Kungenzeka ukuthi awukaze uzwe ngegama elithi 'Medullary Sponge Kidney' ngaphambili. Nakuba kungase kuzwakale kunzima ukuchaza, empeleni kuyisimo sokuzalwa esihlobene nezinso. Kalula nje, yilapho kwakheka khona amabhamuza amancane anamanzi, abizwa ngokuthi ama-cyst, ngaphakathi kwezinso zakho, ikakhulukazi engxenyeni ephakathi yezinso (medulla). Ake sixoxe ngalokhu ngokuningiliziwe namuhla, akunjalo?
Iyini ngempela i-Medullary Sponge Kidney?
Ake siqale sibheke ukuthi ziyini izinso nokuthi zisebenza kanjani. Njengoba wazi, izinso ziyingxenye ebaluleke kakhulu ohlelweni lomchamo emzimbeni wethu. Izinso ngalinye linengxenye ephakathi, esiyibiza ngokuthi i-medulla. Le medulla ineziteshi ezincane kakhulu ezibizwa ngokuthi ama-tubule amancane. Lezi ziteshi ziqoqa imfucuza ehlungiwe egazini bese zenza umchamo. Bese lezi ziteshi zihlangana futhi zixhumane neziteshi ezinkulu kancane ezibizwa ngokuthi ama-collecting ducts. Ukusuka kulezi, umchamo uya endaweni eyinhloko yokuqoqa phakathi kwezinso, i-renal pelvis. Ukusuka lapho, umchamo udlula kuma-ureter uye kwesinye, bese udlula kwi-urethra ukuze uphume emzimbeni.
Kulungile, manje okwenzekayo kumuntu one-'Medullary Sponge Kidney' ukuthi imigudu eqoqayo engikhulume ngayo ikhula ama-cysts amancane, futhi leyo migudu iyavuvukala futhi ibe mikhulu. Ibukeka njengesiponji. Yingakho ibizwa ngokuthi 'iSponge Kidney'. Lesi simo sivame ukuthinta zombili izinso, kodwa ngezinye izikhathi singathinta inso eyodwa kuphela.
Lesi simo sezinso zesiponji esingapheli sikhula kanjani?
Manje unombuzo mayelana nokuthi kwenzekani uma la ma-cyst eba khona. Uma la ma-cyst eba khona, lawo ma-channel amahle (ama-tubules) awakwazi ukusebenza kahle. Bese, izinto ezifana ne-calcium ziqala ukufakwa ngaphakathi kwala ma-channel. Lokhu sikubiza ngokuthi (i-nephrocalcinosis). Akuyona i-calcium kuphela, kodwa nezinye izinto ezifana ne-phosphate ne-oxalate nazo zinganqwabelana ngale ndlela. Ngokuhamba kwesikhathi, lezi zinto eziqongelelekile ziyanamathelana futhi zakhe amatshe ezinso .
La ma-cyst namatshe avimba nokugeleza komchamo ngendlela yomchamo, okwandisa ingozi yokutheleleka kwezifo zomchamo (UTIs) .
Uyini umehluko phakathi kwalokhu kanye nesifo sezinso i-Polycystic?
Kungenzeka ukuthi uke wezwa ngePolycystic Kidney Disease (PKD). Futhi kuyisifo lapho kwakheka khona ama-cyst ezinso. Ngakho-ke uyini umehluko phakathi kwalokhu okubili?
Isifo sezinso se-Polycystic (PKD) yisifo esibangelwa ufuzo esivame ukutholwa njengefa. Sibangela ukuba izinso zikhule, kube nama-cyst amaningi akhiwa emzimbeni wonke. I-PKD ngezinye izikhathi ingaholela ezinkingeni ezinkulu.Kungabangela izinkinga zokuphila konke. Abantu abaningi abane-PKD bahlushwa ukungasebenzi kahle kwezinso futhi badinga i-dialysis ukuze bahlanze igazi labo.
Kodwa-ke, ukwehluleka kwezinso akuvamile kubantu abane-medullary sponge kidney (MSK). Yilowo umehluko omkhulu.
Ubani othinteka kakhulu yilesi simo? Sivame kangakanani?
Lesi simo "se-medullary sponge kidney (MSK)" okwamanje kucatshangwa ukuthi senzeka ngokungahleliwe. Okungukuthi, ngaphandle kwesizathu esithile. Kodwa-ke, njengoba sibonakala kweminye imindeni, kungase kube nethuba lokuthola ifa. Kodwa-ke, iphethini ecacile yezakhi zofuzo ayikatholakali okwamanje.
