Ngaba ngamanye amaxesha uziva ngathi ulahlekelwa lulawulo lomzimba wakho? Ngaba uziva ngathi uyashukuma xa umi okanye uhamba, okanye uziva ngathi amazwi akho ayabhideka xa uthetha? Ezi zinto azizenzeki nje ngengozi. Mhlawumbi kungenxa yengxaki ekwinxalenye encinci yobuchopho bethu. Yiloo nto siza kuthetha ngayo namhlanje.
Yintoni iCerebellar Degeneration? Masiyiqonde ngokulula!
Kulungile, masiqale sijonge ukuba yintoni le cerebellum . Kukho inxalenye encinci yobuchopho bakho, esezantsi kancinci, esiyibiza ngokuba yi-cerebellum . Incinci, kodwa yenza umsebenzi omninzi obalulekileyo. Cinga ngayo, ilawula ibhalansi yakho, ikunceda ume kwaye uhambe ngaphandle kokushukuma, igcina intetho yakho icacile, kwaye yenza amalungu akho asebenze kakuhle.
Ngoku, yintoni ukuwohloka ? Ngamafutshane, ukuwohloka kukonakala okanye ukufa kancinci kancinci kweeseli zemithambo-luvo kwi-cerebellum. Ngoko ke, ukuwohloka kwe-cerebellar yimeko apho iiseli zemithambo-luvo kwi-cerebellum zonakele kwaye zingakwazi ukusebenza kakuhle.
Kutheni oku kusenzeka? Zithini izizathu zoku?
Kunokubakho izizathu ezininzi ezibangela le meko. Makhe sijonge ezona ziphambili.
1. Ukusetyenziswa kakhulu kotywala kunye nokungabikho kokutya okunempilo
Esi sesona sizathu siphambili esibonakala rhoqo. Xa sisela utywala obuninzi, imizimba yethu ayifumani ngokwaneleyo i-vitamin B1 ebizwa ngokuba yi-thiamine . Oku kusenokuba kungenxa yokuba asifumani ngokwaneleyo ekutyeni, okanye kungenxa yokuba umzimba awukwazi ukuyifunxa. I-Thiamine ibaluleke kakhulu ekusebenzeni kweeseli zengqondo. Xa incipha, iiseli zengqondo ziqala ukonakala.
2. Iingxaki ze-Neurodegenerative
Kukho izifo ezithile ezibangela ukuba iiseli zemithambo-luvo kwintambo yethu yomqolo kunye neendawo ezahlukeneyo zobuchopho, ingakumbi i-cerebellum, zife kancinci kancinci.
- I-Ataxia sisifo esiphambili solu hlobo. Sibonakaliswa kukulahlekelwa kulawulo lomzimba kunye nokulungelelaniswa kwawo.
- I-Multiple System Atrophy yenye isifo esinjalo.
- Isifo esingaqhelekanga esibizwa ngokuba yiCreutzfeldt-Jakob Disease naso sisenokuba ngunobangela.
- Isifo i-multiple sclerosis (MS) ngamanye amaxesha siyayichaphazela le nto.
Ezinye zezi zifo zenkqubo yemithambo-luvo zinokufunyanwa njengelifa , oko kuthetha ukuba zidluliselwa kubazali ukuya ebantwaneni ngee-genes. Ezinye zinokukhula ngexesha lobomi.
3. Iimeko ezenzekayo xa umntu enesifo somhlaza (iiParaneoplastic Syndromes)
Eli libali elinzima kancinci. Xa abanye abantu bevelisa iiseli zomhlaza, inkqubo yabo yokuzikhusela komzimba izama ukulwa nomhlaza. Nangona kunjalo, ngamanye amaxesha le nkqubo yokuzikhusela komzimba iqala ngempazamo ukuhlasela iiseli eziphilileyo engqondweni. Xa i-cerebellum yonakele, siyibiza ngokuba yiParaneoplastic Syndromes . Le meko ixhaphake kakhulu kubantu abaneemhlaza ezifana nomhlaza webele, umhlaza wesibeleko, umhlaza wesibeleko, iHodgkin's Lymphoma yabantu abadala, kunye nomhlaza wemiphunga weeseli ezincinci.
Ngubani ochaphazeleka kakhulu yile meko?
