I mōhio koe i ētahi wā ka tīmata ētahi momo pūtau i roto i ō tātou tinana ki te whanonga rerekē? Ko tētahi o aua mate onge ko te Histiocytosis. Tērā pea he ahua whakamataku tēnei ki a koe, engari kaua e manukanuka. Me kōrero noa iho, me te whai tikanga hoki.
He aha te Histiocytosis? I ngā kupu māmā noa iho...
Kei roto i tō tinana tētahi momo toto mā e kiia nei ko ngā histiocytes. I roto i aua toto mā, kei reira tētahi momo pūtau motuhake e kiia nei ko ngā histiocytes . He rite ēnei ki ngā kaitiaki haumaru o tō tātou tinana. Ko rātou te hunga e whawhai ana ki ngā iroriki e puta ai te mate e kiia nei ko ngā pathogens - ngā huaketo , ngā huakita , me ngā harore - ā, e āwhina ana ki te pupuri i te hauora o tō tātou pūnaha ārai mate .
Heoi, i ētahi wā ka tīmata te tipu rerekē o ēnei pūtau histiocyte, arā, ka huri hei " whakarerekētanga " . Kātahi ka nui rawa te tipu o ēnei pūtau histiocyte rerekē, ka kohia ki ngā wāhanga rerekē o tō tātou tinana. Ina kohia nui rawa, ka raru pea tō tātou pūnaha ārai mate. Ko te mea nui ko te mumura , arā, he āhua pupuhi, ka puta i roto i ngā kiko o te tinana. Ka taea e tēnei mumura te kino i ō tātou whekau i ētahi wā.
Ka taea e ēnei pūtau histiocyte rerekē te hanga i roto i ō pona lymph (e kiia ana ko ngā pona lymph), te kiri, ngā wheua, ngā pukahukahu, te ate, te whēkau, tetahi atu wāhi rānei o tō tinana. I ētahi wā ka pā ki te wāhanga kotahi o tō tinana. Ka kiia tēnei he āhuatanga 'pūnaha kotahi' . I ētahi wā ka pā ki ngā wāhanga maha o tō tinana. Ka kiia tēnei he āhuatanga 'pūnaha maha' .
Ko te mea nui, ehara te histiocytosis i te mate pukupuku . Heoi, i ētahi wā ka rite te whanonga ki te mate pukupuku, ā, ka whakaatu i ngā tohu e rite ana ki te mate pukupuku. Koia te take he mate e hiahia ana kia aro nui atu. Nā te mea he rerekē ngā tohu o tēnei i ia tangata, i ia tangata, ā, he rerekē hoki te kaha o te mate, he uaua pea i ētahi wā te tere o te tautuhi i te histiocytosis.
He aha ngā momo matua o te histiocytosis?
Kua mārama pea koe ki te tikanga o te histiocytosis. Neke atu i te 100 ngā momo. Engari e toru ngā momo matua e kitea ana, e kōrerohia ana hoki e tātou. Me titiro tātou ki a rātou.
1. Te histiocytosis pūtau Langerhans (LCH):
- Koinei te momo histiocytosis tino noa .
- Ko ngā tamariki nohinohi te nuinga o te wā ka pāngia e tēnei āhuatanga. E 5 ki te 9 o ia miriona tamariki ka pāngia.
- I te nuinga o te wā, kāore tēnei i te tino kino, ā, he rite tonu ki te "kore tohu" . Heoi, he mea nui kia mahara i ētahi wā, ka kino pea tēnei, ā, ka mōrearea pea te ora.
2. Te mate Erdheim-Chester (ECD):
- Ka pāngia ngā pakeke e tēnei momo.
- He āhuatanga tino onge anō hoki tēnei.
- Pērā i te LCH, ka rerekē te ECD mai i te ngawari ki te kino, ā, ka morearea hoki ki te ora.
3. Te mate Rosai-Dorfman (RDD):
- Pērā i te LCH, ko te nuinga o te wā ka pā te RDD ki ngā tamariki , engari ka pā anō hoki ki ngā pakeke.
- He tino onge hoki tēnei. Tata ki te kotahi i roto i te rua rau mano tāngata kua kitea kua pāngia e tēnei mate.
- Ko te momo matua o tēnei ko te 'classical RDD' . Koinei te wā ka pupuhi ai ō pona lymph (pupuhi).
- Ko tētahi atu momo ko te 'extranodal RDD' . I roto i tēnei, ka pāngia ngā whekau ehara i te pūnga lymph. Ko te tikanga ka taea e ngā pūtau histiocyte nui te kohikohi ki roto i te kiri, i ngā wheua, i ētahi atu wāhi rānei.
E pēhea te onge o te ingoa o tēnei mate ko te Histiocytosis?
