Sickle Cell Disease i nei em? Chuvangin i rilru na i neih chuan inkhelh kual suh! Hei hi Acute Chest Syndrome chungchang a ni!

A chang chuan rang takin i rilru a na a, thawk harsa i ti em? Heng harsatnate hi khuh leh khawsik ang chi thil nen a lo awm a nih chuan, a bik takin Sickle Cell Disease (SCD) tih natna nei i nih chuan hei hi ngaihthah suh. A chhan chu heng symptoms te hi natna khirh zawk `Acute Chest Syndrome` tih chhinchhiahna a ni thei a ni. Ngaihtuah buai suh, vawiin hian he thu hi chiang tak leh awlsam takin kan sawi dawn a ni.

Acute Chest Syndrome hi eng nge ni? A awlsam zawngin...

Okay, tunah chuan en teh. He `Acute Chest Syndrome` hi sickle cell natna (`SCD`) avanga harsatna lian tak thlen thei a ni. A awlsam zawngin, i rilru natna, khuh, khawsik, i thisena oxygen level hniam, leh thil pangngai lo, a bik takin tui, lung tissue-a lo awm tan (`lung infiltrates`) a ni.

He dinhmun hi a na thei hle a ni . Dik tak chuan he `Acute Chest Syndrome` hi sickle cell natna vei te tan damdawi ina dahna leh a chang chuan thihna thlentu lian ber a ni . Chuvang chuan hei hi kan hriat chian a pawimawh hle a ni.

Tunah chuan Sickle Cell Disease (SCD) hi eng nge ni tih i ngaihtuah mai thei. Chumi chungchang tlem han hriat nawn tir leh ila. Genetic natna a ni a . Chu chu rochun a ni tihna a ni. Kan thisen sen chhunga protein hemoglobin an tih chu a nghawng a ni . Mi hrisel thisen zam (red blood cells) chu a zungbun a nih laiin, SCD vei mi thisen sen (red blood cells) chu sickle (crescent ang mai) ang maia insiam a ni. Chuvangin heng sickle ang cell te hian kan thisen kalna kawng te tak te hi awlsam takin an paltlang thei lo. Tichuan, hemoglobin hian taksa pum puiah oxygen a phur tha thei lo. Hei hi SCD buaina ber a ni.

Acute Chest Syndrome hi engtiang chiahin nge a awm?

Dik tak chuan `Acute Chest Syndrome` hi sickle cell natna (`SCD`) vei zingah a awm fo thin . Statistics atanga a lan dan chuan `SCD` vei zinga a chanve vel chuan an dam chhungin vawi khat tal he natna hi an tawk ang . Naupang kum 2 leh 4 inkar ah a tam ber nia lang mahse naupang aiin puitling ah a na zawk thei Tin, `SCD` leh Asthma vei te chu midang aiin `Acute Chest Syndrome` vei an tam zawk tih hmuhchhuah a ni bawk.

Engvangin nge Acute Chest Syndrome hi a lo awm? A chhante chu engte nge ni?

Scientist-te chuan `Acute Chest Syndrome` thlentu dik tak chu an la sawi chiang thei lo. Mahse thil pakhat emaw, a aia tam emaw avanga lo awm a nih an ring. Eng nge an nih hi han thlir ila:

• Ruhro (bone marrow necrosis) a awm thin:Kan ruh lian tak tak chhunga a nem leh spongy part chu bone marrow hi a ni tih i hria em? He ruhro hi eng emaw ti takin a thih chuan (chu chu `necrosis` an ti a), a hnah te te te chu a inthen a, thisenah a lut thei a, taksa pum puiah a kal thei a ni. Heng piece te hi lungah an kal chuan `Acute Chest Syndrome` a thlen thei a ni.
• Fat embolism: A chunga kan sawi tak bone marrow failure awm thei dang chu fat embolism a ni. A awlsam zawngin, hei hi thau chi (oil drop angin ngaihtuah rawh) chu thisen kalna kawngah a tlakbuak a, thisen kalna tur a tihkhawtlai hian a ni . Hei hian Acute Chest Syndrome a thlen thei bawk.
• Infection : Infection hrang hrang, a bik takin bacteria emaw virus emaw avanga pneumonia , acute chest syndrome a thlen thei. Naupang tê tête zingah hian natna hrik hi natna thlentu ber a ni . Mahse, puitlingah chuan , thau embolism vang a ni zawk.

