Fungidzira, une hutano hwakanaka uye kamwe kamwe rimwe remaoko ako kana makumbo ako rinopera simba wobva wafa. Kana kuti muviri wako wese unopera simba zvekuti haugone kufamba. Zvakajairika kuti unzwe kutya zvakanyanya kana chimwe chinhu chakadai chikaitika. Vanhu vazhinji vanofunga kuti izvi zvinokonzerwa nekuneta kana chimwe chinhu. Zvisinei, dzimwe nguva panogona kunge paine chikonzero chekurapa chiri shure kweizvi chinoda kukurukurwa zvakadzama. Nhasi tiri kutaura nezvechirwere chisingawanzoitiki asi chakakosha kwazvo chekuziva.
Zvichitaurwa zviri nyore, chii chinonzi Primary Periodic Paralysis (PPP)?
Kuomarara Kwenguva Pfupi, kana kuti PPP muchidimbu, iboka rezvirwere zvisingawanzoitiki zvinongoerekana zvakanganisa tsandanyama dzedu. Chinoitika ndechekuti, pasina yambiro , tsandanyama dzako dzinongoerekana dzashaya simba, dzaoma, kana kuti dzaoma zvachose. Dambudziko iri rinogona kugara kwemaminitsi mashoma kune vamwe vanhu, nepo kune vamwe rinogona kugara kwemazuva.
Chikonzero chikuru cheizvi chiri mumasero edu emhasuru. Fungidzira kuti masero edu emhasuru ane migero midiki. Migero iyi ndiyo inopinda zvicherwa zvakakosha zvakaita sepotassium, sodium, uye calcium uye zvinobuda mumasero. Kuti tsandanyama ishande zvakanaka, huwandu hwezvicherwa izvi mukati nekunze kwesero hunofanira kunge hwakaringana zvakakwana. Chinoitika kumunhu ane PPP ndechekuti kuenzana uku kunorasika nekuda kwekusakwana kwematanho aya. Zvadaro tsandanyama hadzigone kushanda zvakanaka.
Kazhinji, zviratidzo izvi zvinotanga paudiki kana kuyaruka, asi vamwe vanhu vanogona kusaratidza zviratidzo kusvika vava nemakore makumi matanhatu kana makumi manomwe.
Ndeapi marudzi makuru echirwere ichi?
PPP yakakamurwa kuita mhando huru dzakasiyana-siyana. Kupatsanurwa uku kunonyanya kukonzerwa nekuti ndeapi mamineral channel defect ari mumasero emhasuru dzako.
| Rudzi rwechirwere | Chii chiri kuitika (nemashoko akareruka) |
|---|---|
| Kuomarara Kwenguva Nenguva kweHypokalemic (hypoKPP) | Chinoitika apa ndechekuti huwandu hwepotassium muropa hunongoerekana hwadzikira zvakanyanya. |
| Kuomarara Kwenguva Nenguva Kunokonzerwa NeHyperkalemic (hyperKPP) | Chinoitika apa ndechekuti huwandu hwepotassium muropa hunongoerekana hwawedzera zvakanyanya. |
| Paramyotonia Congenita | Pano, kuenzana kwe sodium ne potassium mumasero emhasuru kunokanganiswa. |
| Chirwere cheAndersen-Tawil (ATS) | Mumamiriro ezvinhu aya, maitiro ekuti potassium inopinda nekubuda mumasero haaitike zvakanaka. Huwandu hwe potassium muropa hunogona kunge hwakakwira, hwakaderera, kana kuti hwakajairwa. |
Dzimwe nguva, kushaya simba kwetsandanyama kunogona kukonzerwa nezvimwe zvirwere. Muenzaniso ndeweThyrotoxic Periodic Paralysis (TPP) . Ichi chirwere apo thyroid gland inoburitsa thyroid hormone yakawandisa. Izvi zvinoperekedzwa nekushomeka kwepotassium muropa, izvo zvinogona kukonzera zviratidzo zvakafanana neHypoKPP.