Āe, e ai ki taku kōrero i mua, he tino onge te mate histiocytosis. Inaa, ko ngā momo matepukupuku kaha ake, e pāngia ana e te matepukupuku, he iti iho i te 1% o ngā matepukupuku katoa e kitea ana i roto i ngā kiko ngohengohe me ngā kōpū lymph. Nō reira, ka taea e koe te whakaaro he aha te onge o tēnei.
He aha ngā tohu o te Histiocytosis?
Nā, kia tirohia tātou he aha ngā tohu e whakaatuhia ana i roto i tēnei āhuatanga histiocytosis. Ka rerekē pea ēnei tohu i ia tangata, i ia tangata . Ko te take o tēnei, nā te mea ko ngā okana me ngā kiko e kohia ai ngā pūtau histiocyte nui rawa, e ai ki taku kōrero, me te nui o te kino ki aua kiko, ka pā ki tēnei.
Anei ētahi o ngā tohu ka kitea pea e koe (ā, tera pea he maha atu anō):
- Ngā ponana kiri : Ka kitea ēnei i ngā wāhi huruhuru o te mahunga o ngā pēpi (e kiia ana e mātou ko te 'cradle cap' ) i te wāhi nāpi rānei.
- Kirika .
- Ngenge, ngenge .
- Te mamae o te upoko.
- Te maremare, te poto rānei o te manawa .
- Te whakahekenga taumaha kāore i te whakamāramatia .
- Te mamae o te wheua .
- Ngā kōpū waikura pupuhi (koinei te tikanga o te pupuhi).
- Ngā panonitanga o te tirohanga, ngā kanohi pupuhi rānei .
- Te mimi pinepine me te matewai nui .
- Ngā puku kiri (tērā pea ka puta ki ngā kamo).
- Te uaua ki te arotahi, te maumahara rānei ki ngā mea .
- Ngā raruraru ki te taurite me te taunga .
He pēhea te puta o ngā tohu? Kei te wāhi e kohia ai ngā histiocytes!
Ka whakawhirinaki ēnei tohu ki te wāhi o te tinana e kohia ai ngā pūtau histiocyte. Ka rerekē ngā wāhi matua e kohia ai i runga i te momo histiocytosis.
Ngā wāhi ka pāngia e te Langerhans cell histiocytosis (LCH):
- Wheua
- Kiri
- Ngā pūngāwerewere lymph (pupuhi)
- Ate
- te whēkau
- Waha
- Ngā pūkahukahu
- Te pūnaha io matua (arā, te roro me te taurakira)
Ngā wāhi ka pāngia e te mate Erdheim-Chester (ECD):
- Ngā wheua roa (ina koa i ngā waewae)
- Ngā kanohi
- Pūnaha io matua
- Ngā pūkahukahu
- Ngākau
- Ngā uaua toto
- Ngā whatukuhu
- Ngā whekau kei muri o te puku (e kiia ana ko te 'retroperitoneum' )
Ngā wāhi ka pāngia e te mate Rosai-Dorfman (RDD):
- Ngā pona lymph (ina koa i te kaki, engari ka taea hoki te puta ki hea atu)
- Kiri
- kiko ngohengohe
- Ara manawa o runga
- Wheua
- Retroperitoneum (ngā whekau kei muri o te puku)
- Ngā kanohi
He aha te take o te histiocytosis?
Kāore anō kia tino mōhiotia e ngā kaipūtaiao he aha te take o te histiocytosis, engari kua kitea e rātou he hononga pea ki ngā whakarerekētanga ira .
He kupu ngāwari noa iho, he rauemi ira kei roto i ia pūtau o tō tātou tinana, he huinga tohutohu rānei. Mā ēnei tohutohu ka whakatau te whanonga o aua pūtau. Nō reira, ina puta he panoni i roto i ēnei tohutohu, e kiia nei ko ngā whakarerekētanga ira , ka tīmata ngā pūtau ki te whanonga rerekē. Hei tauira, ka taea e te whakarerekētanga ira te mea ka tāruatia e te pūtau pērā i te histiocyte ia ia anō, ka tīmata te horapa me te kore e taea te whakahaere.
Nā te tautuhi i ēnei whakarerekētanga ira kua taea e ngā kairangahau te whakawhanake i ngā maimoatanga hou mō te histiocytosis. Ka mahi ēnei maimoatanga mā te aukati i ngā huringa pūtau kino e āhei ai ngā pūtau histiocyte ki te tipu haere i waho o te mana whakahaere.
Me pēhea te tautuhi i te histiocytosis?
