Wake waphawula okuthile okuhlukile uma ubheka amehlo engane yakho encane? Mhlawumbe iso elilodwa libukeka lingavamile, noma umbono walo ubonakala ungacacile? Uma ubona into efana naleyo, ungakuthathi kalula. Namuhla sizokhuluma ngenkinga engase ifike engqondweni yakho ngaleso sikhathi, futhi leyo yisimo esibizwa ngokuthi i-Coats Disease . Lesi yisifo samehlo esingavamile esivame ukuhlasela izingane ezincane, ikakhulukazi abafana.
Kuyini isifo samaCoats? Masiqonde kalula.
Kalula nje, i-Coats Disease yisimo esenzeka lapho imithambo yegazi engaphakathi kweso lengane yakho ingakhuli kahle. Lokhu kuthinta ngqo i-retina, okuyingemuva kweso. Cabanga ngale ndlela: uma iso lethu lifana nekhamera, i-retina ifana nefilimu engaphakathi kwalo. Uma ukukhanya kungena esweni, kuthola izithombe bese kuthumela imiyalezo ebuchosheni ngale retina.
Ngakho-ke, ku-Coats Disease, imithambo yegazi emincane e-retina iyavuvukala futhi iphenduke, bese iqala ukuvuza noma ukuvuza uketshezi olufana ne -plasma . Lokhu kufana nepayipi lamanzi elinembobo kulo futhi livuza amanzi. Nakuba kungase kungabangela umonakalo omkhulu ngokushesha, ngokuhamba kwesikhathi, lokhu kuvuza kungalimaza i-retina futhi kuthinte umbono.
Lesi sifo sivame ukuthinta iso elilodwa. Kodwa-ke, asivamile ukuthinta amehlo womabili ngesikhathi esisodwa. Nakuba sivame ukutholakala ezinganeni ezincane kanye nasebasha, singaba khona kunoma yimuphi ubudala. Lokhu kungaholela ekulahlekelweni umbono, izinkinga ezinkulu njengokuqhekeka kwe-retinal, kanye nokungaboni kulelo liso ekugcineni. Ngakho-ke, kubalulekile ukubona udokotela ngokushesha uma ubona noma yiziphi izinguquko emehlweni noma ekuboneni kwengane yakho.
Ziyini lezi zimpawu? Uzibona kanjani?
Isifo se-Coats singase singabangeli zimpawu ezigabeni zokuqala. Kodwa-ke, njengoba lesi sifo siqhubeka, ingane ingabonisa izimpawu ezifana nalezi:
- Ukubona kuncipha kancane kancane: Ingane yakho ingase izizwe sengathi ayikwazi ukubona kahle ngeso elilodwa. Ungase uqaphele izinto ezifana nokusondela lapho ubuka i-TV noma ukufiphaza amehlo lapho ufunda incwadi.
- I-Strabismus: Iso elilodwa libonakala sengathi liphendukele kwelinye icala.
- Ubuhlungu bamehlo: Ezinye izingane zingase zikhononde nangobuhlungu bamehlo.
- I-Leukocoria: Lesi yisibonakaliso esingajwayelekile. Uma ubheka inhlamvu yeso lengane yakho, noma uthatha isithombe, singase sibonakale simhlophe noma sinombala wesiliva. Lokhu ngezinye izikhathi kubizwa ngokuthi "iso lekati." Uma ubona lesi sibonakaliso, kufanele nakanjani ubone udokotela ngokushesha.
Cabanga nje, lapho indodana yakho idlala, uqaphela ukuthi ayikwazi ukubona kahle ngeso elilodwa, noma uma uthatha isithombe ebusuku, kukhona ibala elimhlophe embotsheni emnyama yeso elilodwa. Yilokho okungenzeka ukuthi kwenzeka lapha.
Yiziphi izigaba zesifo se-Coats?
Isifo se-Coats sihlukaniswe ngezigaba eziningana, kuye ngokuthi siqhubeka kanjani, okufana nezitebhisi.
