He aha te Spindle Cell Sarcoma? Me kōrero māmā tātou ki a Nirogi Lanka!

Kua āwangawanga koe mō te mamae rerekē, te pupuhi rānei i roto i ō wheua, i ō kiko ngohengohe rānei, pērā i ō uaua? Ahakoa he maha ngā take iti e puta mai ana i ēnei tohu, i ētahi wā ka taea e rātou te tohu i tētahi mate kino ake. I Nirogi Lanka, e hiahia ana mātou kia mōhio koe ki ngā mea e pā ana ki a koe, nō reira i tēnei rā kei te kōrero mātou mō tētahi momo mate pukupuku onge engari he mea nui me mōhio koe: te Spindle Cell Sarcoma.

He aha rawa te Spindle Cell Sarcoma?

He whakarāpopototanga noa iho, he momo mate pukupuku onge te Spindle Cell Sarcoma e puta ana i roto i ō wheua, i ō kiko ngohengohe rānei. I Nirogi Lanka, e hiahia ana mātou kia mārama koe ko te "sarcoma" te kupu hauora mō te pukupuku e puta ake ana i roto i ēnei kiko hanganga o te tinana.

Ko te mea e motuhake ai te Spindle Cell Sarcoma ko te āhua o ngā pūtau ina tirohia i raro i te karuārai. He rite ki te "spindel"—he āhua angiangi i ngā pito e rua, he matotoru hoki i waenganui. Nā tēnei āhua motuhake i tapaina ai te mate.

Nā ngā whanaketanga o ngā tātaritanga taiwhanga, ka taea e ngā tākuta te tautuhi i ngā momo sarcomas neke atu i te 75. Ko te Spindle Cell Sarcoma he kāwai e whakamahia ana ina kore e taea e ngā whakamātautau motuhake—pērā i te tae pūtau, te tātari ira rānei—te whakarōpū i te mate pukupuku ki tētahi momo motuhake ake. Ko te tikanga, he whakarōpūtanga whānui e whakamahia ana e ngā tohunga mate pukupuku ina kore ngā pūtau pukupuku e uru ki ētahi atu kāwai kua tautuhia pai.

Kei hea te nuinga o te wā e puta ai ēnei pukupuku?

Ko te Spindle Cell Sarcoma te mea e pāngia ana e ngā wheua roa o tō tinana, pērā i:

• Tō wheua huha (femur)
• Tō wheua hope (tibia)
• Tō wheua ringa o runga (humerus)

Heoi, kāore i te herea ki ēnei wāhi anake. Tērā pea ka pāngia ētahi tūroro e ēnei pukupuku i roto i te hope, i te rohe o te mahunga me te kaki, i ētahi atu wāhi rānei o te tinana.

He aha ngā momo matua o te Spindle Cell Sarcoma?

Ka ahu mai ngā sarcomas katoa i ngā kiko ngohengohe—tae atu ki te ngako, te uaua, ngā uaua toto, ngā io, me ngā kiko e karapoti ana i ngā wheua. Ka whakarōpūhia e tō tākuta ēnei pukupuku i runga i te momo pūtau motuhake i ahu mai ai.

Mā te mārama ki ēnei āhuatanga pūtau ka āwhina i tō rōpū hauora ki te aromatawai i te mōrearea o te horapa me te whiriwhiri i te mahere maimoatanga tino whai hua māu. Ahakoa he kupu whānui te "Spindle Cell Sarcoma", kei roto i tēnei he maha ngā momo matua:

• Te Sarcoma Pleomorphic Kāore i Whakarerekētia (UPS): E ai ki te ingoa, he "kore whakarerekētia" ngā pūtau, arā, kāore i te mārama ko tēhea momo pūtau i ahu mai ai te mate pukupuku. He "pleomorphic" ēnei pukupuku, arā, he rerekē te rahi me te āhua o ngā pūtau.
• Fibrosarcoma: Ka puta mai ēnei i ngā fibroblast, arā, ngā poraka hanga matua o ngā kiko honohono o tō tinana.
• Leiomyosarcoma: Ka tīmata ēnei i roto i ngā pūtau uaua maeneene. Kāore i rite ki ngā uaua angaanga e whakamahia ana e koe mō te nekehanga, ka kitea ngā pūtau uaua maeneene i roto i ō whekau o roto, i ngā kōhao tinana, me ētahi kiko ngohengohe.

