Masifunde yonke into malunga nee-capsules ze-cysteamine ngendlela elula.

Ngaba wena okanye umntu omaziyo unikwe iyeza elibizwa ngokuba yi-cysteamine ngugqirha? Ukuba kunjalo, kubalulekile ukufunda kancinci ngale mithi. Usenokuziva ungaqhelekanga xa usiva eli gama, kodwa ungakhathazeki. Masithethe ngalo ngokulula, ngokungathi uthetha nomhlobo.

Luhlobo luni lweyeza i-cysteamine?

Ngamafutshane, i-cysteamine liyeza elinceda ekuqhekezeni into ebizwa ngokuba yi-cystine emizimbeni yethu. Ngokukodwa, isetyenziselwa ukunyanga imeko ebizwa ngokuba yi-nephropathy cystinosis . Esi sisifo esinokuchaphazela abantwana abancinci kunye nabantu abadala.

Cinga ngale nto, xa izinto emizimbeni yethu zingasebenzi kakuhle, izinto ezithile zinokuqokelelana ngokugqithisileyo. Umzekelo, kumntu one-nephropathic cystinosis, i-amino acid ebizwa ngokuba yi-cystine iqokelelana emzimbeni, ingakumbi ezintso. Oku kungonakalisa izintso. I-Cysteamine inceda ekunciphiseni ubungakanani be-cystine.

Into ebalulekileyo ekufuneka uyikhumbule: Eli yeza alilonyango olupheleleyo lwesi sifo. Nangona kunjalo, linokunceda ekulawuleni isifo kwaye linciphise umonakalo waso. Kungoko ke, kubalulekile ukulisebenzisa kanye njengoko ugqirha wakho ekuyalele.

Eli yeza ngamanye amaxesha linokumiselwa ngoogqirha kwezinye iimeko. Ukuba unemibuzo ngalo, buza ugqirha wakho okanye ikhemisti. Eli yeza likwafumaneka phantsi kwegama lebrendi elithi Cystagon .

Ndimele ndixelele iqela lezonyango ntoni ngaphambi kokuba ndisebenzise eli yeza?

Ngaphambi kokuba uqale ukusebenzisa i-cysteamine, qiniseka ukuba uxelela ugqirha wakho okanye iqela lezempilo malunga noku:

• Ukuba unayo nayiphi na kwezi zinto:
• Iingxaki zamathambo (umz., amathambo abuthathaka, ukwaphuka lula)
• Ukuxinezeleka okanye ezinye iingxaki zenkqubo yeemvakalelo
• Ukuba unembali yesifo segazi
• Ukuba ukhe wopha isisu ngaphambili (imbali yokopha esiswini)
• Isifo sesibindi - kuba amayeza amaninzi acutshungulwa sisibindi.
• Ukuxhuzula, okufana nesifo sokuwa
• Iimeko zesikhumba okanye ukuva ubunzima
• Iingxaki zesisu okanye zamathumbu
• Ukuba une-allergy kule nto:
• Nge-cysteamine
• Iyeza le-penicillamine
• Naliphi na elinye iyeza, ukutya, idayi okanye izithinteli
• Ukuba ukhulelwe okanye uzama ukukhulelwa.
• Ukuba ungumama oncancisayo.

Kubaluleke kakhulu ukuxelela ugqirha wakho lonke olu lwazi, kuba kulapho kuphela apho baya kukwazi ukugqiba khona ukuba eli yeza likulungele na okanye kufuneka unyamekele ngokukodwa.

Ndingayisebenzisa njani le yeza?

Eli yeza liza likwimo yekhaphu oyisebenzisa ngomlomo. Lithathe neglasi yamanzi. Landela imiyalelo ekwileyibhile kagqirha njengoko ugqirha wakho ekuyalele.