Acute Chest Syndrome vei tan eng symptoms nge a neih?

`Acute Chest Syndrome` natna lan chhuah dan hi mi hrang hrangah a inang lo thei. A bik takin naupang te leh puitling inkarah hian danglamna engemaw zat a awm. Naupang tê tête hian hri kai lan chhuah tam ber chu:

• Khuh
• Khawsik
• Thisen a oxygen awm zat tlahniam (hypoxemia) .
• Thâwk chak lutuk (tachypnea) .
• Wheezing (thaw chhuah laiin rilru atanga thawm lo chhuak) .

Puitling pawhin heng symptoms te hi an nei thei bawk. Chu bakah, hetiang hian i hre thei bawk ang:

• Chest pain , a bik takin thawk chhuah hian a pung thei.
• Thisen kal dan khar (`vaso-occlusive crisis` an tih bawk) avanga kut, ke leh hnungzang natna nasa tak, rang taka natna .
• Lung leh rilruah tui a awm khawm (pleural effusion).
• Thâwk harsa (dyspnea).

Heng symptoms pakhat emaw a aia tam emaw i neih chuan, a bik takin SCD i neih chuan doctor thurawn lak nghal a pawimawh hle .

Engtin nge Acute Chest Syndrome hi hriat theih? (Diagnosis) tih a ni.

`Acute Chest Syndrome` hriat hmasak hian mi nunna a chhanhim thei a ni.SCD i vei a, damdawi inah i awm a nih chuan enkawl reng a ngai ang a, a tul anga test neih a ngai bawk ang. He harsatna hi doctor-te’n an hriat theih nan test engemaw zat a awm a:

• Arterial blood gas analysis: Hei hian i thisen acidity (pH), oxygen leh carbon dioxide level a teh thei a ni.
• Thisen test: Thisen chhiar kim chuan i thisen sen (red blood cells), thisen var, leh platelet te chungchang hriatna a pe thei a ni.
• Chest X-ray: Hei hi lung infection emaw, a hmaa kan sawi tawh thil danglam (infiltrates) te hi a awm khawm leh awm loh enfiah nan hman theih a ni .
• Cultures: Heng test te hian i thisen, mucus emaw taksa tui dang emaw enfiahin natna chi hrang hrang hriat theihna a pui thin.

Heng test result leh i symptoms te hi a zirin i doctor chuan Acute Chest Syndrome hi mild, moderate, or severe tiin a classified thei a ni .

Acute Chest Syndrome hi eng enkawlna nge ni?

Hetiang dinhmunah hian enkawl tan hma hi harsatna lian tham lo thleng tur venna tha ber a ni . Enkawlna kawng hrang hrangte chu:

• Thisen pek: Hei hian i thisen thenkhat la chhuakin thisen petu hnen atanga thisen emaw, thisen peng hrang hrang emaw pek che a huam a ni.
• IV fluids: Hei hian dehydration (water retention) a veng thei a, chu chuan sickle cell natna a tizual thei a, natna a tizual thei bawk.
• Painkillers: Natna control nan damdawi `ketorolac` emaw `opioids` emaw pek theih a ni.
• An Incentive Spirometer: He hmanraw te tak te hian thawk thûk takin a pui che a ni. I lung a thianghlim a, a thawk tha thei bawk.
• Supplemental oxygen therapy: Thisen a oxygen level a hniam chuan oxygen pek a ni.
• Antibiotics: Hetiang dinhmun hi bacteria infection avanga lo awm a nih chuan antibiotics pek thin a ni.
• Antivirals: A chhan chu Viral infection a nih chuan antiviral damdawi \ha tak tak pek a ni.

