Ngaba ngamanye amaxesha ufumana amadyungudyungu kunye nezilonda ezibuhlungu emzimbeni wakho, ingakumbi emlonyeni wakho? Ngaba ziyaqhuma lula kwaye zenze kube nzima ukutya okanye ukusela? Ngoko ke le yinto enokuba yinto ebalulekileyo kuwe. Le meko siyibiza ngokuba yiPemphigus Vulgaris. Ungakhathazeki, masithethe ngayo ngokulula.
Yintoni iPemphigus Vulgaris?
Ngamafutshane, iPemphigus Vulgaris yimeko ebangelwa kukungasebenzi kakuhle kwenkqubo yakho yokuzikhusela komzimba . Oku sikubiza ngokuba yimeko yokuzikhusela komzimba. Indima yenkqubo yethu yokuzikhusela komzimba kukusikhusela kwiintsholongwane zasemzini, iibhaktheriya, kunye neentsholongwane. Kufana nomkhosi okhusela ilizwe. Nangona kunjalo, kwiPemphigus Vulgaris, inkqubo yakho yokuzikhusela yomzimba ihlasela ngempazamo iiseli zakho zolusu ezisempilweni kunye neenwebu ze-mucous. Iinwebu ze-mucous ziindawo ezithambileyo nezimanzi ezijikeleze umlomo wakho, impumlo, umphimbo, indlela yokuphefumla, indlela yokugaya ukutya, indlela yomchamo, kunye nendlela yokuzala.
Olu hlaselo lubangela ukuba kubekho amadyungudyungu eluswini nakwimifinya. Rhoqo, abantu abanePemphigus Vulgaris baqala babe namadyungudyungu emlonyeni . La madyungudyungu athambile kakhulu kwaye aqhuma lula. Emva koko ajika abe zizilonda ezibuhlungu.
I-Pemphigus vulgaris lolona hlobo luqhelekileyo lwe-pemphigus.
Ixhaphake kangakanani le nto? Ngubani oyifumana rhoqo?
I-Pemphigus Vulgaris yimeko engaqhelekanga . Nangona inokuchaphazela nabani na, idla ngokuchaphazela abantu abangaphezu kweminyaka engama-40 ubudala. Ayiqhelekanga kakhulu kwiintsana nabantwana.
I-Pemphigus Vulgaris ichaphazela njani umzimba wam?
Iimpawu zePemphigus Vulgaris zihlala ziqala emlonyeni wakho . Amadyungudyungu abuhlungu aqala apho, nto leyo eyenza kube nzima ukutya okanye ukusela. Khawuthelekelele unezilonda ezibuhlungu emlonyeni wakho wonke. Awunakukwazi nokujonga ukutya okuthandayo kuba kuyabuhlungu kwaye kuyahlaba. Abanye abantu bade babe neengxaki zokusela amanzi.
Emva kokuchaphazela i-mucous membranes yomlomo, iimpawu zinokusasazeka ziye kulusu kwezinye iindawo zomzimba wakho. La maqhuqhuva abhityile kakhulu, ngoko ke aqhuma lula. Xa amaqhuqhuva eqhuma, anokukhupha ulwelo, kwaye ngamanye amaxesha ubomvu buya kuphuma. Ezi ndawo ke ziba zizilonda ezivulekileyo.
Zithini iimpawu zoku?
Ayingomntu wonke onePemphigus Vulgaris oneempawu ezifanayo, kwaye ubukhali bazo bungahluka kumntu nomntu . Iimpawu eziqhelekileyo ziquka:
- Kuvela iblista egcwele ulwelo. Le isenokuba nesangqa esibomvu esijikelezileyo, kwaye embindini inokuba nombala okhanyayo opinki-mhlophe.
- Amadyungudyungu aqhuma lula, ekhupha ulwelo olucacileyo okanye mhlawumbi igazi.
- Iqokobhe okanye amaxolo angase akhiwe phezu okanye ngeenxa zonke kwi-blister.
- Ulusu olukwi-blister okanye olujikeleze i-blister luyaxobuka.
- Xa i-blister iqhuma, kuvela amanxeba avulekileyo.
- Kukho iintlungu eziqatha ngaphakathi nangaphandle kwamadyungudyungu.
Musa ukuzifaka emaqatheni - zinokosulelwa!
