Nu emaw pa emaw chuan naute piang thar an en a, an taksaah inthlak danglamna tenau engemaw zat an hmuh hian engzat nge a ngaihtuah? A châng chuan thil awm lo tak tak pawh hian kan naute hi a nghawng thei a, min ti lungngai hle bawk. Vawiin hian kan sawi dawn a, hriat tur awm lo, mahse hriat a pawimawh em em dinhmun kan sawi dawn a ni. Hei hi (Urogenital Sinus) kan ti a.
Hei hi eng nge ni (Urogenital Sinus)? A awlsam zawngin i hrethiam ang u?
A awlsam zawngin sawi ila, Urogenital Sinus hi hmeichhe zun leh chi thlah danah pianpui chhiatna a ni. Tunah chuan, en teh, a tlangpuiin naute hmeichhia chuan bawlhhlawh chhuahna tur kawng pathum a nei a: pakhat chu rectum a ni a, chutah chuan bawlhhlawh a chhuak a, pakhat chu urethral opening a ni a, chutah chuan zun a chhuak a, a pathumna chu vagina a ni Mahse, naute Urogenital Sinus nei chuan hawnna pahnih a nei a. Pakhat chu rectum a ni a, chutah chuan bawlhhlawh a chhuak a, pakhat chu urethra leh vagina pahnih tan pawha hawnna tlangpui a ni. Chumi awmzia chu zun a chhuak a, hmun khat atang hian vagina nen a inzawm tihna a ni.
Hetiang (Urogenital Sinus) dinhmun hi nausen pian tirh lamah a awm thin. Ngaihtuah teh, nausen stage-a hun rei vak lo chhung chu system pathum – intestinal tract (rectum), genital tract (vagina), leh urinary tract (urinary bladder) te hi cavity leh opening pakhatah an inzawm vek a ni. Hei hi ( Cloaca ) kan ti a. Nausen chu a lo seilian chhoh zel chuan heng system pathumte hi an inthen a, kawngkhar hrang hrang pathum (vagina, urethra , leh anus) an siam a. Mahse, a châng chuan, eng emaw chhan vangin, zun kawng leh reproductive system – a bik takin urethra leh vagina – chu a inthen ṭha lo va, hawnna pakhat chauh a awm chhunzawm zel a ni. Chu hawnna tlangpui chu (Urogenital Sinus) an ti a. Mi thenkhat chuan hei hi (Persistent Urogenital Sinus - PUGS) an ti bawk.
Urogenital Sinus hi eng thilin nge a thlen tlangpui?
A lo thanglian dan pangngaiah chuan he hmun (Urogenital Sinus an tih) hi a hnuah chuan urethra leh vagina hawnna chhehvel vun (vulvar vestibule) a lo ni ang. Urethra hi i taksa atanga zun chhuahna tube a ni. Vagina hawnna vel vun (vulvar vestibule) chu labia chhunga vun, urethra leh vagina hawnna inkar vun a ni.
Taksaah hian Urogenital Sinus hi khawiah nge a awm?
Hei (Urogenital Sinus) hi urethra leh vagina nen a inzawm tlat a ni.
Urogenital Sinus chi hrang hrang a awm em?
Ni e, Urogenital Sinus hi chi hnih a awm a. Hei hi hriatchhuah hi enkawlna ruahmanna atan a pawimawh hle.
1. Low-joined / Low confluence: Hetiang chi ah hian urethra leh vagina te hi taksa pawn lam hawnna hnaih takah, chu chu a hnuai lamah a inzawm tlat a ni. Chuvangin he thu tlanglawn tak hi a tawi hle a ni. Chutiang a nih chuan urethra leh vagina hi a lian leh a awmnaah chuan a pangngai nen a inang hle. Hei hi a nasat loh deuh a ni.
2. High-joined / High confluence: Hetiang a nih chuan urethra leh vagina chu taksa pawn lam hawnna atanga hla takah , chu chu a chung lamah a inzawm a ni. Tichuan he common passage hi a sei hle a ni. Hetiang chi high confluence hi a pawi ber a ni. A chhan chu, hei nen hian harsatna dang a awm thei a ni. Entirnan, taksaah hian a tlangpui aia hmalam zawkah hnute hi a awm thei a.