Iningi labantu lithola ukuthi linalesi sifo ngemva kokuvela kwezimpawu, ngokuvamile lapho sebeneminyaka engu-20. Kuthiwa abesifazane nabo basengozini enkulu kunabesilisa .
Kuvamile kakhulu, ngokwesilinganiso somuntu oyedwa kwabangu-5,000 une-MSK. Kodwa-ke, kuvame kakhulu kubantu abanamatshe ezinso. Lokhu kusho ukuthi phakathi kuka-12% no-20% wabantu abanjalo bangase babe ne-MSK.
Ingabe i-medullary sponge kidney ibangela umfutho wegazi ophakeme?
Abanye bangase bazibuze ukuthi le "MSK" ibangela umfutho wegazi ophakeme noma ingcindezi. Ngokusho kocwaningo lwamanje, abukho ubufakazi bokuthi "i-medullary sponge kidney" ibangela umfutho wegazi ophakeme.
Yini ebangela i-medullary sponge kidney?
Odokotela abasazi kahle ukuthi kungani abanye abantu beba nalesi simo. Kucatshangwa ukuthi sibangelwa inkinga yokukhula kwezinso ngesikhathi sokukhulelwa, lapho umntwana esesesibelethweni .
Ziyini izimpawu zalesi sifo?
Ngokumangalisayo, abantu abaningi abane-Medullary Sponge Kidney (MSK) ababi nazo izimpawu . Lokhu kusho ukuthi baphila ngaphandle kokwazi ukuthi banalesi sifo. Amaphesenti amancane kuphela, cishe angu-10%, aba nezimpawu.
Uma kuvela izimpawu ezinjalo, zivame ukuhlotshaniswa nokutheleleka komgudu womchamo (UTIs) kanye namatshe ezinso. Lezi yizimpawu eziyinhloko:
- Igazi emchameni (i-hematuria): Lokhu kusho ukuthi umchamo ungase ube bomvu, ngezinye izikhathi ube nombala wamanzi etiye.
- Ubuhlungu besifuba: Ubuhlungu obuvela kuzo zombili izinhlangothi zomhlane wakho, ngaphansi kwekheji lakho lezimbambo.
- Ubuhlungu lapho uchama (i-dysuria): Kungase kube nokusha kanye nobuhlungu lapho uchama.
- Amatshe ezinso: Lokhu kuyinto abantu abaningi abaye babhekana nayo. Kungahambisana nobuhlungu obukhulu emhlane.
- Ukutheleleka komgudu womchamo: Izimpawu ezifana nokuchama njalo kanye nomkhuhlane zingase zibe khona.
I-medullary sponge kidney ihlolwa kanjani?
Uma unalezi zimpawu, udokotela wakho uzoqala ngokukuhlola ngokomzimba. Uzobuza ngomlando wakho wezokwelapha, umlando womndeni, kanye nanoma yiziphi izimpawu ozizwayo.
Uma udokotela wakho esola ukuthi unesifo sezinso, cishe uzoyala ukuhlolwa kwegazi nomchamo okuningana. Lokhu kuzobheka:
- Ingabe kukhona igazi emchameni?
- Izinso zisebenza kanjani?
- Ingabe kukhona ukutheleleka komgudu womchamo?
Ngaphezu kwalokho, ukuhlolwa okukhethekile kwezithombe kungenziwa ukuhlola lawo ma-cyst engiwakhulume ngawo ezinso. Izinhlobo ezivame kakhulu zokuskena yilezi:
- I-CT scan: Lokhu kusebenzisa i-X-ray ukukhiqiza isithombe sezinso esinezinhlangothi ezintathu (3D).
- I-Intravenous Pyelogram (IVP): Lokhu kuhilela ukufaka idayi ekhethekile emthanjeni wakho. Ngemuva kwalokho, kuthathwa izithombe eziningana ze-X-ray. Idayi ihlungwa ngegazi elivela ezinso bese lingena emchameni, ngakho izithombe ze-X-ray zibonisa indlela yomchamo ngokucacile. Lokhu kungasiza ekutholeni ama-cysts nezindawo lapho umchamo uvalekile khona.
- Ukuskena nge-ultrasound: Lokhu kusebenzisa amaza omsindo ukuthatha izithombe zezinso.