Musa ukukrwela okanye ukukrwela amaqhuqhuva akho, kuba oku kunokubangela ukuba abe zizilonda ezivulekileyo kwaye zikhokelele ngokulula kwiintsholongwane. Iimpawu zosulelo zingabandakanya:
- Kuphuma ulwelo olumhlophe okanye olumthubi olufana nobovu kwi-blister.
- I-blister ivuvukele kwaye ivakala ibuhlungu kakhulu.
- Iqokobhe elimthubi lenzeka phezu okanye ngeenxa zonke kwi-blister.
- Ulusu olujikeleze i-blister luyadumba kwaye lukhule.
- I-blister ayipholi.
Khumbula, ukuba uneempawu ezinje, kufuneka ubone ugqirha ngokukhawuleza.
Zivela phi ezi mpawu?
Iimpawu zePemphigus Vulgaris zichaphazela ulusu lwakho kunye ne-mucous membranes. Iindawo eziqhelekileyo apho iimpawu zibonakala khona zezi:
- Umlomo nomqala
- Impumlo
- Amehlo
- Indawo ye-genital `(izitho zangasese)`
- Isifuba
- Ngaphandle
- Izandla nemilenze
- Ukhakhayi `(intloko yentloko)`
Yintoni ebangela iPemphigus Vulgaris?
Unobangela ochanekileyo wePemphigus Vulgaris awukafunyanwa .
Njengoko besitshilo ngaphambili, le yimeko yokuzikhusela komzimba, apho ii-antibodies zenkqubo yakho yomzimba - iiproteni ezikhusela umzimba wakho kwiintsholongwane, iibhaktheriya, nezinye izinto - zichonga iiseli zakho eziphilileyo kwaye zizihlasele ngokungathi ziintsali zangaphandle. Olu hlaselo kwiiseli eziphilileyo lubangela iimpawu zokudumba eluswini nakwiinwebu ze-mucous.
Ngaba le meko inokubangelwa ngamayeza athile?
Kunqabile kakhulu ukuba umzimba wakho ungasabela kakubi kumayeza athile uze ubangele iimpawu ze-pemphigus vulgaris. Amanye ala mayeza aquka:
- Izithinteli ze-ACE: La ngamayeza anikwa uxinzelelo lwegazi oluphezulu.
- `Ii-chelating agents`: La ngamayeza asusa izinto ezithile egazini.
- Ii-antibiotics
- Amayeza angengowe-steroidal alwa nokuvuvukala (ii-NSAID)
Ingaba oku kuyasulela?
Hayi, iPemphigus Vulgaris ayisosifo esosulelayo. Awunakusidlulisela komnye umntu. Ngoko ke akukho nto ibalulekileyo.
Uyixilonga njani le nto?
Ugqirha wakho uza kuqala akuhlole aze akubuze ngeempawu zakho. Baza kukubuza ngembali yakho yempilo kunye nokuba kukho umntu kusapho lwakho okhe waba nezimo ezifanayo na. Emva koko, banokwenza uvavanyo oluthile ukuqinisekisa imeko.
Zeziphi iimvavanyo ezenziwayo?
Ukuqinisekisa ukuxilongwa, ugqirha wakho angenza i-skin biopsy . Oku kuquka ukuthatha iqhekeza elincinci lesicwili eluswini oluchaphazelekayo, nokuba likwindawo apho kukho khona amaqhuqhuva, aze alihlolisise phantsi kwe-microscope. Oku kungabandakanya uvavanyo olukhethekileyo olubizwa ngokuba luvavanyo lwe-immunofluorescence.
Olunye uvavanyo luvavanyo lwegazi . Olu vavanyo lujonga ii-antibodies egazini lakho ezibangela iimpawu zakho.
Zithini iindlela zonyango?
Unyango lwe-pemphigus vulgaris lugxile ekulawuleni iimpawu kunye nokuthintela iingxaki ezifana nosulelo . Iindlela zonyango zinokwahluka kumntu nomntu. Zingabandakanya:
- Ukuba kukho usulelo, lunike amayeza.
- Ukuba kukho amayeza abonakala ebangela iimpawu, yeka ukuwasebenzisa.
- Ukusebenzisa amayeza, iikhrimu, kunye namafutha okuthambisa ukuphilisa amanxeba nokunciphisa iintlungu.
- Nyanga amanxeba kunye namadyungudyungu ngononophelo, njengokuba ubuya kunyanga ukutsha okanye inxeba.
- Ukuba awukwazi ukutya ngenxa yezilonda emlonyeni, ukutya ukutya okungeyondlwan’ iyanetha, okanye ngamanye amaxesha ukutya okunesondlo nge-IV, kunokunceda ekuthinteleni ukungondleki kakuhle.
