Kumelwe ukuba wesaba kakhulu futhi washaqeka lapho udokotela ekutshela ukuthi ingane yakho esanda kuzalwa inomgodi owodwa kuphela lapho kufanele kube khona isitho sangasese sowesifazane, i-urethra, kanye ne-anus. Kuvamile kakhulu. Akekho okulungele ukuzwa into efana nale. Kodwa ungakhathazeki. Lesi yisici sokuzalwa esingavamile kakhulu esingalungiswa ngempumelelo ngokuhlinzwa. Ake sixoxe ngakho konke kalula nangokucacile.
Kalula nje, kuyini i-Cloacal Malformation?
I-Cloacal Malformation iyisici esingavamile kakhulu sokuzalwa esithinta amantombazane kuphela. Ngokuvamile, indawo yesitho sangasese sowesifazane kanye ne-anus (esiyibiza ngokuthi le ndawo ngokuthi i-perineum) kufanele ibe nezimbobo ezintathu . Ziyi,
1. I-Urethra ( ipayipi lapho umchamo uphuma khona)
2. Isitho sangasese sowesifazane , lapho kwenzeka khona ukuya esikhathini kanye nocansi.
3. Indunu ( indlela lapho kuphuma khona indle)
Kodwa-ke, ingane ene-Cloacal Malformation inomgodi owodwa kuphela esikhundleni salezi ezintathu. Lokhu kusho ukuthi umchamo, indle, kanye noketshezi lwesitho sangasese sowesifazane konke kuphuma emzimbeni ngalo mgodi owodwa. Lesi yisimo esikhethekile esiseqenjini leziphambeko zokuzalwa ezibizwa ngokuthi `(Anorectal Malformation)`.
Cabanga nje, phakathi namasonto okuqala okukhula komntwana ngesikhathi sokukhulelwa, lezi zinhlelo ezintathu—uhlelo lwamathumbu, uhlelo lomchamo, kanye nohlelo lokuzala—zonke zixhunywe ekamelweni elivamile elibizwa ngokuthi “i-cloaca.” Njengoba umntwana ekhula, leli gumbi lihlukana kancane kancane libe izingxenye ezintathu, okwenza izikhala ezintathu esikhulume ngazo ekuqaleni. Ngezinye izikhathi le nqubo yokuhlukanisa ayenzeki kahle. Yilapho zonke izinhlelo ezintathu zixhunywe khona epayipini elivamile, elivuleka emzimbeni ngomnyango owodwa.
Ukwelashwa kwalesi simo ukwenza izikhala ezintathu ezihlukene ngokuhlinzwa esikhundleni salesi sikhala esivamile. Lokhu kuhlinzwa kuvame ukwenziwa phakathi nonyaka wokuqala wokuphila kwengane.
Ingabe kunezinhlobo ezahlukene zalesi simo?
Yebo. Ubunzima besimo se-Cloacal Malformation bunqunywa ubude "besiteshi esivamile" esixhumanisa izinhlelo ezintathu esixoxe ngazo. Lesi siteshi esivamile singaba noma yikuphi kusukela kusentimitha eli-1 kuya ku-10 amasentimitha ubude. Lobu bude bunquma ubunzima bokuhlinzwa ingane edingayo.
- Ukuba Nomzila Omfushane Ovamile: Yilapho lezi zinhlelo ezintathu zihlangana khona eduze kakhulu nomgodi ongaphandle komzimba. Lokhu kusho ukuthi umzila ovamile umfushane. Ezimweni ezinjalo, kulula ukudlulisa imfucuza emzimbeni. Ukuhlinzwa nakho kulula. Futhi, impilo yengane yesikhathi esizayo ingcono kakhulu.
- Ukuba Nesiteshi Esivamile Eside:Lesi yisimo esiyinkimbinkimbi kakhulu. Lapha, lezi zinhlelo ezintathu zihlangana zijule emzimbeni. Ngakho-ke, umsele ovamile mude. Lokhu kwenza kube nzima ukuthi imfucuza iphume emzimbeni. Ukuhlinzwa nakho kuba nzima kakhulu.
Lesi simo asivamile kakhulu, senzeka cishe koyedwa ezinsaneni ezisanda kuzalwa ezingu-25,000 kuya ku-50,000.
Yiziphi izimpawu zalesi simo kanye nezinye izinkinga ezihlobene naso?
Isici esiyinhloko nesisobala kakhulu ukuthi ingane yesifazane izalwa inomgodi owodwa kuphela esikhundleni sezintathu okufanele zibe khona. Ngaphezu kwalokho, lesi simo singadala nezinye izinkinga zempilo. Ake sibheke kuleli thebula.
| Inkinga yezimpawu/ehlobene | Incazelo elula |
|---|---|
| Isici esiyinhloko | Imbobo eyodwa endaweni yendunu, isitho sangasese sowesifazane, kanye ne-urethra. |
| Ukwandiswa kwe-clitoris | Ezinye izitho zangasese zezingane zingabukeka njengepenis yomfana. |
| I-rectum engavamile | Ushintsho endaweni yendunu noma ukubukeka okungavamile. |
| Izinkinga zesistimu yokuzala | Ngezinye izikhathi kungaba nezitho zangasese zowesifazane, isibeletho, noma umlomo wesibeletho ezingaphezu kwesisodwa. |
| Izinkinga zesistimu yomchamo | Izinkinga ezahlukahlukene zingavela ezinso, kuma-ureter, noma esinyeni. |
| Izinkinga kwezinye izinhlelo | Kukhona ingozi yezinye izinkinga ngenhliziyo, umgogodla, noma uhlelo lokugaya ukudla. |
Kungani lokhu kwenzeke enganeni yami? Iyini imbangela?
