Ingaba oku kurhawuzelela okungaqhelekanga kuyayichaphazela intliziyo yakho? Masifunde ngeCardiac Sarcoidosis!

Ngaba ngamanye amaxesha uziva udiniwe nje? Okanye ngaba uneentlungu esifubeni okanye ubunzima bokuphefumla? Usenokucinga ukuba ezi zizinto eziqhelekileyo. Nangona kunjalo, ezi zizinto ezingaqhelekanga kakhulu ezichaphazela intliziyo. I-Cardiac Sarcoidosis yenye yezifo ezinjalo, eyinkimbinkimbi kancinci, kodwa ukuba unolwazi olufanelekileyo, inokulawulwa. Namhlanje, siza kuthetha ngale nto ngendlela elula onokuyiqonda.

Yintoni iCardiac Sarcoidosis?

Ngamafutshane, iSarcoidosis sisifo esingaqhelekanga sokudumba esifumaneka emizimbeni yethu. Kule meko, iiseli ezincinci zokudumba ziyaqokelelana kwaye zenze amaqhuma (iigranuloma) kwizitho ezahlukeneyo zomzimba, ingakumbi kwiindawo ezifana nemiphunga, ii-lymph nodes, ulusu, kunye namehlo. La maqhuma anokuphazamisana nokusebenza ngokuqhelekileyo kwala malungu.

Ngoku, ukuba le meko ye-sarcoidosis ichaphazela intliziyo, yiloo nto siyibiza ngokuba yi-cardiac sarcoidosis . Le yinto engaqhelekanga kakhulu nakubantu abanesifo se-sarcoidosis. Nangona kunjalo, xa intliziyo ichaphazeleka ngolu hlobo, amanxeba anokwakheka kwimisipha yentliziyo nakwiindlela ezihamba ngazo imiqondiso yombane entliziyweni. Cinga ngayo njengesilonda eluswini emva kokwenzakala. La manxeba anokubangela ukubetha kwentliziyo okungaqhelekanga kunye neengxaki ngentliziyo.

Ixhaphake kangakanani le meko?

I-Cardiac sarcoidosis ayisosifo sixhaphakileyo. Kwihlabathi liphela, oogqirha badla ngokuxilonga kuphela i-2% ukuya kwi-5% yabantu abane-sarcoidosis kwezinye iindawo emzimbeni njengabanemeko yentliziyo. Nangona kunjalo, ezinye izifundo zibonisa ukuba kumazwe afana ne-United States, i-20% ukuya kwi-30% yabantu abane-sarcoidosis banokuba nale meko entliziyweni, kodwa basenokungaxilongwa.

Le meko ixhaphake kakhulu kumazwe afana neJapan, apho abantu abangaphezu kwesiqingatha abane-sarcoidosis nabo banesi sifo entliziyweni yabo. Nangona kunjalo, i-cardiac sarcoidosis ayiqhelekanga xa ithelekiswa ne-sarcoidosis echaphazela amanye amalungu omzimba.

Enye into ebalulekileyo ekufuneka uyiqaphele kukuba malunga nesithathu sabantu abane-cardiac sarcoidosis ababonisi zimpawu ze-sarcoidosis naphi na emzimbeni. Oku kuthetha ukuba intliziyo yakho isenokuba sisitho sokuqala esichaphazeleka sesi sifo.

Zithini iimpawu zesi sifo?

Iimpawu zeCardiac Sarcoidosis zingahluka kumntu nomntu. Abanye abantu basenokungabi nazo kwaphela iimpawu. Nangona kunjalo, kukho ezinye iimpawu eziqhelekileyo:

• Intlungu yesifuba: Isenokuvakala ngathi kukucinezelwa okanye ukucinezelwa.
• Ukuqhawukelwa ngumphefumlo:Usenokuziva uphelelwa ngumphefumlo, nokuba udiniwe kancinci okanye uphumle nje.
• Ukuquleka okanye isiyezi: Ungalahlekelwa zingqondo ngequbuliso uze uwe.
• Ukudinwa: Ukuziva udiniwe ngalo lonke ixesha, nokuba wenza ntoni na.
• Ukukhwehlela: Kusenokubakho ukukhwehlela okomileyo okungapheliyo.
• Ukudumba emilenzeni yakho: Iindawo ezifana nendawo yeqakala zinokudumba.
• Ukubetha kwentliziyo okungaqhelekanga / Ukubetha kwentliziyo okungaqhelekanga: Isantya sentliziyo sinokunyuka ngequbuliso, sehle, okanye sivakale ngathi asiphumeleli.

