I vunah emaw, i hriat mi pakhat emaw vunah hmun chu a sen nghal a, a hring a, a hring ang maiin a lang mai thei, mahse hliam avanga lo awm tak tak a ni lo tih i hmu ngai em? A nih loh leh vun chu a sen a, tuar theih loh khawpa natna nen a kang ang maiin a lang em? Heng thilte hi taksa khawi hmunah pawh a thleng thei. Hetiang thil hi i tawng tawh a nih chuan
Wells’ Syndrome tih hming pu, vawiinah hian kan sawi dawn a ni. Ngaihtuah buai suh, he thu hi
chipchiar takin kan sawi dawn a ni .
Wells-a Syndrome hi eng nge ni? A awlsam zawngin...
Wells’ Syndrome hi vun natna hmuh tur awm lo tak a ni.
"Eosinophilic Cellulitis" an ti bawk. Tunah chuan, "Celulatis i tih hian infection a ni tihna a ni lawm ni?" Ni e, cellulitis hi bacteria infection avanga vun sen leh vun hring a ni tlangpui. Mahse, Wells’ Syndrome-ah chuan vun chu a sen, a hring, leh a hmin angin lang mah se,
a takah chuan natna hrik a awm lo . Chu chu a danglam bikna chu a ni. Chuti a nih chuan engvangin nge hetiang hi a lo awm? Kan taksaah hian sipai te tak te ang maia che thin cell chi hrang hrang a awm a. Sipai pawl bik pakhat chu
eosinophils an ti a . Kan taksa venhimtu ang mai an ni. Hmelma, hrik emaw, parasite emaw ang chi taksaah a luh chuan heng eosinophils te hian an kal a, an bei a, min chhanchhuak thin. Allergy a awm chuan an inrawlh bawk. Mahse a chang chuan, heng eosinophil sipaite hi an phur lutuk thin. A nih loh leh, taksaah eosinophils siam chhuah tur aia tam a awm bawk. Tichuan thil thleng chu anmahni taksa peng hrisel tak tak, a bik takin vun te chu an bei tan ta a ni. Mahni inah lung an vawm ang mai a ni. Chutah chuan he harsatna Wells’ Syndrome an tih hi a lo intan ta a ni. Chuvang chuan vun chu a hring a, a sen a, a hring bawk.
Hetiang dinhmun hi engtiang chiahin nge a tlem? Tuin nge dawng duh zawk?
Dik tak chuan hei hi thil
awm lo tak a ni. I ngaihtuah pawh i ngaihtuah thei lo. Tun thlengin khawvel pumah hri kai 100 aia tlem lo an awm tawh a ni. Chu chu mi maktaduai khat zinga pakhat pawhin a tipung ang em tih chu rinhlelh awm a ni tihna a ni. A tam zawkah chuan he natna hi puitlingah hmuh tur a awm. Mahse, a tlem hle a, naupang tê têah pawh a lo awm tawh tih hriat a ni. Hmeichhia leh mipa inthlauhna a awm lo, an pahnih hian inang tlangin an tipung thei a ni. Chuvangin, heng symptoms te hi i nei a nih pawhin hei hi Wells’ Syndrome a ni tih hlau nghal suh, a chhan chu hei hi a tlem hle a ni. Mahse, damdawi lam thurawn lak a pawimawh hle.
Engvangin nge Wells’ Syndrome hi a lo awm? A chhan chu eng nge ni?
Hei hi ngaihtuah tur a ni.
Doctor-te chuan Wells’ Syndrome hi eng nge a thlen tih chiang takin an la hre chiang lo.Thuruk a la ni reng a ni. Mahse, doctor-te chuan hei hi kan taksa hriselna (immune system) a thawh that loh vang a ni thei niin an ngai. Chu chu,
autoimmune disorder a ni thei tihna a ni . A awlsam zawngin kan taksa venghimtu tur immune system hian a taksa hrisel leh tissue hrisel te chu hmelma niin a ngai sual a, a bei tan ta a ni. A tam zawkah chuan he natna hi random takin a lo awm a, chhan chiang tak a awm lo. Mahse, he natna hi chhungkaw hrang hrangah a kal tlem
hle tih hmuhchhuah a ni. Hei bakah hian thil dang thenkhat chu Wells’ Syndrome lo awm tanna tur
trigger angin an thawk thei niin an ring bawk. Chu chu heng thilte hian natna lo awm tanna kawngah nawrna a pe thei tihna a ni. Anni chu:
- Insect seh leh seh (arthropod seh leh seh): A bik takin rannung, rulhut leh rulhut te seh .