He pēhea te noa o tēnei āhuatanga?

Pērā i ētahi atu sarcoma, he tino onge te Spindle Cell Sarcoma. E 10% noa iho o ngā mate pukupuku wheua me ngā kiko ngohengohe katoa e kitea ana. Nā tēnei onge, kāore pea tō tākuta matua e whakaaro wawe kei te pāngia koe e te sarcoma. Me kōrero pea koe ki ētahi tohunga me te whai i ngā whakamātautau tātaritanga maha i mua i te taenga ki tētahi tātaritanga tuturu.

Ahakoa ka taea e te tangata te pāngia e tēnei mate, he mea tino noa tēnei i roto i te hunga neke atu i te 40 tau te pakeke . Ina koa, ko te Undifferentiated Pleomorphic Sarcoma ka kitea i roto i ngā tūroro i waenga i te 60 me te 70 tau te pakeke.

He aha ngā tohu?

Ka rerekē pea ngā tohu i runga i te rahi, te wāhi, me te maha o te pukupuku. Me aro nui koe ki ngā tohu whakatūpato e whai ake nei :

• Mamae wheua: Tērā pea ka roa, ka mutu rānei, ā, he maha ngā wā ka whakaahuatia he mamae hohonu.
• Whati mate: He wheua e whati ngāwari ana, i ētahi wā ahakoa he hinganga iti noa, nā te ngoikore o te pukupuku.
• Te ngawari, te pupuhi rānei: Tērā pea ka kite koe i tētahi puku, i tētahi puranga rānei e kitea ana i te wāhi e pāngia ana.
• Te nekehanga iti: Mena kei te tata te puku ki tētahi hononga, ka raru pea koe ki te neke, ki te piko rānei i taua hononga (hei tauira, tō turi, tō tuke rānei).
• Ngenge: He ngenge nui, pumau, kāore e pai ake i te okiokinga, i te moe rānei.
• Mate pāwera: He āhua whānui o te kore e pai te hauora, te ngenge, te kore rānei e hiahia ki ngā mahi o ia rā.

He aha te take o te Spindle Cell Sarcoma?

Pērā i ngā mate pukupuku katoa, ka tīmata te sarcoma pūtau spindle ina 'kino' ngā pūtau hauora. Ka tipu haere ēnei pūtau kino, ka hanga he pukupuku ka kino ki ngā kiko hauora e karapoti ana. Ko te āwangawanga nui ko te wā ka wehe atu ēnei pūtau mate pukupuku i te pukupuku tuatahi ka horapa puta noa i tō tinana ka pā ki ētahi atu kiko me ngā whekau. Ka kiia tēnei tukanga ko te 'metastasis', ka hua ake ko te mea e mōhiotia ana ko te 'mate pukupuku metastatic'.

Heoi, he mea nui kia mārama koe, i roto i tō rātou āhua noa, he tino whai hua ngā 'pūtau whīra'. Ka hangaia ēnei e tō tinana hei āwhina i te whakatika i ngā kiko kua pakaru—he tohu tūturu ēnei kei te ora koe. Kia ora te whara, ka ngaro atu ēnei pūtau.

Mō te sarcoma pūtau porowhita, ka tipu tonu, ka whakarea tonu ēnei pūtau. Kāore anō kia kitea e ngā kaipūtaiao tētahi take motuhake mō te hurihanga o ēnei pūtau hei mate kino.

