Doctor khan i naute lu chu a tlangpui aia lian deuh a ni tih a hrilh che em? A nih loh leh naupai lai scan-ah chuan naute thluaka tui tlem a tam zawk tih a lang em? Nu leh pa tu pawhin hetiang thil an hriat hian hlauhna leh rilru hahna an neih hi thil pangngai tak a ni. Mahse, lungngai suh. Vawiin hian ' hydrocephalus ' tih natna kan sawi dawn a ni. Hemi chungchang hi a awlsam zawngin, mi zawng zawngin an hriatthiam theih tur angin sawi ila.
Hydrocephalus hi eng nge ni?
He hming i hriat hian mi thenkhat chuan thluak tuiin a khat natna niin an ngai thin. A hming ngei pawh hi "tui" leh "lu" tih thumal inzawmkhawm a ni. Mahse a nihna takah chuan hei hi tui a ni lo. Hei hi kan thluak leh ruhro vel a tui pawimawh tak a ni. Damdawi lamah chuan hei hi Cerebrospinal Fluid (CSF) kan ti a.
A awlsam zawngin kan thluak chhunga system hi tuikhuah angin ngaihtuah rawh. Khawthlang lamah chuan he CSF fluid hi siam chhuah reng a ni a, a lehlamah chuan taksain a hip lut a, a paih chhuak zel bawk. Hei hi a siam chhuah rate leh taksain a lakluh rate inkarah hian balance tha tak a awm a ngai a ni.
Hydrocephalus-ah chuan eng emaw chhan vangin he balance hi a buai a, thluak chhungah CSF fluid a awm khawm tan thin. Fluid a pung khawm chuan thluak chhunga pressure a sang chho zel a, naute lu pawh a lian thei hle.
"Congenital" tih thumal hian naute pian tirh atang khan he natna hi a awm tihna a ni .
Engvangin nge naute chungah hetiang hi a thlen? A chhan engte nge ni?
He CSF fluid hi thluak chhungah a awm khawm theih chhan lian tak pathum a awm a, chungte chu:
1. Fluid siam chhuah tam: Thluak chhunga ventricles te hian a tul aia tam CSF fluid an siam chhuak thin.
2. Fluid flow-a blockage: Fluid siam chhuah luang chhuakna kawngpuiah hmun khata blockage awm. Hei hi a chhan tam ber a ni.
3. Taksa chhunga tui lut tlem: Tui luang chhuak chu thisenah a lut leh thei lo.
Congenital hydrocephalus hi genetic factors avanga lo awm thei a ni a, chubakah nu naupai laiin thil engemaw tak a awm thei bawk . A hnuaia table-ah hian a chhan lian ber ber thenkhat han thlir ila.
| Chhan | A awlsam zawngin... |
|---|---|
| Tui kawngkhar (Aqueductal Stenosis) a awm | Thluak ventricle pahnih inkar kawng a tawi emaw, a block emaw. Hei hi infection, tumor emaw, thisen chhuah vang emaw a ni thei. |
| Neural Tube-a chhiatna awm thei | Entirnan, spina bifida ang chi condition, pian tirh atanga spinal cord thenkhat a lang chhuak hian CSF fluid luang chhuak a tikhawlo thei a ni. |
| Arachnoid Cysts te hi a awm a | Hengte hi thluaka awm tumor chi khat a ni a, CSF fluid kalna kawng a tikhawlo thei a ni. |
| Dandy-Walker Syndrome natna a ni | Thluak peng hrang hrang a lo thanglian tha lo tihna a ni. Hei hian thluaka cell pakhat chu tui kalna kawng a tawi emaw, a block emaw avangin a ti lian thei a ni. |
| Chiari Malformations a awm a | Thluak leh ruhro inzawmna (junction) tichhe thei dinhmun. Thluak hnuai lam hian ruhro (spinal cord) a nawr a, chu chuan blockage a siam thei a ni. |
Engtin nge doctor-te hian he natna hi an hriat theih?
Vawi tam tak chu doctor-te chuan naute thluak hmasawnna lama inthlak danglamna, ventricles lian deuh te chu i naupai laiin ultrasound scan dan pangngaiah an hmu thei a ni.