Nangona kungenakwenzeka ukutsho ngqo ukuba ngubani oza kuphuhlisa oku, abanye abantu basengozini enkulu.
- Umzekelo, imeko ye-paraneoplastic ekhankanyiweyo apha ngasentla ibonakala rhoqo phakathi kwabasetyhini abangaphezu kweminyaka engama-50 ubudala.
- Kodwa ngokubanzi, amadoda anokuba neengxaki zokulinganisela kunye nokulungelelanisa njengoko ekhula.
- Ukuwohloka kobuchopho okubangelwa kukungaseli kotywala okanye ukungondleki kakuhle kudla ngokubonakala kubantu abakwiminyaka ephakathi, ingakumbi kubantu abasele besebenzisa utywala ixesha elide.
- Le meko inokwenzeka nakubantwana abanezifo ezithile ezizuzwe njengelifa.
"Olu hlobo lokuwohloka kwengqondo aluqhelekanga kangako. Ngaphantsi kwe-1% yabantu abanomhlaza baba neemeko ezibangela ukuba umntu angakwazi ukuzikhusela. Nangona kunjalo, ukuwohloka kwengqondo okubangelwa butywala kuxhaphake kancinci."
Zeziphi iimpawu ekufuneka siziqwalasele?
Iimpawu zesi sifo zingahluka kancinci kumntu nomntu, kodwa kukho ezinye iimpawu eziqhelekileyo:
- Ukulahlekelwa yibhalansi (Iingxaki zokulinganisela) , ukuziva unesizungu okanye ujikeleza (iVertigo okanye isizungu). Kungavakala ngathi uqengqeleka phantsi.
- Ukuziva ungenawo amandla emisipha (Hypotonia) . Amalungu asenokuziva ngathi awanabomi okanye atyhafile.
- Iingxaki zamehlo: Ukubona izinto ezimbini ngaxeshanye (ukubona kabini), iintshukumo zamehlo ezikhawulezayo nezingalawulekiyo (nystagmus).
- Ukungakwazi ukulungelelanisa iintshukumo zamalungu ngendlela eyiyo (i-Ataxia) . Umzekelo, xa uthatha ikomityi, isandla sakho siyangcangcazela, okanye awukwazi ukufikelela kwikomityi ngendlela eyiyo.
- Iingxaki ngezakhono zomzimba ezicothayo . Izinto ezifana nobunzima bokuphakamisa intloko yakho, ukungakwazi ukusebenzisa iingalo okanye imilenze yakho ngokufanelekileyo.
- Ukungcangcazela okanye ukungcangcazela kwamalungu omzimba xa uzama ukwenza isenzo .
- Ukuhamba ngokungazinzi okanye ngokungalungelelananga kunye nokuhamba okubanzi, ukushukuma ukusuka kwelinye icala ukuya kwelinye, kunye nokuhamba ngemilenze yomibini isasazeke ngokubanzi .
Ukongeza kwezi mpawu, abantu abanemeko yeparaneoplastic banokufumana ezinye iimpawu ezininzi, ngakumbi:
- Ukuncipha kwenkumbulo, amandla okuqiqa, kunye nokukwazi ukucinga `(Dementia)`.
- Intetho iyacotha kwaye ayicaci (iDysarthria) .
Kwakhona, abanye abantu abane-cerebral palsy banokuhlangabezana nezinye iimeko ezifana nezi:
- Ingxaki Yokunqongophala Kwengqalelo/Ukuphazamiseka Kokusebenza Kakhulu (ADHD)
- Ingxaki ye-Autism Spectrum I-Schizophrenia-yeemvakalelo `(Schizophrenia)`
Oogqirha bayibona njani le nto?
Ukuba unale mpawu, xa ubona ugqirha, baya kuqala bakubuze imibuzo emininzi malunga neempawu zakho. Zithini iimpawu zakho, zinzima kangakanani, ziyichaphazela njani imisebenzi yakho yemihla ngemihla, kwaye ingaba kukho nabani na kusapho lwakho okhe waba nale meko.
