Kei te taka hoki ō kamo? Kei te ahua kore ora koe? He myasthenia gravis tēnei?

I ētahi wā, kei te pai koe ina ara ake koe i te ata, engari i te roanga o te rā, ka tīmata te ngaro o te kaha o tō tinana? Ina koa ka taumaha, ka piko ō kamo, ka pōturi ō kupu ina kōrero koe, ka uaua rānei ki te hiki i te ringa, i te waewae rānei? Mena kua mōhio koe ki ēnei, he mea nui kia mōhio koe ki te mate e kōrerohia ana i tēnei rā, e kiia nei ko te Myasthenia Gravis , ko te MG rānei te whakarapopototanga.

He aha te Myasthenia Gravis?

He mate pūnaha ārai mate tēnei ka roa pea mō te wā katoa. Ki te kī ngāwari, ka tīmata te pūnaha ārai mate o tō tātou tinana ki te whakaeke i ngā wāhanga hauora o tō tātou tinana. I roto i te MG, ka aro tēnei whakaeke ki ngā hononga i waenga i ō tātou io me ngā uaua.

Whakaarohia, e kī ana tō tātou roro ki te uaua, "Āe, ka kōpiri koe ināianei." Me haere tēnei karere mā roto i ngā io, ka tae atu ki te uaua. Engari i roto i te tangata whai MG, ka whakararuraruhia ngā "kaiwhakawhiwhi" e haria ana tēnei karere e tō rātou ake pūnaha ārai mate. He rite ki te ngaronga o te tohu ina ngana koe ki te waea atu.

Nā reira, ka ngoikore haere ngā tohu e tukuna ana ki ngā uaua i a rātou e whakamahia ana, ā, ka memeha haere te kaha o ngā uaua. Engari i muri i te wā okioki poto, ka hoki anō ki te āhua noa. Koinei te āhuatanga tino motuhake o MG. Ahakoa ka taea tēnei āhuatanga te puta i ngā tau katoa, he mea tino noa i roto i ngā wāhine kei raro iho i te 40 tau te pakeke me ngā tāne neke atu i te 60 tau te pakeke.

He aha te take e pēnei ai te āhua o tō tātou tinana ki a ia anō? He aha ngā take?

Kāore i te tino mōhiotia he aha te take e whakaeke ai te pūnaha ārai mate i tō tātou ake hononga io-uaua pēnei. Engari ko te take matua he hanga paturopi te tinana hei ārai i ngā kaiwhakawhiwhi e whiwhi ana i te neurotransmitter acetylcholine. Ko tēnei acetylcholine te "karere" e kawe ana i te karere e kī ana ki ngā uaua kia kōpiri. Nō reira, ina āraia te wāhi mahi a tēnei karere, kāore ngā uaua e mahi tika.

Ka whakawhanakehia hoki e ētahi tāngata he paturopi ki ētahi atu pūmua. Ahakoa e whakaarohia ana he pānga ira tēnei, he maha ngā tāngata whai MG kāore he tangata kē atu i roto i ō rātou whānau e pangia ana e te mate.

Kua kitea hoki te repe thymus , he okana i te uma o runga, e pāngia ana. Ka nui haere tēnei repe i roto i ētahi tāngata whai MG. E whakapono ana ngā kairangahau i ētahi wā ka hē te whakamōhio a tēnei repe ki te tinana, ā, ka puta ai ēnei paturopi kāore e hiahiatia.

He aha ngā tohu matua ka kitea?

He rerekē ngā tohu o te MG i ia tangata, i ia tangata. Tērā pea ka puta ohorere ngā tohu ki ētahi tāngata. Tērā pea ka puta mārire ētahi. Me titiro tātou ki ngā wāhi matua e pāngia ana, me ngā tohu hoki.

Me pēhea koe e tino mōhio ai he mate tēnei?

Mena kei a koe ēnei tohu, me toro atu koe ki tō tākuta whānau i te tuatahi. Mena ka whakapae ia i tēnei, ka tukuna koe e ia ki tētahi tākuta roro. Ka pātai atu ia ki a koe mō ō tohu, ā, ka tirotirohia hoki e ia tō tinana. Hei tāpiri, he maha ngā whakamātautau ka taea te mahi hei whakaū i te mate:

• Ngā whakamātautau toto: Tirohia ō toto mō ngā paturopi kino (ngā paturopi kaiwhakawhiwhi acetylcholine) i kōrerotia e tātou i mua ake nei.
• Whakamātautau Edrophonium: Ka tirohia e tēnei whakamātautau mēnā he rongoā e whakanui ana i tō kaha uaua mō te wā poto. Mēnā ka piki ake te kaha, he tohu pea tēnei nō te MG.
• Ngā whakamātautau whakaohooho roro: Ka werohia he ngira iti ki roto i te uaua, ā, ka inehia te tere o ngā tohu io. Ka taea tēnei te whakamahi hei tirotiro i te tere o te ngoikore o te uaua ina whakamahia tonutia (electromyography).
• Whakamātautau tio: Ka whakatakotoria he tio ki runga i te kamo e takoto ana mō ētahi meneti hei tirotiro mēnā ka ara ake te kamo. Mā tēnei ka taea te whakaatu i te āhua o te mate nā te mea ka pai ake te whakawhitiwhiti kōrero uaua-io i te wā poto mā te makariri.
• Whakaahua: Kia whakaūtia te mate, ka taea te mahi i tētahi matawai CT, MRI rānei hei tirotiro mō ngā raruraru o tō repe thymus, pērā i te pukupuku (thymoma).

He aha ngā maimoatanga e wātea ana?

He mate kāore e taea te whakaora katoa i te MG, engari ka taea te whakahaere angitu. Mā tō tākuta e whiriwhiri te maimoatanga tino tika māu i runga i te kaha o ō tohu, tō tau, me tō hauora whānui.

1. Ngā rongoā whakapakari uaua: Ko te rongoā tuatahi ko ngā rongoā pēnei i te pyridostigmine. Ka mahi ēnei mā te whakanui ake i te nui o te acetylcholine i te hononga io-uaua. Ka puta te kaha i roto i te 15-30 meneti o te tangohanga, ā, ka roa mō te 3-4 hāora.

2. Ngā rongoā ārai mate: He maha ngā tāngata e hiahia ana ki ēnei rongoā nā te mea ko tō tātou ake pūnaha ārai mate te take o te mate. Tuatahi, ka hoatu he steroids pēnei i te prednisone, kātahi ka whakawhitihia ētahi atu rongoā pēnei i te azathioprine. E hia marama pea ēnei e puta ai ngā hua.

3. Te tango i te manawa: Ahakoa he pukupuku kei roto i te repe manawa, mā te tango pokanga ka tino whakaitihia ngā tohu i roto i ētahi tūroro.

4. Whakaora IV:Ka hoatu tēnei maimoatanga ina tino kaha ngā tohu, i ngā wā rānei pēnei i te myasthenia crisis.

• Plasmapheresis: Ka tangohia e tētahi mīhini motuhake ngā paturopi kino mai i ō toto ka whakahokia mai te plasma hauora ki tō tinana.
• Whakaora IVIG: Mā te tuku i ngā paturopi (immunoglobulin) i tangohia mai i ngā kaituku hauora ki te tinana, ka whakarerekētia te mahi a te pūnaha ārai mate mō te wā poto.
• Ngā paturopi monoclonal: He paturopi motuhake ēnei i hangaia i roto i te taiwhanga e aro ana, e whakaeke ana hoki i ngā wāhanga motuhake o te pūnaha ārai mate e kore e mahi tika ana.

Me pēhea koe e tiaki ai i a koe anō?

Haunga te maimoatanga hauora, ka taea e koe te whiwhi i te oranga nui mai i ngā huringa iti ki tō momo noho.

• Kia pai te kai: Kia maha ngā kai iti i te rā, kaua e kai nui kotahi. Kai i ō kai matua i te wā e nui ana tō kaha. Kōrero ki tō tākuta mō te tango i ngā rongoā whakapakari uaua i mua i te kai.
• Whakakorikori tinana, engari kia mōhio ki ō rohe: Ahakoa ka taea e te whakakorikori tinana te hoatu i te kaha mō te wā roa, karohia te whakapau kaha rawa. Pātai atu ki tō tākuta, ki tō kaiwhakaora tinana rānei, he aha ngā whakakorikori tinana e tika ana māu.
• Okioki ina ngenge koe: Me haere tonu ki tāu mahi o ia rā. Engari ina tīmata koe ki te ngenge, okioki. Whakarongo ki tō tinana.
• Kia mōhio ki ngā mea e whakaoho ana i te mate: Tērā pea ka piki ake ngā tohumate o te MG i ētahi tāngata ina mate ana rātou, ina ahotea ana rātou, i te wā paheketanga o ngā wāhine, me te mea hoki e pā ana ki ētahi rongoā. Kōrero ki tō tākuta mō tēnei.