Xa ugqirha ekuxelela ukuba umntwana wakho omncinci unesifo sentliziyo esibizwa ngokuba yi "Shone's Complex," usenokuziva wothukile, woyika, kwaye udidekile . Kuqhelekile kakhulu. Usenokuba awukaze uve ngeli gama ngaphambili. "Siyintoni esi sifo? Kuza kwenzeka ntoni kumntwana wam?" Usenokuba nemibuzo emininzi engqondweni yakho. Ungakhathazeki. Masithethe ngale nto ngokulula nangokucacileyo. Yintoni iShone's Complex? Masiqonde ukuba yenza ntoni na kumntwana.
Ngamafutshane, yintoni le Shone's Complex?
I-Shone's Complex sisifo sentliziyo esizalwa naso . Okwenzekayo koku kukuba kukho ukuvaleka kwindawo ezingaphezu kwesinye kwindlela yokuhamba kwegazi ukuya kwicala lasekhohlo lentliziyo yomntwana wethu. Khawuthelekelele, icala lasekhohlo lentliziyo yethu lelo lithatha igazi elicocekileyo nelicebileyo kwimiphunga lize limpompe umzimba wonke. Njengenjini yamanzi. Ngoku kwenzeka ntoni ukuba kukho ukuvaleka okanye izilonda kule ndlela yokuhamba kwegazi? Kuba nzima entliziyweni ukungenisa igazi, kwaye kuba nzima ukupompa igazi emzimbeni. Yiloo nto eyenzekayo kwi-Shone's Complex.
Le meko ibizwa ngokuba yiShone's Complex, igama likagqirha owayichaza okokuqala. Nangona efumanise iziphene ezine zentliziyo ezinxulumene nayo, oogqirha ngoku bafumanise ukuba kukho ezinye iziphene ezininzi ezibandakanyekileyo.
Zeziphi iziphene zentliziyo ezinokunxulunyaniswa neShone's Complex?
Ukuze kufunyaniswe ukuba une-Shone's Complex, umntwana kufuneka abe neziphene ezimbini kwezisibhozo zentliziyo esiza kuthetha ngazo apha ngezantsi. Makhe sibone ukuba zeziphi. Amanye amagama asenokubonakala entsonkothile, kodwa ndiza kuwachaza ngokulula.
| Isiphene sentliziyo | Kalula nje, kwenzeka ntoni ngale nto? |
|---|---|
| I-Cor triatriatum | I-membrane eyongezelelweyo iyenzeka ngaphakathi kwigumbi eliphezulu lasekhohlo lentliziyo (i-atrium yasekhohlo). Oku kwahlula igumbi libe ngamacandelo amabini, okuthintela igazi ukuba lingangeni kwigumbi elingezantsi (i-ventricle yasekhohlo). |
| Indandatho ye-Supravalvular mitral | Isangqa sezicubu ezinemicu sikhula ngaphezulu nje kwevalvu ye-mitral entliziyweni. Oku kunciphisa umngxuma ovuleka ngawo ivalvu, nto leyo ethintela ukuhamba kwegazi. |
| Ivalvu ye-mitral yeparachute | Ngokwesiqhelo, kukho izihlunu ezimbini (izihlunu zepapillary) ezinceda ivalvu ye-mitral ivuleke kwaye ivaleke. Kule ngxaki, kukho enye kuphela. Kufana nokuba zonke iintambo zeparashuti ziqokelelwe kwindawo enye. Oku kunokubangela ukuba ivalvu inciphe okanye igazi livuza ngasemva. |
| I-ventricle yasekhohlo engaphantsi kweplastiki | Igama elithi "Hypoplastic" lithetha ukungaphuhli kakuhle. Apha, i-ventricle yasekhohlo, igumbi eliphambili lokumpompa lentliziyo, ayiphuhli kakuhle. Incinci. Ngoko ke ayikwazi ukupompa igazi ngokufanelekileyo. |
| I-stenosis ye-Subaortic | Izicubu ezongezelelweyo ziyaqokelelana phantsi kwevalvu ye-aorta, epompa igazi kwi-aorta, nto leyo enciphisa indawo. Oku kuncipha kwenza kube nzima ngentliziyo ukupompa igazi. |
| Ivalvu ye-aortic yeBicuspid | Ngokwesiqhelo, ivalvu ye-aorta ineeflaphu ezintathu. Kodwa abantwana abanesi siphene banezimbini kuphela. Oku kunokubangela ukuba ivalvu inciphe okanye ivuze igazi. |
| I-annulus yevalvu encinci ye-aortic | Isangqa esiqinileyo (i-annulus) esijikeleze isiseko sevalvu ye-aorta siba ncinci kunesiqhelo, ngoko ke inani legazi elinokudlula kwivalvu liye kwi-aorta liyancitshiswa. |
| Ukudibana kwe-aorta | Ukuncipha kwe-aorta, umthambo wegazi oyintloko othwala igazi emzimbeni, kubangela ukuba intliziyo isebenze nzima ukupompa igazi kwindawo enciphileyo. |
Into ebalulekileyo kukuba ukuba kukho iziphene ezimbini okanye ngaphezulu kwezi zisibhozo, yiloo nto oogqirha bayibiza ngokuba yiShone's Complex. Uninzi lwexesha, kukho isithintelo esinye xa umntu engena kunye nesithintelo esinye xa ephuma.