Emva koko, ugqirha uya kucebisa iimvavanyo ezininzi ukuqinisekisa imeko:
- Iskena se-MRI (Magnetic Resonance Imaging) okanye i-CT (Computed Tomography): Ezi zithatha imifanekiso ecacileyo yengqondo kunye nezicubu zayo. Ukuba kukho i-brain atrophy, ezi skena zinokubonisa indlela i-cerebellum enciphe ngayo kwaye inciphe ngayo. Zinokubona nezinye iingxaki, ezifana nomhlaza wobuchopho, okanye iimpawu zestroke.
- Ukubethelwa koMgogodla/Ukubhaqwa kweLumbar: Ulwelo olujikeleze ubuchopho bethu kunye nomqolo lubizwa ngokuba yiCerebrospinal Fluid (CSF) . Kuthathwa isampulu encinci yolu lwelo kwaye ivavanywe. Ngamanye amaxesha, umxholo wolu lwelo unokusetyenziswa ukufumanisa isifo sokuzikhusela komzimba, njenge-paraneoplastic syndrome.
- Uvavanyo lweGazi: Ngamanye amaxesha inqanaba lee -antibodies egazini liyajongwa. Ezi antibodies zinokuphakama kubantu abanomhlaza kunye neemeko ze-paraneoplastic.
- Uvavanyo lweMfuzo: Ukuba ugqirha ucinga ukuba le yimeko yemfuza, angenza uvavanyo lwemfuza.
Ngaba ikho indlela yokunyanga le nto? Zithini iindlela zonyango?
Inyaniso kukuba okwangoku akukho nyango lwe-cerebral palsy. Nangona kunjalo, unyango luxhomekeke kwisizathu. Kukwakho namayeza okunceda ukulawula ezinye zeempawu (ezifana nokungcangcazela, ubunzima bokuhamba, kunye nesiyezi).
- Unyango lweemeko ze-paraneoplastic:
- Unyango lomhlaza: I-Chemotherapy , Unyango lweMisebe .
- Izinto ezithintela amajoni omzimba .
- Unyango lwe-immunotherapy .
- Utyando lokususa ithumba elinomhlaza, kunye ne-chemotherapy kunye nonyango lwe-radiation, zinokudityaniswa.
- Unyango lweemeko ezibangelwa butywala:
- Yeka ukusela utywala ngokupheleleyo. Le yeyona nto ibalulekileyo.
- Utshintsho kwindlela yokutya: Kufuneka wongeze ukutya okune-thiamine kunye nezinye iivithamini ze-B (umz., ukutya okuziinkozo, inyama engenamafutha, intlanzi) ekutyeni kwakho.
- Ukuthatha izongezo ze-thiamine .
Nokuba yintoni na imbangela ye-cerebral palsy, unyango olufana nonyango lomzimba, unyango lomsebenzi, okanye unyango lokuthetha lunokufuneka. Ezi zinokunceda:
- Phuhlisa izakhono zomzimba ukuze ukwazi ukwenza imisebenzi yemihla ngemihla ngokuzimela.
- Yomeleza izihlunu kwaye uphucule ukulungelelaniswa kwazo .
- Ukuphucula ubunzima bokuginya, ubunzima bokuthetha, kunye nezakhono zolwimi .
Ngaba oku kungathintelwa?
Isifo sengqondo esibangelwa butywala sinokuthintelwa kakhulu ngokuzikhwebula etywaleni . Nangona kunjalo, okwangoku akukho ndlela iqinisekisiweyo yokuthintela ezinye iintlobo zesifo sengqondo esibangelwa butywala.
Kuza kwenzeka ntoni emva koko? Iza kwenzeka njani imeko?
Uqikelelo lwesi sifo luxhomekeke kwisizathu esiyintloko.
- Ukunyanga umhlaza, ukuyeka utywala, okanye ukutshintsha indlela otya ngayo ngamanye amaxesha kunokucothisa okanye kumise oku kwehla.
- Nangona kunjalo, kwezinye iimeko zokuwohloka kwemithambo-luvo, esi sifo sinokuqhubeka ngokuhamba kwexesha ngamanani ahlukeneyo.
Njengoko isifo siqhubeka, abantu banokulahlekelwa kukulungelelanisa amalungu omzimba baze bakhubazeke kakhulu. Basenokufuna ukusebenzisa isitulo esinamavili okanye esinye isixhobo sokuncedisa ukuhamba. Oku kunokunceda nasekuthinteleni ukuwa. Ukuba abakwazi ukwenza imisebenzi yemihla ngemihla bodwa, banokulahlekelwa kukwazi kwabo ukuphila ngokuzimela . Abanye banokude balale ebhedini.
