I hmangaih tak pakhat chu damdawi inah routine surgery nei turin admit a ni ang tih han ngaihtuah teh. Engkim a kal tha vek kan beisei. Mahse, anesthesia an pek hnuah chuan taksa lumna chu hlauhawm takin a sang nghal a, taksa ruhte a tikhauh a, heart rate pawh a mumal lo hle. Hei hi tunlaia kan sawi tum chu a ni a, thil awm lo mahse hlauhawm tak, nunna atana hlauhawm tak, ' malignant hyperthermia ' an tih hi a ni. Hei hi hriat chian a pawimawh hle.
A awlsam zawngin, Malignant Hyperthermia hi eng nge ni?
A hmasain ‘Hyperthermia’ tih hi eng nge a nih i hrethiam ang u. Hyperthermia chu kan taksa lum lutuk a, kan thunun theih loh vang a ni. A tlangpuiin kan taksa lumna chu 37 degree Celsius (98.6 Fahrenheit) vel a ni a, chu chu thawk hah ang chi thil hmangin a ni . Mahse hyperthermia-ah chuan he control hi a bo a, temperature chu 40 degree Celsius (104 Fahrenheit) aia sangin a sang chho ta a ni. Hei hi khawsik pangngai a ni lo va, a hlauhawm zawk hle.
Hyperthermia hi pawn lam thil, environment temperature sang leh dehydration ( taksaa tui tlakchhamna ) vang a ni tlangpui.
Mahse Malignant Hyperthermia (MH) hi thil danglam tak a ni. Anesthetics chi hrang hrang taksain a chhan dan dik lo a nih chuan a thleng thin . Heng anesthetics te hi surgery natna nei lo tura siam nan a pawimawh hle. Mahse mi thenkhatah chuan heng damdawi te hi taksaa genetic defect nen an inzawm khawm a, he dinhmun hlauhawm tak hi a thlen thin.
Eng thilin nge malignant hyperthermia hi a thlen?
Hetiang dinhmun hi anesthetic damdawi chi hrang hrang avanga lo awm a ni ber. A châng chuan exercise tam lutuk emaw, boruak lum lutuk vang emaw pawh a ni thei. ‘Awake Hyperthermia’ tih a ni.
A pawimawh ber chu, tun hmain mi tu emaw chuan harsatna nei lovin heng damdawi te hi lo ei tawh mahse, a dawt leh hunah pawh he natna hi a la tawng thei tho a ni . Chuvang chuan a hlauhawmna hriat chian a pawimawh hle .
Hetiang dinhmun thlentu ber chu engte nge ni tih hi han en ila.
| Trigger Type a ni | Entirna leh sawifiahna |
|---|---|
| Inhaled Anesthetics hmanga tihdam theih a ni | Surgery neih laiin damlo mut tir nana gas chi hrang hrang hman thin. Entirnan: Desflurane, Sevoflurane, Isoflurane, Halothane, Enflurane te hi a tha ber pawl a ni. |
| Muscle Relaxants a ni | A bik takin, damdawi Succinylcholine chu hei hi a thlentu ber nia hriat a ni. Surgery neih laiin taksa ruhte tih hahdam nan hman a ni. |
| Trigger dangte pawh | A tlem hle a, he dinhmun hi exercise nasa lutuk emaw, khaw lum lutuk avanga lo awm emaw pawh a ni thei. |
Hetiang natna lan chhuah dan hi engte nge ni?
Heng symptoms te hi anesthesia pek lai emaw, pek hnu lawkah emaw a lang fo thin a, chuvangin operation room-a doctor leh staff te chuan hei hi an ngaihven hle a ni.
A pawimawh ber chu mi pakhat chu Malignant Hyperthermia vei hlauhawm tak pawh ni se, a dam chhungin symptoms nei lovin a awm thei a ni. Symptoms hi triggering drug ei a nih chauhvin a lang thin.
| Symptom a ni | Eng thil nge thleng? |
|---|---|
| Muscle a nghet lo va, a khur bawk | Taksa chhunga jaw leh taksa ruh dangte chu lung atanga siam ang maiin a nghet nghal vek a. |
| Thinlung thawk chak leh mumal lo | Heart rate a sang lutuk a, rhythm pawh a mumal lo. |
| Carbon dioxide (CO2) level sang chho zel | Exhaled air-a CO2 awm zat hi a pung chak hle. Hei hi doctor-te’n chhinchhiahna an hmuh hmasak ber zinga mi a ni. |
| Taksa lumna sang lutuk | Hei hi natna dang hnua lo awm chhinchhiahna a ni fo. Temperature chu hlauhawm takah a kai chho ta a ni. |
| Thisen a acidity tihpun (Metabolic Acidosis) . | Taksa chhunga metabolic disorder vangin thisen chu acidic a lo ni ta a ni. |
| Thil dang pawh a awm | Thawmhnaw tam lutuk, vunah hmun sen, thawk harsa leh thawk harsatna te pawh a awm thei bawk. |
Malignant hyperthermia awm chhan bulpui ber chu eng nge ni?