- Viral infection : Virus chi hrang hrang taksaa a luh hian.
- Dermatitis : Vun natna dang awm tawh.
- Giardiasis: Hei hi parasitic infection a ni a, intestine-ah a awm a.
- Leukemia: Hei hi thisen cancer chi khat a ni.
- Fungal infection : Fungal infection hi vunah emaw taksa hmun dangah emaw a awm thin.
- Damdawi emaw, metal emaw thenkhat avanga thil tha lo awm thei.
Mahse, hengte hi 100% confirmed cause a la ni lo tih hre reng ang che. Hengte hi tuna rinhlelhna awmte chauh a ni.
Wells’ Syndrome natna lan chhuah dan chu engte nge ni?
Okay, tunah chuan he natna hi a lo awm chuan eng symptom nge a rawn chhuah tih hi han en ila. A tlangpuiin vun hmun khat emaw a aia tam emaw
a itchy sensation emaw
burning sensation emaw atanga tan a ni. Tichuan, ni engemaw zat chhungin chu hmun chu
a sen a, a hring tan ta a ni . Heng hmun hring te hi khawih a
na thei hle . Mi thenkhat tan chuan hliam ang maiin a lang a, mi pakhatin a vuak ang maiin a lang. A châng chuan, a chhinchhiahna hmasa ber chu vun hnuaia lo lang thar
, tuiin a khat blisters emaw
nodules emaw a ni. Mi dangte tan chuan
ring ang maia lang thei patch angin an lang thei bawk.A lo thleng thei a ni. A dang pawhin taksa pum puiah
itchy welts a lo lang thei a, eczema ang mai a ni.
Ngaihtuah teh, ni khat chu kan u Sunil-a chuan a keah chuan tuar theih loh khawpin a na nghal a. Eng emawin a seh niin a ngai a. Ni hnih emaw ni thum emaw hnuah chuan a hmun chu a hring nasa hle a, a na hle bawk. Miin thil a tihlum ang mai a ni. Doctor hnena a entir chuan a kang hle a, doctor chuan hei hi natna danglam tak a nih thu a hrilh a, Wells’ Syndrome pawh a ni mai thei.
Internal symptom dang,
asthma- ang chi thawk harsatna,
ruh natna , emaw
khawsik te hi he natna nen hian a tlem hle. Mahse, thil theih loh a ni lo va, chutiang symptoms chu an report tlem hle. Hun a kal zel a, he natna vei vun pawh hi a rawng a danglam tan bawk. A tir lama sen rawng chu zawi zawiin
brown-red rawng-ah a chang ta a ni. Tichuan
, blue-gray color-ah a inthlak thei a, a tawpah chuan
greenish-gray color-ah a inthlak thei bawk. Bruise a dam chuan a rawng a thlak ang bawkin. Thu lawmawm tak chu heng spot leh swellings te hi kar tlemte atanga thla engemaw zat chhungin
nghawng nghet nei lovin an dam tlangpui. Mahse, a chang chuan a lo let leh thei.
Engtin nge he natna hi dik taka hriat theih a nih?
Hetiang symptoms i neih hian eng nge a nih chiang taka hriat a pawimawh. Wells’ Syndrome hmuhchhuah dan ber chu
vun biopsy tih hi a ni . Hei hian a natna hmun atanga vun te tak te tak te chu anesthesia hmanga lak a, microscope hmanga enfiah tihna a ni. Chu bakah,
thisen chhiar kim chuan a hmaa kan sawi tawh ang khan thisenah hian thisen var chi eosinophils an tih chu a tlangpui aia tam a awm tih a lang thei bawk. Skin biopsy an enfiah hian doctor-te chuan vun leh vun hnuaia tissue-ah eosinophils a tam em tih an hmu thei a ni. Wells’ Syndrome-a awm danglam bik inflammation pattern thenkhat an zawng bawk. Heng test te hian a natna lan chhuah dan hi thil dang – allergy tlanglawn, parasite infestation, vun natna dang (dermatitis), insect seh, emaw, Churg-Strauss syndrome ang chi natna hmuh tur awm lo emaw avanga lo awm a nih loh thu a nemnghet thei a ni.
Hei hi engtin nge enkawl theih ang? Dam theih a ni em?