Hetiang (Urogenital Sinus) natna hi engtiang chiahin nge a tlem?
Urogenital Sinus hi a awm lo hle a ni . A tlangpuiin nau piang thar 10,000 zinga 0.6 vel a nghawng a ni.
Urogenital Sinus natna lan chhuah dan chu engte nge ni?
Urogenital Sinusitis symptoms hi a natna nasat dan azirin a danglam thei. A lan chhuah dan langsar zawk thenkhat chu:
- Feces chhuahna tur outlet pakhat chauh neih leh vagina leh urethra pahnih tan pawha common outlet dang pakhat neih.
- Zun tam lutuk avanga vagina a hring. Hei hi (Hydrocolpos) an ti bawk.
- Vagina hi a pangngai lo takin a khar thei bawk.
- A châng chuan vagina a awm lo thei bawk.
- Uterus, ovaries, fallopian tubes te hi a lo thang tha lo hle.
Urogenital Sinus hi engte nge ni?
Dik tak chuan damdawi lam mithiamte pawhin Urogenital Sinus awm chhan chiang tak chu hriat harsa an ti hle.
A then phei chuan hei hi Congenital Adrenal Hyperplasia (CAH) tih natna nen a inzawm thei bawk. CAH hi genetic diseases group pakhat a ni. CAH i neih chuan i adrenal gland pakhat emaw pahnih emaw hian hormone siamna atana enzyme mamawh an siam chhuak lo. Hei hian sex organs te chu a pangngai lo takin a tipung thei a ni. CAH hian tu pawh a nghawng thei a, mahse hmeichhe naupangte hian sex organ pangngai lo an nei tam zawk.
Virilization an tih hian urogenital sinusitis a thlen thei bawk. Virilization chu mipa naupangin a taksaah mipa sex hormone (androgens) a tam lutuk hi a ni. Androgens hi taksa puitlinna tura puitu a ni a, aw thuk zawk, taksa sam, leh taksa ruh thanna te pawh a nghawng bawk.
Engtin nge Urogenital Sinus natna hi hriat theih?
(Urogenital Sinus) hi natna enkawl dan tur hriat chian nan a pawimawh hle . Hei hian i fate serh chauh ni lovin, an thanlenna leh an thanlenna zawng zawng pawh a nghawng thei a ni.
A châng chuan, naute chu naute pum chhunga a la awm laiin ultrasound hmangin doctor-te chuan he natna (Urogenital Sinus) hi an hmu thei a ni. Mahse, a tam zawkah chuan naute pian hnua taksa enfiahna hmasa ber doctor-te chuan an hmu chhuak thin. Chumi hnuah chuan naute hriselna zawng zawng leh genetic lama harsatna awmte hriat belh tumin thisen test an nei thei a ni.
Doctor chuan a natna hriat chian nan emaw, Urogenital Sinus zau zawng hriat belh nan emaw test dang neih belh turin a ti thei bawk. Chûng zîngah chuan:
- Ultrasound: Hei hian high-frequency sound wave hmangin taksa chhunga taksa peng hrang hrangte video emaw thlalak emaw a la thin. Hei hian i naute kal (kidney), bladder, vagina, leh rectum-ah harsatna a lantir thei a ni. I naute hian a zun (hydrocolpos) a awm leh awm loh pawh a hre thei bawk.
- Retrograde genitogram: Hei hi imaging test chi khat a ni bawk. He test-ah hian doctor chuan urethra/vagina-ah dye bik a inject a, X-ray a la thin. He dye hian tissue leh organ te lian leh te, a pianzia leh a awmna hmun chu chiang takin a hriat theih a ni.
- Magnetic Resonance Imaging (MRI) Test: MRI hian magnet, radio wave leh computer hmangin taksa thlalak chiang tak a la a. Hei hian Urogenital Sinus thlalak chipchiar tak tak a pe thei a ni. MRI hmangin naupang pelvis leh spine-ah harsatna a awm leh awm loh enfiah theih a ni bawk.