Hei hi a chhan ber chu genetic defect vang a ni . A awlsam zawngin kan taksaah hian taksa peng hrang hrang (muscle function) control tu genes-ah hian chhiatna a awm a. He chhiatna hi pian tirh atanga rochun theih a ni a, a hnu lamah pawh a thawk chhuak thei bawk.
Scientist-te chuan he natna thlentu genetic defect 80 chuang an hmuchhuak tawh a ni. Chhuan khat atanga thlah danga kal zel theih dinhmun a ni . Chumi awmzia chu i nu, i pa, i unaupa emaw, i unaunu emaw hian he natna hi i neih chuan nang pawhin i vei a rinawm zawk tihna a ni. Tin, hmeichhia aiin mipa hian he natna hi an vei tam zawk deuh bawk.
He hlauhawmna hi a awm leh awm loh hriat lawk theih a ni em?
Ni e, he hlauhawmna hi a awm leh awm loh finfiah nan medical test pahnih a awm.
1. Genetic Blood Test: I thisen sample lak theih a ni a, a chhunga gene awmte chu he thil nena inzawm genetic defect lian tham a awm leh awm loh enfiah theih a ni. Mahse, heng test te hi 100% a dik lo. Hei hi a chhan chu he natna hi genetic defects la hmuhchhuah loh vang pawh a ni thei a ni.
2. 2. A rilru a hah lutuk chuan a rilru a buai em em a.Muscle Biopsy: Hei hi test dik ber a ni. He test-ah hian doctor chuan i ke atanga taksa ruh te tak te tak te chu a la a, lab-ah a test a, MH thlentu damdawi te chu engtin nge a chhan tih a enfiah thin. He test hi mi zawng zawng tan tih a ni lo. Doctor-te chuan he test hi i chhungkuaa mi tu emaw chuan he natna hi an neih emaw, rinhlelh awm tak tak i neih emaw chauhvin an rawt thin.
He natna hi a lo awm nghal a nih chuan engtin nge kan enkawl ang?
Malignant Hyperthermia hi damdawi lam thil pawimawh tak a ni. Enkawl vat a ngai tihna a ni. Operating room-ah hetiang thil hi a thleng a nih chuan medical team-in hma an la nghal ang.
- A hmasa ber chu a natna thlentu anesthetic pek kha tihtawp nghal a ni .
- A dawtah chuan damdawi bik ` Dantrolene` tih chu thisenah an inject leh a. Hei hi MH enkawlna dik tak awmchhun a ni.
- Damlo chu taksa lumna tihhniam nan `cooling blanket` -ah an khuh a. Ice pack hi armpit leh groin ang chi hmunah pawh dah a ni bawk.
- Taksa tihlum nan cold saline (cold IV fluids) pek thin a ni.
- Damlo hi an dinhmun uluk taka enfiah turin Intensive Care Unit (ICU) emaw Emergency Treatment Unit (ETU)-ah dah a ni.
He hlauhawmna laka inven nan eng nge kan tih ang?
Hei hi a thlentu genetic defect hi damdawi a la awm lo a, chuvangin a tha ber chu a hlauhawmna enkawl leh emergency lo thleng tur ven hi a ni.
Nangmah emaw, i chhungte zinga mi emaw chu Malignant Hyperthermia vei nia hriat a nih chuan, emaw, rinhlelhna a awm a nih chuan, eng operation pawh i tih hmain anesthesiologist leh surgeon hnenah i hriattir hmasa tur a ni.
Hei hi hriat reng tur pawimawh ber a ni. Min hriattir hunah doctor-te chuan MH thlen lo tur anesthetics him chauh hman an tum ang. Chuvang chuan chhungkaw medical history hriat chian a pawimawh hle.
Take-Home Thuchah a ni
- Malignant Hyperthermia (MH) hi anesthetic damdawi thenkhat avanga natna hlauhawm tak, nunna atana hlauhawm thei a ni.
- Hei hi a chhan ber chu thlah kal zelah genetic defect a ni.
- I chhungkuaa mi tu emaw hian he natna hi a neih chuan nang pawhin i hlauhawm thei bawk.
- Eng surgery pawh tih hmain doctor hnenah i chhungkaw history-a MH chungchang hriattir hmasak a pawimawh hle. Hei hian i nunna a chhanhim thei a ni.
- He hlauhawmna hi hriat chian hi emergency laka invenna tha ber a ni.











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