Ukuba abantwana bakhula nale meko, banokufumana ukulibaziseka kokukhula .
Ufanele uye nini ngokuqinisekileyo kugqirha?
Ukuba ubona naluphi na utshintsho okanye ubunzima malunga nokulinganisela kwakho, intetho, umbono, okanye imisebenzi yemihla ngemihla, bona ugqirha ngoko nangoko . Abanye abantu bacinga ukuba olu lutshintsho oluqhelekileyo njengoko bekhula. Nangona kunjalo, lunokuba ziimpawu zengxaki enkulu ngakumbi. Ngoko ke ukuba uneengxaki, kungcono ukuya kuhlolwa.
Yeyiphi imibuzo omele uyibuze ugqirha?
Ukuba wena okanye umntu ohlala nawe une-cerebral palsy, kungcono ukubuza ugqirha wakho le mibuzo:
- Zeziphi iinguqu endinokuzitshintsha kwindlela endiphila ngayo ukuze ndiphile kakuhle nesi sifo?
- Ndingalufumana phi uncedo? (umz. amaqela enkxaso)
- Ngaba kufuneka ndiqale unyango lomzimba, unyango lomsebenzi, okanye unyango lokuthetha?
- Yintoni unobangela wesi sifo?
- Ingaba esi sifo siza kusasazeka ngakumbi? Ukuba kunjalo, siza kusasazeka ngokukhawuleza kangakanani?
Eyona nto ibalulekileyo ekufuneka siyikhumbule!
Ukonakala kweCerebellar yimeko echaphazela inxalenye yengqondo yethu elawula ulungelelwano, intshukumo yemisipha, kunye nentetho. Oku kunokubangela ubunzima bokuhamba, ukuthetha, kunye nokwenza imisebenzi yemihla ngemihla. Zininzi izizathu zoku. Amayeza kunye nokuvuselelwa kunokunceda ukulawula iziphumo zale meko. Ke ngoko, kubalulekile ukufuna iingcebiso zonyango ukuba uneempawu.
👩🏽⚕️ Imibuzo eyongezelelweyo (Ii-FAQ)
💬 Ingaba iCerebellar Degeneration sisifo esibangela ukuba ingqondo inyibilike?
Asikuko konke ubuchopho. Emazantsi entloko yethu kukho i-'Cerebellum' - le yiyo elawula ibhalansi yemizimba yethu. Le yimeko apho iiseli zemithambo-luvo kwi-cerebellum zifa kancinci kancinci ngenxa yemeko yempilo (umzekelo, ukusela utywala ngokugqithisileyo, isifo semfuza, okanye umhlaza).
💬 Isigulana siziva njani xa inxalenye yomthambo isifa?
Ngenxa yokuba isigulane silahlekelwa yibhalansi, sihamba sishukuma, njengomntu onxilileyo. Kwakhona, xa sisenza imisebenzi ngezandla (njengokucofa iqhosha ngokuchanekileyo), izandla ziqala ukungcangcazela (ukungcangcazela ngenjongo), ilizwi liyadideka, kwaye amehlo aqala ukuhamba ukusuka kwelinye icala ukuya kwelinye ngokungalawulekiyo (nystagmus).
💬 Ngaba ikho indlela ehlala ihleli yokunyanga oku?
Ngelishwa, akukho nyango luhlala luhleli lokufa kweeseli zemithambo-luvo. Nangona kunjalo, ukuba unobangela woku (umzekelo, ukusela utywala okanye ukunqongophala kweevithamini) uchongiwe kwaye unyangwa kwangethuba, esi sifo sinokuthintelwa ukuba singabi mandundu. Kubalulekile nokuziqhelanisa nokulinganisela ngokusebenzisa unyango lomzimba.
Ukuwohloka kobuchopho , ukuwohloka kobuchopho, izifo zobuchopho, ukulahleka kokulinganisela, ubunzima bokuhamba, izifo zemithambo-luvo, ukusetyenziswa kotywala











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