Ese muganga yakubwiye ko umutwe w'umwana wawe ari munini gato kuruta uko bisanzwe? Cyangwa se, isuzuma ryakozwe mu gihe utwite ryagaragaje ko hari amazi menshi mu bwonko bw'umwana? Ni ibisanzwe ko umubyeyi cyangwa se yumva afite ubwoba kandi aremerewe iyo yumvise ikintu nk'iki. Ariko ntugahangayike. Uyu munsi turimo kuvuga ku ndwara yitwa ' hydrocephalus '. Reka tubiganireho mu buryo bworoshye, mu buryo buri wese ashobora gusobanukirwa.
Hydrocephalus ni iki?
Iyo wumvise iri zina, hari abantu batekereza ko ari indwara aho ubwonko bwuzuza amazi. Izina ubwaryo ni uruvange rw'amagambo "amazi" n' "umutwe". Ariko mu by'ukuri, aya si amazi. Aya ni amazi y'ingenzi cyane azenguruka ubwonko bwacu n'umugongo wacu. Mu buvuzi, aya mazi tuyita Cerebrospinal Fluid (CSF) .
Mu magambo make, tekereza ko sisitemu iri mu bwonko bwacu ari nk'amazi. Ku ruhande rumwe, iyi CSF ihora ikorwa, naho ku rundi ruhande, umubiri urayinjiza kandi ukayisohora. Hakenewe uburinganire bwiza hagati y'umuvuduko ibi bikorwaho n'umuvuduko umubiri ubyinjizaho.
Ku bijyanye na hydrocephalus, kubera impamvu runaka, iri teraniro rirahungabana maze amazi ya CSF agatangira kwirundanya mu bwonko. Uko amazi yiyongera, umuvuduko w'ubwonko uriyongera kandi umutwe w'umwana ushobora kwiyongera.
Ijambo "congenital" risobanura ko iyo ndwara iba mu mwana kuva akivuka .
Kuki ibi bibaho ku bana bato? Impamvu ni izihe?
Hari impamvu eshatu z'ingenzi zituma iki gipimo cya CSF gishobora kwirundanya mu bwonko:
1. Kongera umusaruro w'amazi: Inkondo zo mu bwonko zikora amazi menshi ya CSF kuruta uko bikenewe.
2. Kuziba kw'amazi mu nzira: Kuziba ahantu runaka mu nzira amazi yavuyemo anyuramo. Iyi ni yo mpamvu ikunze kugaragara.
3. Kugabanuka kwinjiza amazi mu mubiri: Amazi asohoka ntasubizwa mu maraso neza.
Indwara ya hydrocephalus ivukanwa ishobora guterwa n'ibintu bigize imiterere y'umubiri, ndetse n'indwara zimwe na zimwe ziba mu gihe umubyeyi atwite . Reka turebe zimwe mu mpamvu nyamukuru ziri mu mbonerahamwe iri hepfo.
| Impamvu | Mu magambo make ... |
|---|---|
| Stenose yo mu mazi | Kugabanuka cyangwa kuziba inzira iri hagati y'imitsi ibiri y'ubwonko. Ibi bishobora guterwa n'ubwandu, ibibyimba, cyangwa kuva amaraso. |
| Ubusembwa bw'imiyoboro y'ubwonko | Urugero, indwara nka spina bifida, aho igice cy'umugongo kigaragara mu gihe cyo kuvuka, zishobora kubangamira urujya n'uruza rw'amazi ya CSF. |
| Ibisebe bya Arachnoid | Ibi ni ubwoko bw'ikibyimba kiba mu bwonko kandi gishobora kuziba inzira z'amazi ya CSF. |
| Indwara ya Dandy-Walker | Indwara aho ibice by'ubwonko bidakura neza. Ibi bishobora gutuma ingirabuzimafatizo imwe mu bwonko yaguka bitewe no kugabanuka cyangwa kuziba kw'inzira z'amazi. |
| Ubusembwa bwa Chiari | Indwara igira ingaruka ku ihuriro ry'ubwonko n'umugongo. Igice cyo hasi cy'ubwonko gisunika umugongo, ibyo bikaba bishobora gutuma habaho kuziba. |
Ni gute abaganga basuzuma iyi ndwara?
Akenshi, abaganga bashobora kubona impinduka mu mikurire y'ubwonko bw'umwana, nko kwaguka gato kw'imitsi yo mu bwonko, mu gihe cyo gupima ultrasound mu gihe utwite.