- Isigaba 1: Lesi yisigaba esiyisisekelo kakhulu. Lapha, udokotela wamehlo angabona ukuthi ingane inemithambo yegazi engajwayelekile ngaphakathi kweso, kodwa ingane ayikazizwa ubuhlungu noma izimpawu ngenxa yayo.
- Isigaba sesi-2: Yilapho uketshezi luqala khona ukuvuza emithanjeni yegazi engajwayelekile. Lokhu kungathinta umbono wengane.
- Isigaba 3: Lapho lesi sifo sifika kulesi sigaba, i-retina yengane iqala ukuhlukana. Lesi yisimo esibi kakhulu.
- Isigaba 4: Esigabeni sesine, amehlo engane angase abe ne- glaucoma , isifo lapho ingcindezi ngaphakathi kweso ikhuphuka khona.
- Isigaba 5: Lesi yisigaba esibi kakhulu nesokugcina sesifo samaCoats. Kuleli qophelo, iso elithintekile lingase libe yimpumputhe ngokuphelele.
Into ebaluleke kakhulu ukuthi kungakhathaliseki ukuthi lesi sifo sikusiphi isigaba, uma sisheshe sitholakale futhi selashwe, amathuba okugcina umbono wengane ayanda.
Kungani kwenzeka isifo se-Coats?
Eqinisweni, ochwepheshe abakakwazi ukuthola imbangela yesifo se-Coats (idiopathic ). Okusho ukuthi, kuvame ukwenzeka ngokuzenzekelayo, ngaphandle kwesizathu esithile.
Enye into ebalulekile ukuthi i-Coats Disease ayisona isifo sofuzo . Okusho ukuthi, akusona isifo esizuzwe njengefa esidluliselwa ezizukulwaneni ngezizukulwane. Ngisho noma kungekho muntu emndenini wakho oke waba naso, ingane yakho isengakwazi ukusithola. Futhi, ngenxa yokuthi omunye wabantwana bakho wayenaso, asikho isidingo sokukhathazeka ngokuthi nezinye izingane zizosithola.
Ubani onamathuba amaningi okuthuthukisa lokhu? (Izici eziyingozi)
Nakuba noma ubani engaba ne-Coats Disease, abanye abantu basengozini enkulu.
- Kutholakale ukuthi abafana banamathuba aphindwe kathathu okuthola lesi sifo kunamantombazane.
- Ukubheka iminyaka:
- Odokotela bavame ukuxilonga lokhu ezinganeni nakubantu abadala abangaphansi kweminyaka eyi-16 .
- Akuvamile kakhulu ukuthi ezinye izingane zizalwe zinalesi simo, noma singavela ezinyangeni ezimbalwa ngemva kokuzalwa.
- Kubikwa nokuthi cishe ingxenye eyodwa kwezintathu yabantu abaneCoats Disease bangabantu abadala abangaphezu kweminyaka engama-30 .
Udokotela ukubona kanjani lokhu? (Ukuxilongwa)
Uma ubona udokotela, ikakhulukazi udokotela wamehlo , ngemva kokubona okuthile okuhlukile emehlweni engane yakho, into yokuqala azokwenza ukuhlola amehlo engane ngokucophelela.
- Uhlola amehlo engane kusukela ngaphandle nangaphakathi esebenzisa izinsimbi ezikhethekile.
- Ukuhlolwa kokubona kahle kwenziwa ukuhlola umbono wengane. Lokhu kuhilela ukulinganisa umbono ngokuyibonisa izinhlamvu nezithombe bese izifunda.
Ngaphezu kwalokho, ukuhlolwa okukhethekile okukodwa noma ngaphezulu kwezithombe ezilandelayo kungenziwa ukuqinisekisa isifo se-Coats:
- Iskeni se -Optical Coherence Tomography (OCT) : Lokhu kuthatha isithombe sengxenye evundlile ye-retina.
- Ukuhlolwa kwe-Angiography: Lokhu kuhilela ukufaka idayi ekhethekile emthanjeni osesandleni sakho bese uthatha izithombe njengoba idlula emithanjeni yegazi esesweni lakho . Lokhu kukuvumela ukuthi ubone ngokucacile noma yikuphi ukuvuza.