- Endoscopy: Endoscopy-ah hian tube (endoscope) te tak te, sei tak, a tawp khatah light leh camera dah a ni. He endoscope hi common urethra/vagina ah dahin a chhunga anatomy en a ni.
Urogenital Sinus hi engtin nge kan enkawl ang?
Urogenital Sinus condition enkawl dan awmchhun chu i naute vagina leh urethra thliar hrang tura operation neih hi a ni. A châng chuan, a bik takin naupang virilized (Congenital Adrenal Hyperplasia (CAH) vang) leh Disordered Sexual Development (DSD) vei nia hriatteah chuan surgery tih chungchangah ngaihdan hrang hrang a awm thei. Chuvangin, operation i neih hmain i fa enkawltu medical team te nen chipchiar takin i sawipui tur a ni. He team-ah hian a tlangpuiin:
- Urinary system leh reproductive system natna hrang hranga specialist doctor ((Urologist)).
- Endocrinologist chu endocrine system nena inzawm natna hrang hranga specialist doctor a ni. I endocrine system hi hormone siamtu leh chhuaktu a ni.
Naute kum khatna chhungin surgery hi tih thin a ni tlangpui . He surgery hi urologist-in a ti thin.
Low-joined (Urogenital Sinus) condition tan chuan (Urologist) chuan (Flap vaginoplasty) tih surgery a ti tam ber ang. Chutah chuan taksa pawn lam hawnna hrang hrang pahnih an siam a – pakhat chu vagina atan, pakhat chu urethra atan.
Joined sang (Urogenital Sinus) natna tan chuan (Urologist) chuan (Pull-through vaginoplasty) tih surgery a ti tlangpui. Hei hi surgery buaithlak deuh a ni. Hetah hian (Urologist) chuan vagina chu common opening atanga a then a, a hranpa a siam a, chu common opening chu a khar ta a ni. Tichuan, common opening awmna hmun atang chuan zun a luang chhuak chhunzawm zel a.
High-joined (Urogenital Sinus) thenkhatah chuan (Urologist) chuan (Flap vaginoplasty) nen (Urogenital mobilization) tih procedure a ti thei bawk. (Urogenital mobilization) chhung hian:
- Rectum chu a inthen a.
- Urethra leh vagina chu an inthen a, an mobilize khawm a, perineum-ah an hruai lut a ni.
- Rectum hi anal sphincter nen a inzawm a ni.
- Tichuan (flap vaginoplasty) an ti leh thin.
Naupang thenkhat chu Clitoroplasty leh/ emaw Labiaplasty tih surgery an neih a ngai thei bawk. Clitoroplasty hian tissue chu a siam danglam a, clitoris pangngai siam a ni. Surgeon hian naupang chu a lo puitlin hunah sex nun hrisel tak a neih theih nan nerve tam thei ang ber humhalh a tum thin. Labiaplasty hian labia, vagina vel hmui awmte chu a siam danglam a ni.
Urogenital Sinus enkawl hnuah naute a dam leh theih nan eng chen nge a mamawh?
I fa chu (Urogenital Sinus) surgery hnuah ni engemaw zat damdawi inah a awm a ngai dawn a ni. Kar khat chhungin a natna chu a reh tan tur a ni a, thla khat chhungin naupang chu a dam kim vek tur a ni. Mahse, i fa (Urogenital Sinus) natna nasat dan azirin i fa doctor chuan hei hi chiang zawkin a hriattir ang che.
Urogenital Sinus hi a veng thei ang em?
I chhungkuaa mi tu emaw chuan Congenital Adrenal Hyperplasia (CAH) tih natna a nei a, naupai emaw, nau pai tum emaw i nih chuan i doctor nen inbiakna neih a pawimawh hle. Urogenital Sinus a awm loh nan hormone hi nau neih hmain pek theih a ni.
Ka fa hian Urogenital Sinus a neih chuan eng nge ka beisei ang?