Ukuba unenye okanye ngaphezulu kwezi mpawu, musa ukuzityeshela. Kungcono ukufuna ingcebiso kagqirha.

Kutheni i-Cardiac Sarcoidosis isenzeka?

Enyanisweni, oogqirha abakafumani sizathu sithile sesi sifo. Nangona kunjalo, abaphandi bakholelwa ukuba ukwakheka kwemfuza yabanye abantu kunye nezinto ezingqongileyo zinokudlala indima. Oko kukuthi, imizimba yabanye abantu inokusabela kwinto ethile ekwindawo (umzekelo, intsholongwane, intsholongwane, okanye uthuli) ebangela le meko yokudumba. Nangona kunjalo, oku kusekwinqanaba lophando.

Sifunyaniswa njani esi sifo?

Ukuba ukrokrela ukuba une-cardiac sarcoidosis, ugqirha wakho uza kuqala akuhlole umzimba. Emva koko uza kubuza ngembali yakho yezonyango . Oku kuthetha izinto ezifana nezigulo zakho zangaphambili kunye nokuba kukho umntu kusapho lwakho okhe waba neemeko ezifanayo.

Ukongeza, kuza kuhlolwa iindlela ezahlukeneyo zokuvavanya ukubetha kwentliziyo okungahambelaniyo. Ugqirha uza kujonga iimpawu ze-sarcoidosis kwenye indawo emzimbeni wakho, kunye nobungqina beempawu ezifanayo entliziyweni yakho.

Zithini iimvavanyo zokuxilonga?

Kukho iimvavanyo ezininzi zokuxilonga ngokuchanekileyo esi sifo:

• I-Electrocardiogram (EKG/ECG): Le irekhoda umsebenzi wombane wentliziyo yakho njengepateni. Ingabona naziphi na iingxaki kwisingqisho sentliziyo yakho.
• I-Echocardiogram: Oku kufana nokuskena kwentliziyo. Kusebenzisa amaza esandi ukujonga imilo nobukhulu bentliziyo, indlela amagumbi entliziyo kunye neevalvu ezisebenza ngayo, nokunye. Ngamanye amaxesha kwenziwa i-transthoracic echo.
• Isixhobo sokubona iHolter: Esi sisixhobo esincinci osinxiba iiyure ezingama-24 ukuya kwezingama-48. Sinceda ukurekhoda rhoqo imisebenzi yentliziyo yakho ngelixa usenza imisebenzi yakho yemihla ngemihla.
• I-Positron Emission Tomography (i-PET scan):Olu luvavanyo olukhethekileyo. Luluncedo kakhulu ekuchongeni iindawo ezinokuvuvukala kunye namanxeba entliziyweni.
• I-MRI yentliziyo (Cardiac Magnetic Resonance Imaging): Oku kusebenzisa amasimi emagnethi kunye namaza erediyo ukuvelisa imifanekiso eneenkcukacha zentliziyo. Oku kunokunceda ukubona ngokucacileyo umonakalo kunye namanxeba kwimisipha yentliziyo.

I-Sarcoidosis idla ngokufunyaniswa kwezinye iindawo zomzimba ngokuthatha i-biopsy (isampulu encinci yezicubu uze uyihlolisise phantsi kwe-microscope). Nangona kunjalo, oku akuqhelekanga entliziyweni, njengoko kunzima ukufumana isampuli kwindawo echanekileyo yentliziyo apho ingxaki ikhoyo.

Olu vavanyo lwemifanekiso lukwanceda oogqirha ukuba bafumanise amanqanaba e-cardiac sarcoidosis. Ingahluka ukusuka kwencinci ukuya kwenzima. Ingadlula kumanqanaba okuqala, amanqanaba aqhubekekayo, kunye namanqanaba asebenzayo, okukhokelela ekuphazamisekeni kwentliziyo kunye ne-fibrosis.

Zithini iindlela zonyango?