Ki te whakapae koe he histiocytosis tōu, ka tirotirohia e tō tākuta tō tinana , ā, ka pātai atu mō tō hītori hauora. Kātahi ka whakatauhia e rātou ngā whakamātautau hei mahi i runga i ō tohu me ngā okana e whakaarohia ana kua pāngia e te nui rawa o ngā histiocytes.
Anei ētahi whakamātautau ka taea e koe:
- Ngā tukanga whakaahua :
- Tērā pea ka tonoa e tō tākuta tētahi matawai motuhake e kiia nei ko te matawai FDG PET/CT . Ka taea e tēnei te kite i ngā mea pēnei i ngā pukupuku puta noa i te tinana.
- Hei tāpiritanga , tera pea e hiahiatia ngā whakamātautau pēnei i te matawai CT, te matawai MRI, te matawai wheua, te matawai ultrasound, te hihi-X, te echocardiogram rānei (he matawai o te ngākau).
- Ngā whakamātautau taiwhanga :
- Ka whakamātautauhia e tō tākuta ngā tauira wai, pērā i tō toto, i tō mimi rānei, kia kitea ai mēnā he tohu o te histiocytosis.
- Ka tirohia te maha o ō pūtau toto. Ka rapua hoki e rātou ngā homoni, ngā pūmua rānei e tohu ana i te mahi a ō whekau. Mena kāore te whekau e mahi tika ana, tera pea he tohu he nui rawa ngā histiocytes i roto i taua whekau.
- Whakamātautau koiora `(Biopsy)` :
- Ko te mahi a tēnei, ka tangohia e te tākuta tētahi tauira kiko ka tirohia i raro i te karuārai hei tirotiro mēnā he histiocytosis tōu.
- Ka rapua hoki ngā whakarerekētanga ira motuhake e pā ana ki te histiocytosis.
- I ētahi wā, ki te kore e taea te whakamahi i te koiora, ka taea te whakamātautau i ngā rauemi ira i roto i tō toto. Ka kiia tēnei he 'koiora wai' .
He aha ngā maimoatanga mō te Histiocytosis?
He maha ngā āhuatanga e whakawhirinaki ana ki te maimoatanga o te histiocytosis. Ina koa:
- Te kaha o ō tohumate .
- Ahakoa kotahi, he maha rānei ō whara (he wāhi kiko rerekē ēnei).
- Kei hea ēnei 'whara' o te tinana ?
- Ahakoa he mate pukupuku ēnei puku, kāore rānei .
Ka whakatau ngā tākuta i te maimoatanga i runga i ēnei āhuatanga. Anei ētahi kōwhiringa maimoatanga:
- Mātakitaki, tatari : Ki te kore tō histiocytosis e kino rawa, ā, kāore he tohu nui e pā mai ana ki a koe, ka kī atu pea tō tākuta kia mātakitaki koe i tō āhua.
- PokangaMena kua kohia ngā pūtau histiocyte ki te wāhanga kotahi anake o te tinana, ka taea te mahi pokanga hei tango i taua wāhanga.
- Te rongoā irahiko : Ko te whakamahi i tētahi mīhini hei tuku i ngā hihi irahiko kaha-nui ki ngā whara. Ka patua e ēnei hihi ngā pūtau rerekē, ka whakaroa hoki i te tipu o ngā pukupuku. I ētahi wā ka āwhina anō hoki te rongoā irahiko ki te whakaiti i ngā tohu.
- Te rongoā matū (e kiia ana ko te 'chemo') : Ko te tuku matū ki roto i tō toto hei whakangaro i ngā pūtau histiocyte nui kua horapa puta noa i tō tinana. Ka tūtohu noa ngā tākuta i te 'chemo' mēnā kua horapa ngā pūtau histiocyte puta noa i tō tinana.
- Corticosteroids : Kei roto i tēnei kāwai ngā rongoā pēnei i te prednisone . Ka taea e ēnei te whakaiti i te mumura (pupuhi) e haere tahi ana me te histiocytosis. Ka taea te hoatu ko ēnei rongoā anake, te hoatu tahi rānei me ētahi atu maimoatanga, pēnei i te chemotherapy.
- Te Whakaora Ārai Mate : Ka mahi tēnei mā te whakapakari i tō ake pūnaha ārai mate, ka āwhina i a ia ki te kite me te whakangaro i ngā pūtau kino, pērā i ngā histiocytes rerekē.
- Te rongoā arotahi : He maimoatanga motuhake tēnei. Ka whakamahia tēnei maimoatanga mō ngā āhuatanga histiocytosis e pā ana ki ētahi whakarerekētanga ira.
Ka taea te whakaora katoa i te histiocytosis?