• Ngamanye amaxesha ungayivula ikhapsuli uze uyixube iyeza ibe kukutya okugutyiweyo. Kodwa jongana nogqirha wakho okanye nekhemisti ngaphambi kokuba wenze njalo.
• Sela amayeza ngexesha elifanelekileyo, ngomlinganiselo ofanelekileyo . Musa ukuwasela amaxesha amaninzi okanye ngaphezulu kunokuba ugqirha wakho ekuxelela.

Ukuba unika abantwana eli yeza:

Eli yeza likwanikwa abantwana kwiimeko ezithile. Nangona kunjalo, qiniseka ukuba uxoxa ngale nto nogqirha wezingane kwaye ulandele imiyalelo yakhe. Kusenokubakho amanyathelo akhethekileyo okhuseleko ekufuneka athathwe xa kunikwa abantwana amayeza.

Yintoni omawuyenze ukuba uthatha amayeza amaninzi kakhulu? (Ukusebenzisa amayeza amaninzi kakhulu):

Ukuba ucinga ukuba usele kakhulu eli yeza, fowunela iziko lokulawula ityhefu okanye igumbi likaxakeka elikufutshane ngoko nangoko. Musa ukuchitha ixesha.

Kubalulekile: Eli yeza limiselwe wena wedwa. Ungaze wabelane ngalo nabanye, nokuba baneempawu ezifanayo nezakho.

Yintoni omawuyenze ukuba uphoswe yidosi yeyeza?

Ukuba ulibele ukuthatha idosi, yithathe kwangoko xa ukhumbula. Nangona kunjalo, ukuba kungaphantsi kweeyure ezi-2 ngaphambi kokuba uthathe idosi elandelayo, yitsibe idosi oyiphosileyo uze uthathe idosi elandelayo ngexesha elicwangcisiweyo. Ungaze uthathe idosi ephindwe kabini okanye idosi eyongezelelweyo.

Ziziphi ezinye izinto ezinokusebenzisana nale mithi?

Eli yeza akulindelekanga ukuba libangele naluphi na unxibelelwano olukhulu. Nangona kunjalo, olu luhlu lusenokungabi nazo zonke iindlela zonxibelelwano.

Ngoko ke, xelela ugqirha wakho ngazo zonke ezinye iziyobisi ozisebenzisayo (ezibhalwe ngugqirha okanye ezithengiswa ngaphandle kwemvume kagqirha), imifuno, kunye nezongezo zokutya. Kwakhona, xelela ugqirha wakho ukuba uyatshaya, usela utywala, okanye usebenzisa iziyobisi ezingekho mthethweni. Ezinye izinto zinokuchaphazela amayeza akho.

Zeziphi izinto ekufuneka uzilumkele xa usebenzisa eli yeza?

• Bona ugqirha wakho ukuze ahlolwe rhoqo. Kuya kufuneka wenze uvavanyo lwegazi rhoqo ukuze ujonge inani legazi lakho ngelixa usebenzisa eli yeza.
• Uziva ulele okanye unesizungu.Usenokuba nesiyezi. Kuphephe ukuqhuba, ukusebenzisa oomatshini, okanye ukwenza nantoni na efuna ukuphaphama ude wazi kakuhle ukuba eli yeza likuchaphazela njani.
• Musa ukuma okanye ukuhlala phantsi ngequbuliso, ingakumbi ukuba sele ukhulile. Oku kunokunciphisa umngcipheko wokuba nesiyezi kunye nokuwa.

Zithini iziphumo ebezingalindelekanga ezinokubakho zale yeza?

Njengalo naliphi na iyeza, i-cysteamine inokubangela ezinye iziphumo ebezingalindelekanga. Ezinye zinzima, ngelixa ezinye zihlala zingengobungozi.

