Ingabe nawe uzizwa ungacacile uma uvuka ekuseni? Ingabe kubonakala kuba kubi njengoba usuku luqhubeka? Noma ingabe ngezinye izikhathi ukuthola kunzima ukubona izibani lapho ushayela ebusuku? Nakuba lokhu kungase kubonakale njengezinto ezivamile, kungaba ukuqala kwenkinga encane yamehlo. Yilolo hlobo lwesifo esizokhuluma ngaso namuhla, futhi yilolo uhlobo lwe-Fuchs' Dystrophy .
Kuyini i-Fuchs' Dystrophy?
Kalula nje, i-Fuchs' Dystrophy yisimo esithinta i-cornea yamehlo akho womabili. Uyazi ukuthi iyini i-cornea? Yi-membrane ecacile, efana nengilazi emboza ingaphambili leso lakho. Ingxenye enombala yeso lakho, i-iris , kanye nomfundi weso imbozwe yile cornea. Lokhu kubizwa nangokuthi i-'Fuchs' corneal dystrophy' kanye ne-'Fuchs' endothelial dystrophy'.
Ngakho-ke uma une-Fuchs' dystrophy, amaseli angaphakathi kwengqimba ye-cornea yakho, ebizwa ngokuthi i-cornea endothelium, ayafa kancane kancane. Le endothelium iyingxenye ebaluleke kakhulu. Isebenza njengephampu encane yamanzi. Iyasiza ekususeni amanzi angadingekile ku-cornea futhi igcine icacile futhi ihlanzekile.
Cabanga nje, kwenzekani lapho amangqamuzana asebenza kule phampu efa? Amanzi aqala ukuqongelela ngaphakathi kwe-cornea. Bese i-cornea ivuvukala, ibe njengesiponji esigcwele amanzi. Yingakho amehlo eqala ukubonakala efiphele, futhi ngezinye izikhathi kungabonakala sengathi inkungu yakheke phezu kweso. Ezimweni ezimbi kakhulu, ama-blister amancane amanzi angakheka ebusweni be-cornea. La ma-blister angabangela ubuhlungu nokungakhululeki esweni.
Ziyini izigaba ze-Fuchs' Dystrophy?
Kunezigaba ezimbili eziyinhloko ze-Fuchs' dystrophy.
- Isigaba sokuqala: Uphawu oluyinhloko ozoba nalo kulesi sigaba ukubona okufiphele ekuseni . Kufana nesibuko esifiphele lapho uvuka. Kodwa-ke, njengoba uqhubeka nemisebenzi yakho yansuku zonke, phakathi namahora ambalwa, lokhu kufiphala kuncipha kancane kancane futhi umbono wakho uba sobala. Abanye abantu bangase bangabi nazimpawu ezinkulu kulesi sigaba.
- Isigaba sokugcina: Njengoba lesi sifo siqhubeka, ukufiphala okwakukhona ekuseni kuphela kuqala ukuqhubeka usuku lonke. Ukuvuvukala kwe-cornea kuba yinto ehlala njalo. Lokhu kusho ukuthi umbono wakho ungase ufiphale nganoma yisiphi isikhathi sosuku, ebusuku, noma ekuseni.
Ziyini izimpawu ze-Fuchs' Dystrophy?
Ezigabeni zokuqala, ungase ungabi nazo izimpawu. Kodwa-ke, njengoba isifo siqhubeka, ungase ube nezimpawu ezifana nalezi:
- Ukubona okunciphile ebusuku: Lokhu kufana nokubona ukukhanya okukhanyayo kanye nama-halo azungeze izibani zemoto lapho ushayela ebusuku.
- Ubunzima bokubona ngezinsuku zemvula: Lapho indawo ezungezile iba mnyama kancane, kunzima ukubona izinto ngokucacile.
- Ubunzima bokuhlukanisa phakathi kwezinto (ukuzwela okungekuhle kokungafani): Isibonelo, kungaba nzima ukuthola inkinobho emhlophe odongeni olumhlophe.
- Ukuzwela ukukhanya okukhanyayo: Amehlo aba luhlaza okwesibhakabhaka kangangokuthi awakwazi ukubheka ukukhanya kwelanga noma izibani ezikhanyayo ekhaya.
- Kuzwakala sengathi kukhona isihlabathi noma ukungcola emehlweni akho. Kumane nje kuyisimo esicasulayo njengokungathi kukhona okunamathele ngaphakathi.
- Amaqhubu e-cornea ayaqhuma futhi abangele ubuhlungu emehlweni. Lokhu kuyimpawu embi kakhulu.
- Izibazi: Lezi zibazi zivame ukwakheka kuqala maphakathi ne-cornea. Lezi zibazi zingalimaza umbono unomphela.
Yini ebangela i-Fuchs' Dystrophy?
