I ke, i ke ruh, i kut leh i hmaiah sawifiah theih loh khawpin a hring chhuak em? I zun chu foamy angin a lang tih i hmu tawh em? Hengte hi i taksa peng pawimawh ber pakhat i kal (kidney)-a buaina awm chhinchhiahna a ni thei. Vawiin hian kal (kidney) tichhe thei dinhmun pakhat kan sawi dawn a ni—a sawi tam loh, mahse hriatthiam a pawimawh hle: Glomerulosclerosis.
A awlsam zawngin Glomerulosclerosis hi eng nge ni?
I kal pahnih hian high-efficiency filter angin hna an thawk a. I thisen chu bawlhhlawh paih chhuakin zun-ah an chantir a, an tifai thin. He filtering process hi i kal chhunga thil te tak te, nalh tak tak, glomeruli tih hmangin a thleng thin.
Glomerulosclerosis tih hian heng filtering unit te tak te te hi a hliam emaw, a khauh emaw tihna a ni. Vun hliam hnua scar lo awm ang bawkin, heng filter te hian an chhiat chuan scar tissue an siam a, chu chuan an thawk dik thei lo.
Chumi avang chuan i thisena awm reng tur protein pawimawh tak takte chu filter chhia hmangin a luang chhuak a, i zun chhungah a bo ta a ni . Damdawi lam hawi chuan he natna hi `Proteinuria` ( zun chhunga protein ) tia hriat a ni.
He natna hian kum eng pawh ni se, tu pawh a nghawng thei a, mahse mipaah chuan a tam zawk deuh a ni.
Engin Nge He Condition Hi A Chhan?
A châng chuan Glomerulosclerosis hi a chhan hriat theih a awm lo. Mahse, a hnuaia damdawi lam dinhmun dangte aiin a pahnihna a ni fo.
A awm dan tlangpui chu `FSGS` (Focal Segmental Glomerulosclerosis) a ni. Hei hian chhiatna chu a inang lo tihna a ni a; hmun thenkhat chauh a nghawng (Focal), chu hmun chhungah chuan filter tin segment khat chauh a scarred (Segmental).
FSGS leh general Glomerulosclerosis thlentu thil tlanglawn tak takte chu:
- Diabetes Mellitus: Thisen sugar control loh hi kal hriselna atana hlauhawm tak a ni.
- Obesity : Taksa rihna tam lutuk hian kal (kidney) ah harsatna nasa tak a siam thin.
- HIV Infection : He virus hian kal cells direct-in a tichhe thei a ni.
- Lupus ang chi autoimmune natna: Heng natnate hian i immune system hian i kal (kidney) a rawn bei sual a ni.
- Sickle cell disease: Genetic condition a ni a, kal hnathawh a tichhe thei.
- Reflux nephropathy: Zun chu bladder atanga hnunglam hawia kal lam pan a, chhiatna thlen thei dinhmun a ni.
- Glomerulonephritis: Glomeruli natna (glomeruli) a natna.
- Damdawi leh toxin thenkhat: Kidney tana tha lo thila inhnimhnawihna.
Eng Symptoms Nge Ni?
In the early stages, you may have no obvious symptoms , chuvang chuan hriat loh a ni fo thin. A kal zel chuan a hnuaia mite hi i hmu mai thei:
| Symptom a ni | Hrilhfiahna |
|---|---|
| A hring (Edema) . | Fluid retention hi kal (kidney) a filter tha thei lo vang a ni. I ke, i ke ruh, i kut, i pum, a nih loh leh mit vêlah a hring chhuak tih i hmu thei . |
| Zun a inthlak danglam | Protein a hloh avangin i zun chu foamy emaw bubbly emaw angin a lang thei . |
| Thisen sang lutuk | Kidney chhiatna hian hypertension a thlen fo a, chu chu enkawl harsa tak a ni thei. |
| Cholesterol sang tak a ni | Thisenah protein level a tlahniam chuan liver hian cholesterol tam zawk siamin a compensate thin. |
He natna hi hriselna endikna pangngaiah hmuhchhuah a ni fo a, zun test hmanga proteinuria hmuhchhuah emaw, thisen test-a protein level hniam (hypoproteinemia) emaw hmanga hmuhchhuah a ni.
