Kāore he whatukuhu o tāu pēpi? Kotahi anake rānei tana whatukuhu? Me ako tātou mō (Renal Agenesis)!

Kua rongo kē koe i ētahi pēpi e whānau mai ana me te whatukuhu kotahi anake, kāore rānei e rua ngā whatukuhu? Tērā pea he ahua whakamataku tēnei, engari he mea nui kia mōhio ki tēnei mate. I tēnei rā ka kōrero tātou mō tēnei mate e kiia nei ko te `(Renal Agenesis)`. Kaua e manukanuka, me whakamārama ngāwari noa iho.

He aha te `(Renal Agenesis)`? Me mārama noa iho tātou, me pēhea?

Ki te kī ngāwari, ko te `(Renal Agenesis)` he whānautanga o te pēpi me te whatukuhu kotahi anake, kāore rānei he whatukuhu e rua. E rua ngā whatukuhu o te tinana o tātou katoa. Me mahi tika te whatukuhu kotahi kia ora ai. He mate `(Congenital)` tēnei, arā, he mea kei roto mai i te whānautanga.

Nā, ki te tirohia motuhaketia te tikanga o ēnei kupu e rua, ka mārama ake ki a koe:

• Whatukuhu: Koinei te ingoa hauora mō ngā " whatukuhu ".
• Agenesis: E pā ana tēnei ki te korenga o tētahi okana e tino whanake i te wā e noho ana te pēpi i roto i te kōpū o te whaea, arā, te kōpū.

Nō reira, ina kī tātou ko `(Renal Agenesis)`, ko tōna tikanga kāore anō kia tika te hanganga o ngā whatukuhu o te pēpi.

He aha ngā momo matua o te `(Renal Agenesis)`?

E rua ngā huarahi matua e kitea ai tēnei āhuatanga:

1. Te Agenesis o te Tākihi Kotahi-Taha

Ko te mea e tupu ana i roto i tēnei, e ai ki te ingoa, ko te ngaro o te whatukuhu i te taha kotahi o te pēpi. Ko te tikanga he pai te whatukuhu o tetahi atu. He waimarie, ka taea te noho i te oranga noa, ki tonu i te whatukuhu kotahi anake. I roto i te nuinga o ngā wā, ka taea e te whatukuhu kotahi e toe ana te tīmata ki te tango i te mahi a te whatukuhu ngaro, kia nui ake ai. He rite ki te tamaiti e mahi ana i ngā mahi kāinga e rua i roto i te akomanga.

2. Te ngaronga o ngā whatukuhu e rua (Bilateral Renal Agenesis)

He āhua kino ake tēnei. I konei, kāore ngā whatukuhu e rua o te pēpi. Waihoki, kāore anō kia hangaia ngā ngongo iti "Ureters" e kawe ana i te mimi mai i ngā whatukuhu ki te "Bladder". Haunga tēnei, kāore ngā "pūkahukahu" o te pēpi e whanake tika ana, arā, he "Pulmonary Hypoplasia" tino iti. Ko te whakakotahitanga o tēnei ngoikore o te whatukuhu me te ngoikore o te pūkahukahu ka kiia hoki ko te "Potter Syndrome". Heoi anō, he maha ngā wā ka mate tēnei āhua.

He aha te mea ka pā ki ō tātou whatukuhu?

He wāhanga tino nui o te pūnaha mimi ngā whatukuhu e rua o te tinana. Whakaarohia rātou hei pūnaha tuku para i roto i tō tātou whare. Ko te mahi matua a ngā whatukuhu he tātari me te tango i ngā para kāore e hiahiatia ana i roto i ō tātou toto. Kātahi ka tukuna atu ēnei para i te tinana hei mimi.

He pēhea te noa o tēnei āhuatanga `(Renal Agenesis)`?

E ai ki ngā tatauranga, tata ki te kotahi i roto i te 2,000 pēpi e whānau ana, ka pāngia pea e te mate e kiia nei ko te "Unilateral Renal Agenesis", arā, ko te ngaronga o te whatukuhu kotahi. Ko te mate o te "Bilateral Renal Agenesis", arā, ko te ngaronga o ngā whatukuhu e rua, he mea onge ake. Ka pā tēnei mate ki te tata ki te kotahi i roto i te 8,500 pēpi hou. Ahakoa kāore i te mōhiotia te take tuturu, he nui ake te kitea o tēnei mate o te ngaronga o ngā whatukuhu e rua i roto i ngā pēpi tāne.

He aha ngā take o te `(Renal Agenesis)`?

I te nuinga o te wā, ko te tino take o te `(Renal Agenesis)` he panoni, he whakarerekētanga rānei i roto i ngā ira `(Gene mutation) .` Kua kitea e ngā kairangahau e whitu ngā whakarerekētanga ira e pā ana ki tēnei. Nā tēnei whakarerekētanga ira, ka whakararuraruhia te hanganga o ngā whatukuhu i roto i te kōpū o te pēpi i ngā marama tuatahi e toru o te hapūtanga `(First trimester).`

Ko ētahi atu take iti ko:

• Ka pāngia te whaea e te mate huka i te wā e hapu ana (gestational diabetes).
• Ngā haputanga maha (pērā i ngā māhanga, ngā mātoru).
• Te whakamahi i ētahi rongoā kino i te wā e hapu ana.

He aha ngā tohu o te `(Renal Agenesis)`?

Ka pāngia te pēpi e te Mate Potter, arā, kāore ōna whatukuhu e rua, ā, kāore anō hoki ōna pukahukahu kia tino whanake, i muri tonu i tōna whānautanga ka pāngia e ngā raruraru manawa e morearea ai te ora.