Heoi, kua kitea e ngā kairangahau ka taea e ētahi whakarerekētanga ira te whakanui ake i tō mōrearea. Ko te 'whakarerekētanga' he hapa i roto i ō ira - te pūnaha e whakarato ana i ngā tohutohu ki ō pūtau mō te mahi. I roto i te sarcoma pūtau spindle, he maha ngā wā ka tukuna iho ēnei whakarerekētanga, arā, ka taea te tuku iho i roto i ngā whānau.

He aha ngā āhuatanga mōrearea mō tēnei mate pukupuku?

He maha ngā āhuatanga ka whakanui ake i tō tupono ki te whakawhanake i te spindle cell sarcoma:

• Te Pukupuku Wheua: Ka puta tēnei ina mate te kiko wheua nā te korenga o te toto e rere ana. E mōhio ana koe, me whai toto whai hāora te kiko wheua kia ora ai.
• Te Dysplasia muka: I tēnei āhua, ka whakakapia te wheua hauora e te kiko muka, rite ki te koha. Ka piki ake te mōrearea o ngā whati, ā, i ētahi wā tino onge, ka arahi pea ki te whanaketanga o ngā fibrosarcomas.
• Osteomyelitis: He mate tēnei kei roto i te kiko hautai i roto i te wheua, e mōhiotia ana ko te hinu wheua. Ka puta pea mēnā ka uru mai ngā huakita, ētahi atu iroriki rānei ki roto i te wheua mā roto i tō toto, ka pangia ngā pūtau o reira.
• Te Mate a Paget o te Wheua: He mate mau tonu tēnei e ngoikore ai ō wheua, ka pakarukaru ake, ka ngawari hoki te whati. Ka whakanui ake hoki i te tūponotanga o ngā mate pukupuku wheua, tae atu ki te spindle cell sarcoma.
• Te Whakaora Irahiko o Mua: Ka whakamahia e te rongoā irahiko ngā hihi kaha-nui, pērā i ngā hihi-X kaha, hei whakangaro i ngā pūtau matepukupuku. Ahakoa he onge, ka taea e te sarcoma pūtau spindle te whanake i ētahi wā i ngā wāhi i rongoatia i mua ki te irahiko. Mena ka puta tēnei, ka tupu i ētahi tau (i te nuinga o te wā i roto i te 7 ki te 20 tau) i muri i te maimoatanga. Kia mahara he iti iho i te 1% o te hunga e whiwhi ana i te rongoā irahiko ka pāngia e ngā matepukupuku i puta mai i te irahiko.

He aha ngā raruraru o te Spindle Cell Sarcoma?

Nā tēnei mate pukupuku, ka ngāwari ake te whati o ō wheua i te wāhi i puta ai te pukupuku. Mēnā ka whati te wheua, ka horapa pea ngā pūtau mate pukupuku o te pukupuku ki ngā wāhi e karapoti ana.

Heoi anō, kei te tautohe tonu ngā tohunga hauora mō te mea ka rerekē te āhua o te mate pukupuku i te whati wheua, mehemea rānei ka whakawhirinaki noa ngā putanga ki te horapa o te mate pukupuku.

Me pēhea te tātaritanga o te Spindle Cell Sarcoma?

I mua i te taea e tō tākuta te tātaritanga i te mate pukupuku me te whakatau i tōna taumata, tera pea ka whai koe i ētahi whakamātautau me ngā tikanga. Mā te 'whakatakotoranga mate pukupuku' ka āwhina i ngā tākuta ki te whakarōpū i te kaha o te mate pukupuku i runga i te rahi o te pukupuku, tōna wāhi, me te mea kua horapa. I roto i ngā mate pukupuku wheua, ka whakatau hoki ngā tākuta mēnā he 'teitei' te pukupuku, he 'iti rānei te taumata.' Kei roto i ngā pukupuku teitei ngā pūtau tino rerekē e tere ake ana te tipu me te horapa.

He kounga teitei te nuinga o ngā sarcoma pūtau spindle.