Acute Chest Syndrome vei theihna hi a tlahniam thei ang em?

Sickle cell disease (SCD) i neih chuan Acute Chest Syndrome laka inven dan tur i medical team te nen inbiakna neih a pawimawh hle. Anni chuan hetiang hi an rawt mai thei:

• Bottle chhunga puak fo: Thil awlsam tak angin lang mah se, hei hian i thawkna kawng a tifai a, i lung chhehvela tui tul lo tak tak awmkhawm a ti tlem bawk.
• Exercise neih fo: Hei hian i lung chakna a tipung thei a ni.
• Thisen pek fo: Mi thenkhat chuan hei hi an mamawh mai thei.
• Damdawi `Hydroxyurea` emaw `L-glutamine` emaw ei: Heng damdawi te hian natna tihziaawmna leh damdawi ina awm fo theihna a tiziaawm thei a ni. Mahse, hengte hi damdawi lam thurawn hnuaiah chauh lak tur a ni.

Hetiang natna vei tan hian eng ang thlirna (recovery) nge a awm?

`Acute Chest Syndrome` a lo awm chuan enkawl vat a pawimawh hle . Chutianga tih loh chuan harsatna lian tak tak a thlen thei a, chungte chu:

• Acute Respiratory Distress Syndrome (ARDS): Hei hi lung natna khirh tak a ni a, nunna atana hlauhawm tak a ni.
• Rilru dinhmun danglam.
• Kidney hliam a awm.
• Liver a thawk tha lo.
• Multi-organ a hlawhchham.
• Thluak lama harsatna tawk vek.
• Natna nasa tak a ni.
• Vanduaithlak takin thihna pawh a thleng thei.

Statistics atanga a lan dan chuan puitling zingah `Acute Chest Syndrome` vanga thihna hi 4% vel a ni . Naupang zingah chuan he zat hi 1% vel a ni . Hei hian a hmaa enkawl hmasak chuan nunna tam tak chhanchhuah theih a ni tihna a ni.

Tin, `Acute Chest Syndrome` hi hlawhtling taka enkawl leh tihdam ni mahse, `SCD` vei chuan nakin lawkah he natna hi a tawng leh thei tih hre reng ang che

Sickle cell natna ka nei a. Acute Chest Syndrome symptoms ka neih chuan eng nge ka tih ang?

Hei hi a pawimawh ber a ni. SCD i vei a, Acute Chest Syndrome symptoms (i rilru natna, thawk hah, khuh, khawsik) i neih tan chuan minute khat pawh tikhawtlai suh la, doctor lam pan nghal rawh

• Emergency room emaw, damdawi in dang emaw i kal hian doctor-te hnenah sickle cell natna i vei tih hrilh rawh .
• Chest X-ray dil nghal rawh . Hei hian Acute Chest Syndrome i neih leh neih loh a nemnghet nghal thei a, enkawlna pawh a tan nghal thei bawk.

Hetiang hunah hian rang taka thil tih hian i nunna chhanhimna kawngah kawng thui tak a zawh thei tih hre reng ang che.

Take-Home Thuchah a ni

Tunah chuan kan sawi fo thin `Acute Chest Syndrome` hi sickle cell natna avanga harsatna lian tak awm thei a ni tih in hre tawh ang. A lan chhuah dan ber chu rilru na, thawk hah, khuh, leh khawsik te hi a ni . Sickle cell natna i neih chuan heng symptoms te hi i neih chuan doctor rawn la nghal rawh .. I doctor te hnenah sickle cell natna i vei tih hriattir theihnghilh suh. He natna laka invenna tha ber chu a hmaa hriatchhuah leh enkawl vat hi a ni. Hrisel takin awm rawh! Acute Chest Syndrome, Sickle Cell Disease, Chest Pain, Thâwk harsa, Acute Chest Syndrome, Sickle Cell Disease, Lung Infection