Iphathwa kanjani i-medullary sponge kidney?
Okwamanje akukho ukwelashwa okuqondile kwalesi simo esaziwa ngokuthi i-medullary sponge kidney (MSK). Ukwelashwa kuhloselwe kakhulu ukulawula nokwelapha izifo zomgudu womchamo (UTIs) kanye namatshe ezinso.
Ukwelashwa okuyinhloko kwezifo zomgudu womchamo ama-antibiotic .
Ukwelashwa kwamatshe ezinso kuncike ngobukhulu betshe. Amatshe amancane avame ukudlula emchameni ngokwawo. Udokotela wakho angakutshela ukuthi uphuze amanzi amaningi ukuze asize itshe lidlule ngokushesha. Bangase bakunike nemithi yokuqeda izinhlungu kanye nemithi yokukhulula imisipha kuma-ureter akho.
Amatshe amakhulu angadinga ukwelashwa okwengeziwe. Nazi izibonelo ezimbalwa:
- I-Shock Wave Lithotripsy: Lokhu kuyindlela yokwelapha engangenisi magciwane esebenzisa amaza okushaqeka anamandla amakhulu ukuphula amatshe ezinso. Izingcezu eziphukile zibe sezikhishwa emzimbeni ngomchamo.
- I-Ureteroscopy: Lokhu kuhilela ukusebenzisa ithubhu elide nelincane elibizwa ngokuthi i-ureteroscope ukuze libheke indawo lapho itshe likhona. Leli thuluzi lingasetshenziswa ukususa amatshe amancane, noma i-laser ingasetshenziswa ukuphula amatshe amakhulu.
- I-Percutaneous Nephrolithotomy:Odokotela basebenzisa le ndlela kuphela uma ezinye izindlela zingaphumeleli. Lokhu kuhilela ukwenza ukusika okuncane emhlane bese kuchotshozwa itshe lezinso bese kukhishwa. Lokhu futhi kuyindlela yokuhlinzwa engadingi ukungenelela okuningi.
Ingabe i-medullary sponge kidney ingavinjelwa?
I-Medullary sponge kidney (MSK) yisimo sokuzalwa esingaziwa imbangela, ngakho-ke asinakuvinjelwa . Kodwa-ke, ungathatha izinyathelo zokuvimbela ukutheleleka komgudu womchamo (UTIs) kanye namatshe ezinso angabangelwa yiso.
Udokotela wakho angase akunike imithi efana nale:
- Ama-antibiotic aphansi ukuvimbela ukutheleleka okuphindaphindekayo kwendlela yomchamo.
- Imithi efana ne -potassium citrate noma i-thiazide (eyaziwa nangokuthi amaphilisi amanzi) inganciphisa amazinga e-calcium emchameni futhi ivimbele ukwakheka kwamatshe ezinso.
Ukushintsha indlela odla ngayo kungasiza nasekuvimbeleni izifo zomgudu womchamo kanye namatshe ezinso:
- I-Calcium: Ukuthola i-calcium eyanele ekudleni kwakho kungasiza ekunciphiseni ingozi yamatshe ezinso. (Abanye abantu bangase bacabange ukuthi ukuthatha i-calcium eningi kakhulu kuzokwandisa ingozi yamatshe, kodwa akunjalo. Kufanele uyithathe ngokulinganisela. Xhumana nodokotela wakho.)
- Uketshezi: Ukuphuza amanzi amaningi kubaluleke kakhulu. Lokhu kunciphisa umchamo futhi kunciphisa ingozi yokwakheka kwamatshe. Kuphinde kusize ekukhipheni amagciwane ezinso. Zama ukuphuza okungenani amalitha angu-2-3 amanzi ngosuku.
- Ukudla okunamaphrotheni amaningi: Ukunciphisa ukudla okunamaphrotheni amaningi njengenyama, inhlanzi namaqanda kungasiza ekuvimbeleni amatshe ezinso.
- Usawoti: Ukunciphisa usawoti ekudleni kwakho nakho kubaluleke kakhulu. Ukudla usawoti omningi kwandisa ingozi yamatshe ezinso. Ngakho-ke qaphela inani likasawoti olifaka ekudleni kwakho. Izinto ezifana nokudla okusemathinini nama-noodle asheshayo zinosawoti omningi.
Okubalulekile: Njalo thintana nodokotela wakho noma isazi sokudla ngaphambi kokwenza noma yiziphi izinguquko ekudleni kwakho.