Ngā Whakamātautau Whakaahua

Ahakoa kāore e taea e ngā whakamātautau whakaahua te tautuhi i te momo mate pukupuku tuturu, ka taea e rātou te whakaatu i te rahi me te wāhi o te puku, me te whakaatu mēnā kua horapa atu ki tua atu i te wāhi tuatahi o te puku.

• Ngā hihi-X: Ka taea e ēnei te whakaatu i ngā pukupuku, i ētahi atu āhuatanga rerekē rānei o ō wheua. Ka taea e te hihi-X o te uma te whakatau mēnā kua horapa te mate pukupuku ki ō pukahukahu, he wāhi noa tēnei mō te metastatic spindle cell sarcoma.
• Matawai MRI: Ka whakamahia e te MRI he aukume kaha, ngā ngaru reo irirangi, me te rorohiko hei hanga whakaahua taipitopito o roto o tō tinana. He rerekē ki ngā hihi-X, ka whakaratohia e ngā MRI he tirohanga tino mārama o ngā kiko ngohengohe, he mea tino āwhina mō te tautuhi i ngā puku kiko ngohengohe he sarcomas pea.
• Ngā Matawai CT: Ka whakamahia e ngā matawai CT ngā hihi-X me te tukatuka rorohiko hei hanga whakaahua 3D o ngā wheua me ngā kiko ngohengohe. Ka āwhina ēnei ki te whakatau mēnā kua horapa te mate pukupuku ki ngā kiko ngohengohe e karapoti ana, ā, he tino pai mō te tautuhi i ngā wheua ngoikore, ngā whati rānei.
• Ngā Matawai PET: Ka whakamahia e ngā matawai PET he tohu irahiko hei kimi i ngā pūtau matepukupuku puta noa i te tinana. He mea whai hua ēnei mō te tautuhi i te sarcoma pūtau porowhita metastatic me te aroturuki i te pai o te mahi a tō maimoatanga. Kia mahara kāore ngā matawai PET e whakamahia mō ngā momo sarcoma katoa; mā tō tākuta e whakatau mēnā he tika tēnei māu.

Ngā Whakamātautau Toto

Kāore he whakamātautau toto motuhake hei tautuhi i te sarcoma pūtau spindle. Heoi, mā ngā whakamātautau toto ka hoatu ki tō tākuta ngā mōhiohio nui e pā ana ki tō hauora whānui, he mea nui hoki tēnā. I te nuinga o te wā, ka taea e ngā whakamātautau toto te whakarato mōhiohio mō ēnei e whai ake nei:

• Ō pūtau toto
• Te mahi a te okana
• Ngā taumata whākōkī (he matū motuhake ngā whākōkī e whakahaere ana i ngā tukanga nui o te tinana)

Te koiora

Ko te koiora te huarahi tino whai hua hei whakaū mēnā he mate pukupuku te pukupuku. Koinei hoki te tikanga nui mō te tautuhi i te momo me te taumata motuhake o te mate pukupuku. I te wā o te koiora, ka kohia e tō tākuta he tauira kiko mai i te pukupuku ka tukuna ki te taiwhanga hei tātaritanga ngaio.

Mō te nuinga o ngā tūroro e pāngia ana e te sarcoma pūtau spindle, ka mahia he 'koiora ngira'. Ka whakangāwarihia e tō rōpū hauora te rohe e karapoti ana i te puku i mua i te whakamahi i tētahi ngira angiangi, tuwhera hei tango i te tauira. Tērā pea me whai matawai X-ray, CT rānei koe hei āwhina i tō tākuta ki te ārahi tika i te ngira ki te wāhi ūnga.

Me pēhea te rongoā i te Spindle Cell Sarcoma?

Ko tō mahere maimoatanga whaiaro ki Nirogi Lanka ka whakawhirinaki ki tō hauora whānui, te wāhi o te pukupuku, te rahi, te momo, me ētahi atu āhuatanga takitahi. Ka whakaarohia hoki e mātou mēnā koinei tō tātaritanga tuatahi, mēnā rānei kua hoki mai te mate pukupuku (ka hoki anō) whai muri i ngā maimoatanga o mua.