- Ukuskena nge-ultrasound: Lokhu kungabheka ingaphakathi leso.
- Isikeni se-MRI (Magnetic Resonance Imaging).
- I-CT scan (i-Computed Tomography scan).
Lezi zivivinyo zivumela udokotela ukuthi azi kahle ukuthi kwenzekani ngaphakathi kweso, izinga lomonakalo emithanjeni yegazi, nokuthi ngabe uketshezi luyavuza yini.
Yiziphi izindlela zokwelapha?
Ukwelashwa kwesifo se-Coats kuncike esigabeni sesifo enganeni. Isibonelo, uma lesi sifo sitholakala kusenesikhathi (isigaba 1 noma isigaba sokuqala sesi-2) , ingane ingase ingadingi ukwelashwa nhlobo. Ezimweni ezinjalo, udokotela wamehlo uzohlola amehlo engane njalo futhi abheke izinguquko emithanjeni yegazi ku-retina.
Kodwa-ke, uma ingane inezimpawu ezinzima, noma uma lesi sifo sisesigabeni esibi kakhulu, kunezindlela zokwelapha ezifana nalezi:
- Ukwelashwa nge-cryotherapy: Lokhu kuhilela ukusebenzisa umkhuhlane omkhulu ukuze kuqandiswe futhi kubhujiswe imithambo yegazi engavamile, bese kuyivimba ukuthi ingavuzi uketshezi.
- Ukwelashwa Ngemithi: Udokotela wamehlo angajova umuthi we-anti-VEGF (Anti-vascular endothelial growth factor) ngqo kwi-retina yengane. Lo muthi usiza ekuvimbeleni ukuvuza koketshezi kuleyo mithambo yegazi futhi uvimbele ukuqhekeka kwe-retina.
- Ukuhlinzwa: Uma ingane isesigabeni esibi kakhulu salesi sifo, noma uma isimo esifana nokuqhekeka kwe-retina sesivele sikhona, kungase kudingeke ukuhlinzwa ukuze kulungiswe umonakalo.
Yini engingayilindela uma ingane yami ine-Coats Disease?
Indlela i-Coats Disease ethinta ngayo amehlo engane kanye nokubona kwayo kuncike ekutheni isifo sitholakala nini nokuthi iso lisabela kahle kangakanani ekwelashweni. Ucwaningo luthole ukuthi uma ingane isikhulile lapho lesi sifo siqala, mancane amathuba okuthi iqhubekele esigabeni esibi kakhulu .
Uma i-Coats Disease itholakala kusenesikhathi (isigaba 1 noma 2), ingane ayinamathuba amaningi okuba nemiphumela emibi yesikhathi eside. Kodwa-ke, ngisho noma ingelashwa, iso elithintekile lingase libe nokulahlekelwa umbono ngezinga elithile (ukubona okuphansi).
Uma lesi sifo sesifinyelele esigabeni esibi kakhulu, kunethuba elikhulu lokuba yimpumputhe esweni elithintekile. Yingakho sincoma ukuthi ubonane nodokotela ngokushesha okukhulu, noma ngabe ubona ushintsho oluncane.
Yiziphi ezinye izinkinga ezingabangelwa yilokhu?
Ngesikhathi sesifo se-Coats, ingane isengozini enkulu yokuthola ezinye izimo zamehlo, njenge:
- I-Glaucoma
- Ama-cataract
- I-Uveitis ( ukuvuvukala kwezicubu ngaphakathi kweso)
- Ukuvuselelwa kwemithambo yegazi
Ngakho-ke, kubaluleke kakhulu ukulandela imiyalelo kadokotela ngokucophelela nokuya kohlolwa ngesikhathi.
Ingabe isifo samaCoats singavinjelwa?
Ngenxa yokuthi lesi sifo senzeka ngokungahleliwe, ngaphandle kwesizathu esithile, akukho lutho esingakwenza ukuvimbela i-Coats Disease.