Scan-a chutiang thil a lan chuan doctor chuan chiang zawka chhui chian nan test dang neih belh turin thu a pe thei a ni.
- MRI scan: Hei hian naute thluak than dan chipchiar takin a en theih a ni .
- Amniotic fluid test dan tur chu:Nausen pum chhunga a awm lai hian amniotic fluid sample te tak te la in naute chromosomes test theih a ni.
- Chhungkaw damdawi lam chanchin: I chhungkuaa mi tu emaw chuan neural tube defects ang chi natna an nei tawh em tih pawh doctor tan a pawimawh hle.
Hei hi eng enkawlna nge ni?
He natna hi naute pum chhunga a la awm laiin hriat chhuah ni mah se, naute pian hnuah enkawl tan a ni tlangpui.
I doctor chuan i naute dinhmun uluk takin a enfiah ang a, i naute tana tha ber enkawl dan tur a thlang ang.
Enkawl dan tlangpui pahnih a awm a.
1. Shunt System install dan tur:
Hei hi enkawl dan tlangpui a ni. Hetiang tih danah hian naute thluaka CSF fluid a khawlkhawmna hmun atang, vun hnuaiah, naute pum ang hmunah plastic tube te tak te, flexible tak mai chu surgery hmangin an dah a ni. Chumi hnuah thluaka tui tam tak awmkhawm chu tube kaltlangin a pum chhungah a awm khawm a, chutah chuan taksain him takin a la lut ta a ni.
2. ETV (Endoscopic Third Ventriculostomy) hmanga zai dan: 1.1.
Hei hi enkawl dan dang a ni. Hetah hian fiber-optic technology hmanga camera te tak te hmangin thluak chhungah lutin thluak ventricle pakhatah khur te tak te siamin fluid kalna kawnga blockage awm chu bypass a ni. Chumi hnuah chuan tui chu khur chhungah a luang lut a, taksaah a lut ta a ni.
Enkawl hnuah eng nge thleng?
Hydrocephalus vei nausen piang hmalam hun chu natna thlentu leh thil dang engemaw zatah a innghat a ni.
Shunt system dah a nih hnuah doctor-in a enkawl reng a ngai a ni . Shunt thlak a ngai thei a, naute a lo seilian chhoh zel chuan operation dang pawh tih a ngai thei bawk. Shunt chungchanga harsatna awmte chu:
- Infection awm thei te
- Pipe chu a khar a ni.
- Mechanical a chhiat avangin
- Naute a lo seilian chhoh zel chuan tube chu a tling tawk lo ta a ni.
ETV surgery hmang hian hlauhawmna engemaw zat a awm bawk. Chu khur chu khar nghal mai theihna a awm a, chu chuan nunna a tichhe thei a ni. Tin, natna hrik kai, khawsik, thisen chhuah te pawh a awm thei bawk.
Enkawlna hmang pawhin he natna hian naupang taksa leh rilru lama hmasawnna a nghawng thei a ni. Chuvangin, naupang chuan rehabilitation, special education , etc. a mamawh mai thei a, mahse, damdawi lam enkawlna dik leh nu leh pa hmangaihna leh enkawlna nen chuan naupang tam tak chu nun pangngai, hlim takin an nung thei a, tihkhawtlai tenau tlemte nen. Chuvangin, thinlung takin awm rawh.
Take-Home Thuchah a ni
- Hydrocephalus hi thluaka ‘tui’ khawlkhawm a ni lo va, tui bik cerebrospinal fluid (CSF) an tih khawlkhawmna a ni.
- Hetiang dinhmun hi naupai laiin scan hmangin hriat theih a ni fo.
- Hei hi enkawlna tha tak tak a awm a, chu chu shunt dah emaw ETV surgery emaw a ni.
- Damdawi lam enkawlna leh enkawl chhunzawm zel hi a pawimawh hle a, enkawl hnuah pawh a pawimawh hle.
- Zawhna emaw hlauhthawnna emaw i neih apiang chu i doctor nen sawiho la, zak leh inhnialna awm lovin.
- Damdawi inenkawlna leh enkawl dan mumal tak an neih chuan naupang tam tak chu nun tha tak an hmang thei a ni.











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