- Ukusebenzisa amayeza okubulala iintlungu ukunciphisa iintlungu zamadyungudyungu emlonyeni.
Ngawaphi amayeza ePemphigus Vulgaris?
Ugqirha wakho angakunika amayeza anjengala ukunciphisa iimpawu, ukuthintela ukudumba kwesikhumba, okanye ukunyanga izifo:
- Ii-corticosteroids, ezisetyenziswa eluswini okanye ezithathwa ngomlomo, zinceda ekunciphiseni ukudumba.
- Izinto ezithintela inkqubo yomzimba yokuzikhusela . Imizekelo ibandakanya i-azathioprine, i-cyclosporine, i-mycophenolate, i-cyclophosphamide, i-methotrexate, okanye i-rituximab. Ezi zisebenza ngokunciphisa umsebenzi wenkqubo yomzimba yokuzikhusela kwaye ziyithintele ekuhlaseleni iiseli eziphilileyo.
- Ii-antibiotics okanye ii-antifungals. Ezi zinikwa ukuba kukho usulelo.
Ngaba kukho naziphi na iziphumo ebezingalindelekanga zonyango?
Ayizizo zonke iindlela zonyango ezifanayo, ngoko ke iziphumo ebezingalindelekanga zinokwenzeka ngokuxhomekeke kuhlobo lwamayeza achazwe ngugqirha wakho. Ngaphambi kokuba uqale amayeza amatsha, kufuneka uxelele ugqirha wakho ngawo onke amayeza owasebenzisayo ngoku, izongezo ozisebenzisayo, kunye nazo naziphi na izinto ezibangela ukuba umzimba wakho ungabi namdla. Ugqirha wakho uza kujonga imeko yakho kunye nenkqubela yonyango lwakho. Unokwenza uvavanyo lwegazi okanye lomchamo rhoqo ukujonga iziphumo ebezingalindelekanga.
Yintoni onokuyitya kwaye uyisele xa ukule meko?
Ukutya nokusela kunokuba nzima xa unePemphigus Vulgaris, ingakumbi ukuba unamaqhuqhuva kunye nezilonda emlonyeni wakho . Ngoko ke, khetha ukutya okuthambileyo, okumanzi, nokungaqhotsiyo . Oku akubuhlungu kangako kwizilonda. Kuphephe ukutya okune-asidi, okuneziqholo, nokuqhotsileyo (umz., ilamuni, iorenji, itshili, neetships zetapile).
Ukuba awukwazi ukutya okanye ukusela, bonana nogqirha ngokukhawuleza.
Ndiza kuziva bhetele nini emva kokuqala unyango?
Ixesha lokuphiliswa liyahluka kumntu nomntu. Ngokwesiqhelo, kungathatha iiveki ezimbalwa emva kokuqala unyango lokuba amaqhuqhuva amatsha ayeke ukwakheka . Emva koko, kungathatha iinyanga ezimbalwa ukuba ulusu lwakho luphile.
I-Pemphigus vulgaris yimeko engapheliyo , oko kuthetha ukuba iimpawu zinokuphinda zibuye nasemva konyango.
Ngaba iPemphigus Vulgaris ingathintelwa?
Ngenxa yokuba unobangela ochanekileyo ungaziwa, akukho ndlela yokuthintela iPemphigus Vulgaris. Nangona kunjalo, unyango lunokunciphisa iimpawu.
Kuza kwenzeka ntoni ukuba ndinePemphigus Vulgaris?
Ngonyango, ungayilawula i-pemphigus vulgaris. Le meko ayichaphazeleki kangako ubomi bakho. Nangona kunjalo, ukuba iimpawu zinzima, zinokukukhubaza okwethutyana. Oku kuthetha ukuba kunokuba nzima ukwenza imisebenzi yakho yemihla ngemihla okanye ukuya emsebenzini. Abanye abantu banokungakwazi ukulala kakuhle okanye banciphise umzimba ukuba abakwazi ukutya kakuhle ngenxa yezilonda emlonyeni.
Amanxeba awafumaneki xa amaqhuqhuva ephola. Nangona kunjalo, ukuba inxeba liqhuma kwaye kunzima ukuphola, linokushiya amanxeba okanye amabala amdaka eluswini.