Iyo isuzuma rigaragaje ikintu nk'icyo, muganga ashobora gutegeka ko hakorwa ibindi bipimo kugira ngo abyige neza kurushaho.
- MRI scan: Ibi bituma umuntu abona neza uko ubwonko bw'umwana buhagaze .
- Gupima amazi ya amniotike:Mu gihe umwana akiri mu nda, hashobora gufatwa urugero ruto rw'amazi ya amniotic kugira ngo hapimwe chromosomes z'umwana.
- Amateka y'ubuzima bw'umuryango: Ni ngombwa kandi ko umuganga amenya niba hari umuntu wo mu muryango wawe wigeze kugira ibibazo nk'ubusembwa bw'imiyoboro y'ubwonko.
Ni ubuhe buryo bwo kuvura ibi?
Nubwo iyi ndwara imenyerewe umwana akiri mu nda, ubusanzwe ubuvuzi butangira umwana amaze kuvuka.
Muganga wawe azasuzuma neza uko umwana wawe ameze, hanyuma ahitemo uburyo bwo kuvura bukwiriye umwana wawe.
Hari uburyo bubiri bw'ingenzi bwo kuvura.
1. Gushyiraho sisitemu ya Shunt:
Ubu ni bwo buryo bukunze kugaragara bwo kuvura. Muri ubu buryo, umuyoboro wa pulasitiki woroshye cyane kandi woroshye ubagwa uhereye aho amazi ya CSF yikusanyiriza mu bwonko bw'umwana, munsi y'uruhu, ukajya ahantu nk'inda y'umwana. Amazi y'inyongera aterana mu bwonko hanyuma akanyura muri uwo muyoboro akawuteranya mu nda, aho umubiri ukayashyira mu buryo butekanye.
2. Kubaga ETV (Endoscopic Third Ventriculostomy):
Ubu ni ubundi buryo bwo kuvura. Aha, kamera nto ifite ikoranabuhanga rya fibre optique ikoreshwa mu kwinjira mu bwonko no gukora umwobo muto mu gice cy'ubwonko kugira ngo irenge aho amazi afunga inzira. Hanyuma amazi anyura mu mwobo maze akinjizwa mu mubiri.
Bigenda bite nyuma yo kuvurwa?
Ahazaza h'umwana uvukanye indwara ya hydrocephalus biterwa n'icyateye iyi ndwara n'ibindi bintu byinshi.
Nyuma yuko sisitemu za shunt zishyizweho, zigomba gukurikiranwa buri gihe na muganga . Shunt ishobora gukenera gusimburwa cyangwa hakabaho ubundi bubagwa uko umwana akura. Ibibazo bya shunt bishobora kuba birimo:
- Indwara zandurira mu mubiri
- Umuyoboro urafunze.
- Ikosa rya tekiniki
- Umuyoboro w'amaraso uba udahagije uko umwana akura.
Hari kandi n'ingaruka zimwe na zimwe zo kubagwa ETV. Hari ibyago byo gufunga umwobo mu buryo butunguranye, bishobora gushyira ubuzima mu kaga. Hari kandi n'ingaruka nko kwandura, umuriro, no kuva amaraso.
Nubwo haba hari ubuvuzi, iyi ndwara ishobora kugira ingaruka ku mikurire y'umwana ku mubiri no mu bwenge. Kubwibyo, umwana ashobora gukenera kwitabwaho, uburezi bwihariye , nibindi. Ariko, iyo akurikiranwe neza n'abaganga kandi agakundwa n'ababyeyi , abana benshi bashobora kubaho ubuzima busanzwe, burangwa n'ibyishimo hamwe n'imbogamizi nke. Humura rero.
Ubutumwa bwo kujyana mu rugo
- Hydrocephalus si ukwirundanya kw'amazi mu bwonko, ahubwo ni ukwirundanya kw'amazi yihariye yitwa cerebrospinal fluid (CSF).
- Iyi ndwara ikunze kugaragara binyuze mu gupima igihe umuntu atwite.
- Hari uburyo bwiza bwo kuvura ibi, nko gushyira shunt cyangwa kubagwa ETV.
- Kwita ku mwana mu buvuzi no kumukurikirana buri gihe ni ingenzi cyane, ndetse no nyuma yo kuvurwa.
- Vugana na muganga wawe ku kibazo cyangwa ubwoba ufite, nta soni cyangwa ngo ugire ubwoba.
- Iyo abana benshi bavuwe kandi bagahabwa ubuvuzi bukwiye, bashobora kubaho ubuzima bwiza.











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