Zithini iimpawu ukuba umntwana wam unale meko?
Abanye abantwana abanesifo esinjalo, ukuba sibi kakhulu, baqala ukubonisa iimpawu phantse emva kokuzalwa . Oku kungenxa yokuba intliziyo yomntwana ayikwazi ukupompa igazi elaneleyo emzimbeni. Nangona kunjalo, ngamanye amaxesha, iimpawu zinokuvela ngexesha lobuntwana okanye nakwiminyaka yokufikisa.
Khangela ezi mpawu kumntwana wakho:
- Ubunzima bokutyeba: Ukungatyebi kakuhle.
- Ukudinwa xa usela ubisi: Emva kokusela ubisi, uqala ukubila kwaye ube nobunzima bokuphefumla.
- Ukuphuma komchamo okunciphileyo: Ukuphuma komchamo omncinci kunesiqhelo.
- Ukubetha kwentliziyo okubuthathaka: Ukubetha kwentliziyo kubuthathaka kakhulu, ingakumbi ezandleni nasezinyaweni.
- Umahluko kuxinzelelo lwegazi phakathi kweengalo nemilenze: Uxinzelelo lwegazi ezingalweni luphezulu kunasemilenzeni.
- Ukuqokelelwa kwe-lactic acid egazini.
Ukuba umntwana wakho unenye okanye ngaphezulu kwezi mpawu, kubaluleke kakhulu ukuthetha nogqirha wakho ngokukhawuleza.
Kutheni oku kwenzeke kumntwana wam? Yintoni imbangela yako?
Ngoku usenokuba uzibuza, "Kutheni oku kwenzeke kumntwana wam? Ingaba lityala lam?" Enyanisweni, oogqirha abakafumani sizathu sithile sale nto. Uninzi lwexesha, kwenzeka ngamaxesha athile. Asinalo ulwazi olwaneleyo lokutsho ngokuqinisekileyo ukuba ingaba yinto ebangelwa lufuzo okanye yimeko-bume.
Nangona uphando oluthile lubonisa ukuba isenokuba yeyofuzo, indlela edluliselwa ngayo kwiintsapho inzima kakhulu. Ngoko ke kufuneka uphando oluthe kratya ukuze kuqondwe ngokupheleleyo oku.
Ngoko ke nceda ukhumbule, oku akulona ityala lakho. Asinalawulo kwezi zinto.
Ziziphi iingxaki ezinokubakho ngenxa yale meko?
I-Shone's Complex inokubangela iingxaki ezithile, yiyo loo nto unyango olukhawulezileyo kunye nokubekwa esweni kwexesha elide kubalulekile.
- Uxinzelelo lwegazi oluphezulu oluphuma kwimiphunga: Ukunyuka okungaqhelekanga koxinzelelo lwegazi kwimithambo yegazi ethwala igazi ukuya emiphungeni.
- Izingqisho zentliziyo ezingaqhelekanga: Izingqisho zentliziyo ezingaqhelekanga.
- Ukusilela kwentliziyo: Imeko apho intliziyo ingakwaziyo ukupompa igazi elaneleyo emzimbeni.
Oogqirha bayifumana njani le nto?
Oogqirha basebenzisa iimvavanyo ezininzi ukufumanisa esi sifo.
- I-echocardiogram yosana olusandul’ ukuzalwa: Olu luvavanyo olukhethekileyo olwenziwa ngelixa umntwana esesesibelekweni. Lunokubona iingxaki zentliziyo ngaphambi kokuba umntwana azalwe.
- I-Transthoracic echocardiogram (TTE): I-ultrasound scan yentliziyo eyenziwa emva kokuba umntwana ezelwe. Olu vavanyo lusetyenziswa kakhulu ekuxilongeni i-Shone's Complex.
- I-Cardiac CT scan okanye i-MRI: Oku akwenzeki rhoqo kuwo wonke umntu, kodwa kwezinye iimeko, olu vavanyo lunokunceda ekunikeni ulwazi oluthe kratya malunga nokwakheka kwentliziyo.
Amaxesha amaninzi, esi sifo sifunyanwa ngaphambi okanye emva kokuzalwa. Nangona kunjalo, ngamanye amaxesha esi sifo sifunyanwa okokuqala ebuntwaneni okanye ebusheni, xa iimpawu zincinci kwaye zingabi nzima kangako. Kwiimeko ezinjalo, ugqirha unokuthumela uvavanyo olongezelelweyo ngenxa yesandi esingaqhelekanga (ukugungqa kwentliziyo) esiviwayo xa kumamele intliziyo.
