: we di valv de sכmtεm (stenosis) de mek di at wok tranga wan. Dis kin mek di at mɔsul tik ɛn big, ɛn leta i nɔ kin ebul fɔ pɔmp blɔd fayn fayn wan. Tin dɛm lɛk fɔ smok ɛn ay kɔlɔstrel kin mek dis prɔses kwik.
- di aortic aneurysm rupture and dissection: Na lεk wan pan tri pipul dεm we gεt bicuspid aortic valv de pan risk fכ di aorta, di big at we de oba di valv, fכ dilayt. Lɛk aw balyɔn kin blo pasmak, di wɔl dɛn na dis blɔd vesel kin wik ɛn bigin fɔ bɔl. Dɛn kɔl dis aortic aneurysm. If i tu big, i kin bɔs wantɛm wantɛm (rupchɔ) ɔ te (dissection). Dis na imejensi we kin mek pɔsin in layf de pan denja ɛn we nid fɔ gɛt tritmɛnt wantɛm wantɛm .
Aw dɛn kin no dis sik?
Bɔku tɛm, dɔktɔ go fɔs sɔspɛkt se at de grɔmbul we dɛn yɛri wan sawnd we nɔ kɔmɔn (a `at grɔmbul`) we dɛn de lisin to yu chɛst wit stɛtoskɔp. Afta dat, yu dɔktɔ go tɛl yu fɔ du sɔm spɛshal tɛst dɛn fɔ si aw yu at tan ɛn aw i de wok. Di men tɛst dɛn na:
- Echocardiogram (echo): Dis na ɔltra saund skan fɔ di at. I kin si klia wan di nɔmba fɔ di liflet dɛn we de na di valv, aw dɛn de wok, ɛn if ɛnitin de lik ɔ smɔl.
- CT scan (Computed Tomography scan): Dis kin mek tri dimɛnshɔnal pikchɔ dɛn bɔt di at ɛn di aorta.
- Hat MRI (Magnetic Resonance Imaging): Dɛn kin yuz dis tɛst fɔ gɛt mɔ ditayla pikchɔ dɛn bɔt di at ɛn di valv dɛn.
Wetin na di tritmɛnt dɛn we yu kin gɛt?
Pan ɔl we sɔm mɛrɛsin dɛn lɛk beta-blɔka kin ɛp fɔ kɔntrol di sik dɛn, dɛn nɔ kin ebul fɔ mɛn di valv prɔblɛm kpatakpata. Na lɛk 4 pan ɔl 5 pipul dɛm wae gɛt Bicuspid Aortic Valve go nid ɔpreshɔn sɔm tɛm na dɛn layf. Ɔpreshɔn kin mek yu valv
fayn ɔ
chenj am wit nyu wan. Yu mɛdikal tim go tɔk to yu bɔt di bɛst tritmɛnt fɔ yu, bay aw yu sik, yu ej, ɛn ɔl yu wɛl bɔdi.
I rili impɔtant fɔ mek dɛn du ɔpreshɔn di rayt tɛm bifo di at pwɛl fɔ ɔltɛm. Ivin if yu nɔ gɛt ɛni sik, yu dɔktɔ kin tɛl yu fɔ du ɔpreshɔn fɔ mek yu nɔ gɛt prɔblɛm dɛn tumara bambay.
Di kayn ɔpreshɔn dɛn we dɛn kin du
Aortic Valve RipairAorta Valv Riplesmɛnt
| Di kayn ɔpreshɔn we dɛn kin du | Tɔk bɔt |
|---|
| We | If yu nɔ pul yu yon valv, yu kin shep am bak ɛn ajɔst am so dat di flap go lɔk fayn fayn wan. dis kin fayn fכ situeshכn dεm we bכdi de lik (`regurgitation`). |
| We | Dɛn kin pul wan valv we dɔn pwɛl we dɛn nɔ ebul fɔ mek am ɛn put nyu valv insay. |
| Nyu valv tayp dɛn | - Bayolojikal valv dεm: Dis na valv dεm we dεn mek wit pig כ kaw at tisu. Dɛn kin las fɔ lɛk 10-15 ia so. Sɔntɛm dɛn go nid fɔ du ɔpreshɔn bak. No nid nɔ de fɔ kɔntinyu fɔ tek mɛrɛsin we de mek yu blɔd tan .