Ndezvipi zvikonzero uye "zvinokonzeresa" mamiriro ezvinhu aya?
PPP inokonzerwa nekusakwana kwemajini . Zvichitaurwa zviri nyore, inokonzerwa nekusakwana kwemajini anodzora nzira dziri mumasero emhasuru dzatakambotaura nezvadzo. Kazhinji, mwana anogara nhaka jini iri kubva kune mumwe wevabereki vake. Zvisinei, kashoma, mwana anogona kuva nechirwere ichi kunyangwe vabereki vasina jini iri.
Iye zvino ngatitarisei zvinogona "kukonzera" kusasimba kwetsandanyama uku. Izvi zvinogona kusiyana kubva pamunhu nemunhu.
- Kudya: Kudya zvekudya zvine potassium yakawanda (mu hyperKPP) kana potassium shoma (mu hypoKPP). Zvakare, kudya zvekudya zvine carbohydrates yakawanda (starch/shuga).
- Kurovedza muviri : Paunenge uchizorora mushure mekurovedza muviri kwakawanda.
- Zorora: Kugara panzvimbo imwe chete kwenguva yakareba, paunomuka mangwanani, kana kuti mushure mekurara.
- Zvimwe zvinokonzera: Kushushikana, kubatwa nechando chakanyanya, kunwa doro, uye mimwe mishonga (semuenzaniso, mishonga inozorodza tsandanyama, mimwe mishonga yeasthma, mishonga inoderedza marwadzo).
Ndezvipi zviratidzo zvikuru?
Chiratidzo chikuru kushaya simba kwetsandanyama kamwe kamwe kana kuoma mitezo zvachose. Izvi zvinogona kukanganisa ruoko rumwe chete kana gumbo panguva imwe chete, kana muviri wese pane dzimwe nguva.
Kuwedzera kune chiratidzo chikuru ichi, vamwe vanhu vanogonawo kusangana nezvimwe zviratidzo kana vasangana nekushaya simba uku:
- Kushaya simba kwetsandanyama dzechiso
- Kurwadziwa kwetsandanyama nekuomarara
- Kurova kwemoyo kusina kurongeka
- Kuoma kufema kana kumedza
HypoKPP (rudzi rwe potassium shoma)
Zviratidzo zvinogona kuitika kakawanda pazuva, kana kashoma kamwe chete pagore. Zvinogona kugara kweawa imwe chete kana maviri, kana kuti zvinogona kugara kwemazuva maviri kana matatu. Nekufamba kwenguva, tsandanyama dzinogona kupera simba zvachose.
HyperKPP (rudzi rwekuwedzera kwepotassium)
Kushaya simba kunogona kugara kwenguva pfupi, asi kunogona kuitika kakawanda. Zviratidzo zvinogona kungoerekana zvaitika, uye dzimwe nguva zvinotora maminitsi mashoma. Kunyangwe pasina kushaya simba, unogona kunzwa kurwadza kwetsandanyama kana kuomarara.
Chirwere cheAndersen-Tawil (ATS)
Kuwedzera pakushaiwa simba kwetsandanyama, zvimwe zviratidzo zvemuviri zvinoonekwawo.
- Kurova kwemoyo nekukurumidza kana kusina kurongeka
- Scoliosis
- Zvigunwe zvewebhu
- Zvidiki pane maoko netsoka zvakajairika
- Kuchinja kwechiso (semuenzaniso, huma yakafara, nzeve dzakaderera)
Nzira yekuziva chirwere ichi nemazvo sei?
Nekuti PPP chirwere chisingawanzoitiki uye zviratidzo zvayo zvakafanana nezvimwe zvirwere zvakajairika, zvinogona kutora nguva kuti chirwere ichi chiongororwe nemazvo. Saka, kana uine zviratidzo izvi, zvakanaka kuona chiremba ane ruzivo rwezvirwere zvine chekuita netsinga (Neurologist) .