He uaua ki te kī 'āe', 'kāo' rānei ki tēnei, nā te mea kei te āhua o te mate. He maha ngā tāngata e pāngia ana e te histiocytosis ka uru ki te mea e kiia nei ko te 'whakakorenga roa'. Arā, ka ngaro atu rātou me te kore he tohu, he tohu rānei o te mate.
Ko ētahi momo histiocytosis, inā koa kei te kotahi noa te wāhi o te tinana e noho ana ngā histiocytes, ka taea te whakaora katoa mā te pokanga . Ka tirohia koe e tō tākuta kia tirohia mēnā ka hoki mai anō.
Heoi, ki te kore e taea te rongoā katoa te momo histiocytosis kei a koe, ka tūtohu tō tākuta i tētahi mahere maimoatanga hei āwhina i a koe ki te whakahaere i te mate.
He aha te matapae mō tēnei āhuatanga?
He maha ngā āhuatanga e whakawhirinaki ana ki te matapae o tō āhua. Mō ētahi tāngata, ka pai ake te histiocytosis i a ia anō me te kore he maimoatanga . Hei tauira, tata ki te 40% o te hunga whai RDD ka pai ake me te kore he maimoatanga. Waihoki, ina pāngia te LCH e te kotahi wāhanga o te tinana (e kiia ana ko te 'LCH ā-rohe') , he maha ngā wā ka pai ake i a ia anō.
Engari, i ētahi atu wā, me nui te maimoatanga me te mātakitaki tupato i te histiocytosis, i roto i ngā tamariki me ngā pakeke.I ngā wā tino kino, ka taea e te histiocytosis te whakakino i ngā okana, ā , ka mōrearea hoki te ora .
Nō reira, he mea pai ki te pātai ki tō tākuta mō te matapae e pā ana ki tō mate.
Ka taea te ārai i te histiocytosis? Me pēhea te whakaiti i te mōrearea?
He pono, kāore he huarahi hei ārai i te histiocytosis, engari ka taea e te maimoatanga te āwhina i a koe ki te whakahaere i ō tohu.
Engari kotahi te mea. Mā te whakamutu i te kai paipa ka taea te whakaiti i tō tupono ki te whakawhanake i te LCH (Langerhans cell histiocytosis), he mate pukupuku pūkahukahu. Mā te whakamutu i te kai paipa, te noho kore kai paipa rānei, ka taea hoki te whakapai ake i tō urupare ki te maimoatanga. Mena kei te hiahia āwhina koe ki te whakamutu i te kai paipa, pātai atu ki tō tākuta mō ngā kaupapa tuku atu ki a koe kia mutu te kai paipa.
He aha ngā pātai me pātai atu e au ki taku tākuta?
Mena kua tāpaetia koe he histiocytosis, he mea noa te maha o ngā pātai kei roto i tō hinengaro. He mea nui kia kōrero koe ki tō tākuta mō ēnei mea katoa, kia mārama ai koe ki tō āhua. Anei ētahi pātai ka taea e koe te pātai:
- He aha te momo histiocytosis kei a au?
- Me whai maimoatanga ahau?
- He aha ngā kōwhiringa maimoatanga e taunaki ana koe?
- He aha ngā pānga taha ka taea te tumanako i te wā e rongoatia ana?
- He aha ngā hua ka puta mai i te maimoatanga?
- Ka taea te whakaora katoa i tōku mate?
Karere Whakamutunga mō te Tango ki te Kāinga
I te whakarapopototanga, ko te histiocytosis te ingoa i hoatu ki tētahi rōpū mate toto onge e puta mai ana i te nui rawa o ngā histiocytes, he momo toto ma, i roto i ngā kiko. Ko ētahi o ēnei he tino māmā, kāore he tohu e puta, ko ētahi he kino rawa atu ka mate .
He nui rawa ngā histiocytes i roto i ngā kiko o te tangata e pāngia ana e te histiocytosis, ā, ka puta te mumura (te pupuhi). Heoi, ka rerekē rawa ngā tohu, ngā maimoatanga, me ngā putanga o te mate, ahakoa i waenga i te hunga e pāngia ana e te momo histiocytosis kotahi .
Ko tō tākuta te tangata pai rawa atu hei mārama ki tō mate me ngā āhuatanga motuhake e pā ana ki tēnā. Nō reira, kia tino mārama ai koe ki tō mate me tō mahere maimoatanga, kaua e wehi ki te pātai. Kōrero ki tō tākuta mō ngā mea katoa e pā ana ki tō hinengaro.
` Histiocytosis, Ngā pūtau toto mā, Ngā histiocytes, Pūnaha ārai mate, LCH, ECD, RDD, Ngā tohu, Te maimoatanga
💬 Comments (0)
Kaore ano kia tukuna he korero. Tāpirihia to korero ki konei mo te wa tuatahi.
Tāpirihia to korero