- Mekanikal valv: Dis na sintetik mɛtal valv dɛn. Dɛn kin las fɔ ɔl yu layf. Bɔt yu go nid fɔ tek mɛrɛsin we de mek yu blɔd tan lɛk yu layf fɔ mek yu blɔd nɔ klɔt.
|
Naw, insted of tradishonal opin-hat opareshon, di modna we dem de lek minimal invasive surgery en TAVR (Transcatheter Aortic Valve Replacement), we de riples di valv tru wan blɔd vesel. Dɛn we ya kin gɛt shɔt tɛm fɔ wɛl.
Aw na fɔ wɛl ɛn di tumara bambay?
98% pan di pipul dεm we dεn du valv כpεrayshכn kin rεkכva fayn fayn wan, εn dεn layf εkspεktεns nכ de afekt. Dis min se
ivin if yu gɛt Bicuspid Aortic Valve kɔndishɔn, wit di rayt tritmɛnt ɛn mɛdikal sɔpɔtishɔn , yu kin liv lɔng, wɛlbɔdi layf lɛk ɛni ɔda pɔsin. Di tin we impɔtant pas ɔl na fɔ go na yu dɔktɔ ɔltɛm fɔ fala yu. Afta dɛn dɔn ɔpreshɔn yu, bɔku tɛm yu nid fɔ go chɛk-ap wan tɛm insay di ia.
Ustɛm yu nid fɔ go na ɔspitul kwik kwik wan? (Wetin fɔ go na di ETU)
Di sayn dɛm we de sho se di aneurism rupchɔ kin rili denja. If yu gɛt wan ɔ mɔ pan dɛn sik ya,
kɔl 911 wantɛm wantɛm fɔ ambulans ɔ go na di ɔspitul Imejɛnsi Dipatmɛnt (ETU) we de nia yu.- Wan pen we kin kam wantɛm wantɛm, we kin shap ɛn we kin te na in chɛst ɔ bak.
- Skin we de stika, we de swet.
- Diziz we pɔsin kin gɛt.
- Fɔ mek pɔsin nɔ ebul fɔ du natin.
- Di at we de blo.
- Nɔs ɛn vɔmit.
- I nɔ kin izi fɔ yu fɔ blo bad bad wan.
Mɛsej we dɛn kin kɛr go na os
- Bicuspid Aortic Valve na wan hat sik wae yu kin bɔn wit wae nɔr kin bɔrku lɛk aw yu kin tink. insay dis kכndishכn, di men valv na di at gεt tu lif dεm insted fכ tri.
- Bɔrku pipul nɔr kin gɛt ɛni sayn fɔ lɔng tɛm. Di sayn dɛm kin bi fɔ taya, nɔs, ɛn pen na yu chɛst.
- dis kכndyushכn kin mek di valv sכmtεm sכmtεm (stenosis) כ bכdi lik (rεgurgitation).
- I impɔtant fɔ mek dɛn chɛk am ɔltɛm na di mɛrɛsin (espɛshali wan ɛkokardiogram). Dis kin ɛp fɔ no prɔblɛm dɛn bifo dɛn mek yu at pwɛl.
- Ɔspitul tritmɛnt dɛn de we kin wok fayn. If yu trit yu fayn, yu go ebul fɔ liv yu layf we gɛt wɛlbɔdi ɛn lɔng layf.
- If ɛnibɔdi na yu famili gɛt dis sik, tɛl yu dɔktɔ bɔt am.
Bicuspid Aortic Valve, At Valve Disease, Aortic Stenosis, Aortic Regurgitation, At Ɔpreshɔn, Chɛst Pen, Shot Breath
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