Isizathu esiyinhloko sokuthuthukisa i-Fuchs dystrophy ukuthi iyifa eliyifa . Lokhu kusho ukuthi uma umama noma ubaba wakho enalesi sifo, nawe kungenzeka ukuthi usithole. Lokhu kubizwa ngokuthi i-autosomal dominant inheritance kwisayensi yezokwelapha. Kodwa-ke, ngezinye izikhathi othile angasithola ngokungahleliwe, ngisho noma kungekho muntu emndenini onalesi sifo.
Futhi, ezinye izinto zingenza i-Fuchs' dystrophy ibe yimbi kakhulu .
- Ukubhema: Abantu ababhema ugwayi banamathuba amaningi okuthola lesi sifo.
- Ukuchayeka elangeni (ukuchayeka ekukhanyeni kwe-UV): Ukuchayeka njalo emisebeni ye-ultraviolet enamandla akukuhle.
- Ukuba Nesifo Sikashukela: Lesi sifo singaba sibi kakhulu nakubantu abanesifo sikashukela.
Ubani osengozini enkulu yokuthola i-Fuchs' Dystrophy?
Abanye abantu banamathuba amancane okuthola isifo i-Fuchs' dystrophy kunabanye. Ake sibone ukuthi ubani lowo.
- Ubudala: Udokotela angase akwazi ukubona izimpawu zokuqala zalesi sifo phakathi kweminyaka engama-30 nengama-40. Kodwa-ke, umbono uvame ukuthinteka ngemva kweminyaka engama-50 .
- Ubulili: Abesifazane banamathuba amaningi okuthola lesi sifo kunabesilisa.
- Umlando womndeni: Njengoba kushiwo ngaphambili, uma othile emndenini ene-Fuchs' dystrophy, nabanye basengozini yokuba nayo.
Odokotela bayixilonga kanjani i-Fuchs' Dystrophy?
Uma unalezi zimpawu, into yokuqala okufanele uyenze ukubonana nochwepheshe wokunakekelwa kwamehlo . Uzoqala ngokukubuza ngezimpawu zakho, abukeze umlando wakho wezokwelapha, bese ekwenza ukuhlolwa kwamehlo okuphelele.
Ngesikhathi sokuhlolwa kwamehlo, udokotela angabona izimpawu eziningana ezibonisa ukuthi une-Fuchs' dystrophy.
- Ungabona ukuthi ezinye zezendlalelo ze-cornea sezijiyile .
- EyakhoIzinguquko ekubukekeni kwe-endothelium zingabonakala.
- Ungase ubone amaqhubu amancane abizwa ngokuthi i-guttae ngaphakathi kwe-cornea. Lokhu kuyisibonakaliso samaseli e-endothelial abuthakathaka.
Ukuhlolwa kokuqinisekisa i-Fuchs' Dystrophy
Ukuqinisekisa ukuxilongwa, udokotela angenza izivivinyo eziningana, njenge:
- I-Microscopy: Lokhu kwenziwa kusetshenziswa ama-microscope akhethekile. Izibonelo zifaka phakathi ukuhlolwa kwesibani esiqhekekile kanye ne-confocal/specular microscope . Lokhu kusenza sikwazi ukubona i-cornea ezingeni lamaseli.
- I-Pachymetry: Lokhu ukuhlolwa okungenabuhlungu. Kulinganisa ubukhulu be-cornea yakho. Uma i-cornea ivuvukele, iwugqinsi kakhulu, akunjalo?
- I-Optical Coherence Tomography (OCT): Lokhu futhi kuyindlela yokuhlola iso engahlaseli, engenabuhlungu. Isebenzisa ukukhanya ukuthatha izithombe ezicacile zengaphakathi leso lakho, ikakhulukazi ingxenye evundlile ye-cornea.
Yiziphi izindlela zokwelapha i-Fuchs' Dystrophy?
Ngentuthuko yesayensi yamanje, i-Fuchs' dystrophy ingelashwa, kodwa ayinakwelashwa . Ezigabeni zokuqala zalesi sifo, uma kungekho zimpawu ezinkulu, udokotela wakho angakugcina uqashwe. Lokhu kusho ukuthi ungase ucelwe ukuthi uze uzohlolwa amehlo ngezikhathi ezithile.
Nazi ezinye izindlela zokwelapha:
- Amafutha kanye namaconsi amehlo: Uma izimpawu zakho zingezimbi kakhulu, udokotela wakho angase akunike imithi yokunciphisa ukuvuvukala kwe-cornea futhi asize ekukhipheni uketshezi oluningi. Impumuzo kulokhu ivame ukuba yesikhashana.
- Isomisi sezinwele esiphathwa ngesandla: Ungamangali, lokhu kuyindlela yokwelapha! Ukuze unciphise ukuvuvuka kwasekuseni, ukufutha umoya opholile ebusweni bakho kusuka ku-hairdryer (kude futhi ngokucophelela) kutholakale ukuthi kusiza ukomisa umswakama owedlulele ku-cornea. Kufanele ubuze udokotela wakho indlela eqondile.