Kodwa-ke, uma lesi sifo sesitholakele, kubalulekile ukuba nokuhlolwa kwamehlo njalo njengoba kunconywe udokotela wamehlo ukuze kuqashwe izinguquko ku-retina yengane. Lokhu kuzosiza ekuboneni noma yikuphi ukuwohloka kwesifo futhi kuthathwe izinyathelo ezidingekayo.
Kufanele ngimbone nini udokotela?
Uma ubona noma yiziphi izinguquko emehlweni noma ekuboneni kwengane yakho, bona udokotela noma udokotela wamehlo ngokushesha. Ungalibali.
Futhi, uma uhlangabezana nanoma yiziphi zalezi zimpawu, hamba uye esibhedlela ngokushesha :
- Ukulahlekelwa umbono ngokuzumayo.
- Ubuhlungu obukhulu bamehlo.
- Kungachazwa njengokubona ukukhanya noma ukubona izinto ezintantayo phambi kwamehlo.
Yimiphi imibuzo okufanele uyibuze udokotela?
Uma uya kudokotela, ungase ufune ukubuza imibuzo efana nale:
- Ingane yami ikusiphi isigaba sesifo se-Coats?
- Kukangaki ngidinga ukuza ezivivinyweni zokulandelela?
- Ingabe ingane idinga ukwelashwa?
- Hlobo luni lokwelashwa aludingayo?
- Ingakanani i-Coats Disease ezoyithinta ngayo indlela abona ngayo?
Buza imibuzo efana nale bese ususa konke ukungabaza kwakho. Udokotela uzokuchazela konke.
Uyini umehluko phakathi kwesifo se-Coats kanye ne-Retinoblastoma?
Isifo samaCoats kanye ne -Retinoblastoma yizimo ezimbili ezithinta i-retina yezingane ezincane.
- Isifo i-Coats yisimo lapho imithambo yegazi ku-retina yengane ikhula ngendlela engavamile, okubangela ukuthi uketshezi luvuzele esweni.
- I-Retinoblastoma uhlobo lomdlavuza olungavamile oluvela ku-retina. Nakuba luwumdlavuza, uma isimila singasakazekanga ngaphandle kweso, izingane eziningi zingaphila zingenawo umdlavuza ngemva kokwelashwa.
Izimpawu zokuqala zalezi zifo zombili zifana kakhulu. Ikakhulukazi, ukubonakala okumhlophe kwe-black iris (i-leukocoria) kungabonakala kuzo zombili. Ngakho-ke, uma ubona noma yiziphi izinguquko noma izimpawu emehlweni engane yakho, kubalulekile ukubona udokotela wamehlo ngokushesha ukuze uthole ukuthi iyini ngempela. Udokotela angenza izivivinyo futhi akutshele ukuthi yisiphi kulezi zifo ezimbili.
Umlayezo Wokuya Nawe Ekhaya
Isifo iCoats yisimo esingavamile esithinta imithambo yegazi emincane ku-retina, ngemuva kweso lengane yakho. Lokhu kubangela ukuvuza koketshezi kuleyo mithambo yegazi, kulimaze ukubona.
Into ebaluleke kakhulu okufanele uyikhumbule ukuthi indlela engcono kakhulu yokunciphisa umthelela walesi sifo emehlweni namehlo engane ukubamba lesi sifo ezigabeni zaso zokuqala.
Ngakho-ke, uma ubona ngisho noshintsho oluncane emehlweni engane yakho noma indlela ebona ngayo izinto, ungalushayi indiva bese ubona udokotela noma udokotela wamehlo ngokushesha. Uma kutholakala kusenesikhathi, kunethuba elikhulu lokuthi umbono wengane yakho ungasindiswa ngokwelashwa. Ungakhathazeki, odokotela bakhona ukukusiza wena nengane yakho.
Isifo sama - Coats, izifo zamehlo ezingane, imithambo yegazi esweni, i-retina, ukulahlekelwa umbono, ukwelashwa kwamehlo, impilo yengane











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