Iziphumo ebezingalindelekanga ekufuneka zixelwe kugqirha okanye kwingcali yezempilo ngoko nangoko:

• Iimpendulo ze-allergy: ukurhawuzelela kwesikhumba, ukurhawuzelela okanye ukurhawuzelela, ukudumba kobuso, imilebe, okanye ulwimi.
• Intlungu okanye ukwaphuka kwamathambo.
• Iingxaki zokuphefumla.
• Utshintsho kwimbono.
• Ukudideka, ukudakumba, okanye olunye utshintsho kwimo yengqondo.
• Umchamo omnyama.
• Intlungu yamehlo.
• Ukuziva utyhafile okanye unentloko ebuhlungu, uyawa.
• Iimpawu ezifana nomkhuhlane okanye ukubanda, umphimbo obuhlungu.
• Ukuziva ugula okanye iimpawu ezifana nomkhuhlane.
• Isicaphucaphu, ukuhlanza.
• Izilonda zesikhumba ezimfusa.
• Ingxolo ezindlebeni.
• Ukuxhuzula.
• Ubunzima bokuchama okanye ukutshintsha ubungakanani bomchamo.
• Ukopha okanye ukukrweleka okungaqhelekanga.
• Ukuziva ubuthathaka okanye udiniwe ngendlela engaqhelekanga.
• Ukutyheli kwamehlo okanye ulusu – Oku kungaba yingxaki yesibindi.

Ukuba ubona into efana nale, funa ingcebiso kagqirha ngokukhawuleza.

Iziphumo ebezingalindelekanga ezihlala zingadingi nyango (kodwa kufuneka zixelwe kugqirha ukuba ziyaqhubeka okanye ziyakhathaza):

• Ukuqhinwa okanye urhudo.
• Ukozela.
• Intloko ebuhlungu .
• Ukulahlekelwa yintliziyo.
• Ukuphazamiseka kwesisu.
• Umoya ongathandekiyo.

Olu luhlu lusenokungabandakanyi zonke iziphumo ebezingalindelekanga. Ukuba ubona nantoni na engaqhelekanga, xelela ugqirha wakho. Ukuba uyafuna, ungaxela iziphumo ebezingalindelekanga kwi-FDA (Food and Drug Administration) ku-1-800-FDA-1088.

Ndingawagcina njani amayeza am?

• Yigcine kude nabantwana. Oku kubaluleke kakhulu.
• Gcina kubushushu begumbi (phakathi kwama-20 nama-25 degrees Celsius, okanye ama-68 nama-77 degrees Fahrenheit).
• Gcina kwindawo eyomileyo, kude nokukhanya okuthe ngqo .
• Lahla amayeza aphelelwe lixesha ngaphandle kokuwasebenzisa.

Okokugqibela, izinto ekufuneka uzikhumbule (Umyalezo Wokuya Ekhaya)

Kulungile, ngoko ke sithethe kakhulu nge-cysteamine. Khumbula, eli liyeza elibalulekileyo elinceda ekunyangeni imeko ebizwa ngokuba yi-nephropathy cystinosis.

Eyona nto ibalulekileyo kukuthatha eli yeza kanye njengoko ugqirha wakho ekuxelela, ngedosi efanelekileyo, ngexesha elifanelekileyo. Ungaze utshintshe idosi okanye uyeke ukulithatha wedwa.

• Ukuba unemibuzo okanye izinto ezikuxhalabisayo, ungathandabuzi ukubuza ugqirha wakho, ikhemisti, okanye umboneleli wezempilo.
• Lumka ngemiphumo emibi, ingakumbi ukuba ubona nayiphi na imiphumela emibi esithethe ngayo, kwaye ufune ingcebiso kagqirha ngokukhawuleza.
• Yiya kuhlolwa rhoqo ngugqirha.

Eli phepha lolwazi lisisishwankathelo nje. Lisenokungagubungeli zonke iinkcukacha. Ugqirha wakho ngumntu ofanelekileyo ukukunika icebiso elifanelekileyo kwimeko yakho. Ngoko ke, thetha naye ngayo yonke into uze uyilungise. Ndikunqwenelela ukuchacha ngokukhawuleza!

I- Cysteamine, i-nephropathy cystinosis, i-cystine, i-Cystagon, amayeza, isifo sezintso