Kungokwemvelo ukuthi lo mbuzo ufike engqondweni yakho. Kodwa odokotela abaqiniseki ukuthi yini ebangela lokhu. Abacwaningi bakholelwa ukuthi kuyinto eyenzeka ngokungahleliwe, engenambangela ethile.
Akulona iphutha lakho nhlobo. Ungazizwa kabi uma ucabanga ukuthi lesi simo sibangelwa yinoma yini oyenzile noma ongayenzanga ngesikhathi sokukhulelwa kwakho. Lokho akulungile neze.
Ungasibona kanjani lesi simo?
Lesi simo singatholakala ngaphambi nangemva kokuzalwa.
Ngaphambi kokubeletha (ngesikhathi sokukhulelwa)
Ngezinye izikhathi, lesi simo singatholakala ngesikhathi sokuhlolwa kwe-ultrasound, okwenziwa cishe emavikini angama-20 okukhulelwa. Odokotela basola lokhu uma ukuhlolwa kubonisa isikhwama esigcwele uketshezi nesivuvukile esithweni sangasese somntwana. Ukuqinisekisa lokhu kusola, ukuhlolwa kwe-Magnetic Resonance Imaging (MRI) kungenziwa ngesikhathi sokukhulelwa.
Ngemva kokuzalwa
Lesi simo sivame ukutholakala ngemva kokuzalwa komntwana. Udokotela wezingane ohlola umntwana uzobona ukuthi kunomgodi owodwa kuphela esikhundleni semithathu. Ingane ingase ibe nesisu esivuvukile. Ngemuva kwalokho, kuzokwenziwa izivivinyo eziningana ukuze kuqondwe kahle ukuthi kwenzekani ngaphakathi emzimbeni.
- Ukuskena nge-ultrasound: Hlola isimo sezinso zengane, esinyeni kanye nomgogodla.
- Ama-X-ray: Amasu akhethekile e-X-ray, njenge-fluoroscopy, angasetshenziswa ukubona ukuthi uhlelo lomchamo lusebenza kanjani.
- I-Echocardiogram: Lokhu kuhlolwa kwenziwa ukuze kubonakale ukuthi kukhona yini izinkinga ngenhliziyo.
Iphathwa kanjani? Ake sifunde ngokuhlinzwa
Ukwelashwa kwe-Cloacal Malformation ukuhlinzwa . Umgomo oyinhloko ukudala izikhala ezintathu ezihlukene (i-anus, i-vagina, kanye ne-urethra) esikhundleni sesikhala esisodwa. Umgomo ukunikeza ingane ikhono lokuzikhulula nokuchama ngendlela evamile kanye nokuzilawula.
Lokhu akuyona into engenziwa ngokuhlinzwa okukodwa. Ngokuvamile, uchungechunge lokuhlinzwa kufanele lwenziwe. Ukuze lokhu kwenzeke, kubalulekile ukufuna usizo lukadokotela ohlinzayo wezingane kanye nodokotela wezifo zomchamo wezingane.
Inqubo yokwelapha ingahlukaniswa ngezinyathelo ezintathu eziyinhloko.
Isinyathelo 1: Ukuhlinzwa kokuqala (kungakapheli amahora angu-48 ezelwe)
Umgomo oyinhloko walokhu ukudala uhlelo lokususa kahle indle (indle nomchamo) emzimbeni wengane.
- I-Colostomy: Ngenxa yokuthi ingane ayinayo indlela yokuzikhulula, kwenziwa inqubo yokuhlinzwa ukuze kudalwe imbobo esiswini ngokuletha ingxenye yamathumbu ebusweni besikhumba. Isikhwama sinamathiselwe kulo mbobo, okuvumela indle ukuthi iqoqeke.
- Ukungakwazi ukuzibamba ngomchamo: I-catheter isetshenziselwa ukukhipha umchamo ngoba isinyi siyavuvukala noma sivalekile.
- Isitho sangasese sowesifazane: Uma kukhona uketshezi oluqongelelekayo esithweni sangasese sowesifazane, udokotela ohlinzayo uzolususa uketshezi.
Isinyathelo 2: Ukuhlinzwa okukhulu okwakha kabusha (phakathi kwezinyanga eziyi-6 neziyi-12 ubudala)
Lokhu kuhlinzwa okukhulu kwenziwa ngemva kokuba ingane isikhulile kancane futhi impilo yayo isizinzile. Okwenzekayo lapha ukuthi isiteshi esivamile sihlukaniswe ngezigaba, okudala i-anus ehlukile, isitho sangasese sowesifazane, kanye ne-urethra. Uma isiteshi esivamile sifushane, lokhu kuhlinzwa kulula kakhulu. Uma isiteshi esivamile side, ukuhlinzwa kuba nzima kakhulu.