Iindaba ezimnandi zezokuba kukho unyango lwe-cardiac sarcoidosis. Ugqirha wakho uya kukhetha unyango olufanelekileyo kwimeko yakho. Nazi ezinye zeendlela zonyango ezisetyenziswa kakhulu:

• Amayeza e-corticosteroid: La asebenza ngokunciphisa ukudumba emzimbeni. I-Prednisolone liyeza elinikwa rhoqo kweli qela.
• Ezinye izinto ezithintela amasosha omzimba: Ngamanye amaxesha, ukuba ii-corticosteroids zodwa azanele, okanye ukuba iziphumo zazo zimbi kakhulu, kunokunikwa amanye amayeza okulawula amasosha omzimba ekubeni asebenze kakhulu.
• Amayeza okulwa nokubetha kwentliziyo: Ukuba ukubetha kwentliziyo akuhambelani kakuhle, kukho amayeza akhethekileyo okukulawula.
• I-Pacemaker: Ukuba intliziyo ibetha ngokukhawuleza kakhulu, esi sixhobo sincinci sifakwa entliziyweni ukuze sihlale sisebenza rhoqo.
• I-ICD (ICD) efakelweyo kwi-Cardioverter Defibrillator: Esi sixhobo sifakelwa xa kukho umngcipheko we-arrhythmias eyingozi esongela ubomi. Ngamaxesha anjalo, senza intliziyo ifumane umbane omncinci ukuze kubuyiselwe isigqi esiqhelekileyo.
• Ukususwa kweCatheter: Olu lunyango lokubetha kwentliziyo okungahambelaniyo. Iindawo ezisentliziyweni ezibangela imiqondiso yombane engahambelaniyo ziyafunyanwa kwaye zonakaliswe kusetyenziswa iCatheter.

Amaxesha amaninzi, ukuba isifo siba sibi kakhulu kangangokuba sikhokelela ekuphelelweni yintliziyo , kunokufuneka ukuba kufakelwe intliziyo .

Ngawaphi amayeza kunye nonyango olusetyenziswa kakhulu?

Oogqirha badla ngokuqala ngedosi ephezulu ye-corticosteroid ebizwa ngokuba yi-prednisone (amagama eempawu aquka iSterapred® okanye iRayos®). Oku kuthathwa iinyanga ezininzi. Emva koko idosi iyancitshiswa kancinci kancinci. Ukuba isifo sifunyenwe kwaye sinyangwa kwangethuba, la mayeza anokulawula kakhulu iimpawu.

Ngaba kukho naziphi na iziphumo ebezingalindelekanga zonyango?

Amayeza e-corticosteroid afana ne-Prednisone anokubangela ezinye iziphumo ebezingalindelekanga xa esetyenziswa ixesha elide. Yiyo loo nto ugqirha wakho eza kukujonga rhoqo. Iziphumo ebezingalindelekanga eziqhelekileyo zezi:

• I-Osteoporosis: Ukubuthathaka kwamathambo.
• Iintsholongwane: Umngcipheko wokufumana izifo unokwanda njengoko amandla omzimba okuzikhusela ehla.
• Igazi elonyukayo.
• Iswekile yegazi ephezulu.
• Ukuhamba kweemvakalelo.
• Ukungalali.

Nangona unyango lwe-catheter ablation luphumelela ekuqaleni, abanye abantu, ingakumbi abo bane -ventricular tachycardia (ukubetha kwentliziyo okukhawulezayo okuqala kwigumbi elisezantsi lentliziyo), banokuphinda babuye kwi-86% yamatyala.

Umngcipheko we-cardiac sarcoidosis ophinda ubuye emva kokufakelwa intliziyo ungaphantsi kwe-10%.

Ngaba iCardiac Sarcoidosis yimeko enzulu?

Oku kuya kwahluka ngokuxhomekeke kwimeko yakho. Iziphumo ezilungileyo ziyafumaneka ukuba isifo sifunyenwe kwangethuba kwaye unyango luqalwe kwangethuba. Ukuba unyango lulibaziseka, imeko inokuba mandundu ngakumbi.

Ukuba uneemeko ezifana noxinzelelo lwegazi oluphezulu kwimiphunga ( uxinzelelo oluphezulu kwimithambo yegazi ethwala igazi ukuya emiphungeni) okanye i-ventricular aneurysm (ubuthathaka bodonga lwenye yeegumbi ezisezantsi zentliziyo ezivuthuluka njengebhaluni), i-prognosis isenokungabi ntle kangako.

Ungaphila ixesha elingakanani nale sifo?

Ukuba unyango luqalwe kwangethuba, abantu abaninzi baphila kakuhle.

Izifundo zifumanise ukuba phakathi kwama-83% nama-93% abantu abaphila ne-cardiac sarcoidosis basaphila emva kweminyaka eli-10.

Izinga lokusinda emva kokufakelwa intliziyo liyi-80% nangaphezulu kunyaka omnye nowesihlanu.