- Ukufakelwa kwe-cornea: Uma ukubona kwakho kuqala ukuvinjelwa kakhulu yi-Fuchs' dystrophy, ukuhlinzwa kuyindlela engcono kakhulu yokwelapha. Ungase ukwazi ukwenza inqubo ye-endothelial keratoplasty (EK) , efaka ingxenye nje ye-cornea. Noma ungase ukwazi ukuthola i-cornea entsha. Ukuhlinzwa kwe-EK sekuphumelele kakhulu manje ngoba kuhilela ukususa ungqimba olugulayo lwe-endothelium bese ulufaka ungqimba olunempilo esikhundleni salo.
- Ukususa Izinwele Kuphela Kwe-Descemet (DSO):Lokhu kuyindlela entsha yokwelapha. Kuhilela ukususa ucezu oluthile lwamaseli agulayo phakathi kwe-cornea. Lokhu kuvumela amaseli anempilo azungeze i-cornea ukuba akhule futhi agcwalise izikhala. Lokhu kungase kungasebenzi kuwo wonke umuntu, futhi kuxhomeke kudokotela ukuthi anqume.
Yimiphi imibuzo okufanele ngiyibuze udokotela wami mayelana ne-Fuchs' Dystrophy?
Kubalulekile ukwakha ubudlelwano obuhle nodokotela wakho wamehlo. Qiniseka ukuthi uya kohlolwa amehlo njengoba kuhleliwe. Tshela udokotela wakho ngokushesha uma uthola izimpawu ezintsha noma uma izimpawu zakho ziba zimbi kakhulu.
Ungabuza udokotela imibuzo efana nale:
- Yiziphi izimpawu okufanele ngikubone ngokushesha okukhulu?
- Yikuphi ukwelashwa ongincomayo? Yiziphi izinzuzo nezinkinga?
- Ingabe kukhona izivivinyo zemitholampilo engingahlanganyela kuzo?
- Uma ngingaboni kahle, ingabe zikhona izinsiza zokubona okuphansi ezingangisiza?
Ingabe i-Fuchs' Dystrophy ingavinjelwa?
Eqinisweni, okwamanje ayikho indlela yokuvimbela i-Fuchs' dystrophy. Kodwa-ke, uma ubhema, ukuyeka ukubhema kungasiza. Uma unesifo sikashukela, kubalulekile futhi ukusebenzisana nodokotela wakho ukulawula amazinga kashukela egazini lakho.
Yini okufanele ngiyilindele uma ngine-Fuchs' Dystrophy?
Kuye ngokuthi i-Fuchs' dystrophy inzima kangakanani, uma ungatholi ukwelashwa okufanele, ungase uzwe ubuhlungu obukhulu, ukulahlekelwa umbono, futhi mhlawumbe ngisho nobumpumputhe .
Kodwa ngokwelashwa okufanele, isimo sakho singathuthuka kakhulu. Ngemva kokuhlinzwa okuthile (kufaka phakathi izibuko), umbono wakho ungabuyela ku-20/20, njengomuntu ophilile, ezinsukwini ezimbalwa. Yingakho kubalulekile ukusebenzisana nodokotela wakho ukuthola ukwelashwa okufanele wena.
Ukuzwa izimpawu zanoma yisiphi isifo samehlo kungaba yinto eyesabekayo, futhi i-Fuchs' dystrophy ayihlukile. Uma unezimpawu ezifana nobuhlungu bamehlo noma ukubona okufiphele, bona udokotela ngokushesha okukhulu. Khumbula, ukuxilongwa kusenesikhathi kanye nokwelashwa kuvame ukuholela emiphumeleni emihle kakhulu. Abacwaningi bahlala bethuthukisa izindlela ezintsha zokuphatha nokwelapha i-Fuchs' dystrophy nezinye izifo zamehlo.
Umlayezo Wokuya Nawe Ekhaya
Kulungile, ngakho-ke ngithemba ukuthi usuyiqonda kangcono i-Fuchs' Dystrophy, esikhulume ngayo namuhla.
- Lesi yisifo esizuzwe njengefa esithinta i-cornea yeso.
- Izimpawu eziyinhloko ukubona okufiphele ekuseni , ukubona okufiphele usuku lonke, ukubona izindandatho lapho ubheka ukukhanya, kanye nobuhlungu bamehlo.
- Izinto ezinjengokubhema, ukukhanya okukhulu kwe-UV, nesifo sikashukela zingasenza sibe sibi kakhulu lesi sifo.
- Udokotela wamehlo angakuxilonga lokhu futhi akunikeze ukwelashwa okufanele .
- Kunezindlela zokwelapha ezifana nemithi kanye nokuhlinzwa okukhethekile (ukufakelwa kwe-cornea, i-DSO).
- Kubaluleke kakhulu ukuqaphela nokwelapha lesi sifo ngokushesha.
Uma unalezi zimpawu, ungesabi ukubona udokotela. Amehlo ayigugu kakhulu, ngakho-ke kungumthwalo wethu ukuwanakekela.
I-Fuchs ' Dystrophy, i-Cornea, Isifo Samehlo, Ukubona Okufiphele, Ukulimala Kwamehlo, Ukufakelwa Kwe-Corneal











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