Isinyathelo 3: Ukuguqulwa kwe-colostomy
Ngemva kokuhlinzwa okuyinhloko, lapho indunu esanda kwenziwa isipholile, i-colostomy yokuqala iyasuswa. Lokhu kusho ukuthi imbobo eyenziwe esiswini ivaliwe futhi amathumbu aphinde axhunywe endaweni yawo evamile. Ingane ingase ikhulule ngendunu esanda kwenziwa.
Ezinye izingane zingadinga ukuhlinzwa okwengeziwe esikhathini esizayo, okuzochazwa udokotela wakho.
Lizoba njani ikusasa lomntwana?
Lona ngumbuzo omkhulu kunayo yonke engqondweni yabazali. Izindaba ezinhle ukuthi imiphumela ivame ukuba mihle kakhulu .
- Ukulawulwa kwamathumbu nesinye: Izingane ezine-common duct emfushane, engenzima kangako, zinethuba elingu-90% lokulawula ngokuphelele amathumbu nesinye. Lokhu kusho ukuthi zingakwazi ukuqeqesha indlu yangasese ngokujwayelekile. Ngisho nezingane ezine-common duct ende, eyinkimbinkimbi kakhulu, zinethuba elingu-70% lokulawula kahle. Ezinye izingane zingase zibe nobunzima bokulawula umchamo wazo (ukungakwazi ukuzibamba ngomchamo). Ezimweni ezinjalo, kungadingeka zisebenzise ipayipi izikhathi eziningana ngosuku ukuze zikhiphe amanzi esinyeni sazo.
- Impilo yocansi nokukhulelwa: Izingane eziningi ezinalesi simo zingaba nokuphila kocansi okuvamile nokwanelisayo sezikhulile. Ziyakwazi nokukhulelwa. Kodwa-ke, kungaba nzima kakhulu kunowesifazane ojwayelekile. Uma zikhulelwa, kuvame ukunconywa ukuthi kwenziwe ukuhlinzwa kokubeletha (ukuhlinzwa kokubeletha) ukuze kubelethwe umntwana.
Yini ongayenza njengomzali?
Umnikelo wakho ubaluleke kakhulu kulolu hambo.
- Sebenza eduze nethimba lezokwelapha: Hlala uxhumana njalo nodokotela ohlinzayo wengane yakho, udokotela wezifo zomchamo kanye nodokotela wezingane.
- Qiniseka ukuthi uyalandela:Ngemva kokuhlinzwa, ingane yakho kuzodingeka iye emtholampilo njalo ukuqinisekisa ukuthi imizimba yayo isebenza kahle. Ungaphuthelwa yinoma iyiphi yazo.
- Mela ingane yakho: Njengoba ingane yakho ikhula, uma kukhona izinkinga ngokulawula umchamo noma amathumbu, ungabi namahloni bese utshela udokotela ngakho.
- Buza imibuzo: Buza udokotela noma yimiphi imibuzo noma ukungabaza onakho. Kuyilungelo lakho.
Eminye imibuzo ongayibuza udokotela:
- Lokuhlinza kwenziwa kanjani? Uneminyaka emingaki?
- Ingabe ingane yami izwa ubuhlungu?
- Yini okufanele ngiyilindele njengoba ingane yami ilulama ngemva kokuhlinzwa?
- Ingabe ingane izodinga ukuhlinzwa okwengeziwe njengoba ikhula?
- Ingabe kuzoba nezinkinga nge-anus, i-urethra, noma isitho sangasese sowesifazane esikhathini esizayo?
- Ingabe ingane yami izokwazi ukuba nomntwana ngokuphephile esikhathini esizayo?
Ukushaqeka, ukwesaba, nokukhathazeka okuhambisana nokufunda into efana nale akunakuchazwa ngamazwi. Kodwa khumbula, isayensi yezokwelapha ithuthuke kakhulu namuhla. Ukuhlinzwa kungalungisa lesi simo ngempumelelo, kunikeze ingane yakho ithuba lokuphila impilo evamile nejabulisayo njengabanye abantwana.
Umlayezo Wokuya Nawe Ekhaya
- I-Cloacal Malformation iyiphutha elingavamile kakhulu lokuzalwa elivela ezinganeni zabesifazane kuphela.
- Lokhu akulona iphutha lakho noma lomlingani wakho. Ungakhathazeki ngakho.
- Ukwelashwa kuhilela uchungechunge lokuhlinzwa, okudala izikhala ezintathu ezihlukene enganeni.
- Imiphumela yokwelashwa ivame ukuphumelela kakhulu, ikakhulukazi ezimweni ezingenzima kangako.
- Ukuhlala uxhumana nodokotela nokuya emitholampilo yokulandelela kubaluleke kakhulu empilweni yengane yesikhathi esizayo.
- Izingane eziningi ezinalesi simo ziphila impilo evamile, enempilo, nejabulisayo.











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