Pokanga

Ko te whāinga matua o te pokanga he tango i te pukupuku me te pupuri i te nui o te wheua hauora e taea ana. Mena ka taea e tātou te tango angitu i ngā tohu katoa e kitea ana o te pukupuku tuatahi me ngā pukupuku tuarua, ka taea te whakaora. Heoi, ki te horapa te mate pukupuku ki tua atu i te wāhi i puta mai ai, ka nui ake te uaua o te tango katoa.

Te rongoā matū

Ka whakamahia e te chemotherapy ngā rongoā kua tohua hei whakangaro i ngā pūtau matepukupuku puta noa i tō tinana. Tērā pea ka whakamahia e tātou te chemotherapy i mua i te pokanga hei whakaiti i te pukupuku, hei whakangāwari ake i te tango, i muri rānei i te pokanga hei whakakore i ngā pūtau matepukupuku moroiti e toe ana. Ka whakamahia hoki te chemotherapy hei 'tiaki whakaora mamae'. Ahakoa kāore e taea te whakaora, ka taea e ia te whakangaro i ngā pūtau matepukupuku hei whakaiti i ngā tohu pēnei i te mamae o te wheua.

Ko te nuinga o ngā tūroro ka whiwhi i te huinga o ngā rongoā chemotherapy hei whakanui ake i te whai huatanga. Ka whakaritea tō tikanga maimoatanga i runga i tō hītori haumanu me te urupare a tō tinana ki te maimoatanga. Ko tā mātou whāinga he whakatutuki i te 'whakamarietanga,' arā, kua tino heke, kua ngaro rānei ō tohu me ō tohumate mate pukupuku.

Te Whakaora Irahiko

Ka whakamahia e te Whakaora Irahiko Hiko o Waho (EBRT) tētahi mīhini motuhake hei tuku i ngā hihi-X kaha-nui ki te puku hei whakangaro i ngā pūtau matepukupuku. Mena kāore koe e hiahia ki te pokanga—nā te mea kei roto rawa pea te puku i te kiko, kei te tata rawa rānei ki ngā whekau nui—ko te rongoā irahiko pea te kōwhiringa pai. He rite ki te chemotherapy, he taputapu kaha hoki mō te whakahaere i ngā tohu mena kua horapa te matepukupuku.

He aha ngā pānga taha pea o te maimoatanga?

He mea noa te pāngia e ngā pānga taha i te wā o te chemotherapy me te radiation therapy. Tērā pea ka roa pea ētahi i muri i te mutunga o tō huringa maimoatanga. He mea nui kia kōrero tuwhera koe ki tō tākuta i Nirogi Lanka mō ngā tūponotanga me ngā pānga taha e pā ana ki tō mahere maimoatanga kua whakaritea.

Āhea ahau me whakarite i ngā haerenga whai muri?

Mā tō rōpū tiaki e whakarite he wātaka mō ō tirotiro me ngā whakamātautau auau hei aroturuki i tō āhua me te tirotiro mō ngā tohu o te hokinga mai anō. I ngā wāhanga tōmua o te whakaoranga, tera pea ka maha ō wā whakarite, engari i te roanga o te wā kāore he tohu o te mate pukupuku, ka iti haere te auau o ēnei haerenga whai muri.

He aha atu ngā tiaki, ngā tikanga rānei e hiahiatia ana e au?

I runga i te whānuitanga o te pokanga, me whai atu pea koe i ētahi atu tikanga hei whakaora i te mahi a te wheua e pāngia ana. Hei tauira, me whai wheua tāpiri – te wāhi e tangohia ai te kiko mai i tētahi atu wāhanga o tō tinana, i tētahi kaituku rānei hei whakakapi i te wheua kua tangohia. I ētahi wā, ka whakamahia pea he peka hangai, he peka horihori rānei. Ma tā mātou tīma e whakarato te tautoko e hiahiatia ana e koe hei urutau ki ēnei huringa.