I fate result chu a urogenital sinus lian leh teah a innghat a ni. Surgery tum ber chu i fa chu a taksa peng hrang hrangte hnathawh dan pangngai leh a lan dan pangngai pek a ni. Naupang surgery nei tam zawk hi an dam hnuah an zun pangngaiin an zun thei a ni.
Naute a lo puitlin chuan a vagina chu a zim (vaginal stenosis) a, a tawi thei bawk. Hei hian vaginal sexual intercourse-ah harsatna a thlen thei a ni.
Naupang Urogenital Sinus condition nei chuan naupai a dal lo. Mahse, surgery chu a zau hle a nih chuan nau neih laiin cesarean section (C-section) neih a tha ber mai thei. I doctor chuan he thu hi i fa nen hun remchang takah a sawipui ang.
Engtin nge ka fa ka enkawl ang?
I fa enkawl dan tha ber ber doctor ten an hrilh ang che. (Urogenital Sinus) nasat dan leh surgery result hian engtin nge i enkawl chhunzawm zel dawn tih a hril ang.
Engtikah nge Doctor ka hmuh ang?
Operation hnuah i fa hian an taksa chu a dam tha em tih leh beisei angin a thawk tha em tih enfiah nan follow-up appointment neih fo a ngai dawn a ni. Heng appointment zawng zawngah hian tel vek ngei ang che.
Natna lan chhuahna thar, zun insum theih lohna ang chi i hmuh chuan i fa naupang enkawltu emaw, zun lam doctor emaw nen inbia ang che.
Ka fa doctor hnenah eng zawhna nge ka zawh ang?
Doctor i zawh theih tur zawhna thenkhat chu hetiang hi a ni:
- Ka fa hian eng ang Urogenital Sinus nge a neih?
- Eng surgery nge i rawt?
- Kum engzat nge operation neih a tha?
- Ka fa hi a na dawn em ni, a hrehawm tawh em?
- Naupang chu a lo puitlin chuan operation tam zawk a mamawh dawn em?
- I fa chu a lo puitlin chuan an urethra emaw vagina emaw-ah harsatna a neih i beisei em?
- Hei hian ka fa thlasik hun chhung a nghawng dawn em?
- Hei hian ka nau pai theihna a nghawng dawn em ni?
- Ka fa hian him takin nau a pai thei dawn em ni?
Pawimawh: Zawhna i neih apiang, eng ang pawhin tlem pawh ni se, i doctor zawh hreh ngai suh. Engkim chiang taka hriat theihna i nei.
Urogenital Disorder hi a tlangpuiin eng nge ni?
Urogenital Disorder chu i zun leh i chi thlah dan tichhe thei natna eng pawh a ni. Entirna dangte chu:
- Tumor tha lo tak tak a awm.
- Hernia a ni.
- Mipat hmeichhiatna hmanga kai theih natna (STIs).
- Cancer chi hrang hrang, bladder cancer, ovarian cancer, emaw uterine cancer te hi a ni.
- Interstitial cystitis/bladder natna natna (IC/BPS) a awm thei.
A tawp berah chuan thil hriat reng tur (Take-Home Message) .
I fain Urogenital Sinus a nei tih i hriat chuan mangang leh hlauhna i neih hi thil pangngai a ni. Mahse hre reng ang che, he natna hi i fa zunthlum leh a hnute inthen nan operation hmanga enkawl theih a ni. Chumi awmzia chu i fa chu hahdam takin a zun theih tur a ni.A lo upat deuh deuh chuan a period pawh a nei tur a ni. Mahse, a chang chuan a lo upat deuh deuh chuan vaginal intercourse-ah hian harsatna engemaw zat a nei thei.
A pawimawh ber chu, heng thilte chauh hi i hmachhawn a ngai lo. I fa doctor nen inbia ang che. I zawhna zawng zawng an chhang thei a, i hlauhthawnna a tiziaawm thei a, i fa enkawlna leh enkawlna tha ber i neih theih nan an pui thei bawk che a ni.
` Urogenital sinus, PUGS, pianpui chhiatna, zun kawng, nau neih dan, surgery, naupang hriselna











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