Khumbula, nangona ezi zibalo zibonisa iimeko eziqhelekileyo, imeko yakho inokwahluka. Ngoko ke thetha nogqirha wakho ukuze ufumane ukuqonda okucacileyo ngemeko yakho.

Ngaba iCardiac Sarcoidosis ingabulala?

Ewe, i-cardiac sarcoidosis ingaba yingozi kwabanye abantu. Umngcipheko wokufa uphezulu, ingakumbi ukuba i-ventricle yasekhohlo yentliziyo yakho ayipompi igazi ngokufanelekileyo.

Ukufa kwentliziyo ngequbuliso kudla ngokubangelwa kukubetha kwentliziyo okungalawulekiyo (ukubetha kwentliziyo okungaqhelekanga kwigumbi elisezantsi lentliziyo). Ukuba usemngciphekweni, ugqirha wakho unokucebisa ukuba ufake isixhobo se-ICD.

Ndingazinyamekela njani?

Ngenxa yokuba le meko inokuba mandundu kwixesha elifutshane, kubalulekile ukusela amayeza njengoko ugqirha wakho ekuyalele. Kusenokufuneka uthathe amayeza afana nePrednisone ukuya kuthi ga kunyaka. Ukuba ufumana naziphi na iziphumo ebezingalindelekanga ezivela kula mayeza, xelela ugqirha wakho. Kodwa ungayeki ukuwasela amayeza ngaphandle kwengcebiso kagqirha.

Ndifanele ndimbone nini ugqirha?

Kuya kufuneka uphinde wenze uvavanyo lwemifanekiso malunga nenyanga okanye iinyanga ezintandathu emva kokuba uqale ukusebenzisa ii-steroids (umz., i-prednisone). Oku kunceda ugqirha wakho ukuba agqibe ukuba iyeza lisebenza kakuhle kangakanani kunye nedosi ekufuneka iqhubeke.

Nokuba emva kokuba ii-steroids ziyekiwe okanye idosi inciphisiwe, kufuneka uqhubeke nokuhlolwa ngugqirha wakho ubuncinane iminyaka emithathu. Oku kungenxa yokuba i-cardiac sarcoidosis inokuphinda ivele. Malunga nama-40% abantu baya kuphinda babuye esi sifo ngale ndlela.

Ndingaya nini kwiYunithi yoNyango oluNgxamisekileyo (i-ETU) ?

Ukuba ngequbuliso ufumana nayiphi na kwezi mpawu , yiya kwigumbi likaxakeka lesibhedlele esikufutshane ngoko nangoko okanye utsalele umnxeba ku-1990:

• Intlungu yesifuba enobunzima bokuphefumla
• Ukubetha kwentliziyo okuqhubekekayo
• Ukudinwa kunye/okanye ukuquleka

Ezi zinokuba ziimpawu zesifo esiyingozi sentliziyo.

Ndingayibuza yiphi imibuzo ugqirha?

Ungalibali ukubuza le mibuzo xa ubona ugqirha:

• Ndingayilawula le meko ngamayeza odwa?
• Injani imbono yam, ingakumbi xa ucinga ngemeko endikuyo ngoku?
• Isebenza kakuhle kangakanani i-ventricle yam yasekhohlo?
• Kufuneka ndithathe amayeza ixesha elingakanani?
• Zeziphi iinguqu endinokuzitshintsha kwindlela endiphila ngayo?

Okokugqibela, izinto ekufuneka uzikhumbule (Umyalezo Wokuya Ekhaya)

I-Cardiac Sarcoidosis ligama eloyikisayo kancinci, kodwa kubaluleke kakhulu ukuliqaphela.

Iziphumo ezilungileyo zinokufumaneka ukuba esi sifo sichongiwe kwangethuba kwaye unyango luqala kwangethuba.

Ngoko ke, ukuba unale mpawu, ungazityesheli kwaye ufune ingcebiso kugqirha. Thatha amayeza achazwe ngugqirha wakho kanye ngexesha. Thetha nogqirha wakho malunga nemiphumo emibi. Yiya kuhlolo lwezonyango ngexesha. Ukuba wenza ezi zinto ngokuchanekileyo, ungaphila kakuhle nale meko. Awuwedwa, kwaye oogqirha bakhona ukukunceda.

Isifo sentliziyo , i-sarcoidosis, ukudumba kwentliziyo, ukuphefumla okufutshane, iintlungu zesifuba, ukubetha kwentliziyo okungahambelaniyo, ii-corticosteroids