Kāore pea he tohu e puta mai i te pēpi i whānau mai me te whatukuhu kotahi. Engari ki te puta mai ngā tohu, ko ēnei pea:

• Te toto toto tiketike i roto i ngā tamariki.
• Te pikinga o te taumata pūmua i roto i te mimi (Proteinuria).
• Te reflux vesicoureteral.

I ētahi wā, ka pāngia pea ngā pēpi i whānau mai me te whatukuhu kotahi e ētahi atu āhuatanga pēnei i:

• Waewae karapu.
• Ngā mate manawa whānau, pērā i ngā kōhao i waenganui i te atria, i ngā ventricle rānei o te manawa (ASD, VSD rānei).
• Ngā āhuatanga rerekē o te urological whānau.
• Te koretake o te anus, te atresia anal rānei.

Me pēhea te tautuhi i te `(Renal Agenesis)` i te wā e hapu ana?

I te nuinga o te wā, ka mahia he matawai ultrasound i te wā e hapu ana te whaea.Ka taea te tautuhi i tēnei mate. Mā tēnei matawai ka kitea kua ngaro ngā whatukuhu. Waihoki, ki te iti te wai amniotic i te taha o te puku o te pēpi (Oligohydramnios), he tohu pea tēnei mō tētahi mate e kiia nei ko Renal Agenesis. Nā te mea kāore ngā whatukuhu o te pēpi e whakaputa mimi, ka heke ai tēnei wai. Ki te kore e nui tēnei wai, kāore e whanake tika ngā pukahukahu o te pēpi.

Me pēhea te tautuhi i te `(Renal Agenesis)` i muri i te whānautanga o te pēpi?

Ka taea te mahi i ngā matawai whakaahua i muri tonu i te whānautanga o te pēpi hei whakaū i te mate. Heoi, i ētahi wā, kāore pea te mate e kitea kia pakeke ake rā anō te tamaiti. I ētahi wā, ka kitea pea te mate i te wā e pāngia ana te tamaiti e ētahi atu tohu, ā, kei te matawaihia, i te wā rānei e mahia ana he matawai ultrasound mō tētahi atu take, pērā i te mate mimi (UTI).

Ko ngā momo matawai matua e whakamahia ana hei tautuhi i te `(Renal Agenesis)` ko:

• Te tirotiro i te puku, te tirotiro rānei i te whatukuhu .
• Matawai CT .
• Matawai MRI `(MRI)`.

Me pēhea te rongoā i te Agenesis Renal Bilateral?

Tae noa ki ēnei wā tata nei, kāore he tūmanako mō te pēpi kāore he whatukuhu e rua, kāore hoki he pukahukahu i whanake, kia ora ake i waho o te kōpū mō ngā haora torutoru. Heoi anō, kei te tukuna mai e ngā maimoatanga whakamātautau hou ētahi tūmanako. Ko te werohanga o te wai tote ki roto i te kōpū i te wā e hapu ana hei whakahoki mai i te taumata o te wai amniotic. Mā tēnei wai ka taea e ngā pukahukahu o te pēpi te whanake. Kātahi, i muri i te whānautanga o te pēpi, ka tukuna te pēpi ki te dialysis kia taea rā anō te mahi i te whakawhitinga whatukuhu. Engari kia mahara, kei roto tonu tēnei maimoatanga i te wāhanga whakamātautau, ā, kāore e wātea ana i ngā wāhi katoa.

Me pēhea te rongoā mō te Agenesis Renal Unilateral?

Ko te hunga kotahi te whatukuhu, me tango rongoā pea i ētahi wā hei whakaheke i te toto toto . Mena kei a koe, kei tāu tamaiti rānei tēnei mate, he mea nui kia toro atu koe ki tētahi tohunga whatukuhu (Ngā Tohunga Matepukupuku) i ia wā, kia tirotirohia hoki tō tinana, kia tātaritanga mimi, kia tirotirohia hoki i te iti rawa i te kotahi i te tau, i ia wā, i ia wā rānei. Tērā pea ka whai whakamātautau anō hoki tāu tamaiti:

• Ngā whakamātautau mahi whatukuhu.
• Whakamātautau pūmua mimi.

He aha tāu e taea ai hei tiaki i tō whatukuhu kotahi?

He tokomaha te hunga kotahi ō rātou whatukuhu e tohutohuhia ana kia whai i tētahi kai e pai ana mō ngā whatukuhu (DASH) . Ko tēnei kai ko te whakaiti i te tote me te huka, me te kai i ngā kai he nui te muka me te pāhare pāporo.

Ka taea e ngā tamariki me ngā pakeke e pāngia ana e te Renal Agenesis te mahi i ēnei e whai ake nei hei tiaki i te hauora o ō rātou whatukuhu:

• Kaua e tango i ngā rongoā anti-inflammatory kore-steroidal (NSAID) me ētahi rongoā whakamamae mamae. Ka kino pea ēnei i ō whatukuhu. Whakamahia he rongoā pēnei i te acetaminophen hei utu.
• Kia mau ki te taumaha hauora, kia noho kaha hoki. Heoi, he pai ake te karo i ngā hākinakina whai pānga nui pēnei i te whutupaoro, te whutupōro, me ngā mahi toi whawhai, nā te mea ka kino pea ki tō whatukuhu e toe ana.
• Tirohia tō toto toto i ia wā, i ia wā ki te kāinga.