Ni e, hei hi enkawlna tur a awm. Damdawi pakhat hlawhtling taka control theih fo chu
Prednisone tih damdawi hi a ni . Hei hi
systemic steroid a ni.A type pakhat. "Systemic" tih awmzia chu pill angin emaw, injection angin emaw pek a ni a, taksa system pumpui a nghawng tihna a ni. Heng steroid damdawi te hian kan immune system (immunosuppressant effect) overactivity tihziaawmna hmangin hna an thawk a ni. Chu chu immune system chu a taksa ngei a beih loh nan an control tihna a ni. A awlsam zawngin kan taksa hian steroid hormone cortisol an nei a, chu chu a pianphungah chuan kal chunga adrenal glands te hian an siam chhuak a, prednisone hi a synthetic version a ni. Hei hi pill anga i ei tan chuan ni engemaw zat chhungin i natna lan chhuah dan a tlahniam ang a, i rilru a hahdam tan ang. Chumi hnuah chuan i doctor chuan thla khat vel chhungin damdawi dose chu a tihhniam zauh zauh ang. Enkawlna dangte chu a châng chuan:
- Antifungals: Entirnan, griseofulvin.
- Antibiotics : Entirnan, dapsone.
Hengte hi doctor-in a pe thei bawk. A châng chuan, a natna lan chhuahna a na lutuk lo a nih chuan, chu chu
a nasat loh chuan , vun natna hmunah
steroid cream (e.g. hydrocortisone) hnawih mai maiin a tidam thei a ni.
He natna hi a lo awm loh nan kawng a awm em?
Hei hi a lungchhiatthlak deuh a ni.
Wells’ Syndrome thlen chhan dik tak hi hmuhchhuah a la nih loh avangin a lo awm loh dan tur chiang tak sawi theih a la ni lo. Nakin lawkah a chhan hmuhchhuah a nih chuan a ven dan tur pawh kan hre mai thei.
Wells’ Syndrome vei tan chuan eng prognosis nge a awm? (Prognosis) tih a ni.
Hei hi
chanchin lawmawm tak a ni! Wells’ Syndrome vei tan chuan prognosis a tha hle. Hei hian a awmzia chu he natna avanga vun natna leh vun natna te hi kar tlemte atanga thla engemaw zat chhungin a reh vek tlangpui tihna a ni.
A tam zawkah chuan hliam nghet tak a awm lo. A châng chuan, a dinhmun a reh hnuah, vun rawng a danglam deuh thei bawk. Chumi awmzia chu vun chu a tlangpui aia a dum deuh emaw, a dum deuh emaw a ni thei tihna a ni. Mahse, he rawng danglam hi hun kal zelah a bo zauh zauh ang. Mahse, hriat reng tur pakhat chu he dinhmun hi
a lo awm leh thei tih hi a ni . Chutiang thil lo thleng leh ṭhinah chuan enkawlna chu a thunun vek theih nân kum tam tak a ngai thei a ni. Mahse, damdawi lam enkawlna mumal tak nen chuan uluk taka enkawl theih a ni.
A tawp berah chuan thil hriat reng tur (Take-Home Message) .
Okay, chuti a nih chuan tunah chuan Wells-a Syndrome chungchang hi i hrethiam tawh a, kan sawi tawh ang khan. Thil pawimawh tak tak hriat reng tur thenkhat chu hetiang hi a ni:
- Wells’ Syndrome hi vun natna hmuh tur awm lo tak a ni.
- Hei hi vun natna a ni lo va , a lan chhuah dan chu natna hrik ang maiin a lang thei.
- A chhan dik tak hriat ni lo mah se, immune system lama harsatna a awm nia rinhlelh a ni .
- A lan chhuah dan ber chu vun natna , kang, sen , leh vun hring .
- Natna hi vun biopsy hmanga finfiah a ni .
- Steroid ang chi damdawi hmangin hlawhtling takin enkawl theih a ni .
- The prognosis of the disease is very good , leh hliam awm lovin a dam thei bawk.
- Mahse, natna chu a lo lang leh thei a ni .
Nangmah emaw i hriat emaw chuan heng symptoms te hi i neih chuan doctor thiam tak pan nghal rawh . Mahni indahdam suh. Doctor chuan diagnosis dik tak a siam thei a, enkawlna dik ber a pe thei che a ni.
Hlauh tur a awm lo. A pawimawh ber chu heng dinhmunte hi fimkhur hi a ni. Hrisel takin awm rawh!
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