Zithini iindlela zonyango zoku?
Eyona ndlela ikuphela kwayo yokunyanga iShone's Complex kukuhlinzwa . Okwangoku akukho mayeza anokunyanga le meko. Nangona kunjalo, ugqirha angakunika amayeza okulawula iimpawu zomntwana nokuxhasa ukusebenza kwentliziyo de kube lutyando.
Akukho tyando lukhethekileyo loku. Endaweni yoko, oogqirha baya kugqiba ukuba loluphi utyando olufunekayo ngokusekwe kwiziphi iziphene zentliziyo umntwana wakho anazo kunye nokuba intliziyo isebenza kakuhle kangakanani.
Umntwana wakho usenokufuna olunye okanye ngaphezulu kwezi ndlela zilandelayo zotyando:
- Ukususwa kweringi yethishu eyongezelelweyo ejikeleze ivalvu ye-mitral.
- Ukulungiswa kwevalvu yeMitral.
- Ukutshintshwa kwevalvu yeMitral (oku akuvamile kangako).
- Ukususwa kwezicubu ezigqithisileyo phantsi kwevalvu ye-aorta.
- Ukwandisa ukuvulwa kwevalvu ye-aorta.
- Ukulungisa inxalenye encinci ye-aorta.
Inkqubo yotyando
Ngamanye amaxesha oogqirha bakwenza oku ngendlela ecwangcisiweyo . Oko kukuthi, abalwenzi lonke utyando ngaxeshanye. Balwenza ngamacandelo amabini, ahlulwe lixesha. Umzekelo, utyando lokuqala lususa ukuvaleka kwendlela igazi eliphuma ngayo entliziyweni. Emva koko, utyando lwesibini lususa ukuvaleka kwendlela igazi elihamba ngayo entliziyweni. Ugqirha wakho uza kukuchazela ukuba zingaphi utyando oluya kufuneka umntwana wakho kunye nexesha elifanelekileyo lokwenza ngalo.
Iyintoni ubomi bomntwana kwixesha elizayo kunye noqikelelo lwakhe?
Ubomi bomntwana kwixesha elizayo kunye nempilo-ntle yakhe ixhomekeke kwizinto ezininzi:
- Ubunzima besifo: Indlela esibi ngayo isiphene sentliziyo.
- Isantya sonyango: Indlela oluqalwa ngayo unyango ngokukhawuleza.
- Iingxaki: Nokuba kuza kubakho ezinye iingxaki okanye akunjalo.
- Ukuphinda-phinda kweengxaki: Ngaba iziphene zentliziyo ebezinyangiwe ngaphambili ziya kuphinda zibuye ekuhambeni kwexesha?
Umzekelo, izinto ezifana nokuqhekeka kwe-aorta zinokuphinda zibuye ngokuhamba kwexesha. Ngoko ke, njengoko umntwana wakho ekhula, kunokufuneka utyando olongezelelekileyo. Ugqirha wakho uya kukunika ulwazi oluthe kratya malunga noku kuxhomekeke kwimeko yomntwana wakho.
Izifundo ezininzi zibonise ukuba izinga lokusinda ixesha elide emva kotyando lingaphezulu kwama-75%, ukuya kuthi ga kwiminyaka engama-20 . Oko kuthetha ukuba abantwana abathathu kwabane baphila ubomi obusempilweni emva konyango.
Usenokuba nemibuzo eliwaka engqondweni yakho emva kokuva ngokuxilongwa komntwana wakho. Yinto eqhelekileyo leyo. Bhala imibuzo efika engqondweni yakho kwincwadi yamanqaku. Xa usiya kubona ugqirha, mbuze yonke. Iqela lezonyango lomntwana wakho liza kukuchazela konke oku kwaye likukhokele kwinto omawuyenze ngokulandelayo.
Umyalezo Wokuya Ekhaya
- I-Shone's Complex sisifo sentliziyo esingaqhelekanga esibangelwa kukuzalwa esibangela ukuba ukuhamba kwegazi kwicala lasekhohlo lentliziyo kuthinteleke.
- Ukuze umntwana afunyaniswe enale sifo, kufuneka ubuncinane abe neziphene ezimbini kwezisibhozo zentliziyo.
- Unyango olulodwa kuphela loku lutyando. Utyando ludla ngokuphumelela.
- Emva kotyando, umntwana uya kufuna ukulandelwa ngugqirha wentliziyo ubomi bakhe bonke. Ungaphoswa naliphi na kwezi zihlandlo.
- Eyona nto ibalulekileyo kukuba le meko ayisiyongxaki yakho okanye yeqabane lakho. Musa ukukhathazeka ngayo.

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