Ngā Pātai hei Pātai atu ki tō Tākuta mō te Spindle Cell Sarcoma

He mea āwhina te whakarite mō ō wā whakarite. Anei ētahi pātai nui hei pātai atu māu:

• Kei hea te puku?
• He aha te wāhanga me te nui o te mate pukupuku?
• He pēhea te pānga o te taumata o taku mate pukupuku ki taku mahere maimoatanga?
• He aha ngā pānga taha tino noa e tika ana kia tumanakohia e au?
• Ka taea te rongoā i taku mate pukupuku?
• He aha ngā whāinga matua o taku maimoatanga?
• Ka taea e koe te tuku mai i ahau ki ngā ratonga tiaki mamae tautoko hei āwhina i ahau ki te whakahaere i taku mate?

Ka taea te whakaora i te Spindle Cell Sarcoma? He aha te kino o tēnei?

Mena ka taea te tango i ngā tohu katoa o te mate pukupuku, ka taea e ngā tākuta te rongoā i te Spindle Cell Sarcoma. He māmā ake te rongoā mena kāore anō te sarcoma kia horapa ki tua atu i tōna wāhi taketake. Heoi, he tino uaua te rongoā i ngā kēhi kua horapa. Engari, kāore e taea te rongoā i ngā Metastatic Spindle Cell Sarcoma.

He maha ngā wā ka whakarōpūtia tēnei momo mate pukupuku hei 'tino mate', arā, ka tere te tipu me te horapa. Ahakoa kua memeha haere, kei reira tonu te tūponotanga ka hoki anō te mate pukupuku, i te wāhi taketake, i tētahi atu wāhi rānei o te tinana.

Kia maumahara he rerekē ia tātaritanga mate pukupuku. Ko tō tākuta te tangata pai rawa atu hei matapaki i tō matapae i runga i te momo pukupuku motuhake, te wāhanga, tō hauora whānui, me te urupare a tō tinana ki te maimoatanga. Ko rātou tō hoa matua ki te mārama ki te tikanga o tēnei tātaritanga ki a koe.

Karere Kawea ki te Kāinga mai i Nirogi Lanka

He mea taumaha rawa te whiwhinga o te tātaritanga mō te Spindle Cell Sarcoma, ā, ka pā kino pea ki tō oranga tinana me tō oranga hinengaro. He uaua pea ngā tikanga maimoatanga, ā, tera pea ka pāngia koe e ngā wero nui, pērā i te urutau ki ngā pokanga whakahou, ki ngā tānga wheua, ki ngā peka hangai rānei.

Nā ēnei take, he mea nui kia mau tonu te kōrero tuwhera me te pono ki tō tīma hauora mai i te rā tuatahi. Mā tēnei koe e āwhina ki te mārama ki tō mate me ngā āheinga tūturu mō te whakaora. Kaua e mangere ki te pātai mō ngā whāinga o tō maimoatanga me te āhua o te urutau o tō oranga o ia rā i te wā me muri i tō maimoatanga.

Ahakoa he mate pukupuku kino, he kaha hoki te Spindle Cell Sarcoma, he maha ngā maimoatanga whai hua hei whakahaere i tōna tipu, ā, i roto i te nuinga o ngā wā, hei whakatutuki i te murunga. Mahi tahi me tō rōpū tiaki kia mārama ai koe ki ngā mea hei tumanako atu. Kaua e ngaro te tumanako.He taputapu kaha te piri ki tō mahere maimoatanga me te pupuri i tētahi hinengaro pai, tautokona hoki, i roto i tēnei haerenga.

Ngā Kupumatua: Spindle Cell Sarcoma, Matepukupuku, Matepukupuku Wheua, Tissue Sarcoma, Pukupuku, Ngā Tohu, Te Maimoatanga