Chiremba wako anogona kubvunza mibvunzo yakaita seiyi kuti aongorore chirwere chacho:
- Zviratidzo izvi zvakatanga rini?
- Pane mumwe munhu mumhuri ane dambudziko rakafanana here?
- Chii chinoitika kana kushaya simba kukaitika?
- Wakambonzwa here kuti chimwe chinhu kana chimwe chinhu chakakonzera izvi?
Uye zvakare, bvunzo dzinoverengeka dzinogona kuitwa kuti dzisimbise chirwere ichi:
- Kuongororwa kweropa: Tarisa huwandu hwepotassium, mahormone ethyroid, nezvimwe zvinhu.
- Electromyography (EMG): Kuedza mashandiro emhasuru netsinga.
- Electrocardiogram (EKG): Kuongorora kugara kwekurova kwemoyo.
- Kuongororwa kwetsandanyama: Kutora chidimbu chidiki chetsandanyama wochiongorora.
Nzira yekurapa uye kubata nayo sei?
Kurapa kukuru kweizvi ndekuona nekudzivirira zvinokukonzera . Izvi zvinoreva kuchinja kudya kwako uye maitiro ako ekurovedza muviri.
Pamusoro pezvo, kune mishonga yekudzora huwandu hwepotassium mumuviri.
- Mushonga weDichlorphenamide (Keveyis) unotenderwa kurapa hypoKPP nehyperKPP.
- Dzimwe nguva vanachiremba vanokurudzirawo mushonga unonzi Acetazolamide (Diamox) .
- Mishonga yePotassium inopiwa kune avo vane HypoKPP.
- Munhu ane HyperKPP dzimwe nguva anogona kudzora kushaya simba kwake nekunwa chinwiwa chine shuga (semuenzaniso, soda) kana changotanga.
Chinhu chinonyanya kukosha ndechekuti, usamborega kutora kana kurega mishonga uri wega. Ita zvese uchingoudzwa nachiremba wako chete. Kana ukasangana nekushaya simba kwakakomba, kunetseka kufema, kana kurwadziwa pachipfuva, enda kuEmergency Department (ETU) yechipatara chiri pedyo nekukasika.
Unogona kudzora dambudziko iri zvakanyanya nekuchinja mararamiro ako zvishoma nezvishoma.
- Chikafu: Kana uine potassium yakawanda (hyperKPP), unofanira kuderedza kudya zvine potassium yakawanda semabhanana, matende, broccoli, nenzungu. Kana uine potassium shoma (hypoKPP), unofanira kuderedza kudya zvine carbohydrate yakawanda sechingwa, pasta, mupunga, uye zvihwitsi. Wana mazano akakodzera kubva kuna chiremba wako nezveizvi.
- Kurovedza muviri: Kungofanana nekurovedza muviri zvakanyanya, kusarovedza muviri kwakaipawo. Taura nachiremba wako nezvedanho rekurovedza muviri rakakunakira.
Mharidzo Yekuenda Nayo Kumba
- Kuremadzwa Kwemuviri Kwekutanga (Primary Periodic Paralysis - PPP) hakusi kuremara kwemuviri chete, asi chikanganiso chemajini chinoitika muma ion channels emasero emhasuru.
- Pane zvinhu zvinogona kukonzera chirwere ichi. Ngwarira zvinhu zvakaita sekudya, kurovedza muviri, uye kushushikana, uye ziva uye dzivisa zvinhu zvinokukanganisa.
- Kana zviratidzo zvikaonekwa, zvakakosha kuona nyanzvi kuti iongorore chirwere nemazvo.
- Vanhu vazhinji vanogona kubudirira kudzora chirwere ichi uye kurarama hupenyu hune simba kuburikidza nekuchinja mararamiro avo uye mishonga yavakapihwa nachiremba wavo.
- Gara uchitevedzera zano rachiremba wako. Usazvisarudzire wega, zvakaita sekutora mishonga kana kuchinja kudya kwako.
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