Ukuba azinyangwa, iimpawu zinokusasazeka emzimbeni wonke kwaye zikhokelele kwiingxaki ezisongela ubomi (umz., ukungondleki kakuhle, ukuphelelwa ngamanzi emzimbeni, i-sepsis - usulelo olunzima). Eyona ngxaki inzima ye-pemphigus vulgaris enganyangwanga lusulelo olunzima nolunganyangwanga.
Akukabikho nyango lwePemphigus Vulgaris. Uphando lusaqhubeka malunga nesizathu kunye nonyango olutsha.
Le meko iza kuhlala ixesha elingakanani?
I-Pemphigus Vulgaris yimeko ehlala ixesha elide (engapheliyo) , ngoko ke unokuba neempawu ubomi bakho bonke. Iimpawu zihlala ziqala phakathi kweminyaka engama-40 nama-60 ubudala. Iimpawu zinokuvela zize ziphele (ukudumba). Unyango lunokunceda ekunciphiseni iimpawu zakho.
Ndingazinyamekela njani?
Ungazinyamekela ekhaya kwaye ulawule iimpawu zePemphigus Vulgaris ngokwenza oku kulandelayo:
- Yitya ukutya okuthambileyo, okumanzi xa unezilonda emlonyeni.
- Nyamekela amaqhuqhuva kunye namanxeba akho, njengokuba ubuya kwenza xa usikiwe okanye utshile.
- Nxiba impahla yokuzikhusela kwaye usebenzise isithambisi selanga ukukhusela ulusu lwakho kwimitha yelanga eyingozi ye-UV.
- Sebenzisa isepha kunye neeloshini ezingenavumba ezithambileyo eluswini lwakho.
Ndifanele ndimbone nini ugqirha?
Ufanele ubone ugqirha ukuba unezi mpawu zilandelayo:
- Ukuba amanxeba awapholi.
- Ukuba kukho amadyungudyungu kwindawo enkulu yomzimba.
- Ukuba amadyungudyungu abuhlungu aphuma ulwelo olumthubi okanye olumhlophe, okanye ukuba kuvela uqweqwe olumthubi oluwajikelezileyo (ezi zisenokuba ziimpawu zosulelo).
- Ukuba kukho ukudumba ngaphakathi okanye kufutshane namadyungudyungu.
- Ukuba kunzima ukutya nokusela.
- Ukuba uneempawu ezinje ngomkhuhlane, ukubanda, kunye neentlungu zemisipha.
Ndingayibuza yiphi imibuzo ugqirha?
Xa usiya kugqirha, ungabuza imibuzo efana nale:
- Luhlobo luni lonyango olucetyiswayo?
- Ngaba kukho naziphi na iziphumo ebezingalindelekanga zonyango?
- Ndingazithintela njani izifo?
- Ndingawanyamekela njani amanxeba am ekhaya?
Yintoni umahluko phakathi kwePemphigus Vulgaris kunye neBullous Pemphigoid?
I-Pemphigus Vulgaris kunye ne-Bullous Pemphigoid zombini ziimeko zokuzikhusela komzimba ezichaphazela ulusu lwakho. Zombini zihlala zichaphazela abantu abangaphezu kweminyaka engama-65 ubudala. Nangona kunjalo, umahluko omkhulu phakathi kwezi meko zimbini ukwizilonda ezenzekayo kunye nesizathu .
I-Pemphigus vulgaris ibangela ukuba kubekho amaqhuqhuva amancinci, azele lulwelo eluswini lwakho nakwiinwebu zomlomo, njengomlomo wakho.
I-bullous pemphigoid ibangela amabala abomvu arhawuzelelayo, aphakanyisiweyo, abizwa ngokuba zii-hive-like welts . La mabala adla ngokugqunywa ngama-blister aqinileyo, angaqhekekanga.
Umyalezo oya ekhaya
I-Pemphigus Vulgaris yimeko yesikhumba ehlala ixesha elide enokuhlala ubomi bonke. Iimpawu zinokuba buhlungu kwaye zinokubangela izilonda zesikhumba nomlomo. Eyona nto ibalulekileyo kukutya kakuhle kwaye uphephe ukunqongophala kwesondlo xa unesi sifo . Thetha nogqirha wakho malunga neendlela zonyango ezilungileyo zeempawu zakho. Musa ukoyika, eyona nto ibalulekileyo kukwazi kwaye ufumane unyango olufanelekileyo.
i- pemphigus vulgaris, isifo solusu, amadyungudyungu, izilonda zomlomo, ukuzikhusela komzimba, ukungakhuseleki komzimba, isifo solusu











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