Engtin Nge A Diagnose?
Heng symptoms te hian dinhmun dang an entawn avangin, diagnosis finfiah dan dik ber chu Kidney Biopsy .
Kidney Biopsy tih hi eng nge ni?
Hlauthawng suh. Instrument te tak te, needle ang chi hmangin i kal atanga tissue sample te tak te tak te chu lakkhawm a ni a, chu chu microscope hmangin enfiahin scarring a awm tih hriat theih a ni.
A châng chuan sample tam tak lak a ngai ṭhin a, a chhan chu scarring hi kidney tissue zawng zawngah a patchy thei a ni.
I doctor chuan hetiang hian a rawt thei bawk ang:
- Glomerular Filtration Rate (GFR) test: I kal (kidney) a filter that dan tehna atan.
- Kidney Ultrasound scan: I kal lian leh te, a pianzia leh a insiam dan enfiah nan.
- Genetic testing: A tlem berah chuan inherited cause a awm leh awm loh hriat nan.
Enkawl Dan Turte Chu Eng Nge Ni?
Vanduaithlak takin tunah hian Glomerulosclerosis hi damdawi a la awm lo va, a tihdanglam theihna tur damdawi chiang tak, khawvel pum huapa pawm a awm lo bawk.
Mahse, hlauthawng suh. Enkawlna hrang hrangte hian natna a zual loh nan a pui thei a, natna lan chhuah dan a enkawl thei a, nunphung tha tak a vawng reng thei bawk. A tum ber chu natna zual zel tur tihkhawtlai leh kal hnathawh venhim a ni.
Enkawlnaah hian a tlangpuiin:
- Thisen sang damdawi: ACE inhibitor leh ARB te hian thisen sang control nan a pui a, zun a protein hloh nasa takin a ti tlem bawk.
- Immunosuppressants: Damdawi steroid ang chi hi immune system hnathawh control nan hman theih a ni.
- Cholesterol tihhniamna damdawi (Statins): Cholesterol level sang zawk enkawl nan.
- Diuretics: Tui leh chi tam lutuk paih chhuah nan, a hring (swelling) a tiziaawm.
- Anticoagulants: Thisen zam venna atana puitu.
- Nunphung thlak danglam: Chi tlem ei leh in, exercise neih fo, leh vitamin supplement \ha tak ei.
A pawimawh ber chu i dinhmun hi zunthlum emaw thau lutuk emaw avanga secondary a nih chuan a hnuaia natna awm enkawl hi a pawimawh ber a ni. Thisen leh zun enfiah reng reng hi a pawimawh hle.
Natna hi kal (kidney failure) thlenga a kal chuan dialysis emaw, kal thlak emaw ang chi enkawlna a ngai mai thei.
Take-Home Thuchah a ni
- Glomerulosclerosis hi kal filter-a hliam awm a ni a, chu chuan hnathawh a tichhe thei a ni.
- Hrisel lohna, zun hring, leh thisen sang te ang chi chhinchhiahna te chu en reng ang che.
- Heng symptoms te hi i hriat chuan doctor rawn vat tur a ni.
- Diagnosis chiang tak hriat theih nan kidney biopsy hi a ngai tlangpui.
- Tunah hian tihdam theih a nih loh laiin, enkawlna kawng \ha tak takte chuan natna hi a tikhawtlai thei a, i hriselna a ti \ha thei bawk. Inrawlh hmasak hi a pawimawh ber a ni.
Glomerulosclerosis, kal natna, kal natna, kal hliam, proteinuria, hring, kal biopsy