Liyini ikusasa lomuntu one-medullary sponge kidney?
Abantu abaningi bangase besabe ukuzwa lokhu, kodwa iningi labantu abaneMedullary Sponge Kidney (MSK) bangakwazi ukugcina ukusebenza kahle kwezinso kukho konke ukuphila kwabo .
Kodwa-ke, iphesenti elincane labantu, cishe u-10%, lingase libe nokwehluleka kwezinso. Izimbangela eziyinhloko izifo zomgudu womchamo eziphindaphindayo (UTIs) kanye namatshe ezinso.
Ubuhlungu obungapheli bungenye inkinga engavamile engenzeka kubantu abavame ukuba namatshe ezinso. Lesi simo singalawulwa ngokuthatha izinyathelo zokuvimbela amatshe ezinso.
I-Medullary sponge kidney (MSK) ingabangela amazinga aphansi e-calcium egazini. Lokhu kungenza amathambo abe buthaka . Lokhu kwandisa ingozi yezifo ezihlobene namathambo. Isibonelo:
- I-Osteoporosis (isifo lapho amathambo eba mancane futhi aqhekeke khona)
- I-hyperparathyroidism yesibili (ukukhishwa ngokweqile kwama-hormone yizindlala ze-parathyroid)
Ukuze uvimbele lolu hlobo lokulimala kwamathambo isikhathi eside, udokotela wakho angase akunikeze imithi efana ne-potassium citrate.
Ungaphila kanjani ne-medullary sponge kidney?
Udokotela wakho uzoqapha ukusebenza kwezinso zakho njalo futhi anikeze ukunakekelwa okusekelayo njengoba kudingeka. Kubalulekile ukuthatha imithi yakho njengoba uyalelwe, ulandele ukudla kwakho, futhi ulandele ama-aphoyintimenti akho okulandelela . Lezi zinto zingasiza ekuvimbeleni ukutheleleka komgudu womchamo kanye namatshe ezinso.
Akukho ukwelashwa kwe-Medullary Sponge Kidney (MSK). Kodwa njengoba ngishilo ngaphambili, abantu abaningi abanalesi simo abanazo izimpawu, futhi abanye abazi nokuthi banazo. Uma izimpawu zivela, zivame ukubangelwa ukutheleleka komgudu womchamo noma itshe lezinso. Zombili lezi zimpawu ziyalapheka kakhulu . Ungavimbela futhi ukutheleleka komgudu womchamo kanye namatshe ezinso ngokwenza izinguquko ekudleni kwakho nasendleleni ophila ngayo. Uma unemibuzo noma ukukhathazeka, ungangabazi ukukhuluma nodokotela wakho .
Umlayezo Wokuya Nawe Ekhaya
Kulungile, ngakho-ke ngithemba ukuthi usuyaqonda kahle i-'Medullary Sponge Kidney' esikhulume ngayo. Ake sizikhumbuze amaphuzu abaluleke kakhulu futhi:
- Lesi yisimo sokuzalwa lapho kuvela khona ama-cyst amancane engxenyeni ephakathi yezinso (i-medulla).
- Iningi labantu alinazo izimpawu . Uma benazo, kungenxa yokutheleleka kwe-urinary tract (UTIs) noma amatshe ezinso.
- Akukho ukwelashwa okuqondile kwalokhu, kodwa izimpawu nezinkinga zingelashwa kahle.
- Kubaluleke kakhulu ukuvimbela amatshe ezinso kanye nokutheleleka komgudu womchamo. Ukuze wenze lokhu, phuza amanzi amaningi, uqaphele ukuthi udlani, bese ulandela imiyalelo kadokotela wakho.
- Abantu abaningi bangakwazi ukugcina ukusebenza kahle kwezinso kukho konke ukuphila kwabo . Ukwehluleka kwezinso akuvamile.
- Uma unemibuzo ngalokhu, qiniseka ukuthi ubona udokotela .
Ungakhathazeki, abantu abaningi bangaphila impilo ejwayelekile nenempilo ngale nkinga!
'I-Medullary Sponge Kidney, Isifo se-Cacchi-Ricci, isifo sezinso, amatshe ezinso, izifo zomgudu womchamo, ama-cyst ezinso, ukuphazamiseka kwezinso kokuzalwa, ama-cyst ezinso, i-nephrocalcinosis, i-hematuria, impilo yezinso IsiSinhala











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